Search results for "Factor D"

showing 10 items of 48 documents

Complement activation and innate immunity

2007

Classical complement pathwayInnate immune systemComplement component 3ImmunologyAlternative complement pathwaybiology.proteinImmunology and AllergyFactor DHematologyComplement receptorBiologyComplement systemCell biologyImmunobiology
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Efficacy and safety of cyclic pyranopterin monophosphate substitution in severe molybdenum cofactor deficiency type A: a prospective cohort study.

2015

Summary Background Molybdenum cofactor deficiency (MoCD) is characterised by early, rapidly progressive postnatal encephalopathy and intractable seizures, leading to severe disability and early death. Previous treatment attempts have been unsuccessful. After a pioneering single treatment we now report the outcome of the complete first cohort of patients receiving substitution treatment with cyclic pyranopterin monophosphate (cPMP), a biosynthetic precursor of the cofactor. Methods In this observational prospective cohort study, newborn babies with clinical and biochemical evidence of MoCD were admitted to a compassionate-use programme at the request of their treating physicians. Intravenous…

Compassionate Use TrialsMalePediatricsmedicine.medical_specialtyGENOMIC STRUCTUREFEATURESEncephalopathyMolybdopterin synthaseCyclic pyranopterin monophosphateDrug Administration ScheduleCohort Studieschemistry.chemical_compoundOrganophosphorus CompoundsmedicineURINEHumansBIOSYNTHESISProspective cohort studyAdverse effectMolybdenum cofactor deficiencyPRECURSORMetal Metabolism Inborn ErrorsMetal metabolismbusiness.industryMUTATIONSInfant NewbornGENES MOCS1CPMPMOLYBDOPTERIN SYNTHASEGeneral Medicinemedicine.diseasePterinsTreatment OutcomechemistryFemalebusinessCohort studyLancet (London, England)
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Relationship and correspondence between different impact indicators in a sample of articles of excellence

2016

The objective was to compare the impact factor to 2 years of self-citations (IF2Y) with impact factor 2 years without self-citations (IF2YWS) and IF2Y with the impact factor to 5 years (IF5Y) as well as IF2YWS with SCImago Journal Rank (SJR) about journals where they were published articles of excellence in smoking by Spanish authors in the period 2008-2012. The search was conducted in the SCI-E and the SSCI-E on November 25, 2013. Were selected documents that had the h index of the strategy global sample (number of articles that have at least that number of citations) to search using the descriptors "smok ∗" OR "tobac ∗". A total of 69 articles by Spanish authors were recovered from 55 jou…

ConcordanciaImpact factorbiologyMedicinaConcordancelcsh:Information resources (General)SmokingCorrelaciónLibrary and Information Sciencesbiology.organism_classificationFactor de impactoTabaquismoCorrelationScImago journal rank indicatorScimago Journal Rank050 - Publicaciones seriadasSCImago Journal RankSmokConcordanceImpact factorHumanitiesMathematicslcsh:ZA3040-5185
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La responsabilidad Social Empresarial: un valor intangible y factor determinante de competitividad en las PYMES

2016

Corporate social responsabilityIntangible Value Regulation 34 67Regulaciónun valor intangible y factor determinante de competitividad en las PYMES Ballester Martínez [1696-1676 2341 Quaderns de ciències socials 520540 2016 34 6967487 La responsabilidad Social Empresarial]1696-1676 2341 Quaderns de ciències socials 520540 2016 34 6967487 La responsabilidad Social Empresarial: un valor intangible y factor determinante de competitividad en las PYMES Ballester MartínezPere Responsabilidad social empresarialVoluntariedadValor intangibleCompetitividadVoluntarinessCompetitiveness
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Robust dynamic comfort modeling for motorcycle riding

2015

Comfort modeling is considered a prerequisite in motorcycle design, primarily to address safety concerns and to position the product on the market. However, a comprehensive methodology for comfort modeling during the earliest development phases of a motorcycle model is still missing. Anthropometrical variation is the main noise factor to consider in comfort modeling in relation to the unavoidable variability of body segments. However, comfort is a subjective concept influencing riders' choice of motorcycle model. This work is a generalization of the robust ergonomic design methodology aimed at designing products whose ergonomic performance is insensitive to anthropometrical variation. This …

ErgonomicHuman modelingMan-machine interactionSettore SECS-S/02 - Statistica Per La Ricerca Sperimentale E TecnologicaMixture noise factor distributionRobust designMotorcycle designComfort assessmentHuman Factors and ErgonomicSettore ING-IND/16 - Tecnologie E Sistemi Di LavorazioneDigital mock-upIndustrial and Manufacturing Engineering
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Robust dynamic comfort modelling for motorcycle riding

2015

Comfort modeling is considered a prerequisite in motorcycle design, primarily to address safety concerns and to position the product on themarket. However, a comprehensive methodology for comfort modeling during the earliest development phases of a motorcycle model is still missing. Anthropometrical variation is the main noise factor to consider in comfort modeling in relation to the unavoidable variability of body segments. However, comfort is a subjective concept influencing riders’ choice of motorcycle model. This work is a generalization of the robust ergonomic design methodology aimed at designing products whose ergonomic performance is insensitive to anthropometrical variation. This w…

ErgonomicMan–machine interactionHuman modelingSettore SECS-S/02 - Statistica Per La Ricerca Sperimentale E TecnologicaRobust designMixture noise factor distributionMotorcycle designComfort assessmentDigital mock-up
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Can we compare haemophilia carriers with clotting factor deficiency to male patients with mild haemophilia?

