Search results for "ROUGH"

showing 10 items of 1198 documents

Translational readthrough of ciliopathy genes BBS2 and ALMS1 restores protein, ciliogenesis and function in patient fibroblasts

2021

Abstract Background Ciliary dysfunction underlies a range of genetic disorders collectively termed ciliopathies, for which there are no treatments available. Bardet-Biedl syndrome (BBS) is characterised by multisystemic involvement, including rod-cone dystrophy and renal abnormalities. Together with Alstrom syndrome (AS), they are known as the ‘obesity ciliopathies’ due to their common phenotype. Nonsense mutations are responsible for approximately 11% and 40% of BBS and AS cases, respectively. Translational readthrough inducing drugs (TRIDs) can restore full-length protein bypassing in-frame premature termination codons, and are a potential therapeutic approach for nonsense-mediated ciliop…

BBS2AdultMaleMedicine (General)AdolescentNonsense mutationAminopyridinesCell Cycle ProteinsCiliopathiesGeneral Biochemistry Genetics and Molecular Biologychemistry.chemical_compoundR5-920AtalurenCiliogenesismedicineHumansReceptors SomatostatinBardet-Biedl SyndromeAlstrom SyndromeCells CulturedOxadiazolesbusiness.industryTumor Suppressor ProteinsTranslational readthroughRProteinsGeneral MedicineFibroblastsmedicine.diseaseNonsense suppressionCiliopathiesAtalurenCiliopathyALMS1chemistryCodon NonsenseAmlexanoxCancer researchMedicineBBS2businessAlström syndromeResearch PaperEBioMedicine
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Performance Assessment of Building Integrated Photovoltaic and Battery Energy System: A Case Study of TERI-Retreat Facilty in India

2019

Building integrated photovoltaic (BIPV) with energy storage can play an important role not only in demand side management but also in a micro-grid system in coordination with other distributed generators. The operational analysis of BIPV system and energy storage with contribution to local load profile is needed for its grid connected operation, as well as for integrating it in the micro-grid system. In this work, a typical institution has been selected, where the PV system and energy storage are operated for supplying local load in coordination with the grid. The institutional load profile has been analyzed with essential and non-essential loads for understanding the operation and contribu…

Battery (electricity)business.industryComputer sciencePhotovoltaic systemBuilding-integrated photovoltaicsSolar energybusinessGridThroughput (business)Load profileEnergy storageReliability engineering2019 4th International Conference on Smart and Sustainable Technologies (SpliTech)
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Using coded excitation to maintain signal to noise for FMC+TFM on attenuating materials

2019

Ultrasonic Non-Destructive Evaluation using Full Matrix Capture (FMC) and Total Focusing Method (TFM) is used for high resolution imaging as every pixel is in optimal focus. FMC excites one element in turn, so operates with lower transmitted energy compared to phased array beamforming. The energy at a reflector is further reduced by the broad directivity pattern of the single element. The large number of Tx/Rx A-scans that contribute to each pixel recover the Signal-to-Noise Ratio (SNR) in the final TFM image. Maintaining this in the presence of attenuating materials is a challenge because relevant information in each A-scan signal is buried in the thermal noise, and the TFM process assumes…

BeamformingComputer sciencePhased arrayAcousticsTK02 engineering and technology01 natural sciencesSignalNoise (electronics)Signal-to-noise ratio0103 physical sciencesTFMUltrasound0202 electrical engineering electronic engineering information engineeringFMChigh attenuation010301 acousticsPixelbusiness.industryQuantization (signal processing)AttenuationUltrasoundorthogonal Golay code020206 networking & telecommunicationsCoded excitationRough surfaceUltrasonic sensorbusinessadditive manufacturingEnergy (signal processing)
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Clustering-Assisted 3D Beamforming for Throughput Maximization in mmWave Networks

