Search results for " Senso"

showing 10 items of 1766 documents

Distribution and phenotype ofGJB2mutations in 102 Sicilian patients with congenital non syndromic sensorineural hearing loss

2014

Objective: To evaluate the frequency of GJB2 mutations and their correlation with phenotype in Sicilian non-syndromic sensorineural hearing loss (NSHL) patients. Design: Sequencing of the coding region, basal promoter, exon 1, and donor splice site of the GJB2 gene; screening for the presence of the two common GJB6 deletions. Study sample: A cohort of 102 Sicilian NSHL patients. Results: Fifteen different mutations in GJB2 and seventeen different genotypes were detected. No GJB6 mutations were found. The hearing impairment was profound in the 64.72% of probands (mean PTA 0.25 – 4 kHz of 88.82 26.52 dB HL). A total of 81.37% of patients harboured at least one c.35delG allele; c.167delT and c…

AdultProbandLinguistics and Languagemedicine.medical_specialtyAdolescentGenotypeHearing Loss SensorineuralAudiologyConnexinsLanguage and LinguisticsYoung AdultSpeech and HearingExonBasal (phylogenetics)Genotypeotorhinolaryngologic diseasesHumansMedicineAlleleChildSicilyAgedRetrospective Studiesbiologybusiness.industrySensorineural hearing loss; GJB2; Genotype-Phenotype; SicilyMiddle Agedmedicine.diseaseGJB2Settore MED/32 - AudiologiaConnexin 26Settore MED/31 - OtorinolaringoiatriaPhenotypeSettore MED/03 - Genetica MedicaSensorineural hearing loGenotype-PhenotypeMutationCohortbiology.proteinSensorineural hearing lossbusinessGJB6International Journal of Audiology
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Identification of D179H, a novel missense GJB2 mutation in a Western Sicily family

2013

The main purpose of this study was to describe a novel missense mutation (p.D179H) found in a Western Sicily family and to examine the genetic and audiologic profiles of all family members by performing a GJB2 and GJB6 mutations analysis and a complete audiologic assessment. The proband was a 3-month-old infant with a congenital profound sensorineural hearing loss; direct sequencing of the GJB2 revealed the presence of a c.35delG mutation in the heterozygous state and a heterozygous G[C transition at nucleotide 535 in trans; this novel mutation, called p.D179H, resulted in an aspartic acid to histidine change at codon 179. It was also evidenced in the heterozygous state in two members of th…

AdultProbandNovel mutationGenotypeHearing Loss SensorineuralDNA Mutational AnalysisNonsense mutationMutation MissenseGenes RecessiveCongenital hearing lossConnexin mutationSeverity of Illness IndexConnexinsmedicineHumansMissense mutationFamilySicilyGeneticsbiologyTransition (genetics)InfantGeneral Medicinemedicine.diseaseGJB2Settore MED/32 - AudiologiaPedigreeNovel mutation Connexin mutation GJB2Sensorineural hearing loss Congenital hearing lossConnexin 26Settore MED/31 - OtorinolaringoiatriaNovel mutation; Connexin mutation; GJB2OtorhinolaryngologyMutation (genetic algorithm)biology.proteinSettore MED/26 - NeurologiaSensorineural hearing lossGJB6European Archives of Oto-Rhino-Laryngology
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Speech perception performance as a function of stimulus pulse rate and processing strategy preference for the Cochlear™ Nucleus®CI24RE device: Relati…

2010

Current cochlear implants can operate at high pulse rates. The effect of increasing pulse rate on speech performance is not yet clear. Habituation to low rates may affect the outcome. This paper presents the results of three subsequent studies using different experimental paradigms, applying the Nucleus CI24RE device, and conducted by ten European implant teams. Pulse rate per channel varied from 500 to 3500 pulses per second with ACE and from 1200 to 3500 pps with CIS strategy. The results showed that the first rate presented had little effect on the finally preferred rate. Lower rates were preferred. The effect of pulse rate on word scores of post-linguistic implantees was small; high rat…

AdultPulse repetition frequencyLinguistics and Languagemedicine.medical_specialtySpeech perceptionAdolescentHearing Loss SensorineuralLoudness Perceptionmedicine.medical_treatmentmedia_common.quotation_subjectAudiologyProsthesis DesignAffect (psychology)Severity of Illness IndexLanguage and LinguisticsCochlear nucleusLoudnessYoung AdultSpeech and HearingProsthesis FittingCochlear implantPerceptionmedicineHumansCorrection of Hearing ImpairmentHabituationAgedmedia_commonAged 80 and overAuditory ThresholdSignal Processing Computer-AssistedMiddle AgedElectric StimulationEuropeCochlear ImplantsPersons With Hearing ImpairmentsAcoustic StimulationAuditory PerceptionSpeech PerceptionAudiometry SpeechPsychologyInternational Journal of Audiology
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Effects of contralateral white noise stimulation on transitory evoked otoacoustic emissions in patients with acoustic neuroma.