2020

Introduction Certain haemophilia carriers demonstrate an increased bleeding tendency, mainly related to clotting factor deficiency. No study has so far formally compared the bleeding phenotype of women and girls with mild FVIII or FIX deficiency and associated management with that of male patients affected by mild haemophilia A and B. Material and methods We retrospectively evaluated 44 women and girls with mild FVIII or FIX deficiency (FVIII or FIX 0.05-0.5 IU/mL) and 77 male patients with mild haemophilia A or B and compared them with respect to clotting factor level, age at and trigger for diagnosis, as well as treatment modalities. Results After excluding gender-related haemorrhagic sym…

FVIIImild haemophiliaAdultMalePediatricsmedicine.medical_specialtycongenital hereditary and neonatal diseases and abnormalitiesHeterozygoteAdolescentMucocutaneous zonecarriersPlasma factorAge at diagnosis030204 cardiovascular system & hematologyHaemophiliaHemophilia AHemostatics03 medical and health sciencesYoung Adult0302 clinical medicinecarrierhemic and lymphatic diseasesmedicineHumansDeamino Arginine VasopressinClotting factor deficiencyChildGenetics (clinical)AgedClotting factorAged 80 and overbusiness.industryFIXHematologyGeneral MedicineMiddle Agedmedicine.diseaseBlood Coagulation Factorsbleeding phenotypebleeding phenotype carriers FIX FVIII mild haemophiliaMale patientChild PreschoolMild haemophilia AFemalebusiness030215 immunologyHaemophilia : the official journal of the World Federation of HemophiliaREFERENCES
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What are the risk and protective factors for the well-being of adolescents with CF?

2021

La fibrosis quística (FQ) es una enfermedad crónica y hereditaria que compromete la vida de quienes la padecen, y se hace especialmente importante su impacto en la adolescencia. El afrontamiento que estos pacientes y sus familiares hagan de estas circunstancias que les han tocado vivir, puede mejorar o empeorar el curso y desenlace de la enfermedad. El objetivo es conocer los factores de riesgo y protectores que influyen en el bienestar de los adolescentes con FQ. Para ello se realizó una búsqueda bibliográfica de la literatura científica siguiendo la guía PRISMA en las siguientes bases de datos: Web of Science, ProQuest y Scopus. Se incluyeron artículos centrados en factores psicológicos d…

Factor de riesgoWeb of scienceSalud mentaladolescenteExperimental and Cognitive PsychologyPeer relationshipsFactores psicológicosSalud mentalDevelopmental and Educational PsychologyApoyo socialFilosofía y psicologíaAdolescentesEvaluaciónFibrosis quísticaPsychiatry and Mental healthClinical Psychologyajuste psicológicoPsicologiaPediatrics Perinatology and Child HealthBibliographic searchInherited diseasePersonalitatPsychologyHumanitiesBienestarFactor de protección
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Blefaritis asociada al tratamiento con Cetuximab en adenocarcinoma colorrectal avanzado

2008

espanolCaso clinico: Mujer de 52 anos diagnosticada de adenocarcinoma colorrectal, remitida a nuestro servicio por presentar tras iniciar tratamiento con Cetuximab reaccion adversa palpebral. Discusion: El Cetuximab es un anticuerpo monoclonal cuya diana es el receptor del factor de crecimiento epidermico. Ha sido incorporado recientemente al tratamiento de tumores, principalmente el cancer colorrectal metastatico y los tumores del area otorrinolaringologica. Su tolerancia es en principio mejor que la de los agentes quimioterapicos clasicos. Sin embargo, no esta exento de efectos secundarios. La toxicidad palpebral asociada a Cetuximab ha sido recientemente descrita, por lo que la patogenia…

Gynecologymedicine.medical_specialtyEpidermal growth factor receptor activityCetuximabbusiness.industryreceptor del factor de crecimiento epidérmicoCancermedicine.diseasedigestive system diseasesSurgeryAdvanced colorectal cancerOphthalmologyblefaritisMedicineAdenocarcinomaanticuerpos monoclonalesbusinessneoplasmsAdenocarcinoma colorrectalmedicine.drugArchivos de la Sociedad Española de Oftalmología
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Literatura científica de autores españoles sobre análisis de citas y factor de impacto en Biomedicina (1981-2005)

2008

This paper analyses the development of Spanish research literature in the field of citation analysis and impact factor (IF) in biomedicine over the period 1981-2005. Bibliometric methods and social network analysis were used to examine papers indexed in the Science Citation Index-Expanded (SCI-Expanded), Social Sciences Citation Index (SSCI), MEDLINE, Índice Médico Español (IME) and Índice de Ciencias Sociales y Humanidades (ISOC) databases. 184 papers were identified, 79.89% of which were original research articles. Only four of these papers had been published before the 1990s. The mid 1990s saw a remarkable increase in the number of papers published (8-14 papers/year) with the highest pro…

International levelResearch literatureHistorysocial network analysisanálisis de redes socialesImpact factorEspañascientific publicationsbiomedicineMEDLINEfactor de impactoLibrary sciencebiomedicinaLibrary and Information SciencesOriginal researchSocial Sciences Citation IndexSpainCitation analysisbibliometríabibliometricsimpact factorCitationpublicaciones científicas
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