Search results for "Sequencing"

showing 10 items of 1087 documents

Autosomal recessive polycystic kidney disease: case report of a newborn with rare PKHD1 mutation, rapid renal enlargement and early fatal outcome

2020

Abstract Introduction Autosomal recessive polycystic kidney disease (ARPKD; MIM#263200) is one of the most frequent pediatric renal cystic diseases, with an incidence of 1:20,000. It is caused by mutations of the PKHD1 gene, on chromosome 6p12. The clinical spectrum is highly variable, ranging from late-onset milder forms to severe perinatal manifestations. The management of newborns with severe pulmonary insufficiency is challenging, and causes of early death are sepsis or respiratory failure. In cases of massive renal enlargement, early bilateral nephrectomy and peritoneal dialysis may reduce infant mortality. However, there is no conclusive data on the role of surgery, and decision-makin…

Pediatricsmedicine.medical_specialtyGenotype-phenotype correlationGenotypemedicine.medical_treatmentARPKDPulmonary insufficiencyReceptors Cell SurfaceCase ReportPeritoneal dialysisSepsis03 medical and health sciencesLiver diseaseConsanguinity0302 clinical medicineFatal OutcomeNext generation sequencingmedicineHumansGenetic Predisposition to DiseaseEthicPotter sequencePolycystic Kidney Autosomal RecessiveEthicsbusiness.industrylcsh:RJ1-570Infant Newbornlcsh:Pediatricsmedicine.diseaseAutosomal Recessive Polycystic Kidney DiseaseRespiratory failure030220 oncology & carcinogenesisMutationFemalebusiness030217 neurology & neurosurgeryInfant PrematureBilateral NephrectomyPotter sequence
researchProduct

Electroclinical features and outcome of ANKRD11-related KBG syndrome: A novel report and literature review.

2021

KBG syndrome (OMIM #148050) is a rare autosomal dominant disorder, typically characterized by macrodontia of the upper central incisors, distinct craniofacial findings, short stature, and skeletal anomalies associated with neurological involvement including intellectual disability, behaviour difficulties, and epilepsy. KBG syndrome is associated with mutations in ANKRD11 gene that plays a chromatin regulator role of histone acetylation and gene expression during neurogenesis in the embryonic brain.

Pediatricsmedicine.medical_specialtyKBGAdolescentseizureOutcome (game theory)ANKRD11EpilepsySeizuresIntellectual DisabilityMedicineHumansAbnormalities MultipleBone Diseases Developmentalbusiness.industryTooth AbnormalitiesFaciesHigh-Throughput Nucleotide SequencingGeneral MedicineKBG SYNDROMESyndromemedicine.diseaseKBG syndromeRepressor ProteinsPhenotypeNeurologySlowing EEG activityANKRD11; KBG; Seizures; Slowing EEG activity; SyndromeFemaleNeurology (clinical)businessSeizure
researchProduct

Evaluation Of Massive Parallel Sequencing As A Diagnostic Tool For Familial Hypercholesterolemia

2015

Abstract Familial hypercholesterolemia (FH) is one of the most common single gene disorders, which is mostly inherited as an autosomal dominant trait. The physical signs of FH are elevated low density lipoprotein cholesterol (LDL-C), elevated total cholesterol (TC) levels and tendon xantomas. Identification and early treatment of affected individuals is desirable and in lack of physical symptoms DNA-based diagnosis provides confirmation of diagnosis and enables early patient management. The majority of FH cases are caused by mutations in four genes (APOB, LADLR, PCSK9, and LDLRAP1). There are commercial kits available for testing of the 20 most common FH causing mutations, but the spectrum …

Pediatricsmedicine.medical_specialtyldlrApolipoprotein Bldlrap1ScienceLow density lipoprotein cholesterolFamilial hypercholesterolemiachemistry.chemical_compoundngsmedicinepcsk9MultidisciplinaryMassive parallel sequencingfamilial hypercholesterolemiabiologyCholesterolPCSK9QAutosomal dominant traitmedicine.diseasechemistryapobLDL receptorbiology.proteinlipids (amino acids peptides and proteins)Proceedings of the Latvian Academy of Sciences. Section B. Natural, Exact, and Applied Sciences.
researchProduct

Exploring the diversity of the human blood virome

2021

This article belongs to the Special Issue Virus Bioinformatics 2022.

