Search results for "LSU"
showing 10 items of 384 documents
CCDC 923558: Experimental Crystal Structure Determination
2013
Related Article: Marta Gonzalez-Alvarez,Alejandro Pascual-Alvarez,Lucas del Castillo Agudo,Alfonso Castineiras,Malva Liu-Gonzalez,Joaquin Borras,Gloria Alzuet-Pina|2013|Dalton Trans.|42|10244|doi:10.1039/C3DT50416F
CCDC 1429795: Experimental Crystal Structure Determination
2015
Related Article: Jérôme Bayardon, Milène Maronnat, Adam Langlois, Yoann Rousselin, Pierre D. Harvey and Sylvain Jugé|2015|Organometallics|34|4340|doi:10.1021/acs.organomet.5b00585
CCDC 1562448: Experimental Crystal Structure Determination
2018
Related Article: Murat Alkan-Zambada, Sarah Keller, Laura Martínez-Sarti, Alessandro Prescimone, José M. Junquera-Hernández, Edwin C. Constable, Henk J. Bolink, Michele Sessolo, Enrique Ortí, Catherine E. Housecroft|2018|J.Mater.Chem.C|6|8460|doi:10.1039/C8TC02882F
CCDC 680518: Experimental Crystal Structure Determination
2009
Related Article: A.Dobrov, V.B.Arion, S.Shova, A.Roller, E.Rentschler, B.K.Keppler|2008|Eur.J.Inorg.Chem.||4140|doi:10.1002/ejic.200800605
CCDC 153862: Experimental Crystal Structure Determination
2001
Related Article: G.Asensio, P.Gavina, A.Cuenca, M.C.R.de Arellano, L.R.Domingo, M.Medio-Simon|2000|Tetrahedron:Asymm.|11|3481|doi:10.1016/S0957-4166(00)00330-X
CCDC 153863: Experimental Crystal Structure Determination
2001
Related Article: G.Asensio, P.Gavina, A.Cuenca, M.C.R.de Arellano, L.R.Domingo, M.Medio-Simon|2000|Tetrahedron:Asymm.|11|3481|doi:10.1016/S0957-4166(00)00330-X
CCDC 751046: Experimental Crystal Structure Determination
2010
Related Article: J.Vicente, I.Saura-Llamas, J.Turpin, D.Bautista, C.R.de Arellano, P.G.Jones|2009|Organometallics|28|4175|doi:10.1021/om9002895
CCDC 977454: Experimental Crystal Structure Determination
2016
Related Article: Christoph Deckert, Denis Bittner, Luca M. Carrella, Dieter Schollmeyer and Eva Rentschler|2016|Eur.J.Inorg.Chem.||1738|doi:10.1002/ejic.201501400
CCDC 164934: Experimental Crystal Structure Determination
2001
Related Article: H.Grove, J.Sletten, M.Julve, F.Lloret|2001|J.Chem.Soc.,Dalton Trans.||2487|doi:10.1039/b103588f
The effect of galsulfase enzyme replacement therapy on the growth of patients with mucopolysaccharidosis VI (Maroteaux-Lamy syndrome).
2017
Mucopolysaccharidosis (MPS) VI is an autosomal recessive lysosomal storage disorder arising from deficient activity of N-acetylgalactosamine-4-sulfatase (arylsulfatase B) and subsequent intracellular accumulation of the glycosaminoglycans (GAGs) dermatan sulfate and chondroitin-4-sulfate. Manifestations are multi-systemic and include skeletal abnormalities such as dysostosis multiplex and short stature. Reference height-for-age growth charts for treatment-naive MPS VI patients have been published for both the slowly and rapidly progressing populations. Categorization of disease progression for these charts was based on urinary GAG (uGAG) level; high (>200μg/mg creatinine) levels identified …