Search results for "Trie"

showing 10 items of 4468 documents

Characteristics and management of primary and other immune thrombocytopenias: Spanish registry study

2017

The natural history and its modulation by treatments administered for immune thrombocytopenia (ITP) in the clinical practice remains unknown. In addition, little information is available on the characteristics and management of ITP in Spain. We conducted an observational, multicenter, registry in 70 Hematology Services from Spain between 2009 and 2011, which included children from 2 months of age and adults with primary ITP or another ITP diagnosed within the last 6 months (platelet count [PC]  484 patients were included (median [Q1, Q3] age 52 [29,74] years, 87.6% adults), 56% women, 10.5% with secondary ITP. Median (Q1, Q3) PC at diagnosis was 12 × 109/l (4, 32); 72% of patients had bleed…

MalePediatricsRegistry studyComorbidity030204 cardiovascular system & hematologycorticosteroids0302 clinical medicineAdrenal Cortex Hormonesimmune system diseaseshemic and lymphatic diseasesRegistriesChildresponseHematologyDisease ManagementImmunoglobulins IntravenousHematologyMiddle AgedClinical PracticeNatural historyPhenotypeTreatment OutcomeIntravenous ImmunoglobulinsChild PreschoolFemaleAlgorithmsAdultmedicine.medical_specialtyAdolescentHemorrhageintravenous immunoglobulinsYoung Adult03 medical and health sciencesImmune systemInternal medicinemedicineHumansAgedPurpura Thrombocytopenic IdiopathicPlatelet Countbusiness.industryInfantImmune thrombocytopeniaImmune thrombocytopeniaSpainObservational studybusinessBiomarkers030215 immunologyHematology
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Disease and patient characteristics in NP-C patients: findings from an international disease registry.

2013

Abstract Background Niemann-Pick disease type C (NP-C) is a rare neurovisceral disease characterized by progressive neurodegeneration and premature death. We report data recorded at enrolment in an ongoing international NP-C registry initiated in September 2009 to describe disease natural history, clinical course and treatment experience of NP-C patients in clinical practice settings. Methods The NPC Registry is a prospective observational cohort study. Participating sites are encouraged to evaluate all consecutive patients with a confirmed diagnosis of NP-C, regardless of their treatment status. All patients undergo clinical assessments and medical care as determined by their physicians. D…

MalePediatricslcsh:Medicine[SDV.GEN] Life Sciences [q-bio]/Genetics0302 clinical medicineMiglustatDiagnosisGenetics(clinical)Pharmacology (medical)Prospective StudiesRegistriesAge of OnsetEnzyme InhibitorsChildProspective cohort studyGenetics (clinical)Medicine(all)0303 health sciencesCholestasisNiemann-Pick disease type CNiemann-Pick Disease Type CGeneral MedicineDysphagia3. Good healthChild PreschoolCohortNeurologicalFemalemedicine.symptomCohort studymedicine.drugHepatomegalymedicine.medical_specialty1-DeoxynojirimycinAtaxiaAdolescent03 medical and health sciencesDisease registrymedicineHumansDisabled PersonsVertical supranuclear palsy030304 developmental biology[SDV.GEN]Life Sciences [q-bio]/Geneticsbusiness.industryResearchlcsh:RInfantMutationSymptomsSplenomegalyAge of onsetbusiness030217 neurology & neurosurgery
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Survival and cure trends for European children, adolescents and young adults diagnosed with acute lymphoblastic leukemia from 1982 to 2002

2013

Proportion cured is a potentially more informative cancer outcome measurement than 5-year survival. We present population-based estimates of cure for young patients diagnosed with acute lymphoblastic leukemia in Europe from 1982 to 2002. Thirty-five European cancer registries provided data. Survival was estimated by age, period of diagnosis and European region, and used as input for parametric cure models, which assume cured patients have the same mortality as the general population. For acute lymphoblastic leukemia diagnosed in 1–14 year olds in 2000–2002, over 77% were estimated cured. The proportion cured improved significantly over the study period: an impressive 26–58% in infants (up t…

MalePediatricsmedicine.medical_specialtyAdolescentLymphoblastic LeukemiaPopulationacute lymphoblastic leukemiaHistory 21st Centuryacute lymphoblastic leukemia; children; adolescents and young adults; survival and cure trendsEurope/epidemiologyYoung AdultchildrenHumansMedicineRegistriesYoung adultChildeducationddc:613education.field_of_studybusiness.industryAge FactorsInfant NewbornAbsolute risk reductionInfantCancerHematologyPrecursor Cell Lymphoblastic Leukemia-LymphomaHistory 20th CenturyEuropean regionmedicine.diseasesurvival and cure trendsPrecursor Cell Lymphoblastic Leukemia-Lymphoma/epidemiology/history/mortalityChild PreschoolEarly adolescentsFemaleOriginal Articles and Brief Reportsbusinessadolescents and young adultsHaematologica
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Incidence, time trends and regional variation of childhood leukaemia in Germany and Europe.

