Search results for "cerebral"

showing 10 items of 1357 documents

Jacobsen syndrome and neonatal bleeding: report on two unrelated patients

2021

Abstract Introduction In 1973, Petrea Jacobsen described the first patient showing dysmorphic features, developmental delay and congenital heart disease (atrial and ventricular septal defect) associated to a 11q deletion, inherited from the father. Since then, more than 200 patients have been reported, and the chromosomal critical region responsible for this contiguous gene disorder has been identified. Patients’ presentation We report on two unrelated newborns observed in Italy affected by Jacobsen syndrome (JBS, also known as 11q23 deletion). Both patients presented prenatal and postnatal bleeding, growth and developmental delay, craniofacial dysmorphisms, multiple congenital anomalies, a…

0301 basic medicinePediatricsmedicine.medical_specialtyGenotype-phenotype correlationHeart diseaseGenetic counselingCase ReportIn situ hybridization030105 genetics & heredityPediatricsRJ1-57003 medical and health sciences0302 clinical medicineaCGHJBSmedicineHumansJacobsen Distal 11q Deletion SyndromeJacobsen syndromeCraniofacialGenetic Association StudiesCerebral Hemorrhage11q23 deletionbusiness.industryInfant NewbornEarly diagnosimedicine.diseaseEarly diagnosisPancytopeniaThrombocytopeniaItalyFemalePresentation (obstetrics)business030217 neurology & neurosurgeryComparative genomic hybridizationItalian Journal of Pediatrics
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On the growth and form of cortical convolutions

2016

International audience; The rapid growth of the human cortex during development is accompanied by the folding of the brain into a highly convoluted structure1-3. Recent studies have focused on the genetic and cellular regulation of cortical growth4-8, but understanding the formation of the gyral and sulcal convolutions also requires consideration of the geometry and physical shaping of the growing brain9-15. To study this, we use magnetic resonance images to build a 3D-printed layered gel mimic of the developing smooth fetal brain; when immersed in a solvent, the outer layer swells relative to the core, mimicking cortical growth. This relative growth puts the outer layer into mechanical com…

0301 basic medicinePhysicsNonlinear phenomenata114growthGeneral Physics and Astronomygyrificationta3112SwellFetal brain03 medical and health sciences030104 developmental biology0302 clinical medicinemedicine.anatomical_structureCerebral cortexbrain geometrymedicineBiophysicscerebral cortexComputational biophysics[PHYS.MECA.BIOM]Physics [physics]/Mechanics [physics]/Biomechanics [physics.med-ph][SPI.SIGNAL]Engineering Sciences [physics]/Signal and Image processing030217 neurology & neurosurgery
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Spike-wave discharges in absence epilepsy: segregation of electrographic components reveals distinct pathways of seizure activity.

2020

Key points The major electrophysiological hallmarks of absence seizures are spike and wave discharges (SWDs), consisting of a sharp spike component and a slow wave component. In a widely accepted scheme, these components are functionally coupled and reflect an iterative progression of neuronal excitation during the spike and post-excitatory silence during the wave. In a genetic rat model of absence epilepsy, local pharmacological inhibition of the centromedian thalamus (CM) selectively suppressed the spike component, leaving self-contained waves in epidural recordings. Thalamic inputs induced activity in cortical microcircuits underlying the spike component, while intracortical oscillations…

0301 basic medicinePhysiologyThalamusLocal field potential03 medical and health sciencesEpilepsy0302 clinical medicineChildhood absence epilepsyThalamusSeizuresmedicineAnimalsHumansChildPhysicsCerebral CortexNeuronsQuantitative Biology::Neurons and CognitionSpike-and-waveElectroencephalographymedicine.diseasePatient DischargeRatsElectrophysiology030104 developmental biologyEpilepsy AbsenceSpike (software development)Centromedian nucleusNeuroscience030217 neurology & neurosurgeryThe Journal of physiologyReferences
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The Novel Oral Anticoagulants for Acute Venous Thromboembolism: Is Warfarin Dead?

2017

The direct oral anticoagulants (DOACs) have been compared with parenteral anticoagulants and vitamin K antagonists (VKAs) for the treatment of venous thromboembolism (VTE) in several robust studies. DOACs have shown similar efficacy in preventing recurrent VTE and significant reductions in critical site (intracranial) bleeding, fatal bleeding, major and nonmajor bleeding. Warfarin and other VKAs are not dead as treatment modalities for VTE. A better way to describe the current situation is to use a boxing expression, “down but not out.” VKAs and parenteral anticoagulants still have a role to play in the management of VTE in several clinical settings. In indications where DOACs can be used, …

