Search results for "Storage"

showing 10 items of 1239 documents

Fetal presentation of Morquio disease type A.

1992

A fetus with mucopolysaccharidosis type IV A (Morquio type A) is described. The family had one affected child exhibiting symptoms of classical Morquio A disease, and late in the subsequent pregnancy prenatal diagnosis was requested. At 23 weeks' gestation, moderate ascites was detected by detailed ultrasound scan and keratan sulphate was found in the amniotic fluid. The pregnancy was terminated by prostaglandin induction and the diagnosis of mucopolysaccharidosis type IV A was confirmed by demonstration of a deficiency of N-acetylgalactosamine-6-sulphate (GalNac-6-S) sulphatase in cultured amniotic cells and in post-mortem fibroblast cultures. The activities of beta-galactosidase and arylsu…

ElectrophoresisMalemedicine.medical_specialtyAmniotic fluidPlacentaMucopolysaccharidosis type IVNeuraminidasePrenatal diagnosisConsanguinityPregnancyHydrops fetalisInternal medicineLysosomal storage diseaseMedicineHumansChildGenetics (clinical)GlycosaminoglycansUltrasonographyFetusPregnancybusiness.industryObstetrics and GynecologyAscitesMucopolysaccharidosis IVmedicine.diseaseAmniotic Fluidbeta-GalactosidaseEndocrinologyKeratan SulfatePregnancy Trimester SecondMucopolysaccharidosis IVAmniocentesisFemaleSulfatasesbusinessPrenatal diagnosis
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39 Formation of a Lysosomal Disease Testing Network to enhance the delivery of diagnostic services to patients with lysosomal storage disorders

2007

Endocrinologybusiness.industryEndocrinology Diabetes and MetabolismGeneticsMedicineSubstrate reduction therapyLysosomal storage disordersDiseaseBioinformaticsbusinessMolecular BiologyBiochemistryMolecular Genetics and Metabolism
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Inovācijas, pētniecība, zinātne

2013

Quantum computing algorithms and peat extracts, a Chinese dictionary and skin stem cells, carbon nanowire switches and a catalogue of stars – the research results produced by the University of Latvia scientists are as varied as the directions of studies at the University of Latvia. Our goal is to provide science-based higher education in the key areas of consequence for Latvia’s people, economy, nature and public health, to make Latvia known in the world through our achievements in science and innovation. Over the past few years the research of the UL scientists has been extremely productive, largely due to the European Union funds to support graduate and doctoral students, new research gro…

Energoresursi un to uzglabāšanaVideCosmeticsEnergy resources and their storageEnvironmentPārtikaComputer scienceHorticulture and breedingDārzkopība un selekcijaDatorikaUzziņu literatūraFoodBūvniecībaReference literatureMedicineSabiedrības attīstība un identitāteDevelopment of society and identityMedicīnaKosmētikaConstruction
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Review of sustainable solar hydrogen production using photon fuel on artificial leaf

2017

Abstract Energy conversion from the renewable energy sources with suitable energy storage plays a vital role in the sustainable development. Sustainable hydrogen production from the solar energy is well suited for energy storage applications because of inherent high mass energy density of hydrogen. This manuscript reviewing the techniques required for the sustainable solar hydrogen production using photon fuel on artificial leaf, i.e. solar cell. The designing and assembling of artificial solar leaf, which is the replica of natural leaf and capable of harnessing full solar spectrum, are deliberated. This technology for sustainable solar hydrogen production will overlay a viable way for more…

Energy Engineering and Power TechnologyNanotechnology02 engineering and technology010402 general chemistry01 natural sciencesEnergy storagelaw.inventionlawSolar cellAstrophysics::Solar and Stellar AstrophysicsEnergy transformationProcess engineeringHydrogen productionRenewable Energy Sustainability and the Environmentbusiness.industry021001 nanoscience & nanotechnologyCondensed Matter PhysicsSolar energySolar fuel0104 chemical sciencesRenewable energyPhotovoltaic thermal hybrid solar collectorFuel TechnologyPhysics::Space PhysicsEnvironmental science0210 nano-technologybusinessInternational Journal of Hydrogen Energy
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Study, project and implementation of new metrics for distributed measurement system in medium voltage smart grid

2022

Energy Management SystemIEEE 1459-2010Arc faultPower qualityenergy storage system batteryUL 1699Bsmart gridBattery Management Systemrenewable energySettore ING-INF/07 - Misure Elettriche E Elettroniche
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Use of the residual capacities of existing reservoirs as storage of the electricity produced by grid-connected intermittent RES plants, by means of p…

