Search results for "PEAR"

showing 10 items of 442 documents

Clinical manifestations and management of four children with Pearson syndrome.

2011

Pearson marrow-pancreas syndrome is a fatal disorder mostly diagnosed during infancy and caused by mutations of mitochondrial DNA. We hereby report on four children affected by Pearson syndrome with hematological disorders at onset. The disease was fatal to three of them and the fourth one, who received hematopoietic stem cell transplantation, died of secondary malignancy. In this latter patient transplantation corrected hematological and non-hematological issues like metabolic acidosis, and we therefore argue that it could be considered as a useful option in an early stage of the disease.

MalePediatricsmedicine.medical_specialtyMitochondrial DiseasesAnemiaMitochondrial diseasemedicine.medical_treatmenttrapianto cellule staminali emopoieticheHematopoietic stem cell transplantationDiseaseDNA MitochondrialLipid Metabolism Inborn Errorsmitochondrial disordersFatal OutcomeMuscular DiseasesCause of Deathhematopoietic stem cell transplantation; mitochondrial disorders; Pearson marrow-pancreas syndrome; trapianto cellule staminali emopoietiche; malattie mitocondriali; sindrome di PearsonGeneticsmedicineCongenital Bone Marrow Failure SyndromesHumansChildGenetics (clinical)Pearson marrow-pancreas syndromeCause of deathPearson syndromebusiness.industryAcyl-CoA Dehydrogenase Long-ChainHematopoietic Stem Cell TransplantationInfantMetabolic acidosissindrome di Pearsonmedicine.diseaseAnemia SideroblasticTransplantationChild PreschoolImmunologymalattie mitocondrialiFemalebusinessGene DeletionAmerican journal of medical genetics. Part A
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Force-velocity profiling in athletes: Reliability and agreement across methods

2021

The aim of the study was to examine the test-retest reliability and agreement across methods for assessing individual force-velocity (FV) profiles of the lower limbs in athletes. Using a multicenter approach, 27 male athletes completed all measurements for the main analysis, with up to 82 male and female athletes on some measurements. The athletes were tested twice before and twice after a 2- to 6-month period of regular training and sport participation. The double testing sessions were separated by ~1 week. Individual FV-profiles were acquired from incremental loading protocols in squat jump (SJ), countermovement jump (CMJ) and leg press. A force plate, linear encoder and a flight time cal…

MalePhysiologyIntraclass correlationExtrapolationVelocitySocial Sciencesmedicine.disease_causeJumpingMathematical and Statistical TechniquesJumpingStatisticsMedicine and Health SciencesPsychologyRange of Motion ArticularLeg pressMathematicsMeasurementNumerical AnalysisMultidisciplinaryPhysicsStatisticsQRClassical MechanicsSoftware EngineeringVDP::Medisinske Fag: 700::Idrettsmedisinske fag: 850Sports ScienceLower ExtremityPhysical SciencessymbolsJumpLegsEngineering and TechnologyRegression AnalysisMedicineFemaleAnatomyResearch ArticleSportsAdultComputer and Information SciencesAdolescentCoefficient of variationScienceLinear Regression AnalysisResearch and Analysis MethodsComputer SoftwareMotionYoung Adultsymbols.namesakeLinear regressionmedicineHumansMuscle StrengthStatistical MethodsExerciseBehaviorBiological LocomotionBiology and Life SciencesReproducibility of ResultsPearson product-moment correlation coefficientStandard errorAthletesPhysical FitnessBody LimbsExercise TestRecreationMathematics
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Evaluation of prostate segmentation algorithms for MRI: The PROMISE12 challenge

2014

Contains fulltext : 137969.pdf (Publisher’s version ) (Open Access) Prostate MRI image segmentation has been an area of intense research due to the increased use of MRI as a modality for the clinical workup of prostate cancer. Segmentation is useful for various tasks, e.g. to accurately localize prostate boundaries for radiotherapy or to initialize multi-modal registration algorithms. In the past, it has been difficult for research groups to evaluate prostate segmentation algorithms on multi-center, multi-vendor and multi-protocol data. Especially because we are dealing with MR images, image appearance, resolution and the presence of artifacts are affected by differences in scanners and/or …

