Search results for " data"

showing 10 items of 7516 documents

Mutations in the skeletal muscle alpha-actin gene in patients with actin myopathy and nemaline myopathy

1999

Muscle contraction results from the force generated between the thin filament protein actin and the thick filament protein myosin, which causes the thick and thin muscle filaments to slide past each other. There are skeletal muscle, cardiac muscle, smooth muscle and non-muscle isoforms of both actin and myosin. Inherited diseases in humans have been associated with defects in cardiac actin (dilated cardiomyopathy and hypertrophic cardiomyopathy), cardiac myosin (hypertrophic cardiomyopathy) and non-muscle myosin (deafness). Here we report that mutations in the human skeletal muscle alpha-actin gene (ACTA1) are associated with two different muscle diseases, 'congenital myopathy with excess o…

AdultMalemedicine.medical_specialtyMyofilamentAdolescentDNA Mutational AnalysisMolecular Sequence Datamacromolecular substancesBiologyMyopathies NemalineTPM203 medical and health sciences0302 clinical medicineNemaline myopathyMuscular DiseasesInternal medicineMyosinGeneticsmedicineHumansPoint MutationAmino Acid SequenceChildMuscle SkeletalPolymorphism Single-Stranded ConformationalActin030304 developmental biologyFamily Health0303 health sciencesPolymorphism GeneticBase SequenceSequence Homology Amino AcidInfantSkeletal muscleDNASequence Analysis DNAmedicine.diseaseCongenital myopathyActins3. Good healthEndocrinologymedicine.anatomical_structureAmino Acid SubstitutionChild PreschoolMutationFemaleMYH7030217 neurology & neurosurgery
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Type of surgical treatment and recurrence of oral leukoplakia: A retrospective clinical study

2017

Background: Oral leukoplakia (OL) is the most typical potentially malignant disorder of the oral mucosa. We aimed to evaluate the clinical outcome of oral leukoplakia treated with several types of lasers and with the use of quantic molecular resonance (QMR) lancet, in terms of recurrence rate. Material and Methods: Eighty-seven previously untreated OL (52 occurring in females and 35 in males, mean age of 59.4 ± 13.9 years) were consecutively submitted to surgical treatment at University Hospital of Parma, Italy, and Hospital de Valongo, Portugal, (1999 to 2012). Interventions were subclassified into 5 groups according to the instrument used for the surgical removal of OL (cold blade – 17; N…

AdultMalemedicine.medical_specialtyOral Surgical ProceduresRetrospective data03 medical and health sciences0302 clinical medicineRecurrencemedicineHumansOral mucosaSurgical treatmentGeneral DentistryUNESCO:CIENCIAS MÉDICASLeukoplakiaAgedRetrospective StudiesAged 80 and overUnivariate analysisOral Medicine and Pathologybusiness.industryResearchRetrospective cohort study030206 dentistryMiddle Agedmedicine.diseaseUniversity hospitalSurgeryOral leukoplakiamedicine.anatomical_structureOtorhinolaryngology030220 oncology & carcinogenesisSurgeryFemaleLaser TherapyLeukoplakia OralbusinessMedicina Oral, Patología Oral y Cirugía Bucal
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Population-based case-control study of essential tremor.

1998

Current epidemiologic data on the association between environmental factors and essential tremor (ET) are scanty. In a population-based case-control study we investigated the relationship between some putative risk factors and ET. In the present study, we included all subjects identified during a door-to-door prevalence survey in a Sicilian community, affected by ET, and alive on 1 November 1987 (n=31). Of the 31 prevalent cases of ET, we were able to contact 28 subjects. Twenty-eight controls were randomly selected from the general population and matched to each case for age and sex. Exposure variables were investigated by interviewing the patients and their controls or close relatives, us…

