Search results for "Arid"

showing 10 items of 1382 documents

Le Climosequenze: strumenti per valutare gli effetti dei cambiamenti climatici su alcune proprietà e caratteri funzionali del suolo - un caso studio …

2013

climosequence Vertisols edaphic properties aridity index climate change
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Serological and molecular characteristics of Vibrio vulnificus biotype 3: evidence for high clonality.

2007

Vibrio vulnificus biotype 3 has been implicated as the causative pathogen of an ongoing disease outbreak that erupted in Israel in 1996. Recent work based on multi-locus sequence typing (MLST) showed that V. vulnificus biotype 3 is genetically homogeneous. The aim of this study was to investigate the existence of subpopulations within this homogeneous biotype by characterizing the surface antigens and analysing the sequence diversity of selected outer-membrane protein (OMP)-encoding genes. Rabbit antisera were prepared against biotype 1, 2 and 3 strains. The results of the slide-agglutination test, dot-blot assay (using fresh and boiled cells), and immunoblotting of lipopolysaccharides (LPS…

clone (Java method)DNA BacterialLipopolysaccharidesPopulationImmunoblottingMolecular Sequence DataSequence HomologyBiologyMicrobiologyDNA sequencingMicrobiologyEvolution MolecularAgglutination TestsCluster AnalysisHumansTypingIsraeleducationGenePathogenVibrio vulnificuseducation.field_of_studyAntigens BacterialMolecular EpidemiologyBase SequenceStrain (biology)Genetic Variationbacterial infections and mycosesVibrio InfectionsbacteriaMultilocus sequence typingBacterial Outer Membrane ProteinsMicrobiology (Reading, England)
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Comparación de los resultados radiológicos, clínicos y analíticos de un vástago con cuello modular y su homólogo monobloque en la artroplastia total …

2022

Introducción: La artroplastia total de cadera es uno de los grandes hitos de la ortopedia moderna. Los vástagos con cuellos modulares fueron introducidos con la ventaja teórica de permitir un ajuste más exacto de la anatomía. La hipótesis de nuestro trabajo es que el vástago modular H-MAX M con cuellos intercambiables permite restaurar el offset femoral y la longitud de miembros, de forma más ajustada que con el vástago monobloque homólogo H-MAX S, obteniendo con ello mejores resultados clínico-funcionales sin añadir los riesgos de una elevación sérica de cromo ni cobalto. El objetivo de nuestro trabajo es comparar los resultados radiológicos, clínicos y analíticos de un vástago con cuell…

cobaltodisimetríaUNESCO::CIENCIAS MÉDICAScuestionario de saludoffset femoraliones metálicos:CIENCIAS MÉDICAS [UNESCO]modularidadescalas de saludcromoartroplastia cadera
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Heparan sulfate levels in mucopolysaccharidoses and mucolipidoses.

2004

Glycosaminoglycans are accumulated in both mucopolysaccharidoses (MPS) and mucolipidoses (ML). MPS I, II, III and VII and ML II and ML III patients cannot properly degrade heparan sulphate (HS). In spite of the importance of HS storage in the metabolic pathway in these diseases, blood and urine HS levels have not been determined systematically using a simple and economical method. Using a new ELISA method using anti-HS antibodies, HS concentrations in blood and urine were determined in MPS and ML II and ML III patients. HS concentrations were determined in 156 plasma samples from MPS I (n = 23), MPS II (n = 26), MPS III (n = 24), MPS IV (n = 62), MPS VI (n = 5), MPS VII (n = 5), ML II (n = …

congenital hereditary and neonatal diseases and abnormalitiesAdolescentMucopolysaccharidosisEnzyme-Linked Immunosorbent AssayUrineSignificant elevationGlycosaminoglycanchemistry.chemical_compoundMucolipidosesGeneticsmedicineHumansElisa methodskin and connective tissue diseasesChildGenetics (clinical)Chromatography High Pressure LiquidGlycosaminoglycansDose-Response Relationship DrugChemistryHeparinInfant Newbornnutritional and metabolic diseasesMucolipidosesInfantHeparan sulfateMucopolysaccharidosesmedicine.diseaseMolecular biologyDose–response relationshipBiochemistryChemistry ClinicalChild PreschoolHeparitin SulfateBiomarkersJournal of inherited metabolic disease
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B and T lymphocytes are affected in lysosomal disorders--an immunoelectron microscopic study.

