Search results for "iNOS"

showing 10 items of 2075 documents

Late infantile neuronal ceroid lipofuscinosis: Quantitative description of the clinical course in patients withCLN2 mutations

2002

We examined 26 individuals with clinical and electron microscopic signs of late infantile neuronal ceroid lipofuscinosis (LINCL). In 22 cases, we found both pathogenic alleles. Sixteen patients exclusively carried either one or a combination of the two common mutations R208X and IVS5-1G > C. In the remaining cases, four missense mutations could be detected, of which R127Q, N286S, and T353P represent novel, previously not described alleles. A clinical performance score was developed by rating motor, visual, and verbal functions and the incidence of cerebral seizures in 3-month intervals during the course of the disease. A Total Disability Score was derived by summing up the single scores for…

Pediatricsmedicine.medical_specialtyDNA Mutational AnalysisCerliponase alfaDiseaseNeurological disorderAminopeptidasesSeverity of Illness IndexNeuronal Ceroid-LipofuscinosesSeizuresEndopeptidasesSeverity of illnessmedicineMissense mutationDipeptidyl-Peptidases and Tripeptidyl-PeptidasesVision OcularGenetics (clinical)Tripeptidyl-Peptidase 1business.industryDNAmedicine.diseaseTripeptidyl peptidase INeuronal Ceroid Lipofuscinosis Type 2MutationNeuronal ceroid lipofuscinosisSerine ProteasesbusinessPsychomotor PerformancePeptide HydrolasesAmerican Journal of Medical Genetics
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Subjective Assessment of Head and Facial Appearance in Children with Craniosynostoses after Surgical Treatment

2018

Background: Craniosynostoses are congenital defects in the construction of the skull involving premature fusion of one or more cranial sutures. Premature fusion of sutures causes characteristic skull deformation(s). This affect the structure and thus the appearance of the entire head and face. The aim of this study was to analyze parents&rsquo

Pediatricsmedicine.medical_specialtyLeadership and ManagementHead (linguistics)craniosinostosis; results of surgery; craniofacial disfigurement; clinical survey; subjective assessment; surgical outcomeslcsh:MedicineHealth Informaticscraniofacial disfigurementCraniosynostosessurgical outcomesAffect (psychology)ArticleCraniosynostosis03 medical and health sciencesInterpersonal relationship0302 clinical medicineHealth Information ManagementmedicinecraniosinostosisSurgical treatmentclinical surveybusiness.industryHealth Policylcsh:Rsubjective assessmentmedicine.diseaseFacial appearanceSkullmedicine.anatomical_structure030220 oncology & carcinogenesisresults of surgerybusiness030217 neurology & neurosurgeryHealthcare
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Ocular Refraction at Birth and Its Development During the First Year of Life in a Large Cohort of Babies in a Single Center in Northern Italy

2020

The purpose of this study was to investigate refraction at birth and during the first year of life in a large cohort of babies born in a single center in Northern Italy. We also aimed to analyze refractive errors in relation to the gestational age at birth. An observational ophthalmological assessment was performed within 24 h of birth on 12,427 newborns. Refraction was examined using streak retinoscopy after the administration of tropicamide (1%). Values in the range of between +0.50 ≤ D ≤ +4.00 were defined as physiological refraction at birth. Newborns with refraction values outside of the physiological range were followed up during the first year of life. Comparative analyses were condu…

Pediatricsmedicine.medical_specialtynewbornsgenetic structuresEmmetropiaamblyopia; newborns; physiological refraction; preterm babies; refractive screeningpreterm babieSingle CenterPediatricsnewbornphysiological refractionMedicineRetinoscopyOriginal ResearchAnisometropiaamblyopiamedicine.diagnostic_testrefractive screeningbusiness.industryCongenital myopialcsh:RJ1-570Gestational agelcsh:Pediatricspreterm babiesmedicine.diseaseRefractioneye diseasesPediatrics Perinatology and Child HealthGestationbusinessFrontiers in Pediatrics
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Can the Caper (Capparis spinosa L.) Still Be Considered a Difficult-to-Propagate Crop?

