Search results for "progress"

showing 10 items of 1620 documents

Clinical, histological and genetic characterization of reducing body myopathy caused by mutations in FHL1

2008

We recently identified the X-chromosomal four and a half LIM domain gene FHL1 as the causative gene for reducing body myopathy, a disorder characterized by progressive weakness and intracytoplasmic aggregates in muscle that exert reducing activity on menadione nitro-blue-tetrazolium (NBT). The mutations detected in FHL1 affected highly conserved zinc coordinating residues within the second LIM domain and lead to the formation of aggregates when transfected into cells. Our aim was to define the clinical and morphological phenotype of this myopathy and to assess the mutational spectrum of FHL1 mutations in reducing body myopathy in a larger cohort of patients. Patients were ascertained via th…

AdultMaleWeaknessPathologymedicine.medical_specialtyMutation MissenseMuscle ProteinsBiologymedicine.disease_causeMuscular DiseasesBiopsymedicineHumansGenetic Predisposition to DiseaseMyopathyChildMicroscopy ImmunoelectronMuscle SkeletalMutationMuscle biopsymedicine.diagnostic_testIntracellular Signaling Peptides and ProteinsInfantGenetic Diseases X-LinkedOriginal ArticlesLIM Domain Proteinsmedicine.diseaseCongenital myopathyFHL1PedigreeChild PreschoolFemaleNeurology (clinical)medicine.symptomProgressive disease
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Gray matter integrity predicts white matter network reorganization in multiple sclerosis

2019

Abstract Multiple sclerosis (MS) is a chronic inflammatory and neurodegenerative disease leading to gray matter atrophy and brain network reconfiguration as a response to increasing tissue damage. We evaluated whether white matter network reconfiguration appears subsequently to gray matter damage, or whether the gray matter degenerates following alterations in white matter networks. MRI data from 83 patients with clinically isolated syndrome and early relapsing–remitting MS were acquired at two time points with a follow‐up after 1 year. White matter network integrity was assessed based on probabilistic tractography performed on diffusion‐weighted data using graph theoretical analyses. We ev…

AdultMalegraph theory610 MedizinneuropsychologytractographyBiologyNeuropsychological Testsmultiple sclerosisGray (unit)050105 experimental psychologyWhite matter03 medical and health sciences0302 clinical medicineAtrophyMultiple Sclerosis Relapsing-Remittingatrophy610 Medical sciencesmedicineHumans0501 psychology and cognitive sciencesRadiology Nuclear Medicine and imagingstructural connectivityGray Matternetwork analysisResearch ArticlesTemporal cortexCerebral CortexClinically isolated syndromeRadiological and Ultrasound TechnologyMultiple sclerosisPutamen05 social sciencesMiddle Agedmedicine.diseaseWhite Mattermedicine.anatomical_structureDiffusion Tensor ImagingNeurologyDisease ProgressionFemaleNeurology (clinical)AnatomyNerve NetNeuroscience030217 neurology & neurosurgeryTractographyResearch ArticleFollow-Up StudiesHuman Brain Mapping
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The Neutrophil-to-Lymphocyte Ratio is Related to Disease Activity in Relapsing Remitting Multiple Sclerosis

2019

: Background: The role of the neutrophil-to-lymphocyte ratio (NLR) of peripheral blood has been investigated in relation to several autoimmune diseases. Limited studies have addressed the significance of the NLR in terms of being a marker of disease activity in multiple sclerosis (MS). Methods: This is a retrospective study in relapsing&ndash