AdultMalemedicine.medical_specialtyPathologyEpidemiologyEssential TremorPopulationDermatologyPopulation basedOddsRisk FactorsEpidemiologymedicinePrevalenceHumanseducationAgedAged 80 and overeducation.field_of_studyNeuroscience (all)Essential tremorbusiness.industryGeneral NeuroscienceCase-control studyCase-control studyGeneral MedicineEnvironmental exposureEnvironmental ExposureMiddle Agedmedicine.diseasePsychiatry and Mental healthCase-Control StudiesSettore MED/26 - NeurologiaFemaleNeurology (clinical)Epidemiologic databusiness2708DemographyItalian journal of neurological sciences
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A systematic approach to medical decision-making of uncommon clinical pictures: A case of ulcerative skin lesions by palm tree thorn injury and a one…

2005

In clinical practice, the clinician is challenged with symptoms and/or signs at times apparently insoluble by diagnostic and/ or therapeutic means. We propose that in these cases, we have to use an EBM approach in which evidence may be looked up in every available clinical report and bibliographic databases are used for searching that evidence. We report on a case of ulcerative skin lesions apparently insoluble by expert dermatologists following a conventional diagnostic and therapeutic process. We use this case report for illustrating a systematic approach to resolve diagnostic and therapeutic questions using a bibliographic database search (like MEDLINE and EMBASE). Both a systematic appr…

AdultMalemedicine.medical_specialtyPathologyOne year follow upmedical decision-makingMEDLINEDecision MakingAlternative medicineMEDLINEthorn injuryulcerative skin lesionWounds PenetratingHealth InformaticsDiagnosis DifferentialClinical reportHealth Information Managementuncommon clinical picturemedicineHumansIntensive care medicineGeneral NursingLegEvidence-Based Medicinebusiness.industryLeg UlcerMedical decision makingDatabases BibliographicBibliographic databasepalm treeItalyPalmbusinessSkin lesionMedical InformaticsMedical Informatics and the Internet in Medicine
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Influence of social factors on avoidable mortality: a hospital-based case-control study.

2005

Objective. The effect of socioeconomic factors on avoidable mortality at an individual level is not well known, since most studies showing this association are based on aggregate data. The purpose of this study was to determine socioeconomic differences between those patients who die of avoidable causes and those who do not die. Methods. A matched case-control study was carried out regarding in-hospital avoidable mortality (Holland's medical care indicators) that occurred in a university hospital serving a Spanish-Mediterranean population during a 30-month period. Results. We studied 82 cases of death from avoidable causes and 300 controls matched on medical care indicators and age. The var…

AdultMalemedicine.medical_specialtyPediatricsAdolescentMatched-Pair AnalysisPopulationLower risk03 medical and health sciences0302 clinical medicineRisk FactorsCause of DeathEpidemiologymedicineHumans030212 general & internal medicineHospital MortalityeducationChildSocioeconomic statuseducation.field_of_study030505 public healthbusiness.industryPublic healthPublic Health Environmental and Occupational HealthCase-control studyInfant NewbornInfantOdds ratioMiddle AgedLogistic ModelsSocioeconomic FactorsSpainCase-Control StudiesChild PreschoolMultivariate AnalysisEducational StatusAggregate dataFemale0305 other medical sciencebusinessDemographyResearch ArticlePublic health reports (Washington, D.C. : 1974)
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Influenza vaccination coverage among medical residents: An Italian multicenter survey

2014

Although influenza vaccination is recognized to be safe and effective, recent studies have confirmed that immunization coverage among health care workers remain generally low, especially among medical residents (MRs). Aim of the present multicenter study was to investigate attitudes and determinants associated with acceptance of influenza vaccination among Italian MRs. A survey was performed in 2012 on MRs attending post-graduate schools of 18 Italian Universities. Each participant was interviewed via an anonymous, self-administered, web-based questionnaire including questions on attitudes regarding influenza vaccination. A total of 2506 MRs were recruited in the survey and 299 (11.9%) of t…