2021

As a perennial xerophytic shrub, characterized by plesiomorphic features, the caper (Capparis spinosa L.) is naturally spread throughout the Mediterranean basin and occupies an important ecological role, as well as an economic one, in traditional and specialized systems for commercial production. This species, in spite of its wide diffusion, is currently considered at risk of genetic erosion, mainly due to overgrazing and overharvesting for domestic uses and for trade. This situation is made more serious because of the lack of efficient propagation techniques, determining the caper as a “difficult-to-propagate species”. In this review, we report the main available sexual and vegetative prop…

Perennial plantvegetative propagationVegetative reproductionved/biology.organism_classification_rank.speciesPlant Science<i>Capparis spinosa</i>HorticultureBiologyShrubCapparis spinosaSB1-1110CropfoodCapparis spinosa; In vitro propagation; Mediterranean basin; Seed propagation; Vegetative propagationin vitro propagationOvergrazingGenetic erosionved/biologyCapparis spinosaMediterranean basinPlant culturefood.foodSettore AGR/03 - Arboricoltura Generale E Coltivazioni ArboreeAgronomyseed propagationDormancyHorticulturae
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ALTERED RATIO BETWEEN AXON CALIBER AND MYELIN THICKNESS IN SURAL NERVES OF CHILDREN

1978

ABSTRACT Maturation of myelin sheaths in normal sural nerves of children proceeds more slowly than axon growth. This asynchronous development of axons and myelin sheaths results in a statistically significant change of the ratio between axon caliber and myelin thickness during normal development. Therefore, myelin thickness of individual nerve fibers must be related to the size of the axons as well as to the age of the individuals studied. Abnormalities of the relationship between myelin thickness and axon diameter (primary hypomyelination of large, or small, or all fibers) were clearly identified in cases with metachromatic leukodystrophy, KRABBE's, DEJERINE-SOTTAS’, COCKAYNE'S and SANFILI…

Peripheral myelinAnatomyGangliosidosisBiologymedicine.diseaseAxon growthMetachromatic leukodystrophyMyelinmedicine.anatomical_structurenervous systemCaliberCeroid lipofuscinosismedicineAxon
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Propolis-Based Nanofiber Patches to Repair Corneal Microbial Keratitis

2021

In this research, polyvinyl-alcohol (PVA)/gelatin (GEL)/propolis (Ps) biocompatible nanofiber patches were fabricated via electrospinning technique. The controlled release of Propolis, surface wettability behaviors, antimicrobial activities against the S. aureus and P. aeruginosa, and biocompatibility properties with the mesenchymal stem cells (MSCs) were investigated in detail. By adding 0.5, 1, and 3 wt.% GEL into the 13 wt.% PVA, the morphological and mechanical results suggested that 13 wt.% PVA/0.5 wt.% GEL patch can be an ideal matrix for 3 and 5 wt.% propolis addition. Morphological results revealed that the diameters of the electrospun nanofiber patches were increased with GEL (from…

Pharmaceutical ScienceBiocompatible Materials02 engineering and technologyGelatinAnalytical ChemistryContact angleQD241-4410302 clinical medicineAnti-Infective AgentsSpectroscopy Fourier Transform InfraredDrug DiscoveryMesenchymal stem cell proliferationDrug CarriersChemistrySSCAFFOLDHYDROGELP<i>S. aureus</i>021001 nanoscience & nanotechnologyControlled releaseaeruginosaElectrospinningpropolisChemistry (miscellaneous)microbial keratitisPseudomonas aeruginosaBLINDNESSMolecular MedicineELECTROSPUN0210 nano-technologyStaphylococcus aureusfood.ingredient<i>P. aeruginosa</i>BiocompatibilitySurface PropertiesFABRICATIONMicrobial Sensitivity TestsCHEMICAL-COMPOSITIONaureusArticle03 medical and health sciencesfoodnanofibersPhysical and Theoretical Chemistrycorneal patchelectrospinningKeratitisCOMPOSITEGELATINOrganic ChemistryPropolisS. aureusDrug LiberationP. aeruginosaPolyvinyl AlcoholNanofiber030221 ophthalmology & optometryPROPERTYMEMBRANENuclear chemistry
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Immunotherapeutic approaches to inflammatory bowel diseases

