Search results for " loss"

302 Hearing Abnormalities in Children with Fabry Disease: Data from FOS - the Fabry Outcome Survey

2005

Background: Fabry disease is an X-linked glycosphingolipid storage disorder due to a deficiency of the enzyme alpha-galactosidase A. Accumulation of substrate results in a progressive and life-threatening multisystemic disease. Early clinical manifestations include pain and gastrointestinal symptoms. Sensorineural hearing loss and vertigo are well-recognized features of the disorder, occurring in approximately 50% of adults with Fabry disease. We have investigated the audiological symptoms of Fabry disease in children using pure-tone and impedance audiometry. Methods: Symptom history was obtained using a standardized questionnaire from FOS − the Fabry Outcome Survey. Hearing was measured us…

Strength and muscle mass loss with aging process. Age and strength loss.

2014

Background aging process is associated with changes in muscle mass and strength with decline of muscle strength after the 30(th) life year. The aim of this study was to investigate these changes in muscle mass and strength. Patients & methods for this analysis 26 participants were subdivided in two groups. Group 1 comprises participants aged 40 years (n=12). We assessed anthropometrics, range of motions, leg circumferences and isometric strength values of the knee joints. Results besides comparable anthropometrics, circumferences and strength were higher in group 1 than in group 2. Circumference of upper leg (20 cm above knee articular space) showed for right leg a trend to a significant (m…

Achalasia with megaesophagus and tracheal compression in a young patient: A case report.

2015

Highlights • This report emphasizes that physicians should be alert and consider airway obstruction and signs of dyspnea as severe and threatening symptoms in extensive cases of achalasia with megaesophagus. • Early surgical treatment provides a therapeutic option to obviate the occurrence of acute respiratory distress and consecutive complications. • In particular, difficulties in intubation prior to surgery must be considered. Due to potential tracheomalacia, the status of “bull frog neck” in achalasia, including severe tracheal compression caused by megaesophagus with concomitant cervical swelling, may also lead to extubation problems and deserves special care in the postoperative period.

Die endoskopische retroperitoneale Adrenalektomie

2008

Aim of study To determine prospectively in consecutive patients the value of endoscopic retroperitoneal adrenalectomy. Patients and methods Between March 1994 and March 1995, endoscopic adrenalectomy via a retroperitoneal approach was performed in eleven patients (three men, eight women; median age 61 [48-73] years), unilateral in nine, bilateral in two. The procedure was indicated if the adrenal tumour was thought to be benign and no larger than 5 cm in diameter (two adrenal and two central Cushing's syndromes; three incidentally detected adrenal adenomas, two phaeochromocytomas, two Conn adenomas). Results Twelve of the 13 procedures were successfully performed. In one case the primary in…

Cessation of Cerebral Blood Flow in Total Irreversible Loss of Brain Function

1969

After the demonstration, by our group [3, 4], that in cases of so-called “cerebral death” there is an absence of clearance from the brain of 133Xe selectively injected into the internal carotid artery, further attention was dedicated to establish possible sources of error in this technique.

Effects of long-term lifestyle and high-intensity interval training intervention on blood pressure reduction in patients with abdominal obesity

2013

Purpose: The aims of this study were: 1) to study the impact of a combined long-term lifestyle and high-intensity interval training (HIIT) intervention on blood pressure (BP) in patients with abdominal obesity; 2) To document BP reduction responses according to the European Society of Hypertension BP classification. Methods: 105 patients with abdominal obesity (age: 53±10 yrs; 32 men; waist circumference (WC): 112±13cm; systolic/diastolic (SBP/DBP): 133±13/82±8 mmHg; 11% diabetics, 11% smokers, 68% with antihypertensive therapy) were retrospectively analyzed before and after a combined long-term lifestyle and HIIT program twice a week. Anthropometric measurements, cardiometabolic risk facto…

Ösophagusresektion bei unspezifischer Motilitätsstörung der Speiseröhre - Bedeutung der neuropathologischen Befunde

2005

A 47-year-old patient presented with a history of dysphagia for solid food for almost 10 years and weight loss of more than 50 kg. Non-resecting surgical as well as endoscopic procedures (laparoscopic cardiomyotomy with secondary antireflux operations, balloon dilation, Botulinum-toxin injection) were without success. A barium esophagogram showed a confinement of the distal esophagus with a filiform passage of the contrast medium and undigested food in the prestenotic dilated esophageal corpus. Manometry displayed a hypertensive lower esophageal sphincter with a resting pressure of 43.8 mmHg - although completely relaxing. The tubular esophagus was aperistaltic with 100 % simultaneous and r…

Clinical update: bariatric surgery.

2007

Beidseitige progrediente Hörminderung als Erstmanifestation eines metastasierenden Pankreaskopfkarzinoms - Kasuistik -

2001

We report the history of a patient who presented first with a progressive unilateral hearing loss and later with a bilateral deafness and an unilateral facial nerve palsy as first and only symptoms of a pancreatic adenocarcinoma. By means of magnetic resonance tomography tumor-suspect lesions in both internal auditory canals were detected. Referring to the results of further examinations these intracanalicular lesions are most probably due to rarely seen bilateral metastasis of a pancreatic adenocarcinoma in the temporal bone. In addition to this rarely diagnosed localisation of metastasis it is rather uncommon that this kind of primary malignoma had not been detected because of gastrointes…

Effekt der kontralateralen Stimulation auf evozierte otoakustische Emissionen bei akutem Hörverlust*

1994

23 patients with unilateral hearing loss and presence of TEOAE on both ears were examined with regard to the association between contralateral acoustic stimulation and evoked otoacoustic emissions. Contralateral white noise of 40 dB HL, 50 dB HL and 60 dB HL decreases the amplitude of TEOAE both at the ear with and without hearing loss. In comparison with a group of subjects with normal hearing, the decrease in the amplitude of TEOAE was less in the group of patients with hearing loss. Two paradoxical cases were found with an increase in the TEOAE amplitude in the ear with hearing loss during contralateral stimulation. It is assumed that impairment of the efferent synapses on the outer hair…