Search results for "STZ"

showing 10 items of 19 documents

Very low doses of muscimol and baclofen ameliorate cognitive deficits and regulate protein expression in the brain of a rat model of streptozocin-ind…

2018

Recent studies devoted to neuroprotection have focused on the role of the gamma-aminobutyric acid (GABA) system in regulating neuroinflammatory processes which play a key role in the neurodegenerative processes observed in Alzheimer's disease (AD) by inducing glial cell overactivation and impairing neurotransmission. Data on the efficacy of classical GABA-A and GABA-B receptor agonists (muscimol and baclofen, respectively) in animal models of AD are not available. Moreover, no published studies have examined the ability of optimal doses of these compounds to prevent neuroinflammation, the alterations in neurotransmission and cognitive deficits. In the present study, we used a non-transgenic…

0301 basic medicineMaleBaclofenGlutamate decarboxylaseSpatial LearningPharmacologyNeuroprotectionStreptozocin03 medical and health scienceschemistry.chemical_compound0302 clinical medicineCognitionGABA receptorSTZAlzheimer DiseaseMemoryGlial Fibrillary Acidic ProteinLearningAnimalsRats WistarNeuroinflammationPharmacologyGlial fibrillary acidic proteinbiologyDose-Response Relationship DrugChemistryGABAA receptorMuscimolBrainRatsDisease Models Animal030104 developmental biologyBaclofennervous systemMuscimolGene Expression RegulationRat model of ADbiology.protein:MEDICINE::Physiology and pharmacology::Pharmacological research [Research Subject Categories]Neuroscience030217 neurology & neurosurgeryEuropean journal of pharmacology
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PORCN mutations in focal dermal hypoplasia: coping with lethality.

2009

Contains fulltext : 81709.pdf (Publisher’s version ) (Closed access) The X-linked dominant trait focal dermal hypoplasia (FDH, Goltz syndrome) is a developmental defect with focal distribution of affected tissues due to a block of Wnt signal transmission from cells carrying a detrimental PORCN mutation on an active X-chromosome. Molecular characterization of 24 unrelated patients from different ethnic backgrounds revealed 23 different mutations of the PORCN gene in Xp11.23. Three were microdeletions eliminating PORCN and encompassing neighboring genes such as EBP, the gene associated with Conradi-Hunermann-Happle syndrome (CDPX2). 12/24 patients carried nonsense mutations resulting in loss …

AdultMaleAdolescentBase SequenceDNA Mutational AnalysisMolecular Sequence DataInfant NewbornInfantMembrane ProteinsGenomic disorders and inherited multi-system disorders [IGMD 3]Focal Dermal HypoplasiaSettore MED/38 - Pediatria Generale E SpecialisticaSettore MED/03 - Genetica MedicaChild PreschoolMutationGoltz syndrome FDH PORCN WNT skewed X-inactivation postzygotic mosaicHumansProtein IsoformsFemaleAmino Acid SequenceChildAcyltransferasesHuman Mutation
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Mosaicism due to postzygotic mutations in women with focal dermal hypoplasia

2019

International audience; Focal dermal hypoplasia (FDH, Goltz syndrome, MIM: #305600) constitutes a rare multisystem genetic disorder of the skin, skeleton, teeth and eyes with considerable variation in the clinical features. FDH is transmitted as an X-linked dominant trait and is caused by mutations in PORCN. In males, hemizygous PORCN mutations are lethal in utero. Around 300 cases have been reported in the literature to date. About 10% of them are males presenting either Klinefelter syndrome (karyotype 47, XXY) or mosaicism of a postzygotic mutation. Here we describe four cases of women with typical features of FDH, in whom a PORCN mutation was found in DNA from affected cutaneous tissue b…

