Search results for "registri"

showing 10 items of 634 documents

Disease and patient characteristics in NP-C patients: findings from an international disease registry.

2013

Abstract Background Niemann-Pick disease type C (NP-C) is a rare neurovisceral disease characterized by progressive neurodegeneration and premature death. We report data recorded at enrolment in an ongoing international NP-C registry initiated in September 2009 to describe disease natural history, clinical course and treatment experience of NP-C patients in clinical practice settings. Methods The NPC Registry is a prospective observational cohort study. Participating sites are encouraged to evaluate all consecutive patients with a confirmed diagnosis of NP-C, regardless of their treatment status. All patients undergo clinical assessments and medical care as determined by their physicians. D…

MalePediatricslcsh:Medicine[SDV.GEN] Life Sciences [q-bio]/Genetics0302 clinical medicineMiglustatDiagnosisGenetics(clinical)Pharmacology (medical)Prospective StudiesRegistriesAge of OnsetEnzyme InhibitorsChildProspective cohort studyGenetics (clinical)Medicine(all)0303 health sciencesCholestasisNiemann-Pick disease type CNiemann-Pick Disease Type CGeneral MedicineDysphagia3. Good healthChild PreschoolCohortNeurologicalFemalemedicine.symptomCohort studymedicine.drugHepatomegalymedicine.medical_specialty1-DeoxynojirimycinAtaxiaAdolescent03 medical and health sciencesDisease registrymedicineHumansDisabled PersonsVertical supranuclear palsy030304 developmental biology[SDV.GEN]Life Sciences [q-bio]/Geneticsbusiness.industryResearchlcsh:RInfantMutationSymptomsSplenomegalyAge of onsetbusiness030217 neurology & neurosurgery
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Survival and cure trends for European children, adolescents and young adults diagnosed with acute lymphoblastic leukemia from 1982 to 2002

2013

Proportion cured is a potentially more informative cancer outcome measurement than 5-year survival. We present population-based estimates of cure for young patients diagnosed with acute lymphoblastic leukemia in Europe from 1982 to 2002. Thirty-five European cancer registries provided data. Survival was estimated by age, period of diagnosis and European region, and used as input for parametric cure models, which assume cured patients have the same mortality as the general population. For acute lymphoblastic leukemia diagnosed in 1–14 year olds in 2000–2002, over 77% were estimated cured. The proportion cured improved significantly over the study period: an impressive 26–58% in infants (up t…

MalePediatricsmedicine.medical_specialtyAdolescentLymphoblastic LeukemiaPopulationacute lymphoblastic leukemiaHistory 21st Centuryacute lymphoblastic leukemia; children; adolescents and young adults; survival and cure trendsEurope/epidemiologyYoung AdultchildrenHumansMedicineRegistriesYoung adultChildeducationddc:613education.field_of_studybusiness.industryAge FactorsInfant NewbornAbsolute risk reductionInfantCancerHematologyPrecursor Cell Lymphoblastic Leukemia-LymphomaHistory 20th CenturyEuropean regionmedicine.diseasesurvival and cure trendsPrecursor Cell Lymphoblastic Leukemia-Lymphoma/epidemiology/history/mortalityChild PreschoolEarly adolescentsFemaleOriginal Articles and Brief Reportsbusinessadolescents and young adultsHaematologica
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Incidence, time trends and regional variation of childhood leukaemia in Germany and Europe.

2008

This paper presents data on the German and Europe-wide incidence, time trends and regional variations of childhood leukaemia. Data were provided by the German Childhood Cancer Registry (GCCR), a population-based cancer registry recording all cases of malignant diseases in children under 15 y of age residing in Germany and by the Automated Childhood Cancer Information System (ACCIS) co-ordinated at International Agency for Research on Cancer, Lyon, that combines and evaluates data from several European population-based cancer registries. The incidence of leukaemia (44.0 per million) has increased in Europe as well as in Germany in the last decades (0.6% annually on average). Germany shows no…

MalePediatricsmedicine.medical_specialtyAdolescentPopulationDisease OutbreaksGermanGermanymedicineHumansRadiology Nuclear Medicine and imagingRegistrieseducationChildChildhood Cancer Registryeducation.field_of_studyRadiationLeukemiaRadiological and Ultrasound TechnologyIncidence (epidemiology)IncidencePublic Health Environmental and Occupational HealthInfant NewbornCancerInfantGeneral Medicinemedicine.diseaselanguage.human_languageChildhood leukaemiaCancer registryEuropeGeographyRegional variationChild PreschoollanguageFemaleDemographyRadiation protection dosimetry
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Cancer patterns among children of Turkish descent in Germany: A study at the German Childhood Cancer Registry