AdultMalemedicine.medical_specialtyPediatricsAttitude of Health PersonnelImmunologySocio-culturaleSettore MED/42 - Igiene Generale E ApplicataInfluenza immunizationmedical residentsPhysiciansHealth careInfluenza Humanmedicineinfluenza vaccination; coverage rateImmunology and AllergyHumansGood practiceCoverage rate; Influenza vaccination; Italy; Medical residents; Multicentre survey; Adult; Female; Humans; Influenza Vaccines; Influenza Human; Italy; Male; Vaccination; Attitude of Health Personnel; Data Collection; Internship and Residency; Physiciansmulticentre surveyEthical responsibilityPharmacologyCoverage rate; Influenza vaccination; Italy; Medical residents; Multicentre surveybusiness.industryinfluenza vaccination; medical residents; multicentre survey; coverage rate; ItalyData CollectionVaccinationInternship and ResidencyItaly coverage rate influenza vaccination medical residents multicentre surveyInfluenzainfluenza vaccinationVaccinationMulticenter studyItalyInfluenza VaccinesVaccination coverageFamily medicineCoverage rate; Influenza vaccination; Italy; Medical residents; Multicentre survey; Immunology and Allergy; Immunology; PharmacologyMulticenter surveyFemalebusinesscoverage rateResearch PaperHuman
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Biopsy Sampling in Upper Gastrointestinal Endoscopy: A Survey from 10 Tertiary Referral Centres Across Europe.

2021

Background: Guidelines give robust recommendations on which biopsies should be taken when there is endoscopic suggestion of gastric inflammation. Adherence to these guidelines often seems arbitrary. This study aimed to give an overview on current practice in tertiary referral centres across Europe. Methods: Data were collected at 10 tertiary referral centres. Demographic data, the indication for each procedure, endoscopic findings, and the number and sampling site of biopsies were recorded. Findings were compared between centres, and factors influencing the decision to take biopsies were explored. Results: Biopsies were taken in 56.6% of 9,425 procedures, with significant variation between …

AdultMalemedicine.medical_specialtyReferralAdolescentBiopsyDemographic dataStomach and Duodenum: Research ArticleEndoscopy GastrointestinalTertiary Care Centers03 medical and health sciencesYoung Adult0302 clinical medicineInternal medicineBiopsymedicineHumansSampling (medicine)Referral and ConsultationAgedAged 80 and overmedicine.diagnostic_testbusiness.industryGastroenterologyGeneral MedicineGuidelineMiddle AgedUpper gastrointestinal endoscopyEuropeCurrent practice030220 oncology & carcinogenesisCohort030211 gastroenterology & hepatologyFemalebusinessDigestive diseases (Basel, Switzerland)
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Analysis of thiamine transporter genes in sporadic beriberi

2014

Abstract Objective Thiamine or vitamin B 1 deficiency diminishes thiamine-dependent enzymatic activity, alters mitochondrial function, impairs oxidative metabolism, and causes selective neuronal death. We analyzed for the first time, the role of all known mutations within three specific thiamine carrier genes, SLC19 A2, SLC19 A3 , and SLC25 A19 , in a patient with atrophic beriberi, a multiorgan nutritional disease caused by thiamine deficiency. Methods A 44-year-old male alcoholic patient from Morocco developed massive bilateral leg edema, a subacute sensorimotor neuropathy, and incontinence. Despite normal vitamin B 1 serum levels, his clinical picture was rapidly reverted by high-dose in…

AdultMalemedicine.medical_specialtySLC19 A- SLC25 A19SLC19 AEndocrinology Diabetes and MetabolismGene mutationBeriberimedicine.disease_causeMitochondrial Membrane Transport Proteinslaw.inventionBeriberilawInternal medicineGenotypemedicineThiamine transporterObjective: Thiamine or vitamin B1 deficiency diminishes thiamine-dependent enzymatic activity alters mitochondrial function impairs oxidative metabolism and causes selective neuronal death. We analyzed for the first time the role of all known mutations within three specific thiamine carrier genes SLC19 A2 SLC19 A3 and SLC25 A19 in a patient with atrophic beriberi a multiorgan nutritional disease caused by thiamine deficiency. Methods: A 44-year-old male alcoholic patient from Morocco developed massive bilateral leg edema a subacute sensorimotor neuropathy and incontinence. Despite normal vitamin B1 serum levels his clinical picture was rapidly reverted by high-dose intramuscular thiamine treatment suggesting a possible genetic resistance. We used polymerase chain reaction followed by amplicon sequencing to study all the known thiamine-related gene mutations identified within the Human Gene Mutation Database. Results: Thirty-seven mutations were tested: 29 in SLC19 A2 6 in SLC19 A3 and 2 in SLC25 A19. Mutational analyses showed a wild-type genotype for all sequences investigated. Conclusion: This is the first genetic study in beriberi disease. We did not detect any known mutation in any of the three genes in a sporadic dry beriberi patient. We cannot exclude a role for other known or unknown mutations in the same genes or in other thiamine-associated genes in the occurrence of this nutritional neuropathy.HumansThiamineGenePolymerase chain reactionGeneticsMutationNutrition and DieteticsbiologyMembrane Transport ProteinsThiamine Deficiencymedicine.diseaseAlcoholismEndocrinologyMutationbiology.proteinThiamineMutations
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The epidemiology of mumps in Italy.

