Search results for "Cng"

showing 6 items of 6 documents

CNGB3 mutations account for 50% of all cases with autosomal recessive achromatopsia

2005

Contains fulltext : 47591.pdf (Publisher’s version ) (Closed access) Achromatopsia is a congenital, autosomal recessively inherited disorder characterized by a lack of color discrimination, low visual acuity (<0.2), photophobia, and nystagmus. Mutations in the genes for CNGA3, CNGB3, and GNAT2 have been associated with this disorder. Here, we analyzed the spectrum and prevalence of CNGB3 gene mutations in a cohort of 341 independent patients with achromatopsia. In 163 patients, CNGB3 mutations could be identified. A total of 105 achromats carried apparent homozygous mutations, 44 were compound (double) heterozygotes, and 14 patients had only a single mutant allele. The derived CNGB3 mutatio…

AchromatopsiaGenetics and epigenetic pathways of disease [NCMLS 6]genetic structuresGATED CATION CHANNELCNGB3 mutationsNonsense mutationMutantCyclic Nucleotide-Gated Cation ChannelsColor Vision DefectsGenes RecessiveLocus (genetics)Gene mutationBiologyTOTAL COLOURBLINDNESSIon ChannelsCLONINGDogscyclic nucleotide-gated channelGNAT2GeneticsmedicineLOCUSAnimalsHumansMissense mutationNeurosensory disorders [UMCN 3.3]ACHM3 locusDog DiseasesAlleleAllelesGenetics (clinical)Geneticstotal colorblindnessGNAT2PHOTORECEPTORSDYSTROPHYmedicine.diseaseCONE DEGENERATIONGENEeye diseasesPhenotypeEvaluation of complex medical interventions [NCEBP 2]MutationRetinal Cone Photoreceptor Cellssense organsachromatopsiarod monochromacyALPHA-SUBUNIThuman activities
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Prospects of Decarbonizing Industrial Areas in the Baltic States by Means of Alternative Fuels

2022

This work has been supported by the National Research Programme, project “Trends, Challenges and Solutions of Latvian Gas Infrastructure Development” (LAGAS), No. VPP-EM-INFRA-2018/1-0003.

Bio-cngBiofuelAlternative fuels:NATURAL SCIENCES [Research Subject Categories]CngHcngGhg emissionsEcology Evolution Behavior and SystematicsGeneral Environmental Science
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A mathematical model for the prediction of the injected mass diagram of a S.I. engine gas injector

2013

A mathematical model of gaseous fuel solenoid injector for spark ignition engine has been realized and validated through experimental data. The gas injector was studied with particular reference to the complex needle motion during the opening and closing phases, which strongly affects the amount of fuel injected. As is known, in fact, when the injector nozzle is widely open, the mass flow depends only on the fluid pressure and temperature upstream the injector: this allows one to control the injected fuel mass acting on the “injection time” (the period during which the injector solenoid is energized). This makes the correlation between the injected fuel mass and the injection time linear, e…

Injector modelEngineeringbusiness.industryMechanical EngineeringNuclear engineeringInjectorDiesel cycleFuel injectionSettore ING-IND/13 - Meccanica Applicata Alle MacchineAutomotive engineeringlaw.inventionFuel mass fractionSettore ING-IND/08 - Macchine A FluidoInternal combustion engineMechanics of MaterialsEngine efficiencylawSpark-ignition engineCNGGas injectorSpark ignition enginePhysics::Chemical PhysicsbusinessPetrol engineJournal of Mechanical Science and Technology
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Performances improvement of a S.I. CNG bi-fuel engine by means of double-fuel injection

2009

Natural gas represents today a promising alternative to conventional fuels for road vehicles propulsion, since it is characterized by a relatively low cost, better geopolitical distribution than oil, and lower environmental impact. This explains the current spreading of Compressed Natural Gas (CNG) fuelled S. I. engine, above all in the bi-fuel version, i.e. capable to run either with gasoline or with natural gas. This characteristic, on the one hand, permits the vehicle to go even when natural gas is not available, on the other hand requires the engine to be designed to run safely with gasoline, i.e. with compression ratio lower than what natural gas would allow. Moreover the electronic co…

Settore ING-IND/08 - Macchine A FluidoEnvironmental scienceCNG double-fuel S.I. engineFuel injectionAutomotive engineering
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Efficiency advantages of the separated electric compound propulsion system for CNG hybrid vehicles

2021

As is widely known, internal combustion engines are not able to complete the expansion process of the gas inside the cylinder, causing theoretical energy losses in the order of 20%. Several systems and methods have been proposed and implemented to recover the unexpanded gas energy, such as turbocharging, which partially exploits this energy to compress the fresh intake charge, or turbo-mechanical and turbo-electrical compounding, where the amount of unexpanded gas energy not used by the compressor is dedicated to propulsion or is transformed into electric energy. In all of these cases, however, maximum efficiency improvements between 4% and 9% have been achieved. In this work, the authors d…

TechnologyControl and Optimizationcompound engineRenewable Energy Sustainability and the EnvironmentThybrid vehicleexhaust energy recoveryEnergy Engineering and Power TechnologyCNG spark-ignition engineCNG spark-ignition engine Compound engine Exhaust energy recovery hybrid vehicleSettore ING-IND/08 - Macchine A Fluidohybrid vehicle; compound engine; CNG spark-ignition engine; exhaust energy recoveryElectrical and Electronic EngineeringEngineering (miscellaneous)Energy (miscellaneous)
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Analysis of the Role of the Latvian Natural Gas Network for the use of Future Energy Systems: Hydrogen from Res

2021

The research has been funded by the Ministry of Economics of the Republic of Latvia, project “Trends, Challenges and Solutions of Latvian Gas Infrastructure Development (LAGAS)”, project No. VPP EM-INFRA-2018/1-0003.

hcng blendingbusiness.industryPhysicsQC1-9990211 other engineering and technologiesdecarbonisationLatvianHCNG blending02 engineering and technology7. Clean energylanguage.human_languagenatural gas13. Climate actionNatural gasEnvironmental protectionhydrogen021105 building & constructionlanguage:NATURAL SCIENCES:Physics [Research Subject Categories]Christian ministryNG networks021108 energyDecarbonisationng networksbusinessLatvian Journal of Physics and Technical Sciences
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