Search results for "Sex Determination"

showing 10 items of 34 documents

Loss of function mutation in the palmitoyl-transferase HHAT leads to syndromic 46,XY disorder of sex development by impeding Hedgehog protein palmito…

2014

The Hedgehog (Hh) family of secreted proteins act as morphogens to control embryonic patterning and development in a variety of organ systems. Post-translational covalent attachment of cholesterol and palmitate to Hh proteins are critical for multimerization and long range signaling potency. However, the biological impact of lipid modifications on Hh ligand distribution and signal reception in humans remains unclear. In the present study, we report a unique case of autosomal recessive syndromic 46,XY Disorder of Sex Development (DSD) with testicular dysgenesis and chondrodysplasia resulting from a homozygous G287V missense mutation in the hedgehog acyl-transferase (HHAT) gene. This mutation…

MaleCancer Research[SDV]Life Sciences [q-bio]medicine.disease_causeCell Fate DeterminationMiceTestisMorphogenesisMissense mutationddc:576.5Genetics (clinical)MutationHomozygoteCell DifferentiationHedgehog signaling pathwayPedigreeCell biologyFemaleSignal transductionSignal TransductionResearch Articlemedicine.medical_specialtylcsh:QH426-470LipoylationMolecular Sequence DataMutation MissenseBiologyPalmitoylationHHATInternal medicineGeneticsmedicineAnimalsHumansHedgehog ProteinsAmino Acid SequenceMolecular BiologyHedgehogEcology Evolution Behavior and SystematicsDisorder of Sex Development 46XY[ SDV ] Life Sciences [q-bio]Sequence Homology Amino AcidBiology and Life SciencesSex Determinationlcsh:GeneticsEndocrinology46 XY Disorders of Sex Development/*genetics; Acyltransferases/chemistry/*genetics/metabolism; Amino Acid Sequence; Animals; Female; Hedgehog Proteins/*metabolism; Homozygote; Humans; Lipoylation/*genetics; Male; Mice; Molecular Sequence Data; *Mutation Missense; Pedigree; Sequence Homology Amino Acid; Signal Transduction/*genetics; Testis/embryologyLipid modificationAcyltransferasesDevelopmental Biology
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Differential metabolic profiling of non-pure trisomy 21 human preimplantation embryos.

2012

Objective To investigate the metabolomic signature of trisomy 21 preimplantation human embryos by a noninvasive approach using mass spectrometry– (MS-) and nuclear magnetic resonance spectroscopy– (NMR-) based metabolic profiling platforms. Design A total of 171 spent media samples were collected from day 3 embryos and comparatively analyzed by MS analysis (chromosomally normal embryos, n=15; trisomy 21 embryos, n=15) and a matched control media group (without embryo, n=14) and by NMR spectroscopy (normal embryos, n=39; trisomy 21 embryos, n=35; monosomy 21 embryos, n=24) and a matched control media group (without embryo, n=29). Setting IVF clinic/preimplantation genetic diagnosis (PGD) uni…

MaleDown syndromeSex Determination Analysisanimal structuresMagnetic Resonance SpectroscopyAneuploidyFertilization in VitroBiologyPreimplantation genetic diagnosisAndrosteroneGas Chromatography-Mass SpectrometryAndrologyEmbryo Culture Techniqueschemistry.chemical_compoundPredictive Value of TestsPregnancymedicineHumansMetabolomicsBlastocystCaproatesIn Situ Hybridization FluorescencePreimplantation DiagnosisGeneticsAndrosteroneObstetrics and GynecologyEmbryomedicine.diseaseAneuploidyCulture Mediamedicine.anatomical_structureBlastocystReproductive MedicinechemistryCase-Control Studiesembryonic structuresFeasibility StudiesFemaleDown SyndromeTrisomyChromosome 21BiomarkersChromatography LiquidFertility and sterility
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Molecular markers for germ cell differentiation in the demosponge Suberites domuncula

2004

Sponges (phylum Porifera) are simple metazoans for which no molecular information on gametogenesis and larval development is available. To support the current study, it was confirmed by histology that oocytes and larvae were produced by the demosponge Suberites domuncula. Three genes/expressed products from S. domuncula whose expression correlated with sexual reproduction were identified and characterized (they are used here as marker genes): i) a receptor tyrosine kinase (RTK) with sequence similarity in the tyrosine kinase domain to fibroblast growth factor receptors; ii) the sex-determining protein FEM1 and iii) the sperm associated antigen (SAA) of triploblasts. Antibodies against the e…