2001

For a long time corticosteroids, aminosalicylic acid preparations and antibiotics have represented the principal approaches in evidence-based drug therapy for chronic inflammatory bowel diseases (IBD), e.g., Crohn's disease (CD) and ulcerative colitis (UC), and are able to suppress disease activity in most cases. However, there are cases that do not respond to conventional drug therapy or remain dependent on high doses of steroids associated with severe side effects in the long run. It is generally accepted now that IBD has an immunological basis and results from a hyperresponsive state of the intestinal immune system. Although the primary etiological defect respectively immunogenic agent s…

PharmacologyAminosalicylic acidbusiness.industrymedicine.drug_classClinical BiochemistryAntibioticsDiseaseInflammatory Bowel Diseasesmedicine.diseaseInflammatory bowel diseaseUlcerative colitisdigestive system diseasesMicechemistry.chemical_compoundPharmacotherapyImmune systemchemistryDrug DiscoveryImmunologyEtiologyAnimalsHumansMedicineImmunotherapybusinessExpert Opinion on Biological Therapy
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Pseudomonas aeruginosa cause epidemic disease in the milkweed bug,Oncopeltus fasciatus dallas (Insecta, Heteroptera)

1976

Pseudomonas aeruginosa was recognized as the causative organism of an epidemic disease occurring in a laboratory breed ofOncopeltus fasciatus. The infection probably occurs peroral and is favoured by high temperature and humidity.Pseudomonas aeruginosa destroys the fat body of the bug.

PharmacologyFat bodybiologyPseudomonas aeruginosaHeteropteraCell Biologybiology.organism_classificationmedicine.disease_causeBreedMicrobiologyCellular and Molecular NeuroscienceCausative organismmedicineMolecular MedicineEpidemic diseaseMolecular BiologyExperientia
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Meropenem Permeation through the Outer Membrane of &lt;i&gt;Pseudomonas aeruginosa&lt;/i&gt; Can Involve Pathways Other than the OprD Porin Channel

1996

The outer membrane protein (OMP) OprD is the major channel through which carbapenems permeate the outer membrane of Pseudomonas aeruginosa. In this study, we analyzed the OMP profiles of several P. aeruginosa clinical isolates showing diminished susceptibility to imipenem while remaining susceptible to meropenem. All these isolates lacked OprD or showed a reduced expression of this porin. Susceptibility to meropenem was thus independent of the level of OprD expression, indicating that the antimicrobial could be taken up via an alternative route. The level of expression of OprC (70 kD) was also unrelated to meropenem susceptibility. Nevertheless, OMPs OprF and OprE were expressed by all isol…

PharmacologyImipenembiologyPseudomonas aeruginosaGeneral Medicinebiochemical phenomena metabolism and nutritionbacterial infections and mycosesbiology.organism_classificationmedicine.disease_causeMeropenemPorinaMicrobiologyInfectious DiseasesOncologyDrug DiscoveryPorinpolycyclic compoundsmedicinebacteriaPharmacology (medical)Bacterial outer membranemedicine.drugPseudomonadaceaeAntibacterial agentChemotherapy
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Inositols in the ovaries: activities and potential therapeutic applications.

2022

Introduction: Myo-inositol (MI) and D-chiro-inositol (DCI) play a key role in ovarian physiology, as they are second messengers of insulin and gonadotropins. Ex-vivo and in-vitro experiments demonstrate that both isomers are deeply involved in steroid biosynthesis, and that reduced MI-to-DCI ratios are associated with pathological imbalance of sex hormones. Areas covered: This expert opinion provides an overview of the physiological distribution of MI and DCI in the ovarian tissues, and a thorough insight of their involvement into ovarian steroidogenesis. Insulin resistance and compensatory hyperinsulinemia dramatically reduce the MI-to-DCI ratio in the ovaries, leading to gynecological dis…

PharmacologyOvarian SteroidogenesiGeneral MedicineToxicologySettore MED/40 - Ginecologia E Ostetriciad-chiro-inositol.EpimeraseSettore BIO/13 - Biologia ApplicataMyo-inositolSettore BIO/14 - FarmacologiaHumansInsulinFemaleInsulin ResistanceGenital Diseases FemaleInositolPolycystic Ovary SyndromeExpert opinion on drug metabolismtoxicology
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