2008

Abstract Background Cancer risks of migrants might differ from risks of the indigenous population due to differences in socioeconomic status, life style, or genetic factors. The aim of this study was to investigate cancer patterns among children of Turkish descent in Germany. Methods We identified cases with Turkish names (as a proxy of Turkish descent) among the 37,259 cases of childhood cancer registered in the German Childhood Cancer Registry (GCCR) during 1980–2005. As it is not possible to obtain reference population data for children of Turkish descent, the distribution of cancer diagnoses was compared between cases of Turkish descent and all remaining (mainly German) cases in the reg…

MalePediatricsmedicine.medical_specialtyAdolescentTurkeyTurkishPopulation610DiseaseGermanyNeoplasmsEpidemiologymedicineHumansRegistriesChildeducationSocioeconomic statusTransients and Migrantseducation.field_of_studyChildhood Cancer Registrybusiness.industryIncidenceIncidence (epidemiology)lcsh:Public aspects of medicinePublic Health Environmental and Occupational HealthInfantCancerlcsh:RA1-1270medicine.diseaselanguage.human_languageChild PreschoollanguageFemalebusinessResearch ArticleBMC Public Health
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Competing-risk analysis of coronavirus disease 2019 in-hospital mortality in a Northern Italian centre from SMAtteo COvid19 REgistry (SMACORE).

2021

AbstractAn accurate prediction of the clinical outcomes of European patients requiring hospitalisation for Coronavirus Disease 2019 (COVID-19) is lacking. The aim of the study is to identify predictors of in-hospital mortality and discharge in a cohort of Lombardy patients with COVID-19. All consecutive hospitalised patients from February 21st to March 30th, 2020, with confirmed COVID-19 from the IRCCS Policlinico San Matteo, Pavia, Lombardy, Italy, were included. In-hospital mortality and discharge were evaluated by competing risk analysis. The Fine and Gray model was fitted in order to estimate the effect of covariates on the cumulative incidence functions (CIFs) for in-hospital mortality…

MalePediatricsmedicine.medical_specialtyCoronavirus disease 2019 (COVID-19)ScienceDiseases030204 cardiovascular system & hematologyCompeting risksRisk AssessmentArticle03 medical and health sciences0302 clinical medicinemedicineHumansCumulative incidence030212 general & internal medicineHospital MortalityRegistriesAgedAged 80 and overMultidisciplinaryIn hospital mortalitybusiness.industryQRCOVID-19Lower intensityMiddle AgedItalyViral infectionHospital admissionCohortMedicineInfectious diseasesFemaleRisk assessmentbusinessHumanScientific reports
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Incidence, Trends, and Survival of Children With Embryonal Tumors.

2015

BACKGROUND: Central nervous system (CNS) and non-CNS embryonal tumors occur principally in children and are rarely seen in adults. The incidence rates for rare entities such as atypical teratoid/rhabdoid tumors (AT/RT) or primitive neuroectodermal tumors in the CNS are rarely published. Incidence rates for certain subgroups, such as hepatoblastomas, have been increasing in some countries. METHODS: Data of 8337 embryonal tumors, registered in children (0–14 years) between 1991 and 2012 (for AT/RT 2000–2012) in the population-based German Childhood Cancer Registry with complete national coverage were analyzed for incidence rates, time trends, and survival. RESULTS: For most entities, the inc…

MalePediatricsmedicine.medical_specialtyHepatoblastomaAdolescentPopulationCentral Nervous System NeoplasmsGermanyMedicineHumansRegistrieseducationChildSurvival rateGanglioneuroblastomaeducation.field_of_studyChildhood Cancer Registrybusiness.industryRetinoblastomaIncidence (epidemiology)IncidenceInfant NewbornInfantNeoplasms Germ Cell and Embryonalmedicine.diseaseCancer registrySurvival RateChild PreschoolPediatrics Perinatology and Child HealthFemalebusinessPediatrics
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Prevalence of microcephaly in Europe: population based study.