0301 basic medicinePulmonary and Respiratory Medicinemedicine.medical_specialtyAdministration OralClinical settingsVitamin kCritical Care and Intensive Care Medicine03 medical and health sciences0302 clinical medicineSecondary PreventionmedicineHumanscardiovascular diseasesIntensive care medicineOral anticoagulationCerebral Hemorrhagebusiness.industryWarfarinAnticoagulantsVenous ThromboembolismSafety profile030104 developmental biologyTreatment modalityvenous thromboembolism oral anticoagulation warfarin non-VKA oral anticoagulants safety efficacy030220 oncology & carcinogenesisWarfarinbusinessVenous thromboembolismmedicine.drug
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Regulatory effects of simvastatin and apoJ on APP processing and amyloid-beta clearance in blood-brain barrier endothelial cells

2017

Amyloid-β peptides (Aβ) accumulate in cerebral capillaries indicating a central role of the blood-brain barrier (BBB) in the pathogenesis of Alzheimer’s disease (AD). Although a relationship between apolipoprotein-, cholesterol- and Aβ metabolism is evident, the interconnecting mechanisms operating in brain capillary endothelial cells (BCEC) are poorly understood. ApoJ (clusterin) is present in HDL that regulates cholesterol metabolism which is disturbed in AD. ApoJ levels are increased in AD brains and in plasma of cerebral amyloid angiopathy (CAA) patients. ApoJ may bind, prevent fibrillization, and enhance clearance of Aβ. We here define a connection of apoJ and cellular cholesterol home…

0301 basic medicineSimvastatinmedicine.medical_specialtyAmyloidSwineMice TransgenicBiologyBlood–brain barrierAmyloid beta-Protein PrecursorMice03 medical and health sciences0302 clinical medicineInternal medicinemedicineAmyloid precursor proteinAnimalsMolecular BiologyCells CulturedAmyloid beta-PeptidesClusterinEndothelial CellsCell Biologymedicine.diseaseLRP1Peptide FragmentsMice Inbred C57BLClusterin030104 developmental biologyEndocrinologymedicine.anatomical_structureBlood-Brain Barrierbiology.proteinFemaleCerebral amyloid angiopathyblood-brain barrier ; amyloid-β ; cholesterol ; simvastatin ; clusterin/apoJ ; LRP1Protein Processing Post-Translational030217 neurology & neurosurgeryIntracellularLipoprotein
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Collapsibility of the internal jugular veins in the lateral decubitus body position: A potential protective role of the cerebral venous outflow again…

2019

Recent research has revealed that patients with neurodegenerative disease sleep longer in the supine position, while healthy controls prefer sleeping in the lateral decubitus position. Thus, sleeping in the lateral position seems to be protective against neurodegeneration. It has also been suggested that a protective role of this body position could be associated with better cerebral venous drainage in this body position, which results in more active glymphatic system of the brain (the system responsible for clearance of the cerebral tissue from waste products, e.g. amyloid-β). Since no published evidence exists regarding venous outflow from the cranial cavity in the lateral decubitus posit…

0301 basic medicineSupine positionModels NeurologicalPostureBlood PressurePilot ProjectsLateral decubitus positionSitting03 medical and health sciencesHabits0302 clinical medicineAlzheimer DiseaseReference Valuesmental disordersCranial cavitymedicineLateral Decubitus PositionSupine PositionHumansNeurodegenerationInternal jugular veinhealth care economics and organizationsUltrasonographyRight Lateral Decubitus PositionAquaporin 4business.industryNeurodegenerationHemodynamicsGeneral MedicineAnatomyAlzheimer's diseasemedicine.diseaseCerebral Veins030104 developmental biologymedicine.anatomical_structureCerebrovascular CirculationPulsatile FlowNerve Degenerationcardiovascular systemInternal jugular veinGlymphatic systemJugular VeinsbusinessSleepGlymphatic System030217 neurology & neurosurgeryBlood Flow VelocityMedical hypotheses
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Impact of Elastin-Derived Peptide VGVAPG on Matrix Metalloprotease-2 and -9 and the Tissue Inhibitor of Metalloproteinase-1, -2, -3 and -4 mRNA Expre…

2018

Degradation products of elastin, i.e. elastin-derived peptides (EDPs), are involved in various physiological and pathological processes. EDPs are detectable in cerebrospinal fluid in healthy people and in patients after ischemic stroke. However, to date, no studies concerning the role of EDP in the nervous system were conducted. Matrix metalloproteinases (MMPs) and tissue inhibitors of metalloproteinases (TIMPs) play important roles during the repair phases of cerebral ischemia, particularly during angiogenesis and reestablishment of cerebral blood flow. Therefore, the aim of this study was to investigate the impact of the specific elastin-derived peptide VGVAPG on Mmp-2, -9 and Timp-1, -2,…