AdultZygoteDNA Mutational AnalysisDermatologyBiologyPostzygotic mutationmedicine.disease_causePORCNYoung Adult030207 dermatology & venereal diseases03 medical and health sciences0302 clinical medicinemedicineHumansMissense mutationGoltz syndromeSkinGeneticsMutationMosaicismMouth MucosaGenetic disorderHigh-Throughput Nucleotide SequencingMembrane Proteinscutaneous mosaicismKaryotypemedicine.diseaseFocal dermal hypoplasia3. Good healthPORCNfocal dermal hypoplasiaFemaleKlinefelter syndromeAcyltransferases[SDV.MHEP.DERM]Life Sciences [q-bio]/Human health and pathology/DermatologyBritish Journal of Dermatology
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Cutaneous mosaic syndromes associated with early postzygotic activating BRAF mutations

2017

IF 3.528; International audience

BRAF V600EBRAF G596[SDV.MHEP.DERM] Life Sciences [q-bio]/Human health and pathology/DermatologyBRAF K601N[ SDV.MHEP.DERM ] Life Sciences [q-bio]/Human health and pathology/Dermatology[SDV.MHEP.DERM]Life Sciences [q-bio]/Human health and pathology/DermatologyPostzygotic BRAF mutations
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Nanovised Control Flow Attestation

2022

This paper presents an improvement of control flow attestation (C-FLAT) for Linux. C-FLAT is a control attestation system for embedded devices. It was implemented as a software executing in ARM’s TrustZone on bare-metal devices. We extend the design and implementation of C-FLAT through the use of a type 2 Nanovisor in the Linux operating system. We call our improved system “C-FLAT Linux”. Compared to the original C-FLAT, C-FLAT Linux reduces processing overheads and is able to detect the SlowLoris attack. We describe the architecture of C-FLAT Linux and provide extensive measurements of its performance in benchmarks and real-world scenarios. In addition, we demonstrate the…

Fluid Flow and Transfer ProcessespääsynvalvontaSoftware_OPERATINGSYSTEMSvirtualisointiProcess Chemistry and TechnologyLinuxhypervisor; ARM; Linux; control flow; SlowLoris; TrustZoneSlowLorisGeneral EngineeringTrustZonecontrol flowComputer Science ApplicationsARMGeneral Materials SciencehypervisortietoturvaInstrumentationApplied Sciences; Volume 12; Issue 5; Pages: 2669
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Exonic Mosaic Mutations Contribute Risk for Autism Spectrum Disorder

2017

AbstractGenetic risk factors for autism spectrum disorder (ASD) have yet to be fully elucidated. Postzygotic mosaic mutations (PMMs) have been implicated in several neurodevelopmental disorders and overgrowth syndromes. We systematically evaluated PMMs by leveraging whole-exome sequencing data on a large family-based ASD cohort, the Simons Simplex Collection. We found evidence that 11% of published single nucleotide variant (SNV)de novomutations are potentially PMMs. We then developed a robust SNV PMM calling approach that leverages complementary callers, logistic regression modeling, and additional heuristics. Using this approach, we recalled SNVs and found that 22% ofde novomutations like…

Male0301 basic medicineProbandZygoteautism spectrum disorderSYNGAP1Biologypostzygoticmedicine.disease_causeArticleGermlineCohort Studies03 medical and health sciencessplicing0302 clinical medicineNeurodevelopmental disorderGermline mutationDatabases GeneticGeneticsmedicineHumansMissense mutationGenetic Predisposition to DiseaseChild[ SDV.GEN.GH ] Life Sciences [q-bio]/Genetics/Human geneticsGenetics (clinical)030304 developmental biologyGenetics0303 health sciencesMutationneurodevelopmentsomaticGenetic VariationExonsmedicine.disease030104 developmental biologymosaicism[SDV.GEN.GH]Life Sciences [q-bio]/Genetics/Human geneticsAutism spectrum disorderCHD2AutismFemalemutation030217 neurology & neurosurgeryexome
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Skaitļu atpazīšana brīvā dabā uzņemtās fotogrāfijās