2021

Beamforming schemes have been widely used to improve network throughput in 5G mmWave networks. However, 3D beamforming schemes have hereto not been investigated in this context. In this work, a cluster-assisted 3D beamforming scheme is proposed to optimize the downtilt angle for network coverage and throughput maximization. User Equipment (UEs) are clustered based on inter-user and the inter-cluster distances. The interference is accounted from the adjacent clusters and thus frequency resources can be assigned to the non-adjacent clusters. Optimal downtilt angles are obtained for every cluster to maximize the throughput while considering the interference from adjacent clusters. 3D beam patt…

BeamformingUser equipmentComputer scienceComputer Science::Networking and Internet ArchitectureContext (language use)ThroughputMaximal-ratio combiningInterference (wave propagation)Cluster analysisAlgorithm5GComputer Science::Information Theory2021 IEEE International Conference on Communications Workshops (ICC Workshops)
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Enable concurrent transmissions with beamforming for broadband wireless access in CSMA/CA-based WLANs

2014

In CSMA/CA based wireless local networks, two stations are not allowed to transmit at the same time due to interference generated to each other, resulting in degraded throughput. Concurrent transmission, which enables simultaneous transmission of two or more stations under certain conditions, is able to overcome this problem, leading to enhanced channel utilization efficiency. Different from earlier work on this topic which focuses on omni-direction concurrent transmission, we introduce in this paper beamforming into a co-channel concurrent transmission scheme and investigate the benefits of concurrency with beamforming. The circumstances for concurrent transmission and frame scheduling are…

BeamformingWireless broadbandbusiness.industryComputer scienceComputerSystemsOrganization_COMPUTER-COMMUNICATIONNETWORKSWirelessThroughputData_CODINGANDINFORMATIONTHEORYbusinessCarrier sense multiple access with collision avoidanceComputer networkCommunication channelScheduling (computing)2014 IEEE Globecom Workshops (GC Wkshps)
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Overland flow hydrodynamic characteristics in rough beds at low Reynolds numbers

2022

This paper considers overland flow resistance at low Reynolds numbers through analysis of experimental runs carried out using water only and water/glycerol mixtures. We first examined the power relationship between the Darcy–Weisbach friction factor f and the Reynolds number Re to obtain the values of the K coefficient and b exponent. These results confirmed the applicability of the values of b suggested in literature, while K required a specific calibration for laminar open-channel flows. The analysis revealed that transition from a laminar to turbulent flow regime for water only flows occurred at a threshold value of Re equal to 500 as described historically. The estimate of f by the powe…

Bed roughneSelf-similarityDimensional analysiMixed flowFlow resistanceVelocity profileSettore AGR/08 - Idraulica Agraria E Sistemazioni Idraulico-ForestaliWater Science and TechnologyJournal of Hydrology
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Experimental observations of upstream overdeepening

2005

The issue of morphodynamic influence in meandering streams is investigated through a series of laboratory experiments on curved and straight flumes. Both qualitative and quantitative observations confirm the suitability of the recent theoretical developments (Zolezzi & Seminara 2001) that indicate the occurrence of two distinct regimes of morphodynamic influence, depending on the value of the width ratio of the channel β. The threshold value βR separating the upstream from the downstream influence regimes coincides with the resonant value discovered by Blondeaux & Seminara (1985). Indeed it is observed that upstream influence may occur only in relatively wide channels, while narrower stream…

BedformMechanics of MaterialsMechanical EngineeringOverdeepeningThe issue of morphodynamic influence in meandering streams is investigated through a series of laboratory experiments on curved and straight flumes. Both qualitative and quantitative observations confirm the suitability of the recent theoretical developments (Zolezzi & Seminara 2001) that indicate the occurrence of two distinct regimes of morphodynamic influence depending on the value of the width ratio of the channel β. The threshold value βR separating the upstream from the downstream influence regimes coincides with the resonant value discovered by Blondeaux & Seminara (1985). Indeed it is observed that upstream influence may occur only in relatively wide channels while narrower streams are dominated by downstream influence. A series of experiments has been carried out in order to check the above theoretical predictions and show for the first time evidence of the occurrence of upstream overdeepening. Two different sets of experiments have been designed where a discontinuity in channel geometry was present such that the channel morphodynamics was influenced in the upstream direction under super-resonant conditions (β >βR) and in the downstream direction under sub-resonant conditions (β <βR). Experimental results give qualitative and quantitative support to the theoretical predictions and allow us to clarify the limits of the linear analysis.MechanicsLinear analysisCondensed Matter PhysicsWidth ratioGeology
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Surface finish on hardened bearing steel parts produced by superhard and abrasive tools