AdultMalelymphocytesmedicine.medical_specialtyAdolescentlymphocyteLogistic regressionmultiple sclerosisArticleNLR; disease activity; lymphocytes; multiple sclerosis; neutrophilsNLRCohort StudiesDisease activityLeukocyte CountYoung AdultMultiple Sclerosis Relapsing-RemittingneutrophilsInternal medicinemedicineHumansNeutrophil to lymphocyte ratiolcsh:QH301-705.5Retrospective StudiesGenetic associationbusiness.industryMultiple sclerosisfungineutrophilRetrospective cohort studyGeneral MedicineMiddle AgedPrognosismedicine.diseaseRelapsing remittinglcsh:Biology (General)multiple sclerosiCohortDisease ProgressionFemalebusinessdisease activityBiomarkers
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The Candy Smell Test in Clinical Routine

2011

Background The “Candy Smell Test” (CST) has been introduced as a new testing method for the evaluation of the human sense of smell. In contrast to other established orthonasal smell tests, the CST addresses the retronasal application of odors, typical for food aroma effects during mastication and swallowing. The aim of this study was to evaluate the CST in a clinical setting in patients with olfactory dysfunction and normal controls against the Sniffin’ Sticks test. Furthermore, cutoff points for normal and pathological results in the CST should be determined. Methods The olfactory performance of 96 patients presenting with olfactory disorders and 71 healthy controls was evaluated with the …

AdultMalemedicine.medical_specialtyAdolescentMEDLINEAudiologyCandyOlfaction DisordersReference ValuesParanasal SinusesHumansImmunology and AllergyMedicineChildAgedDiagnostic Tests Routinebusiness.industryDisease progressionDiagnostic testGeneral MedicineMiddle AgedHuman senseClinical routineTest (assessment)SmellOtorhinolaryngologyReference valuesDisease ProgressionFeasibility StudiesFemalebusinessAmerican Journal of Rhinology & Allergy
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Capecitabine plus oxaliplatin (CapOx) versus capecitabine plus gemcitabine (CapGem) versus gemcitabine plus oxaliplatin (mGemOx): final results of a …

2007

Abstract Background To compare the efficacy and safety of three different chemotherapy doublets in the treatment of advanced pancreatic cancer (PC). Patients and methods At total of 190 patients were randomly assigned to receive capecitabine 1000 mg/m2 twice daily on days 1–14 plus oxaliplatin 130 mg/m2 on day 1 (CapOx), capecitabine 825 mg/m2 twice daily on days 1–14 plus gemcitabine 1000 mg/m2 on days 1 and 8 (CapGem) or gemcitabine 1000 mg/m2 on days 1 and 8 plus oxaliplatin 130 mg/m2 on day 8 (mGemOx). Treatment cycles were repeated every three weeks. The primary end point was progression-free survival (PFS) rate at 3 months; secondary end points included objective response rate, carboh…

AdultMalemedicine.medical_specialtyAdolescentMaximum Tolerated DoseOrganoplatinum CompoundsPhases of clinical researchKaplan-Meier EstimateDeoxycytidineRisk AssessmentGastroenterologyDisease-Free SurvivalDrug Administration ScheduleCapecitabineInternal medicineAntineoplastic Combined Chemotherapy ProtocolsmedicineHumansSingle-Blind MethodProgression-free survivalInfusions IntravenousCapecitabineAgedNeoplasm StagingProbabilityDose-Response Relationship Drugbusiness.industryCAPOX RegimenHematologyMiddle AgedImmunohistochemistrySurvival AnalysisGemcitabineGemcitabineOxaliplatinSurgeryOxaliplatinPancreatic NeoplasmsRegimenTreatment OutcomeOncologyTolerabilityFemaleFluorouracilbusinessFollow-Up Studiesmedicine.drugAnnals of Oncology
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Non respiratory symptoms in asthma as possible predictors of exacerbations