MaleScannerObserver (quantum physics)Computer scienceHealth InformaticsSensitivity and SpecificityArticleProstate cancerSegmentationImaging Three-DimensionalRobustness (computer science)Image Interpretation Computer-AssistedmedicineHumansRadiology Nuclear Medicine and imagingSegmentationChallengeProtocol (science)Modality (human–computer interaction)Radiological and Ultrasound TechnologyProstateProstatic NeoplasmsReproducibility of ResultsReference Standardsmedicine.diseaseImage EnhancementComputer Graphics and Computer-Aided DesignMagnetic Resonance ImagingActive appearance modelUrological cancers Radboud Institute for Health Sciences [Radboudumc 15]Computer Vision and Pattern RecognitionArtifactsAlgorithmAlgorithmsRare cancers Radboud Institute for Health Sciences [Radboudumc 9]MRI
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Freestyle-Like V-Y Flaps of the Eyebrow: A New Outlook and Indication of an Historical Technique

2013

The eyebrow region is of utmost importance for facial movement, symmetry, and the overall cosmetic appearance of the face. Trauma or tumor resection often leave scars that may dislocate the eyebrow producing an alteration both in static symmetry of the face and in the dynamic expressivity. The authors present a technique for eyebrow’s defects repair using the remaining eyebrow advancement by means of a “freestyle-like” V-Y flap. In the past two years a total of eight consecutive patients underwent excision of skin lesions in the superciliary region and immediate reconstruction with this technique. On histology, six patients were affected from basal cell carcinomas, one from squamous cell ca…

MaleSkin NeoplasmsReconstructive Surgical Procedures/methodsEyebrowSettore MED/19 - Chirurgia Plasticalcsh:MedicineScarsOphthalmologic Surgical Procedureslcsh:TechnologySurgical Flapslcsh:ScienceSkin Neoplasms/surgeryNevus Intradermal/surgeryGeneral Environmental ScienceAged 80 and overV-Y flap eyebrow defectGeneral MedicineMiddle AgedCarcinoma Basal Cell/surgerymedicine.anatomical_structureTreatment OutcomeNevus Intradermalmedicine.symptomAdultCosmetic appearancemedicine.medical_specialtyArticle SubjectTumor resectionFree Tissue FlapsGeneral Biochemistry Genetics and Molecular BiologymedicineHumansNeoplasms Squamous Cell/surgeryBasal cellNeoplasms Squamous CellFacial movementSurgical FlapsAgedlcsh:Tbusiness.industrylcsh:ROphthalmologic Surgical Procedures/methodsPlastic Surgery ProceduresSurgeryEyebrow regionCarcinoma Basal CellClinical Studylcsh:QEyebrowsbusiness
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Do factors related to participation in physical activity change following restrictive bariatric surgery? A qualitative study.

2017

Summary Aims To explore participants’ ability to participate in physical activity (PA), and barriers and facilitators to PA, at 12 months following restrictive bariatric surgery, and how these differed from participants’ pre-surgery perceptions. Motivators for PA post-surgery were also explored. Methods Qualitative one-on-one in-depth interviews were conducted pre- and 12 months post-surgery. Data were analysed using inductive thematic analysis. Results Fourteen adults (12 females), with a mean (range) age of 41.4 years (25.0–56.0), body mass index (BMI) of 31.7 kg/m2 (22.3–48.2), and excess weight loss of 66% (2–127) completed both interviews. Lack of participation in PA during the first 3…

