Search results for "registries"

showing 10 items of 615 documents

Worldwide experience of homozygous familial hypercholesterolaemia:retrospective cohort study

2022

[Background]: Homozygous familial hypercholesterolaemia (HoFH) is a rare inherited disorder resulting in extremely elevated low-density lipoprotein cholesterol levels and premature atherosclerotic cardiovascular disease (ASCVD). Current guidance about its management and prognosis stems from small studies, mostly from high-income countries. The objective of this study was to assess the clinical and genetic characteristics, as well as the impact, of current practice on health outcomes of HoFH patients globally.

AdultMaleHomozygous Familial HypercholesterolemiaAdolescentretrospective studyCHILDRENDoenças Cardio e Cérebro-vascularesCohort StudiesYoung AdultMedicine General & InternalGeneral & Internal MedicineCardiovascular DiseaseHumansRegistriesLIPOPROTEIN-APHERESISChild11 Medical and Health SciencesRetrospective StudiesHomozygous Familial Hypercholesterolaemia International Clinical CollaboratorsScience & TechnologyGUIDANCEclinical characteristicEVOLOCUMABHomozygous familial hypercholesterolemia; Worldwide; Therapies; Cardiovascular diseaseGeneral MedicineCARECardiovascular diseaseOPEN-LABELEFFICACYINSIGHTSTherapiesChild PreschooloutcomeFemalegeneticFamilial HypercholesterolaemiaLife Sciences & BiomedicineWorldwide
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The effect of physical activity on long-term income.

2013

Abstract Empirical evidence for the direct effects of physical activities on long-term labor market outcomes is limited. This state of affairs is surprising, because there is a growing amount of support on the positive effects of physical activities on health on the one hand and on the effects of good health on labor market outcomes on the other hand. We examine the long-term income effects of physical activity using a large sample ( N  = 5042) of male twins from Finland (Older Finnish Twin Cohort Study, 1975, 1981, 1990), matched to detailed register-based income data (Finnish Longitudinal Employer-Employee Data, 1990–2004). Our primary income measure is calculated over a fifteen-year peri…

AdultMaleLabour economicsHealth (social science)Control (management)Physical activityTwinsState of affairsEmpirical ResearchMotor ActivityUnobservable03 medical and health sciences0302 clinical medicineHistory and Philosophy of Science0502 economics and businessEconomicsHumans030212 general & internal medicineLongitudinal StudiesRegistries050207 economicsEmpirical evidenceFinland05 social sciencesConfoundingMiddle AgedTerm (time)8. Economic growthIncomeCohort studySocial sciencemedicine (1982)
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High constant incidence rates of second primary cancers of the head and neck: a pooled analysis of 13 cancer registries

2010

Scanty data are available on the incidence (i.e., the absolute risk) of second cancers of the head and neck (HN) and its pattern with age. We investigated this issue using data from a multicentric study of 13 population-based cancer registries from Europe, Canada, Australia and Singapore for the years 1943-2000. A total of 99,257 patients had a first primary HN cancer (15,985 tongue, 22,378 mouth, 20,758 pharyngeal, and 40,190 laryngeal cancer), contributing to 489,855 person-years of follow-up. 1294 of the patients (1.3%) were diagnosed with second HN cancers (342 tongue, 345 mouth, 418 pharynx, and 189 larynx). Male incidence rates of first HN cancer steeply increased from 0.68/100,000 at…

AdultMaleLarynxOncologyCancer Researchmedicine.medical_specialtyPopulationArticlehead and neckTongueInternal medicineEpidemiologymedicineHumanscancerpooled analysiRegistrieseducationAgedAged 80 and overGynecologyeducation.field_of_studybusiness.industryIncidence (epidemiology)second neoplasmsHead and neck cancerPharynxCancerNeoplasms Second PrimaryMiddle Agedmedicine.diseasesecond primaryAdult ; Aged ; Aged 80 and over ; Female ; Head and Neck Neoplasms/epidemiology* ; Humans ; Incidence ; Male ; Middle Aged ; Neoplasms Second Primary/epidemiology*; Registriesmedicine.anatomical_structureOncologyageHead and Neck Neoplasmscancer registriesincidenceFemalehead and neck cancerHigh constant incidence ratebusiness
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Efficacy of caspofungin and itraconazole as secondary antifungal prophylaxis: analysis of data from a multinational case registry

2009

Patients surviving invasive fungal disease (IFD) and needing further antineoplastic chemotherapy are at high risk of recurrent fungal infection. In the absence of randomised controlled trials in this area, secondary prophylactic regimens are diverse. From 448 patients registered with the Multinational Case Registry of Secondary Antifungal Prophylaxis, we performed an analysis of patients receiving caspofungin (CAS) or itraconazole (ITC). All patients had an underlying haematological malignancy and had been diagnosed with an episode of IFD earlier in their course of treatment. Data collected comprised demographics, underlying disease, first episode of IFD, antifungal prophylaxis, incidence a…

