Search results for "g factor"

showing 10 items of 514 documents

Genotypic and phenotypic spectrum in tricho-rhino-phalangeal syndrome types I and III

2000

Tricho-rhino-phalangeal syndrome (TRPS) is characterized by craniofacial and skeletal abnormalities. Three subtypes have been described: TRPS I, caused by mutations in the TRPS1 gene on chromosome 8; TRPS II, a microdeletion syndrome affecting the TRPS1 and EXT1 genes; and TRPS III, a form with severe brachydactyly, due to short metacarpals, and severe short stature, but without exostoses. To investigate whether TRPS III is caused by TRPS1 mutations and to establish a genotype-phenotype correlation in TRPS, we performed extensive mutation analysis and evaluated the height and degree of brachydactyly in patients with TRPS I or TRPS III. We found 35 different mutations in 44 of 51 unrelated p…

AdultMaleanimal structuresAdolescentGenotypeDNA Mutational AnalysisMolecular Sequence DataLimb Deformities CongenitalBiologyOsteochondrodysplasiasPolymorphism Single NucleotideShort statureLanger–Giedion syndromeGeneticsmedicineHumansMissense mutationTricho–rhino–phalangeal syndromeGenetics(clinical)Amino Acid SequenceChildGenetics (clinical)GeneticsAnthropometryBase SequenceBrachydactylyInfantZinc FingersExonsSyndromeArticlesMiddle AgedMicrodeletion syndromemedicine.diseasePenetranceBody HeightPedigreeDNA-Binding ProteinsRadiographyPhenotypeChild PreschoolMutationTrichorhinophalangeal Syndrome Type IErythroid-Specific DNA-Binding FactorsFemalemedicine.symptomChromosomes Human Pair 8Transcription Factors
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Recombinant human granulocyte-macrophage colony-stimulating factor induces secretion of autoinhibitory monokines by U-937 cells

1988

Colony-stimulating factors are required for survival proliferation, differentiation and functional activation of granulocytes, macrophages and their precursor cells. In the present report, however, we demonstrate antiproliferative activity of recombinant human (rh) granulocyte-macrophage colony-stimulating factor (GM-CSF) on monoblast cell line U-937 and provide evidence for the involvement of tumor necrosis factor alpha TNF-alpha and interleukin 1 beta (IL 1 beta) in its growth inhibitory action. GM-CSF (but not granulocyte CSF, G-CSF or macrophage CSF, M-CSF) suppressed DNA synthesis and self renewal of U-937 cells. Similarly, medium conditioned by U-937 cells in response to GM-CSF (GM-CS…

AdultMalemedicine.drug_classImmunologyMonoblastBiologyGranulocyteMonoclonal antibodyMonocytesColony-Stimulating FactorsTumor Cells CulturedmedicineHumansImmunology and AllergyMacrophageTumor Necrosis Factor-alphaMolecular biologyRecombinant ProteinsStimulation ChemicalGranulocyte macrophage colony-stimulating factormedicine.anatomical_structureCell culturebiology.proteinTumor necrosis factor alphaLymphoma Large B-Cell DiffuseAntibodyCell DivisionInterleukin-1medicine.drugEuropean Journal of Immunology
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Cumulative doses analysis in young trauma patients: a single-centre experience

2015

Multidetector computed tomography (MDCT) represents the main source of radiation expo- sure in trauma patients. The radiation exposure of young patients is a matter of considerable medical concern due to possible long-term effects. Multiple MDCT stud- ies have been observed in the young trauma population with an increase in radiation exposure. We have identi- fied 249 young adult patients (178 men and 71 women; age range 14-40 years) who had received more than one MDCT study between June 2010 and June 2014. According to the International Commission on Radio- logical Protection publication, we have calculated the cumulative organ dose tissue-weighting factors by using CT-EXPO software ® . We…

AdultMalemedicine.medical_specialtyAdolescentPopulationDose distributionRadiation DosageEffective dose (radiation)030218 nuclear medicine & medical imagingYoung Adult03 medical and health sciences0302 clinical medicineMultidetector Computed TomographyMultidetector computed tomographymedicineHumansRadiology Nuclear Medicine and imagingYoung adulteducationNeuroradiologyEffective doseeducation.field_of_studymedicine.diagnostic_testbusiness.industryAdsorbed dose; Cumulative doses; Effective dose; MDCT; Tissue-weighting factors; Radiology Nuclear Medicine and ImagingMDCTTissue-weighting factorInterventional radiologyGeneral MedicineCumulative doseSingle centreAdsorbed dose030220 oncology & carcinogenesisWounds and InjuriesFemaleRadiologyNuclear medicinebusinessLa radiologia medica
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Effect of interleukin-3 pretreatment on granulocyte/macrophage colony-stimulating factor induced mobilization of circulating haemopoietic progenitor …