PegivirusDiseaseGenome ViralMicrobiologyGenomeVirusArticleVirologyPegivirusHumansHuman viromeVirus discoveryMassive parallel sequencingbiologyBlood viromeViromebiology.organism_classificationAnellovirusQR1-502Healthy VolunteersOrphan virusInfectious DiseasesEvolutionary biologyMetagenomicsSpainVirusesMetagenomicsOrphan virusorphan virus; blood virome; anellovirus; pegivirus; virus discovery; metagenomics
researchProduct

In vivo phage display: identification of organ-specific peptides using deep sequencing and differential profiling across tissues.

2021

Abstract In vivo phage display is widely used for identification of organ- or disease-specific homing peptides. However, the current in vivo phage biopanning approaches fail to assess biodistribution of specific peptide phages across tissues during the screen, thus necessitating laborious and time-consuming post-screening validation studies on individual peptide phages. Here, we adopted bioinformatics tools used for RNA sequencing for analysis of high-throughput sequencing (HTS) data to estimate the representation of individual peptides during biopanning in vivo. The data from in vivo phage screen were analyzed using differential binding—relative representation of each peptide in the target…

Phage displayT7 phageAcademicSubjects/SCI00010virusesPeptideBiopanningComputational biologyDeep sequencing03 medical and health sciencesMiceIn vivoPeptide LibraryGeneticsAnimalsTissue DistributionMolecular Biology030304 developmental biologychemistry.chemical_classification0303 health sciencesMice Inbred BALB Cbiology030302 biochemistry & molecular biologyRNAHigh-Throughput Nucleotide Sequencingbiology.organism_classificationHigh-Throughput Screening AssayschemistryCell Surface Display TechniquesPeptidesHoming (hematopoietic)Nucleic acids research
researchProduct

Phylogenetic relationships among Flavescence doree strains and related phytoplasmas determined by heteroduplex mobility assay and sequence of ribosom…

2003

Heteroduplex mobility assay (HMA) and DNA sequencing were performed on Flavescence doree (FD) phytoplasma strains and related phytoplasmas belonging to the elm yellows group. Part of the ribosomal RNA gene operon and a nonribosomal DNA region were utilized for phylogenetic analyses. Two FD strains, FD92 and FD-D, detected in France and Italy, respectively, were identical in both DNA fragments, confirming previous results. Other FD strains were all very similar and most closely resembled ALY, an Italian alder phytoplasma. Phytoplasmas associated with German Palatinate grapevine yellows were shown to form a distinct subcluster, also different from the elm yellows phytoplasma subcluster. Strai…

Phylogenetic treegrapevine yellowsGrapevine yellowsPlant ScienceElm yellowsHorticultureRibosomal RNABiology16SrV groupbiology.organism_classificationVirologyDNA sequencinggrapevinePhytoplasmaGenetics16SrV group; epidemiology; grapevine; grapevine yellowsepidemiologyFlavescence doréeAgronomy and Crop ScienceHeteroduplexPlant Pathology
researchProduct

Complete Genome Sequence of Acidaminococcus intestini RYC-MR95, a Gram-Negative Bacterium from the Phylum Firmicutes

2011

ABSTRACT Acidaminococcus intestini belongs to the family Acidaminococcaceae , order Selenomonadales , class Negativicutes , phylum Firmicutes . Negativicutes show the double-membrane system of Gram-negative bacteria, although their chromosomal backbone is closely related to that of Gram-positive bacteria of the phylum Firmicutes . The complete genome of a clinical A. intestini strain is here presented.