1995

Abstract Transitory evoked otoacoustic emissions are normal phenomena observed in most persons with hearing levels greater than 35 dB. Further, masking of the contralateral ear produces amplitude reductions in the transitory evoked otoacoustic emissions. We have undertaken a study of transitory evoked otoacoustic emissions in 20 patients with acoustic neuroma. All patients were assessed for transitory evoked otoacoustic emissions bilaterally, with and without contralateral masking with white band noise at 40, 50, and 60 dB. We found that transitory evoked otoacoustic emissions were present in 30% of ears with tumor and that the presence of transitory evoked otoacoustic emissions is associat…

Adultmedicine.medical_specialtyHearing Loss SensorineuralAcoustic neuromaStimulationAmplitude reductionAudiologyVestibular NerveNeurons EfferentHearingotorhinolaryngologic diseasesMedicineHumansIn patientProspective StudiesAgedTumor sizebusiness.industryHead neckAuditory ThresholdNeuroma AcousticMiddle Agedmedicine.diseaseCochleaHair Cells Auditory OuterWhite bandOtorhinolaryngologyAcoustic StimulationEvoked Potentials AuditoryContralateral earSurgerysense organsbusinessNoisePetrous BoneOtolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery
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C4-dicarboxylate carriers and sensors in bacteria

2002

AbstractBacteria contain secondary carriers for the uptake, exchange or efflux of C4-dicarboxylates. In aerobic bacteria, dicarboxylate transport (Dct)A carriers catalyze uptake of C4-dicarboxylates in a H+- or Na+-C4-dicarboxylate symport. Carriers of the dicarboxylate uptake (Dcu)AB family are used for electroneutral fumarate:succinate antiport which is required in anaerobic fumarate respiration. The DcuC carriers apparently function in succinate efflux during fermentation. The tripartite ATP-independent periplasmic (TRAP) transporter carriers are secondary uptake carriers requiring a periplasmic solute binding protein. For heterologous exchange of C4-dicarboxylates with other carboxylic …

Aerobic bacteriaAntiporterSuccinic AcidBiophysicsOrganic Anion TransportersReceptors Cell Surfacemedicine.disease_causeBiochemistryFumarate (succinate) sensorTwo-component systemBacterial ProteinsFumaratesEscherichia colimedicineAmino Acid SequenceEscherichia coliDicarboxylate uptake SHistidine protein kinasePhylogenyHistidineDicarboxylic Acid TransportersDicarboxylate transport BbiologyEscherichia coli ProteinsBiological TransportPeriplasmic spaceCell Biologybiology.organism_classificationTwo-component regulatory systemBacteria AerobicModels ChemicalBiochemistryAntiportFumarate/succinate transportEffluxDicarboxylate uptake carrierProtein KinasesDicarboxylate transport A carrierBacteriaSignal TransductionBiochimica et Biophysica Acta (BBA) - Bioenergetics
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Ensuring High Performance of Consensus-Based Estimation by Lifetime Maximization in WSNs

2015

The estimation of a parameter corrupted by noise is a common tasks in wireless sensor networks, where the deployed nodes cooperate in order to improve their own inaccurate observations. This cooperation usually involves successive data exchanges and local information updates until a global consensus value is reached. The quality of the final estimator depends on the amount of collected observations, hence the number of active nodes. Moreover, the inherent iterative nature of the consensus process involves a certain energy consumption. Since the devices composing the network are usually battery powered, nodes becoming inactive due to battery depletion emerges as a serious problem. In this wo…

Algebraic connectivityComputer scienceDistributed computingTopology optimizationProcess (computing)EstimatorMaximizationEnergy consumptionNetwork topologyWireless sensor network2015 International Conference on Distributed Computing in Sensor Systems
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A Refractive Index Sensor Based on the Resonant Coupling to Cladding Modes in a Fiber Loop