1991

Circulating lymphocytes of four patients with mucopolysaccharidoses II and IIIA, four patients with juvenile neuronal ceroid-lipofuscinosis, one patient each with glycogenosis type II, infantile neuronal ceroid-lipofuscinosis, and Gaucher disease were classified by immunoelectron microscopy as B or T lymphocytes. Disease-specific lysosomal inclusions as well as non-specific lysosomal organelles, especially Gall bodies were identified in B and T lymphocytes. These non-quantitative studies indicate that both B and T lymphocytes participate in the lysosomal storage process.

congenital hereditary and neonatal diseases and abnormalitiesPathologymedicine.medical_specialtyHistologyImmunoelectron microscopyMucopolysaccharidosisT-LymphocytesCentral nervous systemVacuoleBiologyPathology and Forensic MedicinePhysiology (medical)OrganellemedicineLysosomal storage diseaseHumansMicroscopy ImmunoelectronB-Lymphocytesnutritional and metabolic diseasesT lymphocytemedicine.diseasemedicine.anatomical_structureNeurologyNeuronal ceroid lipofuscinosisNeurology (clinical)Metabolism Inborn ErrorsNeuropathology and applied neurobiology
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Audiological Findings in Children With Mucopolysaccharidoses Type I–IV

2017

Abstract Objective The aim of our study is to reflect hearing impairment of 23 children diagnosed with mucopolysaccharidosis (MPS) type I, II, III and IV. Methods Retrospective study of the clinical, audiological and treatment (medical vs surgical) findings of 23 children diagnosed with MPS type I, II, III and IV followed at a Tertiary Referral Hospital between 1997 and 2015. Results Six cases of MPS I, 8 of MPS II, 4 of MPS III and 5 of MPS IV were reviewed. 71.2% of patients had secretory otitis media (SOM) and 54% of patients had some type of hearing loss (HL). The behaviour of hearing loss was variable in each of the subgroups of MPS, finding greater involvement and variability in types…

congenital hereditary and neonatal diseases and abnormalitiesPediatricsmedicine.medical_specialtyHearing lossbusiness.industryMucopolysaccharidosisnutritional and metabolic diseasesRetrospective cohort studyGeneral MedicineAudiologyTertiary referral hospitalmedicine.disease03 medical and health sciences0302 clinical medicineOtitisQuality of lifemedicinemedicine.symptomskin and connective tissue diseases030223 otorhinolaryngologybusiness030217 neurology & neurosurgeryActa Otorrinolaringologica (English Edition)
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Systemic therapies for mucopolysaccharidosis: ocular changes following haematopoietic stem cell transplantation or enzyme replacement therapy - a rev…

2010

The management of mucopolysaccharidosis (MPS) is focused on the multi-organ, sometimes life-threatening, clinical manifestations that occur over time. In the past, the limited, symptom-based treatment options led physicians to adopt a palliative approach towards individual disease-associated complications. The availability of systemic treatments such as haematopoietic stem cell transplantation (HSCT) and enzyme replacement therapy (ERT) has created a better prognosis for MPS patients, particularly when initiated early in life. As part of an integrated management approach, these therapies could be valuable in managing the ocular features that are present in many children with MPS. HSCT has b…

congenital hereditary and neonatal diseases and abnormalitiesmedicine.medical_specialtyVisual acuitygenetic structuresbusiness.industryMucopolysaccharidosismedicine.medical_treatmentEye diseasenutritional and metabolic diseasesEnzyme replacement therapyHematopoietic stem cell transplantationmedicine.diseaseeye diseasesSurgeryTransplantationOphthalmologymedicineOptic nervesense organsStem cellmedicine.symptomIntensive care medicinebusinessClinical & Experimental Ophthalmology
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Emplazamiento de producto en bestsellers literarios: efectos de la familiaridad con la marca, la repetición y la congruencia sobre la memoria de los …

2015

El emplazamiento de producto es una herramienta emergente de las comunicaciones de marketing que se enmarca en una tendencia general de mercado en la que las líneas entre contenido de entretenimiento y publicidad se difuminan. A pesar de que en los últimos años el emplazamiento de producto ha suscitado un creciente interés tanto entre académicos como entre profesionales del marketing los trabajos académicos sobre el emplazamiento de producto en los medios impresos, y especialmente los trabajos de naturaleza empírica, son prácticamente inexistentes existiendo por tanto un vacío de investigación que debe ser atendido. Esta tesis tiene como objetivo principal aportar nuevo conocimiento a la ef…

congruenciarecuerdo de marcaproduct placementrepeticiónUNESCO::CIENCIAS ECONÓMICASemplazamiento de productoreconocimiento de marcabestsellers literarios:CIENCIAS ECONÓMICAS [UNESCO]familiaridad
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La dirigenza pubblica: criteri di identificazione e specialità della disciplina.