AdultMaleMicrobiology (medical)medicine.medical_specialtyAntifungal AgentsAdolescentItraconazoleAspergillosisChemopreventionEchinocandinsLipopeptidesYoung Adultchemistry.chemical_compoundCaspofunginInternal medicinemedicineHumansAspergillosisPharmacology (medical)RegistriesMycosisAgedFirst episodebusiness.industryIncidence (epidemiology)Stem cell transplantationGeneral MedicineMiddle Agedmedicine.diseaseSurgeryTransplantationTreatment OutcomeInfectious DiseasesMycoseschemistryHematologic NeoplasmsChemoprophylaxisFemaleAntifungal prophylaxisItraconazoleCaspofunginbusinessmedicine.drugInternational Journal of Antimicrobial Agents
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Development and external validation of a clinical prediction model for functional impairment after intracranial tumor surgery

2021

OBJECTIVE Decision-making for intracranial tumor surgery requires balancing the oncological benefit against the risk for resection-related impairment. Risk estimates are commonly based on subjective experience and generalized numbers from the literature, but even experienced surgeons overestimate functional outcome after surgery. Today, there is no reliable and objective way to preoperatively predict an individual patient’s risk of experiencing any functional impairment. METHODS The authors developed a prediction model for functional impairment at 3 to 6 months after microsurgical resection, defined as a decrease in Karnofsky Performance Status of ≥ 10 points. Two prospective registries in…

AdultMaleMicrosurgerymedicine.medical_specialtyFunctional impairmentAdolescentIntracranial tumorNerve manipulationoutcome predictionYoung Adult03 medical and health sciencesPostoperative Complications0302 clinical medicinePredictive Value of TestsHumansMedicineGeneralizability theoryneurosurgeryProspective StudiesRegistriesKarnofsky Performance StatusAgedRetrospective StudiesAged 80 and overBrain Neoplasmsbusiness.industryExternal validationArea under the curveReproducibility of ResultsGeneral MedicineMiddle AgedSurgerypredictive analyticsmachine learningfunctional impairment030220 oncology & carcinogenesisoncologyCohortFemaleNeurosurgerybusiness030217 neurology & neurosurgeryJournal of Neurosurgery
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Survival for patients with rare haematologic malignancies: Changes in the early 21st century

2017

Abstract Introduction Population-level survival has improved for common haematologic malignancies in the early 21st century. However, relatively few population-level data are available for rare haematologic malignancies. Methods Data were extracted from 12 cancer registries in Germany and the Surveillance, Epidemiology and End Results database in the United States (US). Cases of haematologic malignancies with an incidence of less than 1 per 100,000 were selected for analysis. Period analysis was used to determine 5-year relative survival (RS) for the years 2003–2012, and modelled period analysis was used to determine changes in survival between 2003–2007 and 2008–2012. Results Seven individ…

AdultMaleOncologyCancer Researchmedicine.medical_specialtyPathologyTime FactorsAdolescentAnaplastic LymphomaYoung Adult03 medical and health sciencesRare Diseases0302 clinical medicineGermanyInternal medicineHumansMedicineRegistriesHealthcare DisparitiesYoung adultSurvival analysisAgedMycosis fungoidesRelative survivalbusiness.industryIncidenceIncidence (epidemiology)CancerMiddle Agedmedicine.diseaseSurvival AnalysisUnited StatesTreatment OutcomeOncologyHematologic Neoplasms030220 oncology & carcinogenesisFemaleMantle cell lymphomabusinessSEER Program030215 immunologyEuropean Journal of Cancer
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Distribution and risk of the second discordant primary cancers combined after a specific first primary cancer in German and Swedish cancer registries

2015

We aimed at investigating the distribution and risk of all second discordant primary cancers (SDPCs) after a specific first primary cancer in Germany and Sweden to provide etiological understanding of SDPCs and insight into their incidence rates and recording practices. Among 1,537,004 survivors of first primary cancers in Germany and 588,103 in Sweden, overall 80,162 and 32,544 SDPCs were recorded, respectively. Standardized incidence ratios (SIRs) of all SDPCs were elevated at levels between 1.1 and 2.1 after 23 (out of overall 29) cancers in Germany and at levels between 1.1 and 1.6 after 24 cancers in Sweden, and among them, elevated SIRs were found after 19 cancers in both populations.…

