Search results for "EXPRESSION"

showing 10 items of 5168 documents

PIK3R1 Mutations Cause Syndromic Insulin Resistance with Lipoatrophy

2013

International audience; Short stature, hyperextensibility of joints and/or inguinal hernia, ocular depression, Rieger anomaly, and teething delay (SHORT) syndrome is a developmental disorder with an unknown genetic cause and hallmarks that include insulin resistance and lack of subcutaneous fat. We ascertained two unrelated individuals with SHORT syndrome, hypothesized that the observed phenotype was most likely due to de novo mutations in the same gene, and performed whole-exome sequencing in the two probands and their unaffected parents. We then confirmed our initial observations in four other subjects with SHORT syndrome from three families, as well as 14 unrelated subjects presenting wi…

ProbandEXPRESSIONmedicine.medical_specialty030209 endocrinology & metabolismBiologymedicine.disease_causeMICE LACKINGShort stature03 medical and health sciencesHYPOGLYCEMIA0302 clinical medicineInsulin resistancePIK3R1Internal medicineReportmedicineGeneticsKINASEGenetics(clinical)LipoatrophyGenetics (clinical)030304 developmental biology0303 health sciencesMutationAKT2[SDV.GEN]Life Sciences [q-bio]/GeneticsRECEPTORmedicine.disease3-KINASE3. Good healthInsulin receptorEndocrinologyAUTOPHOSPHORYLATIONSHORT syndromebiology.proteinSKELETAL-MUSCLEGROWTHmedicine.symptom[ SDV.GEN ] Life Sciences [q-bio]/Genetics
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Inheritance and variable expression in Rubinstein-Taybi syndrome.

2010

Familial Rubinstein-Taybi syndrome (RTS) is very rare. Here we report on the 6th and 7th case of inherited RTS. Family 1 presents with incomplete or mild RTS over three generations; a 13-year-old girl (proband 1) with mild but typical facial features and learning disabilities, her very mildly affected mother (proband 2), and the maternal grandmother (proband 3). Family 2 includes three females with classical RTS (probands 4-6) and their father (proband 7) with broad thumbs and halluces. Proband 5 also had a brain tumor (ganglioglioma) at the age of 3 years. In probands 1-3, direct sequencing identified a novel CREBBP missense mutation, c.2728A > G (predicting p.Thr910Ala), that was absent i…

ProbandMaleRiskAdolescentDNA Mutational AnalysisMutation MissenseBiologyVariable ExpressionGenetic HeterogeneityGeneticsmedicineMissense mutationHumansPoint MutationFamilyAlleleGenetics (clinical)GeneticsRubinstein-Taybi SyndromeRubinstein–Taybi syndromeGenetic heterogeneityMosaicismPoint mutationmedicine.diseaseCREB-Binding ProteinPedigreePhenotypeChild PreschoolMutation (genetic algorithm)FemaleAmerican journal of medical genetics. Part A
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Quantum Query Algorithms for Conjunctions

2010

Every Boolean function can be presented as a logical formula in conjunctive normal form. Fast algorithm for conjunction plays significant role in overall algorithm for computing arbitrary Boolean function. First, we present a quantum query algorithm for conjunction of two bits. Our algorithm uses one quantum query and correct result is obtained with a probability p = 4/5, that improves the previous result. Then, we present the main result - generalization of our approach to design efficient quantum algorithms for computing conjunction of two Boolean functions. Finally, we demonstrate another kind of an algorithm for conjunction of two bits, that has a correct answer probability p = 9/10. Th…

Product termTheoretical computer scienceParity functionAnd-inverter graphMaximum satisfiability problemQuantum phase estimation algorithmBoolean expressionQuantum algorithmBoolean functionAlgorithmMathematics
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Production of Antibacterial Compounds from Actinomycetes

2016

Actinomycetes are soil-dwelling Gram-positive bacteria, industrially relevant as producers of a wide range of bioactive secondary metabolites, including many antibiotics of clinical and commercial importance.The understanding of actinomycete biology has been based on extensive studies on the model organism Streptomyces coelicolor over many years and on the availability of its complete genome sequence. This bacterium has an unusual complex developmental cycle that includes programmed cell death phenomena that make this bacterium a multicellular prokaryotic model.Morphological differentiation in S. coelicolor is strictly related to physiological differentiation: indeed the onset of morphologi…

Production (economics)Food scienceBiologySettore BIO/19 - Microbiologia GeneraleAntibiotic production Actinomycetes genetic engineering regulation heterologous expression
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COX-2-dependent and COX-2-independent mode of action of celecoxib in human liver cancer cells.