MaleEmbryologyMolecular Sequence DataReceptor tyrosine kinaseDemospongemedicineAnimalsAmino Acid SequenceAntigensPhylogenyGametogenesisCaenorhabditis elegansGeneticsBase SequenceSequence Homology Amino AcidbiologyfungiGene Expression Regulation DevelopmentalReceptor Protein-Tyrosine KinasesCell DifferentiationDNASex Determination Processesbiology.organism_classificationSpermatozoaCell biologySuberites domunculamedicine.anatomical_structureFibroblast growth factor receptorOocytesbiology.proteinFemaleSeasonsSuberitesTyrosine kinaseBiomarkersGerm cellDevelopmental Biology
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Distribution of heterochromatin on the mitotic chromosomes of Musca domestica L. in relation to the activity of male-determining factors

1998

In the housefly, male sex is determined by a dominant factor, M, located either on the Y, on the X, or on any of the five autosomes. M factors on autosome I and on fragments of the Y chromosome show incomplete expressivity, whereas M factors on the other autosomes are fully expressive. To test whether these differences might be caused by heterochromatin-dependent position effects, we studied the distribution of heterochromatin on the mitotic chromosomes by C-banding and by fluorescence in situ hybridization of DNA fragments amplified from microdissected mitotic chromosomes. Our results show a correlation between the chromosomal position of M and the strength of its male-determining activity…

MaleEuchromatinHeterochromatinMitosisBiologyY chromosomePolymerase Chain ReactionChromosomeschemistry.chemical_compoundHeterochromatinHousefliesGeneticsmedicineAnimalsMitosisIn Situ Hybridization FluorescenceGenetics (clinical)GeneticsB chromosomeSex ChromosomesAutosomemedicine.diagnostic_testGene Expression Regulation DevelopmentalSex Determination ProcessesMolecular biologyChromosome BandingchemistryDNA Transposable ElementsFemaleDNAFluorescence in situ hybridizationChromosoma
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Quantitative parameters and ecological implications of a specialized tritrophic interaction involving a seed-feeding tortricid, Pseudargyrotoza conwa…

2014

Producción Científica

MaleLigustrum vulgareLigustrumWaspsPopulationEcologíaHymenopteraMothsDiapause Insectmedicine.disease_causeparasitism rateParasitoidInfestationparasitoid sex ratiomedicineAnimalseducationEcosystemeducation.field_of_studyBosques y silvicultura - Españabiologyseed infestation ratePlantas silvestresEcologyfungiPrivetfood and beveragesPlantas - Enfermedades y plagas - Españaplant fitnessFeeding BehaviorGeneral MedicineSex Determination Processesbiology.organism_classificationseed-inhabiting insectslife cycles3108 FitopatologíaSpain3103.09 Cultivos de Plantas3106 Ciencia ForestalFruitLarvaInsect ScienceOleaceaePapersSeedsFemaleInsectos perjudiciales y útilesBraconidaeJournal of Insect Science
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Amelogenin test: From forensics to quality control in clinical and biochemical genomics.

2007

Abstract Background The increasing number of samples from the biomedical genetic studies and the number of centers participating in the same involves increasing risk of mistakes in the different sample handling stages. We have evaluated the usefulness of the amelogenin test for quality control in sample identification. Methods Amelogenin test (frequently used in forensics) was undertaken on 1224 individuals participating in a biomedical study. Concordance between referred sex in the database and amelogenin test was estimated. Additional sex-error genetic detecting systems were developed. Results The overall concordance rate was 99.84% (1222/1224). Two samples showed a female amelogenin test…

MaleQuality ControlSex Determination AnalysisConcordancemedia_common.quotation_subjectClinical BiochemistryMale sex determinationGenomicsBiologyBioinformaticsBiochemistrystomatognathic systemHumansQuality (business)media_commonRandomized Controlled Trials as TopicAmelogeninBiochemistry (medical)Reproducibility of ResultsGeneral MedicineDNAGenomicsForensic MedicineDNA extractionTest (assessment)MicrosatelliteElectrophoresis Polyacrylamide GelFemaleAmelogeninDatabases Nucleic AcidClinica chimica acta; international journal of clinical chemistry
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Y chromosomes: born to be destroyed