2015

Anxiety 34 37 36 Headache 28 23 26 Abdominal pain 1 3 2 Weakness 13 4 9 Depression 5 0 3 Impaired sleep 4 8 7 Nicturia 7 0 5 Chest pain 11 7 9 Excitement 13 6 10 Nonlocalized pain 4 4 4 Hunger 3 4 3 Lack of appetite 5 5 5 Fever 1 3 2 Nausea 1 5 4 Urticaria 3 0 2 Palpitation 28 23 26 Heartburn 11 7 10 Generalized itching 22 30 25 Non respiratory symptoms in asthma as possible predictors of exacerbations Gennaro Liccardi, MD, Gennaro Baldi, MD, Adriano Berra, MD, Emanuela Carpentieri, MD, Marina Cutajar, MD, Maria D’Amato, MD, Mario Del Donno, MD, Bruno Del Prato, MD, Ilenia Folletti, MD, Federica Gani, MD, Domenico Gargano, MD, Domenico Giannattasio, MD, Michele Giovannini, MD, Antonio Infan…

AdultMalemedicine.medical_specialtyAdolescentPrognosiSettore MED/10 - Malattie Dell'Apparato RespiratorioAutonomic Nervous SystemYoung AdultAdolescent; Adult; Aged; Anxiety Disorders; Asthma; Autonomic Nervous System; Child; Cross-Sectional Studies; Disease Progression; Female; Humans; Italy; Male; Middle Aged; Prognosis; Young AdultmedicineImmunology and AllergyHumansPsychiatryChildAgedAdolescent; Adult; Aged; Anxiety Disorders; Asthma; Autonomic Nervous System; Child; Cross-Sectional Studies; Disease Progression; Female; Humans; Italy; Male; Middle Aged; Prognosis; Young Adult; Immunology and Allergy; Medicine (all)Cross-Sectional Studiebusiness.industryMedicine (all)Disease progressionMiddle AgedPrognosisAnxiety DisordersAsthmaCross-Sectional StudiesItalyDisease ProgressionFemalebusinessAnxiety DisorderHuman
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Nomograms including nuclear matrix protein 22 for prediction of disease recurrence and progression in patients with Ta, T1 or CIS transitional cell c…

2005

ABSTRACT Purpose: We developed and validated nomograms that accurately predict disease recurrence and progression in patients with Ta, T1, or CIS transitional cell carcinoma (TCC) of the bladder using a large international cohort. Methods: Univariate and multivariate logistic regression models targeted histologically confirmed disease recurrence, and focused on 2,542 patients with bladder TCC from 10 participating centers. Variables consisted of pre-cystoscopy voided urine Nuclear Matrix Protein 22 (NMP22) assay, urine cytology, age and gender. Resulting nomograms were internally validated with bootstrapping. Nomogram performance was explored graphically with Loess smoothing plots. Results:…

AdultMalemedicine.medical_specialtyAdolescentUrologyUrinary systemUrologyurologic and male genital diseasesLogistic regressionBladder neoplasmsnuclear matrix protein 22neoplasm stagingnomogramsBladder NeoplasmCytologyBiomarkers TumormedicineHumansStage (cooking)AgedNeoplasm StagingUrine cytologyAged 80 and overCarcinoma Transitional Cellmedicine.diagnostic_testbusiness.industryNuclear ProteinsMiddle AgedNomogramPrognosismedicine.diseasefemale genital diseases and pregnancy complicationsSurgeryNomogramsTransitional cell carcinomaUrinary Bladder NeoplasmsMultivariate AnalysisDisease ProgressionFemalebusiness
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The Neutrophil-to-Lymphocyte ratio as a marker of recovery status in patients with severe dental infection.

2017

Background The aim of the study was to assess the value of pretreatment neutrophil/lymphocyte (N/L) ratio and mean platelet volume (MPV) and the correlation between these markers with progression in patients with severe odontogenic infection. Material and Methods A cohort of 100 patients with severe odontogenic infection were divided into 2 groups according to their length of hospital stay. The N/L ratio and MPV was measured in all patients. The correlation in all patients between preoperative fever, preoperative antibiotic doses, postoperative antibiotic doses, total antibiotic doses and hospital stay with N/L ratio and MPV were analyzed. The Youden index was used to identify the optimal c…

