Search results for "Spherocytosis"

showing 4 items of 4 documents

Recombinant erythropoietin vs. blood transfusion care in infants with hereditary spherocytosis: a retrospective cohort study of A.I.E.O.P. patients (…

2017

MalePediatricsmedicine.medical_specialtyBlood transfusionReticulocytesAnemiamedicine.medical_treatmentSpherocytosisSpherocytosisMEDLINEErythrocyte Count; Erythropoietin; Female; Follow-Up Studies; Hemoglobins; Humans; Infant; Infant Newborn; Italy; Male; Recombinant Proteins; Reticulocytes; Retrospective Studies; Spherocytosis Hereditary; Blood Transfusion; HematologyHereditary spherocytosis03 medical and health sciencesHemoglobins0302 clinical medicinemedicineHumansBlood TransfusionRecombinant erythropoietinErythropoietinErythrocyte Count; Erythropoietin; Female; Follow-Up Studies; Hemoglobins; Humans; Infant; Infant Newborn; Italy; Male; Recombinant Proteins; Reticulocytes; Retrospective Studies; Spherocytosis Hereditary; Blood TransfusionRetrospective Studiesbusiness.industryInfantRetrospective cohort studyHematologymedicine.diseaseNewbornRecombinant ProteinsSurgeryHereditaryItalyErythropoietin030220 oncology & carcinogenesisErythrocyte Count030211 gastroenterology & hepatologyFemalebusinessmedicine.drugFollow-Up Studies
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Sepsis due to Streptococcus pneumoniae associated with secondary hemophagocytic lymphohistiocytosis in a splenectomized patient for spherocytosis

2017

Abstract Rationale: Hemophagocytic lymphohistiocytosis (HLH) is a syndrome that is characterized by an inappropriate hyperinflammatory immune response – primary, as a consequence of a genetic defect of NK cells and cytotoxic T lymphocytes or – secondary, in the progression of infections, rheumatic or autoimmune diseases, malignancies or metabolic diseases. Patient concerns: We present the case of a secondary HLH due to Streptococcus pneumoniae infection in a splenectomised patient for spherocytosis, a 37-year-old patient who was splenectomised in childhood for spherocytosis, without immuneprophylaxis induced by antipneumococcal vaccine. Outcomes: He developed a severe pneumococcal sepsis as…

Secondary Hemophagocytic LymphohistiocytosisAdultMaleendocrine systemsplenectomized patientmedicine.medical_treatmentSpherocytosisSplenectomySpherocytosis Hereditarymedicine.disease_causeLymphohistiocytosis HemophagocyticPneumococcal InfectionsSepsis03 medical and health sciences0302 clinical medicineImmune systemFatal Outcomehemic and lymphatic diseasesSepsisStreptococcus pneumoniaemedicineCytotoxic T cellHumans030212 general & internal medicineClinical Case ReportHemophagocytic lymphohistiocytosisbusiness.industry4900General Medicinemedicine.diseaseStreptococcus pneumoniaehemophagocytic lymphohistiocytosis030220 oncology & carcinogenesisImmunologySplenectomybusinessResearch ArticleHLHMedicine
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Eventi vascolari correlati ad alcune condizioni di iperviscosità sclerocitemica

2014

Settore MED/09 - Medicina Internaerythrocyte membrane hereditary spherocytosis hereditary elliptocytosis acanthocytosis
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Reliability of EMA Binding Test in Diagnosis of Hereditary Spherocytosis in Italian Patients

2010

medicine.medical_specialtySpherocytosisSpherocytosis HereditaryGastroenterologyFluorescenceHereditary spherocytosisPredictive Value of TestsInternal medicinemedicineHumansReliability (statistics)business.industryErythrocyte MembraneHereditary Spherocytosis EMA Binding Test ROC analysisMembrane ProteinsHematologyGeneral MedicineFlow Cytometrymedicine.diseaseErythrocyte membraneItalyROC CurvePredictive value of testsEosine Yellowish-(YS)Electrophoresis Polyacrylamide Gelbusiness
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