1995

Recombinant human colony stimulating factors (CSFs) as single agents are increasingly used for mobilizing peripheral blood progenitor cells (PBPCs) for stem cell transplantation. We have shown in rhesus monkeys that interleukin-3 (IL-3) pretreatment markedly potentiated the increase in PBPC numbers of subsequent administration of granulocyte/macrophage-CSF (GM-CSF). Here we studied the effect of IL-3 pretreatment on GM-CSF-induced mobilization of PB progenitors in patients who were potential candidates for autologous stem cell transplantation (n = 16). Patients were treated with GM-CSF at a dose of 5 micrograms/kg/d for 5 d and after a treatment free interval received another cycle of GM-CS…

AdultMalemedicine.medical_specialtyAdolescentmedicine.medical_treatmentGranulocyteLeukocyte CountInternal medicinemedicineHumansProgenitor cellInterleukin 3business.industryPlatelet CountGranulocyte-Macrophage Colony-Stimulating FactorHematologyColony-stimulating factorHematopoietic Stem CellsTransplantationCytokineEndocrinologymedicine.anatomical_structureGranulocyte macrophage colony-stimulating factorImmunologyErythrocyte CountFemaleInterleukin-3Stem cellbusinessmedicine.drugBritish journal of haematology
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Filgrastim mobilization and collection of allogeneic blood progenitor cells from adult family donors: first interim report of a prospective German mu…

2002

Recombinant human granulocyte colony-stimulating factor (rhG-CSF) mobilized peripheral blood progenitor cells (PBPCs) from healthy individuals are a rapidly emerging alternative source to bone marrow for allogeneic transplantation. Although widely applied in the meantime, only limited information on feasibility and safety of mobilization and collection of PBPCs is currently available from prospective multicenter studies specifically designed to investigate this donation modality. This ongoing multicenter study on the performance as well as the short- and long-term safety profile of rhG-CSF-induced mobilization and collection of PBPCs was initiated in October 1999. The study is designed to r…

AdultMalemedicine.medical_specialtyAllogeneic transplantationAdolescentFilgrastimAntigens CD34Blood DonorsFilgrastimImmunophenotypingNuclear FamilyInternal medicineGranulocyte Colony-Stimulating FactormedicineClinical endpointHumansLeukapheresisProspective StudiesProspective cohort studyAdverse effectbusiness.industryHematologyGeneral MedicineLeukapheresisMiddle AgedHematopoietic Stem Cell MobilizationLymphocyte SubsetsRecombinant ProteinsGranulocyte colony-stimulating factorSurgeryBlood Cell CountRegimenImmune SystemFemalebusinessmedicine.drugAnnals of hematology
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Chemotherapy-induced mobilization of karyotypically normal PBSC for autografting in CML

1998

High-dose chemotherapy with autologous transplantation of in vivo purged PBSC is a new and interesting therapeutic option for CML patients not eligible for allogeneic transplantation. We investigated the feasibility and toxicity of this approach in 57 patients with Ph-positive CML. For mobilization of Ph-negative PBSC, patients were treated either with '5 + 2/7 + 3'- type chemotherapy or with 'mini-ICE/ICE' chemotherapy followed by administration of G-CSF. Fourteen patients were in early chronic phase, 30 patients in late chronic phase and 13 patients in accelerated phase (AP) or blast crisis (BC). Cytogenetic responses in the PBSC harvests were dependent on both disease stage and type of c…

AdultMalemedicine.medical_specialtyAllogeneic transplantationmedicine.medical_treatmentPilot ProjectsLeukemia Myelogenous Chronic BCR-ABL PositiveAntineoplastic Combined Chemotherapy ProtocolsmedicineHumansAutologous transplantationProspective StudiesEtoposideTransplantationMyelosuppressive ChemotherapyChemotherapybusiness.industryHematopoietic Stem Cell TransplantationHematologyMiddle AgedHematopoietic Stem Cell MobilizationGranulocyte colony-stimulating factorSurgeryTransplantationKaryotypingCytarabineFemalebusinessmedicine.drugBone Marrow Transplantation
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Left ventricular mass in hypertensive patients with mild-to-moderate reduction of renal function

2010

Aim: Left ventricular hypertrophy (LVH) is an independent predictor of cardiovascular (CV) morbidity and mortality. The aim of the present study was to evaluate the relationship between LV mass and mild-to-moderate renal dysfunction in a group of non-diabetic hypertensives, free of CV diseases, participating in the Renal Dysfunction in Hypertension (REDHY) study. Methods: Patients with diabetes, a body mass index (BMI) of more than 35 kg/m 2 , secondary hypertension, CV diseases and a glomerular filtration rate (GFR) of less than 30 mL/min per 1.73 m 2 were excluded. The final sample included 455 patients, who underwent echocardiographic examination and ambulatory blood pressure monitoring.…