2005

Suppression of recombination is the prerequisite for stable genetically determined sex systems. A consequence of suppression of recombination is the strong bias in the distribution of transposable elements (TEs), mostly retrotransposons. Our results and those from others indicate that the major force driving the degeneration of Y chromosomes are retrotransposons in remodelling former euchromatic chromosome structures into heterochromatic ones. We put forward the following hypotheses. (1) A massive accumulation of retrotransposons occurs early in non-recombining regions. (2) Heterochromatic nucleation centres are formed as a genomic defence mechanism against invasive parasitic elements. The …

MaleRecombination GeneticTransposable elementGeneticsDosage compensationRetroelementsEuchromatinHeterochromatinGene DosageRetrotransposonSex Determination ProcessesBiologyY chromosomeGene dosageGeneral Biochemistry Genetics and Molecular BiologyEvolution MolecularHeterochromatinY ChromosomeAnimalsHumansDrosophilaFemaleGene SilencingGeneBioEssays
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Sex estimation by tooth dimension in a contemporary Spanish population.

2020

Aim: Sex determination is a fundamental step in the biologic profile reconstruction of unknown individuals. Teeth are frequently recovered intact, even in case of natural or mass disasters, fires, crashes or accidents. Therefore, they are very valuable in sex determination in a forensic and anthropological context. The objective of this study is to identify a method for sex determination using the mesio-distal widths of permanent teeth, in a contemporary Spanish sample. Method: The mesio-distal dimensions of permanent teeth were obtained from study casts derived from patients seeking treatment at the orthodontic clinic of the Universidad Europea de Valencia. A total of 210 patients were inc…

MaleSex Determination AnalysisAdolescentPopulationOdontologíaContext (language use)SexoLogistic regressionPathology and Forensic MedicineStatistical significanceStatisticsMedicineHumanseducationOdontometríaPermanent teethAntropologíaeducation.field_of_studyPrincipal Component AnalysisDentitionbusiness.industryMedicina forenseModels DentalDentition PermanentLogistic ModelsSpainPrincipal component analysisInclusion and exclusion criteriaFemalebusinessLawToothForensic DentistryForensic science international
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Computer-assisted sperm morphometry fluorescence-based analysis has potential to determine progeny sex

2016

This study was designed to determine the ability of computer-assisted sperm morphometry analysis (CASA-Morph) with fluorescence to discriminate between spermatozoa carrying different sex chromosomes from the nuclear morphometrics generated and different statistical procedures in the bovine species. The study was divided into two experiments. The first was to study the morphometric differences between X- and Y-chromosome-bearing spermatozoa (SX and SY, respectively). Spermatozoa from eight bulls were processed to assess simultaneously the sex chromosome by FISH and sperm morphometry by fluorescence-based CASA-Morph. SX cells were larger than SY cells on average (P < 0.001) although with impo…

MaleSex Determination Analysisendocrine systemUrology[SDV]Life Sciences [q-bio]SemenInvited Original ArticleSexingSemen analysisBiologylcsh:RC870-923mammalian spermotozoasperm morphometryAndrology03 medical and health sciencesbull; computer-assisted sperm morphometry analysis; sexing; sperm morphometry0302 clinical medicineDiscriminant function analysismedicineAnimalssexingbullCell Shapereproductive and urinary physiologyx-chromosome-bearingnuclear shapeCell NucleusMorphometrics030219 obstetrics & reproductive medicinemedicine.diagnostic_testurogenital system0402 animal and dairy scienceChromosome04 agricultural and veterinary sciencesGeneral MedicineAnatomylcsh:Diseases of the genitourinary system. UrologySpermatozoa040201 dairy & animal scienceSpermSemen AnalysisMicroscopy FluorescenceSex Determination AnalysisCattlex-chromosome-bearing;mammalian spermotozoa;nuclear shapecomputer-assisted sperm morphometry analysis
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Sex change in plants and animals: a unified perspective

2014

The capacity of organisms to change their sex has evolved independently in several plant and animal lineages. Sex change has been widely studied, but research approaches have differed for plants and animals, and conclusions have often been taxon-specific. Although sex allocation theory provides a unifying framework for the study of sex change, this unity has not always been appreciated, especially in the botanical literature. Here, we review sex change with regard to its representation in relation to taxonomy and other sexual systems, with regard to its suggested adaptive benefits, and to the role of taxon-specific body architecture, such as modularity and gonadal structure. We highlight di…

MaleSex DifferentiationGonadal structureEcologyReproductionfungiFlowersSex Determination ProcessesBiologyBiological EvolutionSex changeEvolutionary biologyAnimalsFemaleHermaphroditic Organismssense organsskin and connective tissue diseasesEcology Evolution Behavior and SystematicsSex allocationJournal of Evolutionary Biology
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