Search results for " Hearing"

showing 10 items of 301 documents

<i>GJB2</i> Mutations and Genotype-Phenotype Correlation in 335 Patients from Germany with Nonsyndromic Sensorineural Hearing Loss: Evide…

2009

We report on 335 patients (319 families) with mild-to-profound nonsyndromic sensorineural hearing loss. We identified 178 mutated <i>GJB2</i> alleles representing 29 different sequence changes (including 3 novel mutations: Q7P, N14D, H100Q), and 2 alleles with the deletion del(GJB6-D13S1830) of the <i>GJB6</i> gene. Eleven <i>GJB2</i> mutations (119 mutated alleles) were truncating (T), and 18 mutations (59 alleles) were nontruncating (NT). Biallelic <i>GJB2</i> mutations were found in 71 patients (21.2%; 67 families; 25 different genotypes). Audiograms of 62 patients (56 families) with biallelic <i>GJB2</i> mutations typically ind…

MaleMild hearing impairmentPathologymedicine.medical_specialtyGenotypePhysiologyHearing lossHearing Loss SensorineuralGenes Recessivemedicine.disease_causePolymerase Chain ReactionConnexinsSpeech and HearingAudiometryGene FrequencyGermanyGenotypeotorhinolaryngologic diseasesmedicineHumansAlleleAllele frequencyAllelesGenetic Association StudiesGeneticsMutationbiologybusiness.industrymedicine.diseaseSensory SystemsConnexin 26PhenotypeOtorhinolaryngologyMutationbiology.proteinFemaleSensorineural hearing lossmedicine.symptombusinessGJB6Audiology and Neurotology
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Abnormal functioning of the left temporal lobe in language-impaired children

2014

Specific language impairment is associated with enduring problems in language-related functions. We followed the spatiotemporal course of cortical activation in SLI using magnetoencephalography. In the experiment, children with normal and impaired language development heard spoken real words and pseudowords presented only once or two times in a row. In typically developing children, the activation in the bilateral superior temporal cortices was attenuated to the second presentation of the same word. In SLI children, this repetition effect was nearly nonexistent in the left hemisphere. Furthermore, the activation was equally strong to words and pseudowords in SLI children whereas in the typi…

MaleNeuropsychological TestsSpecific language impairmentAudiologyVocabularyFunctional LateralityLanguage and LinguisticsN400mChildChildrenta515Temporal cortexBrain MappingLanguage Teststa214MEGmedicine.diagnostic_testSpeech perceptionMagnetoencephalographyAuditory responsesTemporal LobeLanguage developmentMemory Short-TermPattern Recognition VisualSpecific language impairmentEvoked Potentials AuditoryFemaleFunctional imagingPsychologyCognitive psychologyLinguistics and Languagemedicine.medical_specialtySpeech perceptionta221Experimental and Cognitive PsychologyDevelopmentLanguage Developmentbehavioral disciplines and activitiesLateralization of brain functionSpeech and HearingTemporal cortexEvent-related potentialReaction TimemedicineHumansta218Auditory CortexAnalysis of VarianceLanguage Disordersta114Working memoryCognitive neuroscienceMagnetoencephalographymedicine.diseaseBRAIN AND LANGUAGE
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Associations Between Toddler-Age Communication and Kindergarten-Age Self-Regulatory Skills

2014

Purpose In this study, the authors aimed at gaining understanding on the associations of different types of early language and communication profiles with later self-regulation skills by using longitudinal data from toddler age to kindergarten age. Method Children with early language profiles representing expressive delay, broad delay (i.e., expressive, social, and/or symbolic), and typical language development were compared in domains of kindergarten-age executive and regulative skills (attentional/executive functions, regulation of emotions and behavioral activity, and social skills) assessed with parental questionnaires. Results Children with delay in toddler-age language development de…

MaleParentsLinguistics and Languagemedia_common.quotation_subjecteducationitsesäätelyLanguage and LinguisticsSelf-ControlDevelopmental psychologySkills managementExecutive FunctionSpeech and HearingSocial skillsSurveys and QuestionnairesHumansAttentionLanguage Development DisordersLongitudinal StudiestoddlersToddlerChildSocial BehaviorEarly languageviestintämedia_commontaaperotskillscommunicationCommunicationtaidotInfantSelf-controlExecutive functionsLanguage acquisitionLanguage developmentself-regulatoryChild PreschoolRegression AnalysisFemalePsychologyChild LanguageJournal of Speech, Language, and Hearing Research
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The point prevalence of otitis media with eVusion among primary school children in Western Sicily

2009

The objective of this study is to identify the prevalence of otitis media with effusion (OME) in primary school children and to value the possible predisposing factors focusing on relationship between allergy and OME in Western Sicily. 2,097 children attending primary school were screened from September 2006 to June 2007 in Sciacca. Children underwent pneumatic otoscopy, skin tests, tympanogram and acoustic reflex tests. Audiogram was performed if the child had a type B or a type C tympanogram. The criteria for diagnosis of OME were: documented persistent middle ear effusion by otoscopic examination for a minimum of 3 months, presence of B or C tympanogram, absence of ipsilateral acoustic r…

