Search results for "Diol"

showing 10 items of 11756 documents

Missense PANK2 mutation without "eye of the tiger" sign: MR findings in a large group of patients with pantothenate kinase-associated neurodegenerati…

2011

Purpose: To present some unusual MR findings in a group of patients from the south-west of the Dominican Republic suffering from Pantothenate Kinase Associated Neurodegeneration (PKAN). Materials and Methods: Twenty patients and one preclinical case homozygous for the PANK2 mutation, 13 heterozygous gene carriers and 14 healthy volunteers were scanned prospectively using a 3 Tesla system. Results: All patients showed the typical signal reduction within the globus pallidus and the substantia nigra. A surprising finding was the absence of the bright spot (“tiger's eye”) in the medial part of the pallidum in 6 patients, but not in the preclinical case. Both fractional anisotropy (FA) and mean …

AdultMalePathologymedicine.medical_specialtyHeterozygoteInternal capsuleAdolescentMutation MissenseSubstantia nigraSensitivity and SpecificityPantothenate kinase-associated neurodegenerationWhite matterYoung AdultFractional anisotropymedicineMissense mutationHumansRadiology Nuclear Medicine and imagingGenetic Predisposition to DiseaseChildAgedPantothenate Kinase-Associated Neurodegenerationbusiness.industryBrainReproducibility of ResultsMiddle AgedPANK2medicine.diseaseMagnetic Resonance ImagingPhosphotransferases (Alcohol Group Acceptor)medicine.anatomical_structureGlobus pallidusnervous systemFemalebusinessJournal of magnetic resonance imaging : JMRI
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CT-guided intratumoral gene therapy in non-small-cell lung cancer.

1999

The objective of this study was to prove the principle of CT-guided gene therapy by intratumoral injection of a tumor suppressor gene as an alternative treatment approach of incurable non-small-cell lung cancer. In a prospective clinical phase I trial six patients with non-small-cell lung cancer and a mutation of the tumor suppressor gene p53 were treated by CT-guided intratumoral gene therapy. Ten milliliters of a vector solution (replication-defective adenovirus with complete wild-type p53 cDNA) were injected under CT guidance. In four cases the vector solution was completely applied to the tumor center, whereas in two cases 2 ml aliquots were injected into different tumor areas. For the …

AdultMalePathologymedicine.medical_specialtyLung NeoplasmsTumor suppressor geneAdolescentGenetic enhancementGenetic VectorsDNA RecombinantInjections IntralesionalPolymerase Chain ReactionAdenoviridaeCarcinoma Non-Small-Cell LungBiopsyCarcinomaMedicineHumansRadiology Nuclear Medicine and imagingProspective StudiesProspective cohort studyAdverse effectLung cancerAgedmedicine.diagnostic_testbusiness.industryGene Transfer TechniquesGeneral MedicineGenetic TherapyMiddle Agedmedicine.diseaseGenes p53Clinical trialTreatment OutcomeMutationFemalebusinessTomography X-Ray ComputedFollow-Up StudiesEuropean radiology
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Contrast-Enhanced Ultrasonography With SonoVue

2009

Objective. We investigated the ability of contrast-enhanced ultrasonography with SonoVue (Bracco SpA, Milan, Italy), a sulfur hexafluoride microbubble contrast agent, to reveal differences between benign and malignant focal splenic lesions. Methods. In a prospective study we investigated 35 lesions in 35 patients (24 male and 11 female; mean age ± SD, 54 ± 15 years) with focal splenic lesions detected by B-mode ultrasonography. After intravenous injection of 1.2 to 2.4 mL of SonoVue, the spleen was examined continuously for 3 minutes using low–mechanical index ultrasonography with contrastspecific software. The final diagnosis was established by histologic examination, computed tomography, …

AdultMalePathologymedicine.medical_specialtyLymphomaSulfur HexafluorideContrast MediaSensitivity and SpecificityMetastasisHemangiomaLesionHematomamedicineHumansRadiology Nuclear Medicine and imagingCystAbscessPhospholipidsUltrasonographyRadiological and Ultrasound Technologymedicine.diagnostic_testbusiness.industrySplenic NeoplasmsReproducibility of ResultsEchogenicityMagnetic resonance imagingImage Enhancementmedicine.diseaseFemalemedicine.symptombusinessJournal of Ultrasound in Medicine
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Multiple sclerosis: High prevalence of the ‘central vein’ sign in white matter lesions on susceptibility-weighted images

2018

Purpose The aim of this study was to determine the occurrence and distribution of the ‘central vein’ sign in white matter lesions on susceptibility-weighted magnetic resonance images in patients with multiple sclerosis (MS) and cerebral small vessel disease (CSVD). Materials and methods T2-weighted and fluid-attenuated inversion recovery magnetic resonance images of 19 MS patients and 19 patients affected by CSVD were analysed for the presence and localisation of focal hyperintense white matter lesions. Lesions were subdivided into periventricular or non-periventricular (juxtacortical, subcortical, deep white matter and cerebellar) distributed. The number and localisation of lesions present…