2011

Celecoxib (Celebrex((R)), Pfizer) is a selective cyclooxygenase-2 (COX-2) inhibitor with chemopreventive and antitumor effects. However, it is now well known that celecoxib has several COX-2-independent activities. To better understand COX-2-independent molecular mechanisms underlying the antitumor activity of celecoxib, we investigated the expression profile of the celecoxib-treated COX-2-positive (Huh7) and COX-2-negative (HepG2) liver cancer cell lines, using microarray analysis. Celecoxib treatment resulted in significantly altered expression levels of 240 and 403 transcripts in Huh7 and HepG2 cells, respectively. Confirmation of the microarray results was performed for selected genes b…

Programmed cell deathCarcinoma HepatocellularMicroarrayTranscription GeneticHepatocellular carcinomaCell SurvivalAntineoplastic AgentsPharmacologyBiologyBiochemistryCell Line TumorGeneticsmedicineHumansMode of actionneoplasmsMolecular BiologySulfonamidesCyclooxygenase 2 InhibitorsCell growthMicroarray analysis techniquesGene Expression ProfilingLiver NeoplasmsCOX-2Gene expression profilingGene Expression Regulation NeoplasticCell cultureCelecoxibCyclooxygenase 2CelecoxibMolecular MedicinePyrazolesBiotechnologymedicine.drugSignal TransductionOmics : a journal of integrative biology
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Molecular mechanisms of rosmarinic acid from Salvia miltiorrhiza in acute lymphoblastic leukemia cells

2015

Abstract Ethnopharmacological relevance Rosmarinic acid (RA), a major hydrosoluble bioactive compound found in the Chinese medicinal herb, Salvia miltiorrhiza Bunge, which has been used in traditional Chinese medicine to treat various diseases, including cancer. However, the mechanisms have not been fully elucidated. Aim of the study Guided by microarray hybridization and Ingenuity Pathway Analysis, we identified modes of action of rosmarinic acid (RA) isolated from S. miltiorrhiza on acute lymphoblastic leukemia cells. Materials and methods Microarray data were verified by independent methods: Real-time RT-PCR (mRNA expression), resazurin assay (cytotoxicity of RA towards parental CCRF-CEM…

Programmed cell deathCell SurvivalDNA damageNecroptosisCellAntineoplastic AgentsApoptosisSalvia miltiorrhizaPharmacologyCell morphologyDepsidesSalvia miltiorrhizaCell Line TumorDrug DiscoveryCell AdhesionmedicineHumansLymphocytesCells CulturedMembrane Potential MitochondrialPharmacologybusiness.industryGene Expression ProfilingCell CycleNF-kappa BPrecursor Cell Lymphoblastic Leukemia-LymphomaCell cycleMolecular biologyDrug Resistance MultipleMolecular Docking Simulationmedicine.anatomical_structureCinnamatesDrug Resistance NeoplasmApoptosisComet AssayReactive Oxygen SpeciesbusinessDNA DamageJournal of Ethnopharmacology
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Chemically modified tetracyclines induce cytotoxic effects against J774 tumour cell line by activating the apoptotic pathway

2003

Here, we have studied the effects of chemically modified tetracyclines (CMTs) on apoptosis both at the level of the cytoplasmic proteolytic caspase cascade, and on Bcl-2 and c-myc mRNA expression in the J774 macrophage cell line. The results indicate that CMTs induce morphological changes consistent with apoptotic events, as clearly demonstrated both by the acridine orange and ethidium bromide staining, and by TUNEL and fragmentation ELISA assays. Furthermore, the analysis of the cell cycle by flow cytometry shows an evident apoptotic sub-G0G1 peak, without important modifications in the cell cycle distribution. CMTs induce programmed cell death (PCD) in a dose-dependent manner and CMT-8 is…