2008

This paper presents data on the German and Europe-wide incidence, time trends and regional variations of childhood leukaemia. Data were provided by the German Childhood Cancer Registry (GCCR), a population-based cancer registry recording all cases of malignant diseases in children under 15 y of age residing in Germany and by the Automated Childhood Cancer Information System (ACCIS) co-ordinated at International Agency for Research on Cancer, Lyon, that combines and evaluates data from several European population-based cancer registries. The incidence of leukaemia (44.0 per million) has increased in Europe as well as in Germany in the last decades (0.6% annually on average). Germany shows no…

MalePediatricsmedicine.medical_specialtyAdolescentPopulationDisease OutbreaksGermanGermanymedicineHumansRadiology Nuclear Medicine and imagingRegistrieseducationChildChildhood Cancer Registryeducation.field_of_studyRadiationLeukemiaRadiological and Ultrasound TechnologyIncidence (epidemiology)IncidencePublic Health Environmental and Occupational HealthInfant NewbornCancerInfantGeneral Medicinemedicine.diseaselanguage.human_languageChildhood leukaemiaCancer registryEuropeGeographyRegional variationChild PreschoollanguageFemaleDemographyRadiation protection dosimetry
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Cancer patterns among children of Turkish descent in Germany: A study at the German Childhood Cancer Registry

2008

Abstract Background Cancer risks of migrants might differ from risks of the indigenous population due to differences in socioeconomic status, life style, or genetic factors. The aim of this study was to investigate cancer patterns among children of Turkish descent in Germany. Methods We identified cases with Turkish names (as a proxy of Turkish descent) among the 37,259 cases of childhood cancer registered in the German Childhood Cancer Registry (GCCR) during 1980–2005. As it is not possible to obtain reference population data for children of Turkish descent, the distribution of cancer diagnoses was compared between cases of Turkish descent and all remaining (mainly German) cases in the reg…

MalePediatricsmedicine.medical_specialtyAdolescentTurkeyTurkishPopulation610DiseaseGermanyNeoplasmsEpidemiologymedicineHumansRegistriesChildeducationSocioeconomic statusTransients and Migrantseducation.field_of_studyChildhood Cancer Registrybusiness.industryIncidenceIncidence (epidemiology)lcsh:Public aspects of medicinePublic Health Environmental and Occupational HealthInfantCancerlcsh:RA1-1270medicine.diseaselanguage.human_languageChild PreschoollanguageFemalebusinessResearch ArticleBMC Public Health
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The web-based ASSO-food frequency questionnaire for adolescents: relative and absolute reproducibility assessment

2014

Background A new food frequency questionnaire (FFQ) has been recently developed within the Italian Adolescents and Surveillance System for the Obesity prevention (ASSO) Project; it was found to be appropriate for ranking adolescents in food and nutrient levels of intake. The aim of this study was to assess the relative and absolute reproducibility of the ASSO-FFQ for 24 food groups, energy and 52 nutrients. Methods A test-retest study was performed on two ASSO-FFQs administered one month apart of each other to 185 adolescents, aged 14–17 and attending secondary schools in Palermo (Italy). Wilcoxon test assessed differences in median daily intakes between the two FFQs. Agreement was evaluate…

MalePediatricsmedicine.medical_specialtyAdolescentWilcoxon signed-rank testIntraclass correlationFood frequency questionnaireMedicine (miscellaneous)Carbonated BeveragesClinical nutritionSettore MED/42 - Igiene Generale E ApplicataDiet RecordsFood groupSurveys and QuestionnairesEnvironmental healthHumansMedicineObesityInternetReproducibilitySettore M-EDF/02 - Metodi E Didattiche Delle Attivita' SportiveNutrition and Dieteticsbusiness.industryAlcoholic BeveragesResearchdigestive oral and skin physiologyReproducibility of ResultsBreadmedicine.diseaseR1ObesityDiet RecordsReproducibilityDietItalyFood frequency questionnaire Reproducibility Adolescent Nutrient IntakeFoodIntakeFemaleEnergy IntakebusinessRAKappaNutrientNutrition Journal
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Are food intolerances and allergies increasing in immigrant children coming from developing countries ?

2006

There are not available data concerning the occurrence, the clinical features and the environmental risk factors for food intolerances and allergies in immigrant children. The aim of the study was to evaluate rates, distribution, clinical features and environmental risk factors for food intolerances and allergies in immigrant children. Hospital records of 4,130 patients with celiac disease (CD), cow milk protein intolerance (CMPI) and food allergies (FA) diagnosed in 24 Italian Centres from 1999 to 2001 were retrospectively reviewed, comparing immigrant patients with Italian ones. 78/4,130 (1.9%) patients were immigrant: 36/1,917 (1.9%) had CD, 24/1,370 (1.75%) CMPI and 18/843 (2.1%) FA. Th…