AdultMalemedicine.medical_specialtyAdolescentmedicine.drug_classNeutrophilsLymphocyteAntibioticsInfectionsGastroenterologySeverity of Illness Index03 medical and health sciencesLeukocyte CountYoung Adult0302 clinical medicineInternal medicineSeverity of illnessmedicineHumansLymphocytesNeutrophil to lymphocyte ratioMean platelet volumeChildGeneral DentistryRetrospective StudiesOdontogenic infectionOral Medicine and Pathologybusiness.industryResearchRemission InductionRetrospective cohort study030206 dentistry:CIENCIAS MÉDICAS [UNESCO]medicine.diseaseSurgeryAnti-Bacterial Agentsmedicine.anatomical_structureOtorhinolaryngologyTooth Diseases030220 oncology & carcinogenesisCohortUNESCO::CIENCIAS MÉDICASDisease ProgressionSurgeryFemalebusinessMean Platelet VolumeBiomarkersMedicina oral, patologia oral y cirugia bucal
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Susceptibility-weighted magnetic resonance imaging of cerebrovascular sequelae after radiotherapy for pediatric brain tumors

2017

Due to sensitive neuroimaging techniques, cerebrovascular complications such as cerebral microbleeds (CMB) and cerebral cavernous malformations (CCM) are increasingly recognized as considerable late effects after treatment for pediatric brain tumor. The aim of this study was to analyze CMB in a cohort of patients after cranial irradiation therapy for medulloblastoma or other pediatric brain tumors using susceptibility-weighted magnetic resonance imaging (SWI).Forty former pediatric brain tumor patients were enrolled in this prospective cross-sectional study and examined by cranial MRI including SWI sequences. Cerebral microbleeds, clinical symptoms and disability were evaluated.Thirty-six (…

AdultMalemedicine.medical_specialtyAdolescentmedicine.medical_treatmentNeuroimagingCraniospinal IrradiationYoung Adult03 medical and health sciences0302 clinical medicineNeuroimagingmedicineHumansRadiology Nuclear Medicine and imagingProspective StudiesChildRadiation InjuriesProspective cohort studyCerebral HemorrhageMedulloblastomamedicine.diagnostic_testBrain Neoplasmsbusiness.industryInfantMagnetic resonance imagingHematologymedicine.diseaseMagnetic Resonance ImagingRadiation therapyCross-Sectional StudiesOncologyCerebrovascular CirculationChild Preschool030220 oncology & carcinogenesisCohortDisease ProgressionFemaleRadiologyCranial IrradiationbusinessNeurocognitive030217 neurology & neurosurgeryRadiotherapy and Oncology
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Radiofrequency tissue volume reduction for treatment of auricle keloids

2010

Objectives/Hypothesis: Keloids are often refractive to treatment, and recurrences occur quite frequently. Radiofrequency tissue volume reduction (RFTVR) is a surgical technology that induces extensive fibrosis at the target tissues. Methods: We applied RFTVR in 14 patients (19 auricles, 5 patients treated bilaterally; 9 female, 5 male; range, 10–66 years) with keloids of the auricle. Keloids were located at the earlobe in 4 patients (5 auricles), helix in 9 patients (12 auricles), and at both earlobe and helix in 1 patient (2 auricles). In 6 patients (8 auricles) RFTVR was the sole treatment modality applied, and in 7 patients (10 auricles) intralesional steroid injection was also performed…

AdultMalemedicine.medical_specialtyAdolescentmedicine.medical_treatmentYoung AdultFibrosisSurgical technologymedicineHumansMinimally Invasive Surgical ProceduresChildEar DiseasesReduction (orthopedic surgery)EarlobeAgedAuriclebiologybusiness.industryPinnaMiddle Agedbiology.organism_classificationmedicine.diseaseSurgerymedicine.anatomical_structureOtorhinolaryngologyKeloidCatheter AblationFemalebusinessProgressive diseaseEar AuricleTissue volumeThe Laryngoscope
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