2007

New technological process consisting of hard turning (HT) followed by abrasive machining, in place of the widely used method in industry, i.e., hard turning versus grinding, has lately been launched in the automotive industry. This is because, many transmissions parts, such as synchronizing gears, crankshafts and camshafts require superior surface finish along with appropriate fatigue performance. This paper provides a comprehensive characterization of part surface finish produced in dry turning of a hardened AISI 52100 bearing steel using mixed ceramic (MC) and PCBN tools, and also its modification after special abrasive finishing operations including superfinishing (SF) and belt grinding …

Belt grindingMaterials scienceAbrasive machiningMachiningMechanical EngineeringMetallurgyAbrasiveSurface roughnessSurface finishSuperfinishingIndustrial and Manufacturing EngineeringGrindingInternational Journal of Machine Tools and Manufacture
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Antigüedad clásica y cultura nobiliaria en la España de finales del siglo XVIII. Autores y ediciones greco-romanas en la biblioteca de José Alvarez d…

2019

This article analyzes the reception of the classical world in the Spanish nobiliary culture at the end of the 18th century. Our objective is materialized through the study of the Greco-Roman books present in the unpublished catalog of the library of José Álvarez de Toledo, 11th Marqués de villafranca. From the examination of the authors and the different editions conserved by the aristocrat, the work tries to examine the influence of the classical world and its actuality in the development of the most advanced nobiliary culture of eighteenth- century Spain.

Beltrán CorbalánLibraryRevista de historia moderna 529735 2019 45 7107719 Antigüedad clásica y cultura nobiliaria en la España de finales del siglo XVIII. Autores y ediciones greco-romanas en la biblioteca de José Alvarez de Toledo [0210-9093 553 Estudis]xI marqués de villafrancaUNESCO::HISTORIAXI Marqués de Villafranca Precioso Izquierdo11th Marqués de villafranca. From the examination of the authors and the different editions conserved by the aristocratNoble CultureFranciscoSiglo xvIII0210-9093 553 Estudis: Revista de historia moderna 529735 2019 45 7107719 Antigüedad clásica y cultura nobiliaria en la España de finales del siglo XVIII. Autores y ediciones greco-romanas en la biblioteca de José Alvarez de ToledoCultura nobiliariaAntigüedad ClásicaClassical Antiquitythe work tries to examine the influence of the classical world and its actuality in the development of the most advanced nobiliary culture of eighteenth- century Spain. Librería:HISTORIA [UNESCO]Domingo This article analyzes the reception of the classical world in the Spanish nobiliary culture at the end of the 18th century. Our objective is materialized through the study of the Greco-Roman books present in the unpublished catalog of the library of José Álvarez de Toledo18th Century 253 271
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Surface soil moisture retrieval using L-band SMAP SAR data and its validation

2016

Surface soil moisture was retrieved globally by systematically correcting for the effects of vegetation and soil surface roughness. The retrieval is enabled by employing physical-models of radar forward scattering for individual vegetation types to account for vegetation scattering and absorption, and by constraining the surface roughness effect using time-series observations. The L-band SMAP multi-polarized (HH/VV/HV) σ° data acquired globally every three days were used from mid-April to early July, 2015. Assessment was conducted over 13 rigorously-chosen core validation sites covering a wide range of biomass types, biomass amount, and soil conditions. The soil moisture retrieval reached a…

Biomass (ecology)L band0211 other engineering and technologiesSoil science02 engineering and technologyVegetationSurface finishlaw.inventionlawSurface roughnessEnvironmental scienceRadarAbsorption (electromagnetic radiation)Water content021101 geological & geomatics engineeringRemote sensing2016 IEEE International Geoscience and Remote Sensing Symposium (IGARSS)
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