Search results for "ESA"

showing 10 items of 11914 documents

Incomplete Timothy syndrome secondary to a mosaic mutation of the CACNA1C gene diagnosed using next-generation sequencing.

2016

Autosomal dominant genetic diseases can occur de novo and in the form of somatic mosaicism, which can give rise to a less severe phenotype, and make diagnosis more difficult given the sensitivity limits of the methods used. We report the case of female child with a history of surgery for syndactyly of the hands and feet, who was admitted at 6 years of age to a pediatric intensive care unit following cardiac arrest. The electrocardiogram (ECG) showed a long QT interval that on occasions reached 500 ms. Despite the absence of facial dysmorphism and the presence of normal psychomotor development, a diagnosis of Timothy syndrome was made given the association of syndactyly and the ECG features.…

0301 basic medicineCalcium Channels L-TypeLong QT syndromeDNA Mutational AnalysisTimothy syndrome030204 cardiovascular system & hematologyBioinformaticsDNA sequencing03 medical and health sciencessymbols.namesakeElectrocardiography0302 clinical medicineGeneticsmedicineMissense mutationHumansSyndactylyAutistic DisorderChildCodonGenetics (clinical)AllelesGenetic Association StudiesSanger sequencingbiologyMosaicismKCNE2High-Throughput Nucleotide Sequencingmedicine.diseaseLong QT Syndrome030104 developmental biologyPhenotypeAmino Acid SubstitutionMutation (genetic algorithm)Mutationsymbolsbiology.proteinFemaleSyndactylyAmerican journal of medical genetics. Part A
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Thymic Hyperplasia with Lymphoepithelial Sialadenitis (LESA)-Like Features: Strong Association with Lymphomas and Non-Myasthenic Autoimmune Diseases.

2021

Thymic hyperplasia (TH) with lymphoepithelial sialadenitis (LESA)-like features (LESA-like TH) has been described as a tumor-like, benign proliferation of thymic epithelial cells and lymphoid follicles. We aimed to determine the frequency of lymphoma and autoimmunity in LESA-like TH and performed retrospective analysis of cases with LESA-like TH and/or thymic MALT-lymphoma. Among 36 patients (21 males) with LESA-like TH (age 52 years, 32&ndash

0301 basic medicineCancer ResearchPathologymedicine.medical_specialtyPure red cell aplasia610 Medicine & healthautoimmune diseaselymphomathymitismedicine.disease_causelcsh:RC254-282SclerodermaArticleAutoimmunitysurgery03 medical and health sciences0302 clinical medicinethymusimmune system diseaseshemic and lymphatic diseasesmedicineddc:610Autoimmune diseasebusiness.industryLESAimagingHyperplasialcsh:Neoplasms. Tumors. Oncology. Including cancer and carcinogensmedicine.diseaseLESA; autoimmune disease; imaging; lymphoma; myasthenia; pathology; surgery; thymic epithelial tumor; thymitis; thymusSialadenitisMyasthenia gravis3. Good healthLymphomamyasthenia030104 developmental biologyOncologythymic epithelial tumor030220 oncology & carcinogenesis570 Life sciences; biologypathologybusiness
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Betulinic acid induces a novel cell death pathway that depends on cardiolipin modification

2016

Cancer is associated with strong changes in lipid metabolism. For instance, normal cells take up fatty acids (FAs) from the circulation, while tumour cells generate their own and become dependent on de novo FA synthesis, which could provide a vulnerability to target tumour cells. Betulinic acid (BetA) is a natural compound that selectively kills tumour cells through an ill-defined mechanism that is independent of BAX and BAK, but depends on mitochondrial permeability transition-pore opening. Here we unravel this pathway and show that BetA inhibits the activity of steroyl-CoA-desaturase (SCD-1). This enzyme is overexpressed in tumour cells and critically important for cells that utilize de n…

0301 basic medicineCancer ResearchProgrammed cell deathCardiolipinsMitochondrionCell Line03 medical and health scienceschemistry.chemical_compoundSDG 3 - Good Health and Well-beingBetulinic acidGeneticsCardiolipinHumansBetulinic AcidCytotoxicityMolecular BiologyCell DeathbiologyCytochrome cFatty AcidsCytochromes cLipid metabolismAntineoplastic Agents PhytogenicTriterpenesMitochondriaCell biology030104 developmental biologyBiochemistrychemistryCancer cellbiology.protein/dk/atira/pure/sustainabledevelopmentgoals/good_health_and_well_beingPentacyclic TriterpenesStearoyl-CoA Desaturase
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Collective Infection of Cells by Viral Aggregates Promotes Early Viral Proliferation and Reveals a Cellular-Level Allee Effect

