Search results for "Croce"
showing 10 items of 170 documents
Solid state 13C-NMR methodology for the cellulose composition studies of the shells of Prunus dulcis and their derived cellulosic materials.
2020
Lignocellulosic fibers and microcellulose have been obtained by simple alkaline treatment from softwood al- mond shells. In particular, the Prunus dulcis Miller (D.A.) Webb. was considered as a agro industrial waste largely available in southern Italy. The materials before and after purification have been characterized by 13C CPMAS NMR spectroscopy methodology. A proper data analysis provided the relative composition of lignin and holo- cellulose at each purification step and the results were compared with thermogravimetric analysis and FT-IR. To value the possibility of using this material in a circular economy framework, the fibrous cellulosic material was used to manufacture a handmade c…
WWOX-related encephalopathies: delineation of the phenotypical spectrum and emerging genotype-phenotype correlation
2014
International audience; BACKGROUND:Homozygous mutations in WWOX were reported in eight individuals of two families with autosomal recessive spinocerebellar ataxia type 12 and in two siblings with infantile epileptic encephalopathy (IEE), including one who deceased prior to DNA sampling.METHODS:By combining array comparative genomic hybridisation, targeted Sanger sequencing and next generation sequencing, we identified five further patients from four families with IEE due to biallelic alterations of WWOX.RESULTS:We identified eight deleterious WWOX alleles consisting in four deletions, a four base-pair frameshifting deletion, one missense and two nonsense mutations. Genotype-phenotype correl…
Valori perduti e perduta libertà. Croce e il dibattito tedesco sulla relatività dei valori
2017
The relativism of values (Werterelativismus) is a problem very central for the historicism debate, which concerned historians and phi- losophers at the beginning of the twentieth century. The historization of all knowledge and all values leads to their historical devaluation. How can values still be formulated and maintained in face of this relativization? This was the question of theorists such as Otto Hintze, Friedrich Meinecke, Max Weber and Ernst Troeltsch, as well as of the philosopher Benedetto Croce in times of emerging Fascism, that was regarded as a political and moral threat. As representatives of an intellectual and social liberalism, these academics developed their own strategie…
Numerical modelling of the electrochemical behaviour of 316 stainless steel based upon static and dynamic experimental microcapillary-based technique…
2008
objective of this work was to determine the parameters that affect the mass transport and the distribution of species in microcapillaries close to the specimen surface. Local experiments were carried out under static and flow conditions on type 316L stainless steel in 1.7 M NaCl, pH = 3, by means of the electrochemical microcell and the scanning droplet cell technique. The polarisation behaviour of pure iron (used as a model system) in an aqueous environment was calculated adopting a finite element approach and was compared to the experimental results. The corrosion system consists of three parallel electrochemical reactions: the oxygen reduction reaction (ORR), the hydrogen evolution react…
Age-dependent epileptic encephalopathy associated with an unusual co-occurrence of ZEB2 and SCN1A variants.
2020
Mowat-Wilson syndrome is a genetic disorder associated with a variable phenotype including peculiar facial features associated with intellectual disability, epilepsy, language impairment, and multiple congenital anomalies caused by heterozygous mutation of the ZEB2 gene. The ZEB2 protein is a complex transcription factor that encompasses multiple functional domains that interact with the regulatory regions of target genes including those involved in brain development. Recently, it has been documented that ZEB2 regulates the differentiation of interneuron progenitors migrating from the medial ganglionic eminence to cortical layers by repression of the Nkx2-1 homeobox transcription factor. It…
Armonia
2016
Understanding the Strategies and Practices of Facebook Microcelebrities for Engaging in Sociopolitical Discourses
2022
In this paper, we study popular microcelebrities from the Global South to understand their strategies and practices on Facebook. Unlike traditional celebrities who gain their reputation through different types of physical performance, these microcelebrities attain their status by presenting themselves in a favorable way to their online followers. We conducted interviews with 19 microcelebrities from Bangladesh and analyzed our data using actor-network theory (ANT) and Goffman’s dramaturgical analysis (DA) of human interaction. We discuss the complex socio-technical ecosystem of the microcelebrity and the roles of non-human actors, such as platforms and local internet infrastructure along wi…
BCL11A intellectual developmental disorder: defining the clinical spectrum and genotype-phenotype correlations
2021
AbstractPurposeHeterozygous variants in BCL11A underlie an intellectual developmental disorder with persistence of fetal hemoglobin (BCL11A-IDD, a.k.a. Dias-Logan syndrome). We sought to delineate the genotypic and phenotypic spectrum of BCL11A-IDD.MethodsWe performed an in-depth analysis of 42 patients with BCL11A-IDD ascertained through a collaborative network of clinical and research colleagues. We also reviewed 33 additional affected individuals previously reported in the literature or available through public repositories with clinical information.ResultsMolecular and clinical data analysis of 75 patients with BCL11A-IDD identified 60 unique variants (30 frameshift, 7 missense, 6 splic…
La clartè de la distinction. Considérations sur la logique de Croce
2010
Disamina storico-filosofica ed argomentativa delle difficoltà interne alla logica di Croce, e al suo concetto-cardine, la distinzione.