2013

Energy StorageRenewable Energy Sources (RES)Pumped Hydroelectric storage (PHS)
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Perspective on hydrogen energy carrier and its automotive applications

2014

The paper outlines the concept of energy carrier with a particular reference to hydrogen, in view of a more disseminated employment in the field of automotive applications. In particular hydrogen production is analyzed considering the actual state of the art and recent technologies applied in production from the primary sources (fossil fuels, renewable energies, and water electrolysis). Then the problem of hydrogen storage is considered both from technical and economical point of views. In particular, differences between physical and chemical storage are here considered with a particular glance to the most innovative technologies including carbon nanostructures. A review on the main problem…

Energy carrierEnergy carrierRenewable Energy Sustainability and the Environmentbusiness.industryComputer scienceFossil fuelAutomotive industryEnergy Engineering and Power TechnologyStorageNanotechnologyTransportationSettore ING-IND/32 - Convertitori Macchine E Azionamenti ElettriciCondensed Matter PhysicsRenewable energyHydrogen storageFuel TechnologyHydrogen safetyRisk analysis (engineering)Hydrogen fuelbusinessHydrogen productionHydrogen
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Different energy balances for the redesign of nearly net zero energy buildings: An Italian case study

2015

Abstract The currently developing concept of a Net Zero Energy Building introduces new challenges and research problems. The calculation of a net zero energy balance is heavily influenced by the energy carrier weighting factors that are chosen, which can deeply influence the future energy market towards adopting specific energy technologies. The following paper proposes an analysis of different definitions and conventions for Net Zero Energy Buildings that employ different calculation methodologies and apply different weighting factors to an Italian case study. The case study, which is called “the Leaf House”, is one of the first examples of a nearly net zero energy building in Italy. A bui…

Energy carrierEngineeringMathematical optimizationZero-energy buildingSettore ING-IND/11 - Fisica Tecnica AmbientalePrimary energyRenewable Energy Sustainability and the Environmentbusiness.industryBuilding simulation Net Zero Energy Building Redesign Sensitivity analysis TRNSYS energy balance Weighting factors Primary energyMechanical engineeringEnergy accountingEnergy storageRenewable energySpecific energyEnergy marketbusiness
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Mixed heuristic-non linear optimization of energy management for hydrogen storage-based multi carrier hubs

2014

In this paper, an heuristic and non-linear programming based algorithm to optimally operate an energy hub plant is proposed. The energy hub plant described in this work is the test system for the European INGRID research project. The Energy Management System defines the optimal energy flows dispatch in order to obtain the energy balance and the maximum profit for the owner of the plant. The problem is highly constrained and non-linear, for this reason the methodology cannot rely on Linear Programming (LP) methods. The Energy Management System manages two energy carriers, electricity and hydrogen, interfacing three distribution networks: the electricity, the hydrogen and the methane networks…

Energy carrierMathematical optimizationEngineeringLinear programmingEnergy managementHeuristicbusiness.industryEnergy balanceTabu searchDSOEnergy Management SystemsStorage Integrationheuristic methodsnon-linear problemsSettore ING-IND/33 - Sistemi Elettrici Per L'EnergiaEnergy management systemSimulated annealingbusiness2014 IEEE International Energy Conference (ENERGYCON)
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Analysis of operator human errors in hydrogen refuelling stations: Comparison between human rate assessment techniques

2013

Abstract The use of hydrogen as an energy carrier for road transport appears to be an optimal solution for the reduction of greenhouse gas emissions. Nevertheless, the development of this technology depends on the growth and diffusion of production, storage and refuelling infrastructures together with accurate risk analyses to appropriately design the safety and management systems used in these plants. Moreover, to improve safety standards, it is also important to focus attention on the estimation of hazards related to human factors, as this is one of the major causes leading to accidental events, especially in complex industrial technology. The paper reports a case study relevant to operat…

Energy carrierRisk analysisRenewable Energy Sustainability and the EnvironmentComputer scienceFuzzy setFuzzy HEARTEnergy Engineering and Power TechnologySafety standardsCondensed Matter PhysicsHydrogen refuelling stationReliability engineeringRisk analysiFuel TechnologyIndustrial technologyGreenhouse gasManagement systemStorage unitHuman errorHuman error assessment and reduction techniqueCREAMSettore ING-IND/19 - Impianti Nucleari
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