2018

In addition to the conventional release of free, individual virions, virus dispersal can involve multi-virion assemblies that collectively infect cells. However, the implications of collective infection for viral fitness remain largely unexplored. Using vesicular stomatitis virus, here, we compare the fitness of free versus saliva-aggregated viral particles. We find that aggregation has a positive effect on early progeny production, conferring a fitness advantage relative to equal numbers of free particles in most cell types. The advantage of aggregation resides, at least partially, in increasing the cellular multiplicity of infection. In mouse embryonic fibroblasts, the per capita, short-t…

0301 basic medicineCell typevirusesCellBiologyVirus ReplicationArticleGeneral Biochemistry Genetics and Molecular BiologyVirusMice03 medical and health sciencessymbols.namesakeMultiplicity of infectionChlorocebus aethiopsmedicineAnimalsHumansSelection GeneticSalivaVero CellsAllee effectInnate immune systemVesiculovirusbiology.organism_classificationEmbryonic stem cellCell biologyMice Inbred C57BL030104 developmental biologymedicine.anatomical_structureA549 CellsVesicular stomatitis virussymbolsFemaleGeneral Agricultural and Biological SciencesCurrent Biology
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Disparate miRNA expression in serum and plasma of patients with acute myocardial infarction: a systematic and paired comparative analysis

2020

AbstractDespite the promising value of miRNAs in the diagnostic and prognostic of cardiovascular disease (CVD), recent meta-analyses did not support their potential. Methodological variances in studies may interfere with miRNA profile and affect their results. This study determines if the blood starting material is a source of variance in miRNA profile by performing a paired comparison in plasma and serum of the expression of primary miRNAs associated with CVD. Circulating miRNA yield was similar in both plasma and serum, although a significant increase was observed in patients with Non-ST-elevation myocardial infarction (NSTEMI) compared to control volunteers. When normalized by the expres…

0301 basic medicineCirculating mirnasMaleMicro RNAsMyocardial InfarctionOld agelcsh:MedicineGene Expression030204 cardiovascular system & hematologyBlood plasmaPlasma0302 clinical medicineMyocardial infarctionlcsh:ScienceNon-ST Elevated Myocardial InfarctionMultidisciplinaryMiddle AgedPrognosisVellesamiRNAsFemalemedicine.medical_specialtyPaired comparisonFisiologiaPredictive markersArticle03 medical and health sciencesMirna expressionInternal medicinemicroRNAmedicineHumansIn patientCorCirculating MicroRNAAgedbusiness.industrylcsh:RPlasma sanguinimedicine.diseaseInfart de miocardiMicroRNAsMyocardial infarction030104 developmental biologyEndocrinologyROC Curvelcsh:QbusinessTranscriptomeBiomarkers
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Comparison between adenosine triphosphate bioluminescence and aerobic colony count to assess surface sanitation in the hospital environment

2022

Background: Adenosine triphosphate bioluminescence produced by the firefly luciferase has been successfullyintroduced to verify cleaning procedures in the food industry according to the Hazard Analysis Critical Control Pointprogram.Our aim was to evaluate the reliability of bioluminescence as a tool to monitor the effectiveness of sanitation in healthcaresettings, in comparison with the microbiological gold standard.Methods: 614 surfaces of various material were randomly sampled in Policlinico University Hospital units in Palermo,Italy, to detect adenosine triphosphate bioluminescence and aerobic colony count. Linear regression model andPearson correlation coefficient were used to estimate …

0301 basic medicineColony-forming unitVeterinary medicinebusiness.industry030106 microbiologyGold standard (test)Cleaning monitoringPearson product-moment correlation coefficientSurfaces03 medical and health sciencessymbols.namesakechemistry.chemical_compoundsanitation; hospital hygiene; bioluminescencechemistryInterquartile rangeLinear regressionsymbolsColony countBioluminescenceMedicineBioluminescenceSanitationbusinessAdenosine triphosphate
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Differential binding cell-SELEX method to identify cell-specific aptamers using high-throughput sequencing

2018

AbstractAptamers have in recent years emerged as a viable alternative to antibodies. High-throughput sequencing (HTS) has revolutionized aptamer research by increasing the number of reads from a few (using Sanger sequencing) to millions (using an HTS approach). Despite the availability and advantages of HTS compared to Sanger sequencing, there are only 50 aptamer HTS sequencing samples available on public databases. HTS data in aptamer research are primarily used to compare sequence enrichment between subsequent selection cycles. This approach does not take full advantage of HTS because the enrichment of sequences during selection can be due to inefficient negative selection when using live…