AdultMalePathologymedicine.medical_specialtyMultiple SclerosisVeins030218 nuclear medicine & medical imagingWhite matterYoung Adult03 medical and health sciences0302 clinical medicinePrevalencemedicineHumansRadiology Nuclear Medicine and imagingIn patientSWI MR SM Central vein sign susceptibility-weighted imaging multiple sclerosis cerebral small vessel disease magnetic resonance imagingVeinAgedRetrospective StudiesHigh prevalencemedicine.diagnostic_testbusiness.industryMultiple sclerosisBrainMagnetic resonance imagingGeneral MedicineMiddle AgedGeneral Neuroimagingmedicine.diseaseMagnetic Resonance ImagingWhite MatterHyperintensitySWI MR SMmedicine.anatomical_structureCerebral Small Vessel DiseasesSusceptibility weighted imagingFemaleNeurology (clinical)business030217 neurology & neurosurgery
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Transfusional Hemochromatosis: Quantitative Relation of MR Imaging Pituitary Signal Intensity Reduction to Hypogonadotropic Hypogonadism

2000

To assess the relationship between magnetic resonance (MR) imaging pituitary signal intensity reduction in patients with transfusional hemochromatosis and the clinical manifestation of hypogonadotropic hypogonadism.Pituitary MR imaging at 0.5 T was performed in 38 consecutive patients affected by secondary hemochromatosis and in 20 healthy volunteers. Serum ferritin levels were estimated in the affected population. Twenty (53%) of the 38 patients had hypogonadotropic hypogonadism diagnosed. Pituitary-to-fat signal intensity ratios were calculated from coronal gradient-echo (GRE) T2*-weighted MR images. The relationship between the quantitative reduction of the pituitary-to-fat signal intens…

AdultMalePathologymedicine.medical_specialtyPituitary glandAdolescentHemochromatosiPopulationSensitivity and SpecificityPituitary Gland AnteriorHypogonadotropic hypogonadismmedicineHumansBlood TransfusionRadiology Nuclear Medicine and imagingChildeducationHemochromatosisFerritineducation.field_of_studymedicine.diagnostic_testbusiness.industryHypogonadismbeta-ThalassemiaTransfusion ReactionBeta thalassemiaMagnetic resonance imagingmedicine.diseaseMagnetic Resonance Imagingmedicine.anatomical_structureROC CurveCoronal planeFerritinsFemaleHemochromatosisbusinessNuclear medicineHumanHormoneRadiology
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Basilar Artery Diameter Is a Potential Screening Tool for Fabry Disease in Young Stroke Patients

2010

<i>Background:</i> Fabry disease (FD) is a rare hereditary lysosomal storage disease that has been highlighted as a possible etiology of stroke at a young age. Enlarged basilar artery diameters (BADs) have been demonstrated in FD, and we hypothesize that they might be useful for the screening of FD in young stroke patients. The aim of this study was to compare BADs of young stroke patients without FD to those of FD patients and of healthy age-matched controls. <i>Methods:</i> BADs were measured using MR angiography in 3 age- and gender-matched groups: 25 FD patients (aged 36.5 ± 11.0 years), 26 non-FD stroke patients and 20 healthy controls. <i>Results:</i&g…

AdultMalePathologymedicine.medical_specialtyRisk AssessmentSensitivity and SpecificityPredictive Value of TestsRisk FactorsGermanymedicine.arteryInternal medicineLysosomal storage diseaseBasilar arteryHumansMass ScreeningMedicineStrokeRetrospective StudiesAnalysis of VarianceChi-Square Distributionmedicine.diagnostic_testbusiness.industryAge FactorsMagnetic resonance imagingRetrospective cohort studyMiddle Agedmedicine.diseaseMagnetic Resonance ImagingFabry diseaseCerebral AngiographyStrokeNeurologyBasilar ArteryCase-Control StudiesEtiologyCardiologyFabry DiseaseFemaleNeurology (clinical)Cardiology and Cardiovascular MedicinebusinessDilatation PathologicCerebral angiographyCerebrovascular Diseases
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Unusual MRI findings in an immunocompetent patient with EBV encephalitis: a case report.

2011

Abstract Blackground It is well-known that Epstein-Barr virus (EBV) can affect the central nervous system (CNS). Case presentation Herein the authors report unusual timely Magnetic Resonance Imaging (MRI) brain scan findings in an immunocompetent patient with EBV encephalitis. Diffusion weighted MRI sequence performed during the acute phase of the disease was normal, whereas the Fast Relaxation Fast Spin Echo T2 image showed diffuse signal intensity changes in white matter. The enhancement pattern suggested an inflammatory response restricted to the brain microcirculation. Acyclovir and corticosteroid therapy was administered. After three weeks, all signal intensities returned to normal and…

