Search results for "Sensorineural hearing loss"
showing 2 items of 62 documents
Hearing loss in facioscapulohumeral dystrophy.
1986
Bilateral sloping high frequency hearing loss of 20–90 dB was found in six out of ten patients with infantile or adolescent onset FSHD. In all cases the basic defect could be traced to the cochlea. The outer hair cells of the basal turn are predominantly affected. In 20 patients with various other forms of muscular dystrophy or neuromuscular disorders with an FSH distribution, no sensorineural hearing loss was found. Myopathology of FSHD patients extended from mild to severe, often showing inflammatory infiltrates and type I fibre atrophy, without unequivocal differences between the two groups with and without hearing loss. It is concluded that cochlear dysfunction is a specific and frequen…
Speech intelligibility and perception after cochlear implant in deaf children with or without associated disabilities: A review
2014
The ability to make oneself understood is critical to most human interaction, and as such, the failure to develop fully intelligible speech may result in a significant handicap especially in the child in learning phase. World literature has demonstrated improved speech intelligibility and speech perception as well as a good development of communication skills in prelingual profound sensorineural hearing loss (SNHL) children after cochlear implantation. The literature considered as universally-accepted the usefulness/effectiveness of unilateral early cochlear implantation in severely-profoundly deaf children with or without associated disabilities. In fact this procedure, for children implan…