0301 basic medicineComputer scienceAptamerlcsh:MedicineGenomicsComputational biologyCell selexLigandsArticleDNA sequencingCell Line03 medical and health sciencessymbols.namesakeNegative selectionDrug Delivery Systems0302 clinical medicineCell Line TumorHumansGenomic librarylcsh:ScienceCarcinoma Renal CellSelection (genetic algorithm)Gene LibrarySanger sequencingMultidisciplinaryMolecular medicinelcsh:RSELEX Aptamer TechniqueHigh-throughput screeningComputational BiologyHigh-Throughput Nucleotide SequencingNucleotide MetabolismGenomicsAptamers NucleotideFlow CytometryMolecular medicineKidney Neoplasms030104 developmental biologyDrug DesignDrug deliverysymbolsNucleic Acid Conformationlcsh:QFunctional genomics030217 neurology & neurosurgerySystematic evolution of ligands by exponential enrichment
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Automatic detection of hemangiomas using unsupervised segmentation of regions of interest

2016

In this paper we compare the performances of three automatic methods of identifying hemangioma regions in images: 1) unsupervised segmentation using the Otsu method, 2) Fuzzy C-means clustering (FCM) and 3) an improved region growing algorithm based on FCM (RG-FCM). For each image, the starting point of the algorithms is a rectangular region of interest (ROI) containing the hemangioma. For computing the performances of each method, the ROIs had been manually labeled in 2 classes: pixels of hemangioma and pixels of non-hemangioma. The computed scores are given separately for each image, as well as global performances across all ROIs for both classes. The best classification of non-hemangioma…

0301 basic medicineComputer scienceScale-space segmentation02 engineering and technologyOtsu's methodHemangioma03 medical and health sciencessymbols.namesakeMinimum spanning tree-based segmentationRegion of interestHistogram0202 electrical engineering electronic engineering information engineeringmedicineComputer visionSegmentation-based object categorizationbusiness.industryPattern recognitionImage segmentationmedicine.diseaseStatistical classification030104 developmental biologyRegion growingsymbols020201 artificial intelligence & image processingArtificial intelligencebusiness2016 International Conference on Communications (COMM)
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Correlation between micro-hardness and mineral content in healthy human enamel

2016

Background Enamel is the hardest and the stiffest tissue in the human body. The enamel undergoes multidirectional stresses, withstands multimillion chewing cycles, all while protecting the internal dentin and pulp from damage due to mechanical overload and exposure to the harsh chemical environment of the mouth. Raman spectroscopy allows to study enamel mineral content in a non-destructive and site-specific way. While Raman spectroscopy has been applied in other studies to assess tooth mineralization, there are no studies that examine the relationship between micro-hardness and mineral content of the untreated enamel. An understanding of this relationship is extremely important in a clinica…

0301 basic medicineDentistryIndentation hardness03 medical and health sciencessymbols.namesake0302 clinical medicineBrinell scaleIncisorstomatognathic systemBiomaterials and Bioengineering in DentistryDentinmedicineGeneral DentistryEnamel paintbusiness.industryChemistryResearch030206 dentistry:CIENCIAS MÉDICAS [UNESCO]stomatognathic diseases030104 developmental biologymedicine.anatomical_structurevisual_artUNESCO::CIENCIAS MÉDICASvisual_art.visual_art_mediumsymbolsPulp (tooth)Raman microscopebusinessRaman spectroscopy
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On the minimal number of singular fibers with non-compact Jacobians for families of curves over P1

2016

Abstract Let f : X → P 1 be a non-isotrivial family of semi-stable curves of genus g ≥ 1 defined over an algebraically closed field k. Denote by s nc the number of the singular fibers whose Jacobians are non-compact. We prove that s nc ≥ 5 if k = C and g ≥ 5 ; we also prove that s nc ≥ 4 if char ( k ) > 0 and the relative Jacobian of f is non-smooth.

0301 basic medicineDiscrete mathematicsPure mathematicsApplied MathematicsGeneral Mathematics010102 general mathematics01 natural sciences03 medical and health sciencessymbols.namesakeMathematics::Algebraic Geometry030104 developmental biologyGenus (mathematics)Jacobian matrix and determinantFamily of curvessymbols0101 mathematicsAlgebraically closed fieldMathematicsJournal de Mathématiques Pures et Appliquées
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