0301 basic medicineTIMPsAngiogenesisGene ExpressionApoptosisReceptors Cell SurfaceMatrix metalloproteinaseToxicology03 medical and health sciencesMice0302 clinical medicineGlial cellsAnimalsRNA MessengerCells CulturedCerebral CortexGene knockdownbiologyL-Lactate DehydrogenaseMMP-2ChemistryCaspase 3General NeuroscienceTissue Inhibitor of MetalloproteinasesTissue inhibitor of metalloproteinasebeta-GalactosidaseIn vitroMatrix MetalloproteinasesCell biologyElastin-derived peptides030104 developmental biologyApoptosisVGVAPGbiology.proteinOriginal ArticleMMP-9ElastinNeurogliaOligopeptides030217 neurology & neurosurgeryFetal bovine serumNeurotoxicity research
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Networking Brains: Modeling Spatial Relationships of the Cerebral Cortex

2017

Brain mapping has always been a priority in neurobiology and evolutionary neuroanatomy. In the last century, methodological issues and technical advances have generated a vivid debate on the parcellation and functions of the cortical territories. Brain structure is generally analyzed by considering the network of connections associated with neural pathways. Nonetheless, there is still a major debate on the recognition of the spatial and geometrical components of the cerebral cortex. The maps produced by Korbinian Brodmann in the early twentieth century on the basis of histological patterns represented a pioneering and decisive step in this sense, being a reference until the present day. Net…

0301 basic medicineTemporal cortexBrain mapping03 medical and health sciences030104 developmental biology0302 clinical medicinemedicine.anatomical_structureNeuroimagingCerebral cortexCortex (anatomy)medicinePrefrontal cortexNeuroscience030217 neurology & neurosurgerySpatial organizationNeuroanatomy
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Neural oscillations in the infralimbic cortex after electrical stimulation of the amygdala. Relevance to acute stress processing

2017

The stress system coordinates the adaptive reactions of the organism to stressors. Therefore, dysfunctions in this circuit may correlate to anxiety-related disorders, including depression. Comprehending the dynamics of this network may lead to a better understanding of the mechanisms that underlie these diseases. The central nucleus of the amygdala (CeA) activates the hypothalamic–pituitary–adrenal axis and brainstem nodes by triggering endocrine, autonomic and behavioral stress responses. The medial prefrontal cortex plays a significant role in regulating reactions to stressors, and is specifically important for limiting fear responses. Brain oscillations reflect neural systems activity. S…

0301 basic medicineTime FactorsInfralimbic cortexLocal field potentialBiologyAmygdalaRats Sprague-Dawley03 medical and health sciences0302 clinical medicinemedicineAnimalsPrefrontal cortexEvoked PotentialsCerebral CortexNeuronsAfferent PathwaysGeneral NeuroscienceCentral nucleus of the amygdalaAmygdalaElectric StimulationRatsElectrophysiology030104 developmental biologymedicine.anatomical_structureSynaptic plasticityFemaleBrainstemNeuroscience030217 neurology & neurosurgery
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Dibutyl Phthalate (DBP)-Induced Apoptosis and Neurotoxicity are Mediated via the Aryl Hydrocarbon Receptor (AhR) but not by Estrogen Receptor Alpha (…

2016

Dibutyl phthalate (di-n-butyl phthalate, DBP) is one of the most commonly used phthalate esters. DBP is widely used as a plasticizer in a variety of household industries and consumer products. Because phthalates are not chemically bound to products, they can easily leak out to enter the environment. DBP can pass through the placental and blood–brain barriers due to its chemical structure, but little is known about its mechanism of action in neuronal cells. This study demonstrated the toxic and apoptotic effects of DBP in mouse neocortical neurons in primary cultures. DBP stimulated caspase-3 and LDH activities as well as ROS formation in a concentration (10 nM–100 µM) and time-dependent (3–…

0301 basic medicineTime Factorsgenetic structuresPPARγPeroxisome proliferator-activated receptorApoptosis010501 environmental sciencesToxicology01 natural sciencesDBPMicechemistry.chemical_compoundERβReceptorCells CulturedERαCerebral CortexNeuronschemistry.chemical_classificationbiologyCaspase 3General NeurosciencePhthalateDibutyl PhthalatePhthalateOriginal ArticleSignal transductioncirculatory and respiratory physiologymedicine.medical_specialtyCell SurvivalDibutyl phthalateNeuroscience(all)03 medical and health sciencesInternal medicinemedicineAnimalsEstrogen Receptor betaRNA Messengercardiovascular diseasesEstrogen receptor beta0105 earth and related environmental sciencesDose-Response Relationship DrugAhREstrogen Receptor alphaNeuronAryl hydrocarbon receptorPPAR gamma030104 developmental biologyEndocrinologyReceptors Aryl Hydrocarbonchemistrybiology.proteinReactive Oxygen SpeciesEstrogen receptor alphaNeurotoxicity Research
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