AdultMaleOncologyCancer Researchmedicine.medical_specialtyPediatricsPoor prognosisAdolescentDisease-Free SurvivalYoung AdultRisk FactorsGermanyInternal medicinemedicineHumansRegistriesAge of OnsetYoung adultAgedAged 80 and overSwedenbusiness.industryIncidenceIncidence (epidemiology)CancerNeoplasms Second PrimaryMiddle AgedPrimary cancermedicine.diseasehumanitiesCancer registryOncologyEtiologyFemaleAge of onsetbusinessCancer Letters
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Estimation de l’incidence des hémopathies malignes en France entre 1980 et 2012

2016

International audience; BACKGROUND:The classification of hematological malignancies (HMs) has changed in recent decades. For the first time, the French network of cancer registries (Francim) provides estimates for incidence and trends of HM in France between 1980 and 2012 for major HM subtypes.METHODS:Incidence was directly estimated by modeling the incidence rates measured in the cancer registry area. For each HM subtype, a "usable incidence period" was defined a priori, corresponding to the years for which all the registries collected them in a homogeneous way. For both sexes and each HM subtype, age-period-cohort models were used to estimate national incidence trends.RESULTS:Overall in F…

AdultMaleOncologyPediatricsmedicine.medical_specialtyRegistryAdolescentEpidemiologyChronic lymphocytic leukemiaFollicular lymphoma[SDV.CAN]Life Sciences [q-bio]/Cancer[ SDV.CAN ] Life Sciences [q-bio]/CancerHematological malignanciesYoung Adult03 medical and health sciences0302 clinical medicineNeoplasmsInternal medicinemedicineHumansRegistriesAgedAged 80 and overbusiness.industryMyelodysplastic syndromesIncidence (epidemiology)IncidencePublic Health Environmental and Occupational HealthCancer[ SDV.SPEE ] Life Sciences [q-bio]/Santé publique et épidémiologieHémopathies malignesMiddle AgedPlasma cell neoplasmmedicine.disease3. Good healthLymphomaCancer registryTendancesHematologic Neoplasms030220 oncology & carcinogenesisFemale[SDV.SPEE]Life Sciences [q-bio]/Santé publique et épidémiologieFranceTrendsbusinessRegistre de population030215 immunology
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Trends in Epidemiology, Treatment, and Survival of Hepatocellular Carcinoma Patients Between 1998 and 2009

2013

The aim of this study was to analyze clinical presentation, course of disease, and management of patients with hepatocellular carcinoma (HCC) in a German referral center between 1998 and 2009.HCC is a rare tumor in Germany, but its incidence has increased over the last 30 years. New therapies such as chemoembolization with drug-eluting beads, selective internal radiotherapy, and sorafenib were introduced recently; however, the impact on clinical management and overall survival (OS) is unclear.In this retrospective analysis, 1066 patients with HCC, separated into two 6-year periods (n=385; 1998 to 2003 and n=681; 2004 to 2009) were evaluated.The number of patients presenting each year (64 vs…

AdultMaleOncologymedicine.medical_specialtyCarcinoma HepatocellularTime FactorsAdolescentKaplan-Meier EstimateMedical OncologyRisk AssessmentArticleTertiary Care CentersGermanYoung AdultRisk FactorsGermanyInternal medicineEpidemiologymedicineCarcinomaHumansRegistriesYoung adultAgedNeoplasm StagingProportional Hazards ModelsRetrospective StudiesAged 80 and overbusiness.industryProportional hazards modelIncidence (epidemiology)Liver NeoplasmsAge FactorsGastroenterologyRetrospective cohort studyMiddle Agedmedicine.diseasedigestive system diseaseslanguage.human_languageTreatment OutcomeHepatocellular carcinomalanguageFemalebusinessJournal of Clinical Gastroenterology
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Conditional net survival: Relevant prognostic information for colorectal cancer survivors. A French population-based study

2015

Abstract Background Traditionally, survival estimates have been reported as survival from the time of diagnosis. A patient's probability of survival changes according to time elapsed since the diagnosis and this is known as conditional survival. The aim was to estimate 5-year net conditional survival in patients with colorectal cancer in a well-defined French population at yearly intervals up to 5 years. Methods Our study included 18,300 colorectal cancers diagnosed between 1976 and 2008 and registered in the population-based digestive cancer registry of Burgundy (France). We calculated conditional 5-year net survival, using the Pohar Perme estimator, for every additional year survived afte…

AdultMaleOncologymedicine.medical_specialtyColorectal cancerPopulationStage iiConditional survivalInternal medicineStatisticsmedicineHumansIn patientRegistrieseducationNet SurvivalAgedNeoplasm StagingAged 80 and overeducation.field_of_studyHepatologybusiness.industryGastroenterologyCancerMiddle AgedPrognosismedicine.diseaseSurvival AnalysisPopulation based studyFemaleFranceColorectal NeoplasmsbusinessDigestive and Liver Disease
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