Nel tentativo di far luce sui maggiori coni d’ombra che emergono dalla relativa disciplina speciale del rapporto di lavoro, la tesi riflette l’esigenza di un ripensamento sistematico della figura del dirigente pubblico, nell’ottica di prospettare de iure condendo possibili correttivi. A tal fine, sono analizzate le peculiarità ed attribuzioni della dirigenza pubblica, in chiave storico-evolutiva, alla luce dei principi costituzionali e del processo riformatore che ha contrassegnato la magmatica materia, a tutt’oggi in atto. E’, altresì, rivolto uno sguardo comparativistico alla disciplina del personal directivo español, rivelandosi la stessa, speculare a quella del dirigente italiano quanto…

dirigenza; pubblica; criteri; identificazione; specialità; disciplina; riforma pubblica amministrazione; politica; amministrazione; incarico; conferimento; revoca; spoil system; ordinamento spagnolo; comparazione; personal directivo.disciplinaspecialitàSettore IUS/07 - Diritto Del Lavoropubblicapoliticadirigenzapersonal directivo.amministrazioneCon la finalidad de aclarar las zonas de claroscuro que emergen de la disciplina especial de su relación laboral la tesis refleja la exigencia de un replanteamiento sistemático de la figura del dirigente pubblico con el objetivo de proponer de iure condendo posibles soluciones. Para ello se analizan las peculiaridades y los atributos de la dirigenza pubblica en clave histórico-evolutiva a la luz de los principios constitucionales y del proceso reformador que ha caracterizado (y sigue caracterizando) la caótica materia. Asimismo se ha dirigido una mirada comparatista a la institución del personal directivo español la cual presenta tanto analogias como diferencias respecto a la del dirigente italiano sobre todo en lo concerniente a las graves incidencias sobre la gestión de la función pública y al sistema de nombramiento de directivos. [Abstract in spagnolo]comparazionerevocacriteriincaricoconferimentospoil systemordinamento spagnoloidentificazioneAbstract in spagnolo: Con la finalidad de aclarar las zonas de claroscuro que emergen de la disciplina especial de su relación laboral la tesis refleja la exigencia de un replanteamiento sistemático de la figura del dirigente pubblico con el objetivo de proponer de iure condendo posibles soluciones. Para ello se analizan las peculiaridades y los atributos de la dirigenza pubblica en clave histórico-evolutiva a la luz de los principios constitucionales y del proceso reformador que ha caracterizado (y sigue caracterizando) la caótica materia. Asimismo se ha dirigido una mirada comparatista a la institución del personal directivo español la cual presenta tanto analogias como diferencias respecto a la del dirigente italiano sobre todo en lo concerniente a las graves incidencias sobre la gestión de la función pública y al sistema de nombramiento de directivos.riforma pubblica amministrazione
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Structure−Dynamics Coupling between Protein and External Matrix in Sucrose-Coated and in Trehalose-Coated MbCO:  An FTIR Study

2004

We performed FTIR measurements on carboxy-myoglobin (MbCO) embedded in a sucrose−water matrix to study the degrees of freedom coupling between protein and external matrix in such a system. The work was undertaken on the light of recent results by Giuffrida et al. (J. Phys. Chem. B 2003, 107, 13211−13217), who evidenced, in trehalose-coated MbCO, a structured water−sugar environment of the protein, tightly coupled to the heme pocket structure. Such information was obtained through a suitable analysis of the temperature dependence of the CO stretching and of the water association bands in samples of different content of residual water. We applied here the same analysis to sucrose-coated MbCO.…

disaccharides FTIR spectroscopy protein waterSucroseAnalytical chemistryTrehaloseSurfaces Coatings and FilmsCoupling (electronics)Matrix (chemical analysis)chemistry.chemical_compoundProtein environmentCrystallographychemistryMaterials ChemistryPhysical and Theoretical ChemistryFourier transform infrared spectroscopyHemeThe Journal of Physical Chemistry B
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