2022

Palielinoties digitālo tehnoloģiju lomai cilvēku ikdienā, OCR jeb Optiskā teksta pazīšana kļūst arvien biežāk izmantota. OCR pielietojumu iespējas ir plašas – kā vienu no biežāk izmantotajām var minēt dokumentu digitalizēšanu – tomēr brīvā dabā uzņemtās fotogrāfijās ar skaitļiem OCR precizitātei vēl joprojām ir vieta izaugsmei. Darba mērķis ir noteikt, cik liela loma un ietekme ir OCR tehnoloģijām mūsdienās un kāpēc tās efektivitāte krīt, analizējot attēlus ar skaitļiem. Darba uzdevumi ietver iepazīšanos ar OCR tehnoloģijas vēsturi un pielietojumiem mūsdienās, tehnoloģijas algoritmiem un trūkumiem tajos. Darba pētījumā tika izpētīti divi OCR rīki, izmantojot programmēšanas valodu Python, un…

OCRDatorzinātnerakstzīmepirmapstrādePython
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Embryotoxic potential of persistent organic pollutants extracted from tissues of guillemots (Uria aalge) from the Baltic Sea and the Atlantic Ocean

2002

The Baltic Sea is a heavily polluted area. To assess the current contaminant pressure on the common guillemot (Uria aalge) living there, whole-body extracts of guillemots from the Baltic Sea were prepared and subdivided over six fractions, which differed in composition due to lipophilicity and polarity of the contaminants. The fractions were tested in the chicken embryo assay and compared to fractions of Atlantic guillemot extracts. Fertilized chicken eggs were injected with 0.03, 0.3, or 3 bird egg equivalents (BEQ) of the contaminants present in the fractions and then incubated for 19 d. Endpoints were selected to cover several mechanisms that may play a role in reproductive failures of f…

PollutantOostzeemilieuEcologyEcologie en MilieuHealth Toxicology and MutagenesisecotoxicologieZoologyzeevogelsBiologyAtlantische Oceaanbiology.organism_classificationBird eggToxicityUria aalgewaterverontreinigingEnvironmental ChemistryPotencyBioassayComposition (visual arts)Bursa of FabriciusornithologieEnvironmental Toxicology and Chemistry
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Rosyjska koncepcja Eurazjatyckiego Systemu Obrony Powietrzno-Kosmicznej. Analiza problemu

2018

Autorka artykułu omawia na tle uwarunkowań geopolitycznych Rosji najważniejsze tezy planu A. Podbieriezkina, które tworzą paradygmat wspólnego bezpieczeństwa w ujęciu rosyjskim na strategicznym obszarze Eurazji. Ma to szczególne znaczenie w obliczu wzrastających zagrożeń współczesnego świata. Szczególnie niebezpieczny charakter, w związku z przeprowadzaniem prób jądrowych i nieobliczalnym reżimem Kim Dzong Una, przybiera obecnie problem Korei Północnej, co rodzi zagrożenie, że nagły i. ARTYKUŁY i rozprawy 85 konflikt może wciągnąć Półwysep w wojnę. To z kolei z pewnością doprowadziłoby do interwencji Stanów Zjednoczonych. Skutki ewentualnego konfliktu z udziałem supermocarstwa są nie do prz…

RosjaEurazjaObrona Powietrzno-Kosmicznapostzimnowojenna rywalizacjaIndiezmiana ładu międzynarodowegoChinyDoktryna PutinaUSAgeopolitykaPrzegląd Bezpieczeństwa Wewnętrznego
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Per un'"Economia d'azienda" postzappiana. Appunti storici

2017

Il paper intende concorrere ad una ricostruzione in prospettiva storica dei percorsi di nascita, specificazione e rifondazione dell’Economia di azienda. In particolare, esso evidenzia come tale disciplina abbia prediletto in via di principio l’interpretazione dell’azienda in termini di genere, ma altresì come abbia realizzato in via di fatto, nelle opere di Zappa e della più parte dei suoi allievi diretti ed indiretti, un modello dell’azienda in termini di specie. Nel complesso, la disamina di alcune posizioni nel passato e nel presente storico depongono a favore di un ripensamento dei contenuti disciplinari in prospettiva propriamente “postzappiana” che possa essere di maggiore ed attuale …

Settore SECS-P/07 - Economia Aziendaleteoriche postzappianeEconomia d'aziendastoria della Ragioneria
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