2008

In Italy, although vaccination has been recommended for a number of years, vaccination coverage for mumps is still sub-optimal. The objective of the present study was to evaluate the seroprevalence of mumps antibodies in the Italian population, stratified by age, gender and geographical area. The proportion of individuals positive for mumps antibodies remained stable in the age classes 0–11 months and 1 year (25.4% and 30.8%, respectively) and showed a continuous increase after the second year of life. The percentage of susceptible individuals was higher than 20% in persons 2–14 years of age and exceeded 10% in persons 15–39 years of age. No statistically significant differences were observ…

AdultMalemedicine.medical_specialtySettore MED/07 - Microbiologia E Microbiologia ClinicaAdolescentDatabases FactualMumps; Seroprevalence; Vaccination; Adolescent; Adult; Age Factors; Child; Child Preschool; Databases Factual; Disease Outbreaks; Female; Humans; Immunoglobulin G; Infant; Italy; Male; Middle Aged; Mumps; Registries; Seroepidemiologic Studiesmumps; seroprevalence; vaccinationSerologyDisease OutbreaksDatabasesSeroepidemiologic StudiesEpidemiologymedicineSeroprevalenceHumansRegistriesPreschoolChildMumpsFactualGeneral VeterinaryGeneral Immunology and Microbiologyseroprevalencebusiness.industryPublic Health Environmental and Occupational HealthAge FactorsInfantMiddle AgedvaccinationItalian populationVirologyVaccinationMumps Seroprevalence VaccinationInfectious DiseasesItalyVaccination coverageChild PreschoolImmunoglobulin GMolecular MedicineFemaleViral diseasebusinessDemographyVaccine
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Five-year retrospective italian multicenter study of visceral leishmaniasis treatment.

2014

ABSTRACT The treatment of visceral leishmaniasis (VL) is poorly standardized in Italy in spite of the existing evidence. All consecutive patients with VL admitted at 15 Italian centers as inpatients or outpatients between January 2004 and December 2008 were retrospectively considered; outcome data at 1 year after treatment were obtained for all but 1 patient. Demographic characteristics, underlying diseases, diagnostic procedures, treatment regimens and outcomes, as well as side effects were recorded. A confirmed diagnosis of VL was reported for 166 patients: 120 (72.3%) immunocompetent, 21 (12.6%) patients with immune deficiencies other than HIV infection, and 25 (15.1%) coinfected with HI…

AdultMalemedicine.medical_specialtySettore MED/17 - Malattie InfettiveAdolescentAntiprotozoal AgentsSocio-culturaleClinical TherapeuticsAdolescent; Adult; Aged; Amphotericin B; Antiprotozoal Agents; Child; Female; Humans; Italy; Leishmaniasis Visceral; Male; Middle Aged; Retrospective Studies; Treatment Outcome; Young Adult; Pharmacology (medical); Pharmacology; Infectious DiseasesYoung AdultAmphotericin BInternal medicineAmphotericin BmedicineHumansPharmacology (medical)Young adultvisceral leishmaniasis treatment ItalyChildLeishmaniasisAgedRetrospective StudiesVisceralPharmacologybusiness.industryAmbientaleRetrospective cohort studyMiddle Agedmedicine.diseaseSurgeryInfectious DiseasesVisceral leishmaniasisTreatment OutcomeMulticenter studyItalyLeishmaniasis VisceralLiposomal amphotericinFemaleOutcome databusinessAfter treatmentmedicine.drug
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