2013

We report an easy-to-build, compact, and low-cost optical fiber refractive index sensor. It consists of a single fiber loop whose transmission spectra exhibit a series of notches produced by the resonant coupling between the fundamental mode and the cladding modes in a uniformly bent fiber. The wavelength of the notches, distributed in a wavelength span from 1,400 to 1,700 nm, can be tuned by adjusting the diameter of the fiber loop and are sensitive to refractive index changes of the external medium. Sensitivities of 170 and 800 nm per refractive index unit for water solutions and for the refractive index interval 1.40-1.442, respectively, are demonstrated. We estimate a long range resolut…

All-silica fiberMaterials scienceTransducersPhysics::Opticslcsh:Chemical technologyBiochemistryGraded-index fiberRessonància magnètica nuclearArticleAnalytical ChemistryDouble-clad fiberOpticsFiber Optic Technologylcsh:TP1-1185Electrical and Electronic EngineeringInstrumentationbusiness.industryoptical fiber devicesrefractive index sensormode couplingEquipment DesignLong-period fiber gratingCladding (fiber optics)Atomic and Molecular Physics and OpticsÒptica Aparells i instrumentsEquipment Failure AnalysisSolutionsRefractometryNormalized frequency (fiber optics)businessStep-index profilePhotonic-crystal fiberSensors (Basel, Switzerland)
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Sensitivity optimization with cladding-etched long period fiber gratings at the dispersion turning point

2016

This work presents a refractive index sensor based on a long period fiber grating (LPFG) made in a reduced cladding fiber whose low order cladding modes have the turning point at large wavelengths. The combination of these parameters results in an improved sensitivity of 8734 nm/refractive index unit (RIU) for the LP0,3 mode in the 1400-1650 wavelength range. This value is similar to that obtained with thin-film coated LPFGs, which permits to avoid the coating deposition step. The numerical simulations are in agreement with the experimental results. This work was supported in part by the Spanish Ministry of Education and Science-FEDER TEC2013-43679-R. J.L. Cruz also acknowledges financial s…

All-silica fiberMaterials sciencebusiness.industry010401 analytical chemistryFiber optics sensorsLong-period fiber gratingCladding (fiber optics)01 natural sciencesGraded-index fiberAtomic and Molecular Physics and Optics0104 chemical sciencesFibers single-mode010309 opticsOpticsDouble-clad fiberNormalized frequency (fiber optics)Fiber Bragg grating0103 physical sciencesFiber Bragg gratingsDispersion-shifted fiberbusinessOptics Express
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Tesi portanti di un'antropologia di segno sponsale

2015

Il saggio presenta e argomenta alcune affermazioni che consentano di intendere l'amore sponsale come ambito di crescita educativa delle persone: itinerario nel quale sia possibile pervenire ad una conoscenza sempre più adeguata del nome proprio e del desiderio d'essere e di senso costitutivo di ogni soggetto. Assumono rilievo le categorie di relazionalità riconoscente e quella del dono incondizionato di sé all'altro.

Alleanza sponsale Nome proprio Desiderio d'essere e di senso Relazionalità riconoscente Dono di séSettore M-PED/01 - Pedagogia Generale E Sociale
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Influence of mass transport on the competition between corrosion of aluminium alloy surface and the release of primer containing inhibitors : validat…

2014

The conventional aircraft paint scheme for corrosion protection of aluminum structures is partly based on application of a primer containing inhibitors. In such coatings, release of the inhibiting species enables fast healing of a bare metal surface after a mechanical damage of the protective layers. Nevertheless, considering possible depletion of inhibitors by uncontrolled leaching, it appears important to estimate the corrosion risk integrating “corrosion” sensors in the structure. The objective of this work was to understand the operating mode of a sensor simulating a damaged paint coating whose concept is based on the competition between the triggering of localized corrosion and the pas…

Aluminum alloySolid solutionAlliage d’aluminiumMesure de pH de surfaceSolution solide[PHYS.COND.CM-MS] Physics [physics]/Condensed Matter [cond-mat]/Materials Science [cond-mat.mtrl-sci]Surface pH[PHYS.PHYS.PHYS-CHEM-PH] Physics [physics]/Physics [physics]/Chemical Physics [physics.chem-ph]PassivationÉlectrode « tranche »Capteur de corrosionCut-edge electrodeCorrosion sensorsInhibition
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