2016

Objectives: Microcephaly is a congenital anomaly where the baby’s head is smaller than expected when compared with babies of the same sex, age and ethnicity. Many of these babies will have underdeveloped brains. This study aimed to provide contemporary estimates of the prevalence of microcephaly in Europe, determine if the diagnosis of microcephaly is consistent across Europe and to evaluate whether changes in prevalence would be detected using the current European surveillance performed by EUROCAT (the European Surveillance of Congenital Anomalies). Design: A questionnaire and a population-based, observational study Setting: 24 EUROCAT registries covering 570,000 births annually in 15 coun…

MalePediatricsmedicine.medical_specialtyMicrocephalyPrenatal diagnosisEthnic originmicrocephaly ; prevalence surveillance03 medical and health sciencessymbols.namesakeEuropean Surveillance of Congenital Anomalies0302 clinical medicineMicrocefaliaEuropean SurveillancePregnancyEUROCAT030225 pediatricsStatistical significancePrenatal DiagnosisSurveys and QuestionnairesmedicinePrevalenceJournal ArticleHumans030212 general & internal medicinePoisson regressionRegistriesEurope/epidemiology; Female; Fetal Death; Humans; Male; Microcephaly/diagnosis; Microcephaly/epidemiology; Population Surveillance; Pregnancy; Prenatal Diagnosis; Prevalence; Registries; Retrospective Studies; Surveys and QuestionnairesFetal DeathRetrospective StudiesPregnancyZIKA VIRUS-INFECTIONbusiness.industryResearchRENACRetrospective cohort studyGeneral Medicinemedicine.diseaseEstados de Saúde e de DoençaObservação em Saúde e VigilânciaCongenital AnomaliesConfidence intervalEuropeCONGENITAL-ANOMALIESPopulation SurveillancesymbolsMicrocephalyFemalebusiness
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First results of a European multi-center registry of patients with anorectal malformations.

2013

Background: The European consortium on anorectal malformations (ARM-NET) was established to improve the health care of patients and to identify genetic and environmental risk factors. The aim of the present study was to present the first results on clinical data of a large European cohort of ARM patients based on our registry. Methods: In 2010, the registry was established including patient characteristics and data on diagnosis, surgical therapy, and outcome regarding complications. Patients born between 2007 and 2012 were retrospectively added. A descriptive analysis of this cohort was performed. Results: Two hundred and three ARM patients were included. Syndromes or chromosomal abnormalit…

MalePediatricsmedicine.medical_specialtyPatient characteristicsComorbidityGenomic disorders and inherited multi-system disorders [IGMD 3]Anus ImperforatePostoperative ComplicationsEnvironmental riskHealth careFemale patientmedicineHumansAbnormalities MultipleRegistriesRetrospective StudiesChromosome Aberrationsbusiness.industryIncidence (epidemiology)IncidenceInfant NewbornUrogenital AbnormalityGeneral MedicineSyndromeHuman Reproducion Genomic disorders and inherited multi-system disorders [NCEBP 12]Anorectal MalformationsEuropeTreatment OutcomeHuman Reproduction Renal disorder [NCEBP 12]Evaluation of complex medical interventions [NCEBP 2]Urogenital AbnormalitiesPediatrics Perinatology and Child HealthCohortEtiologySurgeryFemalebusiness
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Obesity and poor reproductive outcome: female and male body weight matter

2013

MalePediatricsmedicine.medical_specialtyPregnancyReproductive Techniques Assistedbusiness.industryMEDLINEObstetrics and GynecologyOverweightmedicine.diseaseBody weightObesityOutcome (game theory)Body Mass IndexText miningReproductive MedicinePregnancyPopulation SurveillancemedicineHumansFemaleRegistriesbusinessLive BirthBody mass indexFertility and Sterility
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Clinical Severity, Age, and Sex Overcome Cardiometabolic Morbidities but Not Stroke as Predictors of Mortality in Elderly Inpatients: Data From the R…

2016

MalePediatricsmedicine.medical_specialtyREPOSI studyClinical severity age stroke risk factors elderly REPOSI studySocio-culturale030204 cardiovascular system & hematologyAge and sexelderlySeverity of Illness Index03 medical and health sciencesSex Factors0302 clinical medicineMetabolic Diseasesmedicinerisk factorsHumansClinical severityClinical severityHospital MortalityRegistries030212 general & internal medicineStrokeAgedAged 80 and overInpatientsbusiness.industryAge Factorsmedicine.diseaseStrokeageItalyCardiovascular DiseasesFemaleMorbidityGeriatrics and GerontologybusinessJournal of the American Geriatrics Society
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