MaleTime FactorsEndocrinology Diabetes and MetabolismPsychological interventionphysical activityBariatric SurgeryliikuntaHuman physical appearanceleikkaushoito0302 clinical medicineWeight loss030212 general & internal medicineta315Qualitative Researcheducation.field_of_studyNutrition and Dieteticsta3141Middle AgedfacilitatorsFemaleThematic analysismedicine.symptomfyysinen aktiivisuusAdultmedicine.medical_specialtybarriersPopulation030209 endocrinology & metabolismInterviews as Topic03 medical and health sciencesWeight LossmedicineHumanseducationExerciseMotivationbusiness.industrylaihdutusmedicine.diseaseObesitySelf ConceptlaihdutusleikkausSurgeryqualitativePhysical therapyPatient ParticipationbusinessBody mass indexQualitative researchFollow-Up StudiesObesity researchclinical practice
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Diagnostic Value of Optical Spectral Transmission in Rheumatoid Arthritis: Associations with Clinical Characteristics and Comparison with Joint Ultra…

2020

Objective.To examine the value of optical spectral transmission (OST) in detecting joint inflammation in patients with rheumatoid arthritis (RA) and to evaluate whether OST correlates with certain patient characteristics.Methods.OST measurements were performed in the metacarpophalangeal, proximal intraphalangeal, and wrist joints of 168 patients with RA and 114 controls. OST difference between the 2 groups was statistically examined and subsequently controlled for the effect of possible confounding factors. Diagnostic OST performance was tested by receiver-operating characteristics. Moreover, associations of OST with clinical and serological activity markers (patient group), joint ultrasoun…

MaleWrist Jointmedicine.medical_specialtySpectral transmissionImmunologySeverity of Illness IndexSpearman's rank correlation coefficientArthritis RheumatoidCorrelation03 medical and health sciences0302 clinical medicineRheumatologyInternal medicinemedicineHumansImmunology and Allergy030212 general & internal medicineUltrasonography030203 arthritis & rheumatologySynovitisbusiness.industryfungiUltrasoundConfoundingArea under the curveUltrasonography DopplerAnthropometrymedicine.diseaseRheumatoid arthritisFemalebusinessThe Journal of Rheumatology
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A report on the clinical-pathological correlations of 788 gingival lesion

2017

Background The diagnosis and treatment of a variety of non-plaque related gingival diseases have become an integrated aspect of everyday dentistry. The aim of this study was to analyse the relationship between clinical appearance and histopathological features of gingival lesions in a large Northern Italian population. Material and Methods A retrospective study of 788 cases of gingival and alveolar mucosal biopsies was set up. Statistical analysis was performed by calculating the odds ratio and 95% confidence interval (C.I.), in order to assess the degree of association between the clinical parameters considered (primary lesions) and the single pathologies, statistically evaluated by Mantel…

Malemedicine.medical_specialtyEpulisHistological analysis2734Pathology and Forensic MedicineLesion03 medical and health sciences0302 clinical medicinemedicineHumansGeneral DentistryLeukoplakiaRetrospective StudiesOral Medicine and Pathologybusiness.industryVerrucous carcinomaPyogenic granulomaResearchOtorhinolaryngology2734 Pathology and Forensic Medicine030206 dentistryMiddle Agedmedicine.diseaseGingival lesions:CIENCIAS MÉDICAS [UNESCO]DermatologyClinical appearance; Clinico-pathological correlation; Gingival lesions; Histological analysis; Surgery; Otorhinolaryngology2734 Pathology and Forensic Medicine; Dentistry (all)Clinical appearanceOtorhinolaryngologyItaly030220 oncology & carcinogenesisGingival DiseasesUNESCO::CIENCIAS MÉDICASClinical appearance; Clinico-pathological correlation; Gingival lesions; Histological analysis; Surgery; Otorhinolaryngology; 2734; Pathology and Forensic Medicine; Dentistry (all)Dentistry (all)HistopathologyOral lichen planusFemaleSurgeryClinico-pathological correlationmedicine.symptombusinessGingival disease
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Inhibitory effects of indicaxanthin on mouse ileal contractility: analysis of the mechanism of action.