AdultMalePathologymedicine.medical_specialtySettore MED/07 - Microbiologia E Microbiologia ClinicaEpstein-Barr virus encephalitis MRI Diffusion-weighted imaginglcsh:Medical technologyMononucleosisSettore MED/17 - Malattie InfettiveencephalitisCentral nervous systemCase Reportmedicine.disease_causeWhite matterImmunocompromised HostNeuroimagingmedicineHumansEpstein-Barr virusRadiology Nuclear Medicine and imagingInfectious Mononucleosismedicine.diagnostic_testbusiness.industrySettore MED/37 - NeuroradiologiaMagnetic resonance imagingmedicine.diseaseEpstein–Barr virusMagnetic Resonance Imagingmedicine.anatomical_structurelcsh:R855-855.5Radiology Nuclear Medicine and imagingDiffusion-weighted imagingbusinessEncephalitisDiffusion MRIMRIBMC medical imaging
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Feasibility, reproducibility, and reliability for the T*2 iron evaluation at 3 T in comparison with 1.5 T

2012

This study aimed to determine the feasibility, reproducibility, and reliability of the multiecho T * 2 Magnetic resonance imaging technique at 3 T for myocardial and liver iron burden quantification and the relationship between T * 2 values at 3 and 1.5 T. Thirty-eight transfusion-dependent patients and 20 healthy subjects were studied. Cardiac segmental and global T * 2 values were calculated after developing a correction map to compensate the artifactual T * 2 variations. The hepatic T * 2 value was determined over a region of interest. The intraoperator and interoperator reproducibility for T * 2 measurements at 3 T was good. A linear relationship was found between patients' R (1000/T * …

AdultMalePathologymedicine.medical_specialtyheartliverSensitivity and SpecificityRegion of interestmedicineHumansT*2 magnetic resonanceLiver ironRadiology Nuclear Medicine and imaging3 Tiron overloadReliability (statistics)Observer VariationReproducibilitymedicine.diagnostic_testbusiness.industryHealthy subjectsReproducibility of ResultsMagnetic resonance imagingImage EnhancementMagnetic Resonance ImagingLinear relationshipThalassemiaFemalebusinessNuclear medicineObserver variationMagnetic Resonance in Medicine
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Appropriateness of upper-GI endoscopy: an Italian survey on behalf of the Italian Society of Digestive Endoscopy

2007

BACKGROUND AND OBJECTIVE: Open-access endoscopy allows physicians to directly schedule endoscopic procedures for their patients without prior consultation. An evaluation of both appropriateness and diagnostic yield of endoscopic procedures is critical when assessing the costs and benefits of endoscopy in an open-access setting. The aim of this Italian multicenter study was to assess the appropriate use of upper endoscopy (EGD) in an open-access system and to establish the yield of diagnostic information relevant to patient care. DESIGN AND SETTING: Cross-sectional, prospective, multicenter study. PATIENTS: A total of 6270 patients referred to 44 Italian centers for open-access EGD during 1 …

AdultMalePediatricsmedicine.medical_specialtyAdolescentCross-sectional studyDigestive System DiseasesSettore MED/12 - GASTROENTEROLOGIAMEDLINEPsychological interventionRegional Health PlanningDigestive endoscopymedicineHumansRadiology Nuclear Medicine and imagingEndoscopy Digestive SystemProspective StudiesProspective cohort studyChildAgedAged 80 and overmedicine.diagnostic_testbusiness.industryGeneral surgeryGastroenterologyMiddle AgedUpper GI endoscopyEndoscopyCross-Sectional StudiesMulticenter studyHealth Care SurveysPractice Guidelines as TopicFemalebusiness
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Circulating 25-Hydroxyvitamin D3 in Pregnancy and Infant Neuropsychological Development

2012

OBJECTIVE:To investigate whether circulating 25-hydroxyvitamin D3 [25(OH)D3] concentration in pregnancy is associated with neuropsychological development in infants.METHODS:The Spanish population-based cohort study INfancia y Medio Ambiente Project recruited pregnant women during the first trimester of pregnancy between November 2003 and February 2008. Completed data on 1820 mother-infant pairs were used. Maternal plasma 25(OH)D3 concentration was measured by high-performance liquid chromatography in pregnancy (mean 13.5±2.1 weeks of gestation). Offspring mental and psychomotor scores were assessed by trained psychologists at age 14 months (range, 11–23) by using the Bayley Scales of Infant…

AdultMalePediatricsmedicine.medical_specialtyAdolescentOffspringNeuropsychological TestsBayley Scales of Infant Developmentvitamin D deficiencyCohort StudiesYoung AdultChild DevelopmentPregnancyInterquartile rangemedicineVitamin D and neurologyHumansProspective StudiesPrenatal Nutritional Physiological PhenomenaChromatography High Pressure LiquidCalcifediolPsychomotor learningPregnancybusiness.industryObstetricsInfantVitamin D Deficiencymedicine.diseasePregnancy ComplicationsPrenatal Exposure Delayed EffectsMultivariate AnalysisPediatrics Perinatology and Child HealthLinear ModelsGestationFemalebusinessBiomarkersPsychomotor PerformancePediatrics
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