Search results for "Metacarpus"

showing 3 items of 3 documents

A new heterozygous mutation (L338N) in the human Gsalpha (GNAS1) gene as a cause for congenital hypothyroidism in Albright's hereditary osteodystroph…

2003

OBJECTIVE: To identify the molecular defect by which psychomotor retardation is caused in two brothers with congenital hypothyroidism who received adequate treatment with l-thyroxine. CASE REPORT: A six-year-old boy presented with psychomotor retardation and congenital primary hypothyroidism (CH). The patient had a normal blood thyrotrophin (TSH) level on neonatal screening, but low total serum thyroxine and triiodothyronine concentrations prompting thyroid hormone substitution shortly after birth. Nevertheless, psychomotor development was retarded and the patient underwent further investigation. Typical features of Albright's hereditary osteodystrophy (AHO) such as round face, obesity, and…

Malemedicine.medical_specialtyHeterozygoteGenotypeEndocrinology Diabetes and MetabolismThyrotropinFibrous Dysplasia PolyostoticEndocrinologyHypothyroidismInternal medicinemedicineGTP-Binding Protein alpha Subunits GsHumansOsteodystrophyChildAlbright's hereditary osteodystrophyPseudohypoparathyroidismPsychomotor retardationbusiness.industryThyroidErythrocyte MembranePrimary hypothyroidismGeneral MedicineSequence Analysis DNAmedicine.diseaseCongenital hypothyroidismPedigreeThyroxineEndocrinologymedicine.anatomical_structureMutationTriiodothyroninePseudopseudohypoparathyroidismCalciummedicine.symptomMetacarpusPsychomotor DisordersbusinessEuropean journal of endocrinology
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Osteoblastic osteogenic sarcoma in a 13-month-old girl.

1994

Summary Osteosarcoma is exceptional in early periods of life. Therefore osteosarcomas involvingthe bones of the hand are extremely rare. We present a case of an osteogenic sarcoma involving the second metacarpal bone of a 13-month-old girl who has been remaining free of disease, after treatment — radial amputation and chemotherapy pre- and post-operative-, for a period of 10 years in the follow-up.

medicine.medical_specialtymedicine.medical_treatmentmedia_common.quotation_subjectSecond metacarpal boneAmputation SurgicalPathology and Forensic MedicineFingersAntineoplastic Combined Chemotherapy Protocolsmedicinemedicine.boneHumansGirlmedia_commonChemotherapyOsteosarcomabusiness.industryInfantCell Biologymedicine.diseaseCombined Modality TherapySurgeryRadiographyAmputationOsteosarcomaFemaleSarcomaMetacarpusbusinessAfter treatmentFollow-Up StudiesPathology, research and practice
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Chondrodysplasia punctata, tibia-metacarpal (MT) type.

1990

We describe 7 patients with a new form of chondrodysplasia punctata. Its principal clinical manifestations are flat midface and nose, short limbs, and otherwise normal development. Consistent radiologic manifestations in the newborn infant are discrete calcific stippling, coronal clefts of vertebral bodies, short tibiae, and shortness of the 2nd and 3rd metacarpal bones. Radiologic findings in the older child include shortness of tibiae and the 3rd and 4th metacarpals.

musculoskeletal diseasesMaleChondrodysplasia PunctataAdolescentLimb Deformities CongenitalMetacarpal bonesShort staturemedicineHumansChondrodysplasia punctataAbnormalities MultipleTibiaChildGenetics (clinical)NoseShort tibiaTibiabusiness.industryInfant NewbornInfantAnatomymusculoskeletal systemmedicine.diseaseOsteochondrodysplasiamedicine.anatomical_structureShort limbsChild PreschoolFaceFemalemedicine.symptomMetacarpusbusinessAmerican journal of medical genetics
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