2011

Recently, we have showed that indicaxanthin, the yellow betalain pigment abundant in the fruit of Opuntia ficus indica, has remarkable spasmolytic effects on the intestinal contractility in vitro. Thus, the purpose of the present study was to investigate the mechanism of action underlying the observed response. We used organ bath technique to record the mechanical activity of the mouse ileum longitudinal muscle and ELISA to measure the levels of cAMP. Indicaxanthin induced inhibitory effects on spontaneous mechanical activity, which were unaffected by indomethacin, a non-selective inhibitor of cycloxygenase; 1H-[1,2,4]oxadiazolo[4,3-a]quinoxalin-1-one, a selective inhibitor of nitric oxide-…

Malemedicine.medical_specialtyIBMXPyridinesIndicaxanthinBiologyIn Vitro TechniquesContractilitySettore BIO/09 - FisiologiaAdenylyl cyclaseContractilitychemistry.chemical_compoundMiceSmooth muscleCactus pear fruitIleumSettore BIO/10 - BiochimicaInternal medicinemedicineCyclic AMPAnimalsEnzyme InhibitorsPharmacologyForskolinPhosphodiesteraseMuscle SmoothBetaxanthinsBiomechanical PhenomenaMice Inbred C57BLEndocrinologychemistryPhosphodiesterasesCarbacholZaprinastSoluble guanylyl cyclaseIndicaxanthinMuscle ContractionSignal TransductionEuropean journal of pharmacology
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Scoring systems for Oral Lichen Planus used by differently experienced raters

2017

BACKGROUND: Scoring systems have been widely used to evaluate the severity and activity of oral lichen planus (OLP). The aim of the present study was to compare two existing (one modified) scoring systems in the evaluation of OLP severity and correlation with pain. Three differently experienced raters were involved. MATERIALS AND METHODS: Consecutive patients with OLP were assessed for pain using the Visual Analogue Scale and examined at 10 intraoral sites before starting (T0) and three weeks after (T1) steroid therapy (Clobetasol). Three differently experienced raters evaluated photographs using two scoring systems designated White-Erosive-Atrophic (WEA) modified from an older WEA system (…

Malemedicine.medical_specialtyIntraclass correlationVisual analogue scalePainraterBuccal mucosaSpearman's rank correlation coefficientSeverity of Illness Index03 medical and health sciences0302 clinical medicineSeverity of illnessOral and maxillofacial pathologymedicineHumansGeneral DentistryGlucocorticoidsUNESCO:CIENCIAS MÉDICASPain MeasurementClobetasolOral Medicine and Pathologybusiness.industryResearchscoring system030206 dentistryMiddle Agedmedicine.diseaseDermatologyWEAstomatognathic diseasesOtorhinolaryngologyOral lichen planu030220 oncology & carcinogenesisClobetasolOral lichen planusSurgeryOral lichen planusFemaleVASbusinessOral lichen planus; scoring system; VAS; REU; WEA; raterREULichen Planus Oral
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Clinical presentation of burning mouth syndrome in patients with oral lichenoid disease

2020

Background To analyze the presence of burning mouth syndrome (BMS) in a group of patients diagnosed with oral lichenoid disease (OLD). Material and Methods A retrospective study of 217 patients diagnosed with OLD; 158 (72,8%) women and 59 (27,2%) men, with an average age upon diagnosis of 56,4 years (SD 11,88). We carried out a detailed and complete characterization of symptoms, with special emphasis on BMS diagnostic data specified by the International Headache Society. Results Four patients (1.8%) presented with long-term clinical symptoms of burning mouth, indicative of BMS and they fulfilled the IHS 2018 criteria, except for criterion D, i.e.“Oral mucosa is of normal appearance”. The ob…

Malemedicine.medical_specialtyPainDiseaseBurning Mouth Syndrome03 medical and health sciences0302 clinical medicinemedicineHumansIn patientNormal appearanceMedical diagnosisOral mucosaGeneral DentistryRetrospective StudiesOral Medicine and Pathologybusiness.industryResearchMouth MucosaRetrospective cohort study030206 dentistryBurning mouth syndrome:CIENCIAS MÉDICAS [UNESCO]Dermatologystomatognathic diseasesmedicine.anatomical_structureOtorhinolaryngologyChild PreschoolUNESCO::CIENCIAS MÉDICASSurgeryFemalemedicine.symptomPresentation (obstetrics)businessMouth Diseases
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