Phylum FirmicutesMolecular Sequence DataVeillonellaceaeBiologyMicrobiologyGenomeMicrobiologyEvolution Molecular03 medical and health sciencesGram negative bacteriumHumansAcidaminococcusMolecular Biology030304 developmental biologyGeneticsWhole genome sequencing0303 health sciencesAcidaminococcus intestiniNegativicutesBase Sequence030306 microbiologybiology.organism_classificationGenome AnnouncementsGram-Negative Bacterial InfectionsGenome BacterialBacteriaJournal of Bacteriology
researchProduct

Mapping of Polytene Chromosomes

2000

Principle and Polytene chromosomes consist of up to several thousands of chromatids applications and are therefore especially suitable for direct mapping with the help ofIn situhybridization. With the introduction of nonradioactive labeling and detection methods, e.g., fluorescenceIn situhybridization (FISH) (Lan-ger-Safer et al., 1982), theIn situhybridization procedure has become easy to perform and the results can be obtained within a day. Furthermore, the method described here (Schmidt et al., 1988; Schmidt, 1992) is a simplified version which additionally allows for the hybridization of more than one DNA probe simultaneously. This double or multicolor hybridization results in very prec…

Physicschemistry.chemical_compoundPolytene chromosomechemistryHybridization probefungiChromosomeChromatidA-DNAComputational biologyGeneDNADNA sequencing
researchProduct

Poster Presentations

2014

Administration of recombinant human erythropoietin (rHuEpo) improves performance and hence is subject to abuse by athletes. The detection of rHuEpo doping remains a major challenge at present. The aim of the current study was to investigate whether circulating microRNA (miRNA) can be used for detecting r-HuEpo doping. Twenty trained males received rHuEpo injections of 50 IU∙kg -1 body mass every two days for 4 weeks. Blood was obtained 2 weeks before, during and 4 weeks after administration. For this pilot analysis, plasma miRNA expression was assessed at selected time points using the Affymetrix GeneChip 3.0 and the miScript 384 HC PCR Array (Qiagen). For the Affymetrix microarray data, GC…

PhysiologyBiologyMolecular biologyDNA sequencingFold changelaw.inventionCirculating MicroRNAErythropoietinlawmicroRNAGene chip analysismedicineRecombinant DNAQuantile normalizationmedicine.drugActa Physiologica
researchProduct

Phytophthora Root and Collar Rot of Paulownia, a New Disease for Europe

2021

Paulownia species are fast growing trees native to China, which are being grown in managed plantings in several European countries for the production of wood and biomasses. In 2018, wilting, stunting, leaf yellowing, and collapse, as a consequence of root and crown rot, were observed in around 40% of trees of a 2-year-old planting of Paulownia elongata × P. fortunei in Calabria (Southern Italy). Two species of Phytophthora were consistently recovered from roots, basal stem bark, and rhizosphere soil of symptomatic trees and were identified as Ph. nicotianae and Ph. palmivora on the basis of both morphological characteristics and phylogenetic analysis of rDNA ITS sequences. Koch’s postulates…

Phytophthora heterosporaphPhytophthora palmivoraPaulowniacomplex mixturesPaulownia elongataRoot rotDNA sequencing; phpathogenicityDNA sequencingQK900-989Plant ecologyBiomass and timber DNA sequencing Nursery plants Pathogenicity Paulownia elongata × P. fortunei Phylogenetic analysis Phytophthora heterospora Phytophthora nicotianae Phytophthora palmivora Princess tree Tree of lifeRhizospherePaulownia elongata × P. fortuneibiologyprincess tree; tree of life; Phytophthora nicotianae; Phytophthora palmivora; Phytophthora heterospora; DNA sequencing; phylogenetic analysis; managed plantings; biomass and timber; nursery plants; pathogenicityphylogenetic analysis<i>Phytophthora palmivora</i>fungiSettore AGR/12 - Patologia Vegetalefood and beveragesForestryPhytophthora nicotianaePhytophthora palmivoraPhytophthora nicotianaebiology.organism_classification<i>Phytophthora heterospora</i>Horticulturetree of lifeCollar rot<i>Phytophthora nicotianae</i>princess treePhytophthoraprincess tree; tree of life; <i>Phytophthora nicotianae</i>; <i>Phytophthora palmivora</i>; <i>Phytophthora heterospora</i>; DNA sequencing; phylogenetic analysis; <i>Paulownia elongata</i> × <i>P. fortunei</i>; biomass and timber; nursery plants; pathogenicityForests; Volume 12; Issue 12; Pages: 1664
researchProduct