MalePediatricsmedicine.medical_specialtyAdolescentPrevalenceSeverity of Illness IndexAtopyCatchment Area HealthEpidemiologyotorhinolaryngologic diseasesmedicinePrevalenceHumansAcoustic reflexChildStudentsSicilybusiness.industryOtitis Media with EffusionEustachian TubeGeneral Medicinemedicine.diseaseConductive hearing lossSettore MED/32 - AudiologiaOtitisSettore MED/31 - OtorinolaringoiatriaOtorhinolaryngologyEffusionEl NiñoChild PreschoolFemalemedicine.symptomOME · Otitis media with eVusion · Allergy · Eustachian tube dysfunctionbusiness
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Otitis media with effusion with or without atopy: audiological findings on primary schoolchildren

2011

Objective: The objective of the study was to evaluate the role of atopy in otitis media with effusion (OME) in children attending primary school, focusing on the audiometric and tympanometric measurements among atopic and nonatopic subjects suffering from OME. Materials and Methods: Three hundred ten children (5-6 years old) were screened in Western Sicily by skin tests and divided into atopics (G1) and nonatopics (G2). The samples were evaluated for OME by pneumatic otoscopy, tympanogram, and acoustic reflex tests. The parameters considered were as follows: documented persistent middle ear effusion by otoscopic examination for a minimum of 3 months, presence of B or C tympanogram, absence …

MalePediatricsmedicine.medical_specialtyAudiometry/methods*OtoscopyRisk AssessmentAtopyCohort StudiesAge DistributionAudiometryotorhinolaryngologic diseasesmedicineHypersensitivityPrevalenceHumansMass ScreeningOtitis Media with Effusion/diagnosisSex DistributionAcoustic reflexChildSicilyMass screeningSchool Health ServicesAnalysis of Variancemedicine.diagnostic_testbusiness.industryOtitis Media with EffusionOdds ratiomedicine.diseaseConductive hearing lossSettore MED/32 - AudiologiaOtitisOtorhinolaryngologyEffusionChild PreschoolFemalemedicine.symptomAudiometrybusiness
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Prevalence and risk factors for sensorineural hearing loss: Western Sicily overview.

2013

The objective of this work was to evaluate the prevalence of sensorineural hearing loss (SNHL) and distribution of the main risk factors associated to it focusing on their role in the development of deafness and their interaction. We performed a global audiological assessment (through TEOAE, tympanometry and ABR) in 508 infants at risk studying the main risk factors reported by Joint Committee on Infant Hearing (2007). Fifty-one infants (10.03 %) were diagnosed with SNHL (45 bilateral and 6 unilateral) with a mean hearing threshold of 87.39 ± 28.25 dB HL; family history of hearing impairment (HI) and TORCH infections indicated independent significant risk factors (P < 0.00001 and P = 0.0…

MalePediatricsmedicine.medical_specialtyCraniofacial abnormalityHearing lossHearing Loss SensorineuralAudiologySettore MED/38 - Pediatria Generale E SpecialisticaNeonatal ScreeningRisk Factorsotorhinolaryngologic diseasesEvoked Potentials Auditory Brain StemPrevalenceMedicineHumansFamily historySicilyAbsolute threshold of hearingInfants at risk Neonatal hearing screening Sensorineural hearing loss NICU infantsmedicine.diagnostic_testbusiness.industryIncidence (epidemiology)IncidenceInfant NewbornInfantGeneral MedicineTympanometrymedicine.diseaseConductive hearing lossSettore MED/32 - AudiologiaSettore MED/31 - OtorinolaringoiatriaOtorhinolaryngologySensorineural hearing lossFemalemedicine.symptombusinessEuropean archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
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The role of atopy in otitis media with effusion among primary school children: audiological investigation

2010

The objective of this study was to evaluate the role of atopy in otitis media with effusion (OME) in children attending primary school in western Sicily focusing on the audiological characteristics among atopic and non-atopic subjects suffering from OME. A total of 310 children (5-6 years old) were screened by skin tests and divided into atopics (G1) and non-atopics (G2). The samples were evaluated for OME by pneumatic otoscopy, tympanogram and acoustic reflex tests. The parameters considered were: documented persistent middle ear effusion by otoscopic examination for a minimum of 3 months; presence of B or C tympanogram; absence of ipsilateral acoustic reflex and a conductive hearing loss …