AdultMalemedicine.medical_specialtyAmbulatory blood pressureBody Surface AreaHeart VentriclesPopulationSecondary hypertensionRenal functionBlood PressureKidneyurologic and male genital diseasesLeft ventricular hypertrophyRisk AssessmentSeverity of Illness IndexRisk FactorsInternal medicinemedicineHumansHypertension Glomerular filtration rate Chronic kidney disease Cardiovascular disease Left ventricular mass Left ventricular hypertrophy.educationBody surface areaeducation.field_of_studyChi-Square Distributionbusiness.industryConfounding Factors EpidemiologicGeneral MedicineBlood Pressure Monitoring AmbulatoryMiddle Agedmedicine.diseaseBody HeightCross-Sectional StudiesLogistic ModelsBlood pressureItalyEchocardiographyNephrologyHypertensionCardiologyFemaleHypertrophy Left VentricularKidney DiseasesbusinessGlomerular Filtration RateKidney diseaseNephrology
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Impact of different strategies of second-line stem cell harvest on the outcome of autologous transplantation in poor peripheral blood stem cell mobil…

2005

The optimal approach to obtain an adequate graft for transplantation in patients with poor peripheral blood stem cell (PBSC) mobilization remains unclear. We retrospectively assessed the impact of different strategies of second-line stem cell harvest on the transplantation outcome of patients who failed PBSC mobilization in our institution. Such patients were distributed into three groups: those who proceeded to steady-state bone marrow (BM) collection (group A, n = 34); those who underwent second PBSC mobilization (group B, n = 41); those in whom no further harvesting was carried out (group C, n = 30). PBSC harvest yielded significantly more CD34+ cells than BM collection. Autologous trans…

AdultMalemedicine.medical_specialtyAntigens CD34Bone Marrow CellsCell CountTransplantation AutologousInternal medicineGranulocyte Colony-Stimulating FactorMedicineAutologous transplantationHumansLeukapheresisHematopoietic Stem Cell MobilizationAgedBone Marrow TransplantationRetrospective StudiesTransplantationPeripheral Blood Stem Cell TransplantationHematologyBlood Cellsbusiness.industryHematologyLeukapheresisMiddle AgedHematopoietic Stem Cell MobilizationGranulocyte colony-stimulating factorSurgeryTransplantationmedicine.anatomical_structureTreatment OutcomeHematologic NeoplasmsFemaleBone marrowStem cellbusinessBone marrow transplantation
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Neuropsychological testing of cognitive impairment in euthymic bipolar disorder: an individual patient data meta-analysis

2013

© 2013 John Wiley & Sons A/S. Published by John Wiley & Sons Ltd.

AdultMalemedicine.medical_specialtyBipolar DisorderBipolar disorderTrail Making TestReviewNeuropsychological TestsVerbal learning03 medical and health sciencesMental Processes0302 clinical medicineRisk FactorsmedicineMemory spanHumansMental CompetencyAffective SymptomsBipolar disorderAge of OnsetPsychiatryPsychiatric Status Rating ScalesPsychotropic DrugsNeuropsychologyConfounding Factors EpidemiologicMiddle Agedmedicine.disease030227 psychiatryAffectPsychiatry and Mental healthMoodCognitive impairmentSchizophreniaNeuropsychological testsFemaleVerbal memoryCognition DisordersPsychology030217 neurology & neurosurgeryClinical psychology
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Improved multilineage response of hematopoiesis in patients with myelodysplastic syndromes to a combination therapy with all-trans-retinoic acid, gra…

1996

Differentiation induction therapy is being tested in myelodysplastic syndromes to ameliorate maturation defects and to restore normal hematopoietic function. To this end, 17 patients (eight with refractory anemia, two with refractory anemia and ring sideroblasts, and seven with refractory anemia and excess of blast cells) were treated with a combination of all-trans-retinoic acid (ATRA), granulocyte colony-stimulating factor (G-CSF), erythropoietin (EPO), and alpha-tocopherol for durations of 8-16 weeks. Absolute neutrophil counts increased in all patients; platelet counts increased in five patients with discontinuation of transfusion needs in two of four transfusion-dependent patients. Sti…

AdultMalemedicine.medical_specialtyCombination therapyTretinoinBone Marrowhemic and lymphatic diseasesInternal medicineGranulocyte Colony-Stimulating FactorMedicineHumansVitamin EErythropoietinAgedAged 80 and overHematologybusiness.industryMyelodysplastic syndromesHematologyGeneral MedicineMiddle Agedmedicine.diseaseGranulocyte colony-stimulating factorBlood Cell CountHematopoiesisHaematopoiesisEndocrinologymedicine.anatomical_structureErythropoietinMyelodysplastic SyndromesErythropoiesisDrug Therapy CombinationFemaleBone marrowbusinessmedicine.drugAnnals of hematology
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