Programmed cell deathCell SurvivalImmunologyApoptosisProto-Oncogene Proteins c-mycMicechemistry.chemical_compoundTumor Cells CulturedAnimalsImmunology and AllergyRNA MessengerFragmentation (cell biology)CaspasePharmacologyTUNEL assayDose-Response Relationship DrugbiologyAcridine orangeTetracyclineCell cycleMolecular biologyGene Expression Regulation NeoplasticProto-Oncogene Proteins c-bcl-2chemistryTetracyclinesApoptosisCaspasesMacrophages Peritonealbiology.proteinFemaleSignal transductionInternational Immunopharmacology
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Short-term exposure to cadmium affects the expression of stress response and apoptosis-related genes in immortalized epithelial cells from the human …

2009

Abstract It is known that cadmium (Cd) evokes cell responses that not only involve protective reactions against toxicity but also induces cell death. Increasing interest has been recently focused on the elucidation of the cellular and molecular aspects of Cd-dependent regulation of gene expression in different model systems. Here, we examined the effects of short-term (24 h) exposure of immortalized non-tumoral HB2 cells from human breast epithelium to CdCl2 at 50 μM concentration, corresponding to the IC50 for this time of incubation. The possible occurrence of apoptosis-related events was evaluated via analysis of the physical state of the DNA and of the membrane localization of phosphaty…

Programmed cell deathCellApoptosisPhosphatidylserinesBiologyToxicologyCell LineInhibitory Concentration 50Heat shock proteinGene expressionmedicineHumansSettore BIO/06 - Anatomia Comparata E CitologiaGeneRegulation of gene expressionCell DeathCell MembraneEpithelial CellsDNAGeneral MedicineCell biologyGene Expression Regulation Neoplasticmedicine.anatomical_structurecadmium gene expression apoptosis stress response epithelial cellsCell cultureApoptosisFemaleCadmiumToxicology in Vitro
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Ischemic Preconditioning: Postischemic Structural Changes in the Brain

2008

Ischemic brain damage can be prevented or at least significantly reduced when there is a preceding brief ischemic period that does not exceed the threshold for tissue damage--a phenomenon termed "ischemic preconditioning" (ischemic PC). Experimental PC in rodents is now considered to be a model for transient ischemic attacks in humans, and there is increasing hope for translating the knowledge of underlying mechanisms in the animal models into the clinic to enhance endogenous neuroprotective mechanisms in patients with stroke. However, although PC was originally defined as a subtoxic stimulus without any morphologic damage, there is a growing body of evidence from studies using sensitive te…

Programmed cell deathCentral nervous systemIschemiaStimulus (physiology)NeuroprotectionPathology and Forensic MedicineBrain ischemiaCellular and Molecular NeuroscienceIschemiamedicineAnimalsHumansIschemic PreconditioningStrokebusiness.industryBrainGeneral Medicinemedicine.diseaseReceptors NeurotransmitterDisease Models Animalmedicine.anatomical_structureGene Expression RegulationNeurologyIschemic preconditioningNeurology (clinical)businessNeuroscienceJournal of Neuropathology & Experimental Neurology
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Novel ways to sensitise gastrointestinal cancer to apoptosis.

2009

Gastrointestinal (GI) cancers are major health problems, being the most common cancers worldwide. Resistance to apoptosis is closely linked to carcinogenesis and enables malignant cells to evade therapy-induced cell death. In the recent past, the increasing understanding of molecular pathways of apoptosis has provided novel targets in cancer therapy. Several drugs, either inhibiting antiapoptotic signalling or actively inducing apoptosis in cancer cells, have already entered clinical trials. Until now, agents targeting apoptosis pathways are primarily being tested alone or in combination with chemotherapy. In the near future, personalized combination therapies will probably be beneficial fo…

Programmed cell deathChemotherapybusiness.industrymedicine.medical_treatmentGastroenterologyCancerApoptosismedicine.disease_causemedicine.diseaseClinical trialGene Expression Regulation NeoplasticTNF-Related Apoptosis-Inducing LigandApoptosisCancer cellImmunologyCancer researchMedicineHumansGastrointestinal cancerbusinessCarcinogenesisGastrointestinal NeoplasmsSignal TransductionGut
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