MalePediatricsmedicine.medical_specialtyEustachian tubeHearing lossOME; otitis media with effusion; allergy; Auditory tube dysfunction;Hearing Loss ConductivePrevalenceOtoscopyAtopyotorhinolaryngologic diseasesHypersensitivityPrevalenceMedicineHumansotitis media with effusionOMEAcoustic reflexChildSicilySkin Testsbusiness.industryGeneral Medicinemedicine.diseaseallergyReflex AcousticConductive hearing lossSettore MED/32 - Audiologiabody regionsAuditory tube dysfunctionOtitismedicine.anatomical_structureSettore MED/31 - OtorinolaringoiatriaOtorhinolaryngologyEffusionAcoustic Impedance TestsChild PreschoolFemalemedicine.symptombusiness
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Evaluation of auditory development in infants and toddlers who received cochlear implants under the age of 24 months with the LittlEARS® Auditory Que…

2010

Abstract Background and Aims Newborn hearing screening and early intervention for congenital hearing loss have created a need for tools assessing the hearing development of very young children. A multidisciplinary evaluation of children's development is now becoming standard in clinical practice, though not many reliable diagnostic instruments exist. For this reason, the LittlEARS ® Auditory Questionnaire (LEAQ) was created to assess the auditory skills of a growing population of infants and toddlers who receive hearing instruments. The LEAQ relies on parent report, which has been shown to be a reliable way of assessing child development. Results with this tool in a group of children who re…

MalePediatricsmedicine.medical_specialtyHearing lossmedicine.medical_treatmentPopulationDeafnessAudiologyCongenital hearing lossLanguage DevelopmentPredictive Value of TestsSurveys and QuestionnairesCochlear implantmedicineHumansLongitudinal Studieseducationeducation.field_of_studybusiness.industryHearing TestsAge FactorsInfantGeneral MedicineCochlear ImplantationChild developmentTransplantationLanguage developmentCochlear ImplantsOtorhinolaryngologyChild PreschoolPredictive value of testsPediatrics Perinatology and Child HealthFemalemedicine.symptombusinessInternational Journal of Pediatric Otorhinolaryngology
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On the threshold of effective well infant nursery hearing screening in Western Sicily.

2012

Abstract Objective To determine the feasibility and effectiveness of well-infant nursery hearing screening programme for the early identification of hearing impairment, based on transient evoked otoacoustic emission (TEOAE) with a high “screen sensitivity” reducing the number of more expensive secondary level exams. Methods The newborns were screened by non-specialist health workers in well babies nursery at the twentieth day of life for 6 years consecutive. Based on PASS/FAIL criteria and presence/absence of audiological risk factors the newborns were divided into four groups each one with its personal step programme: G1 – PASS without risk factor, free to go home; G2 – PASS with risk fact…

MalePediatricsmedicine.medical_specialtyReferralHearing lossOtoacoustic Emissions SpontaneousOtoacoustic emissionAudiologyHearing screeningScreening programmeCohort StudiesNeonatal ScreeningClinical ProtocolsPredictive Value of TestsRisk FactorsWell-infant nurseryMedicineHumansRisk factorHearing LossSicilybusiness.industryIncidence (epidemiology)Infant NewbornInfantGeneral Medicinemedicine.diseaseSettore MED/32 - AudiologiaAudiometry Evoked ResponseNeonatal screening; Well-infant nursery; Sensorineural hearing loss; Otoacoustic emission;Settore MED/31 - OtorinolaringoiatriaOtorhinolaryngologySensorineural hearing loPediatrics Perinatology and Child HealthFeasibility StudiesOtoacoustic emissionSensorineural hearing lossFemalemedicine.symptombusinessInternational journal of pediatric otorhinolaryngology
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Cochlear implant users move in time to the beat of drum music.

2015

Cochlear implant users show a profile of residual, yet poorly understood, musical abilities. An ability that has received little to no attention in this population is entrainment to a musical beat. We show for the first time that a heterogeneous group of cochlear implant users is able to find the beat and move their bodies in time to Latin Merengue music, especially when the music is presented in unpitched drum tones. These findings not only reveal a hidden capacity for feeling musical rhythm through the body in the deaf and hearing impaired population, but illuminate promising avenues for designing early childhood musical training that can engage implanted children in social musical activi…

MalePeriodicityTime Factorsmedicine.medical_treatmentMusicalAudiology0302 clinical medicineCochlear implantEarly childhoodPitch Perceptionta515media_commoneducation.field_of_study05 social sciencesMiddle AgedCochlear ImplantationhumanitiesSensory SystemsFeelingta6131Audiometry Pure-ToneFemalePsychologyAdultmedicine.medical_specialtymedia_common.quotation_subjectPopulationMotor Activitybehavioral disciplines and activities050105 experimental psychology03 medical and health sciencesYoung AdultRhythmotorhinolaryngologic diseasesmedicineHumans0501 psychology and cognitive sciencesCochlear implant usersDancingeducationAgedAuditory ThresholdEntrainment (biomusicology)beat of drum musicCochlear ImplantsPersons With Hearing ImpairmentsAcoustic Stimulationhuman activitiesBeat (music)030217 neurology & neurosurgeryMusicHearing research
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