MalePediatricsmedicine.medical_specialtyAdolescentmedia_common.quotation_subjectImmunologyImmigrationPopulationEthnic groupDeveloping countryDiseaseallergieMiddle EastIntolerancesFood allergyEnvironmental healthmedicineHumansImmunology and AllergyEurope Easternfood intoleranceChildeducationDeveloping CountriesAsia SoutheasternRetrospective Studiesmedia_commoneducation.field_of_studybusiness.industryInfantfood intolerances and allergieEmigration and ImmigrationSouth Americaimmigrant childrenmedicine.diseaseFood intoleranceCeliac DiseaseCross-Sectional StudiesItalyChild PreschoolAfricaPediatrics Perinatology and Child HealthFemaleMilk HypersensitivitybusinessFood Hypersensitivity
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Competing-risk analysis of coronavirus disease 2019 in-hospital mortality in a Northern Italian centre from SMAtteo COvid19 REgistry (SMACORE).

2021

AbstractAn accurate prediction of the clinical outcomes of European patients requiring hospitalisation for Coronavirus Disease 2019 (COVID-19) is lacking. The aim of the study is to identify predictors of in-hospital mortality and discharge in a cohort of Lombardy patients with COVID-19. All consecutive hospitalised patients from February 21st to March 30th, 2020, with confirmed COVID-19 from the IRCCS Policlinico San Matteo, Pavia, Lombardy, Italy, were included. In-hospital mortality and discharge were evaluated by competing risk analysis. The Fine and Gray model was fitted in order to estimate the effect of covariates on the cumulative incidence functions (CIFs) for in-hospital mortality…

MalePediatricsmedicine.medical_specialtyCoronavirus disease 2019 (COVID-19)ScienceDiseases030204 cardiovascular system & hematologyCompeting risksRisk AssessmentArticle03 medical and health sciences0302 clinical medicinemedicineHumansCumulative incidence030212 general & internal medicineHospital MortalityRegistriesAgedAged 80 and overMultidisciplinaryIn hospital mortalitybusiness.industryQRCOVID-19Lower intensityMiddle AgedItalyViral infectionHospital admissionCohortMedicineInfectious diseasesFemaleRisk assessmentbusinessHumanScientific reports
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Prolongation du séjour hospitalier dans un service de gériatrie aiguë : identification et analyse des causes

2016

International audience; In France, the population of very old frail patients, who require appropriate high-quality care, is increasing. Given the current economic climate, the mean duration of hospitalization (MDH) needs to be optimized. This prospective study analyzed the causes of prolonged hospitalization in an acute geriatric care unit. Over 6 months, all patients admitted to the target acute geriatric care unit were included and distributed into two groups according to a threshold stay of 14 days: long MDH group (LMDHG) and short MDH group (SMDHG). These two groups were compared. 757 patients were included. The LMDHG comprised 442 with a mean age of 86.7 years, of whom 67.65% were wome…

MalePediatricsmedicine.medical_specialtyGeriatric caregériatrie aiguë[ SDV.MHEP.GEG ] Life Sciences [q-bio]/Human health and pathology/Geriatry and gerontology030204 cardiovascular system & hematologymean duration of hospitalizationpersonne âgée03 medical and health sciences0302 clinical medicinedurée moyenne de séjourMedicineElderly peopleHumans030212 general & internal medicineProspective StudiesBiological PsychiatryAgedfilière gériatriqueAged 80 and overgeriatric careelderly peoplebusiness.industry[SDV.MHEP.GEG]Life Sciences [q-bio]/Human health and pathology/Geriatry and gerontologyacute geriatricsLength of Stay3. Good healthNeuropsychology and Physiological PsychologyTreatment OutcomeGeriatricsEmergency medicineFemaleNeurology (clinical)FranceGeriatrics and GerontologybusinessHospital Units
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Incidence, Trends, and Survival of Children With Embryonal Tumors.

2015

BACKGROUND: Central nervous system (CNS) and non-CNS embryonal tumors occur principally in children and are rarely seen in adults. The incidence rates for rare entities such as atypical teratoid/rhabdoid tumors (AT/RT) or primitive neuroectodermal tumors in the CNS are rarely published. Incidence rates for certain subgroups, such as hepatoblastomas, have been increasing in some countries. METHODS: Data of 8337 embryonal tumors, registered in children (0–14 years) between 1991 and 2012 (for AT/RT 2000–2012) in the population-based German Childhood Cancer Registry with complete national coverage were analyzed for incidence rates, time trends, and survival. RESULTS: For most entities, the inc…

MalePediatricsmedicine.medical_specialtyHepatoblastomaAdolescentPopulationCentral Nervous System NeoplasmsGermanyMedicineHumansRegistrieseducationChildSurvival rateGanglioneuroblastomaeducation.field_of_studyChildhood Cancer Registrybusiness.industryRetinoblastomaIncidence (epidemiology)IncidenceInfant NewbornInfantNeoplasms Germ Cell and Embryonalmedicine.diseaseCancer registrySurvival RateChild PreschoolPediatrics Perinatology and Child HealthFemalebusinessPediatrics
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