Search results for "will"
showing 10 items of 546 documents
Prevalence of Angelman syndrome and Prader-Willi syndrome in Estonian children: sister syndromes not equally represented.
2006
In 2000-2004, we performed a focused search for individuals with Angelman syndrome (AS) and Prader-Willi syndrome (PWS) aiming to establish the prevalence data for the individuals born between 1984 and 2004 in Estonia. All persons with probable AS or PWS (n = 184) were studied using the DNA methylation test. Individuals with abnormal methylation were all further tested by chromosomal and FISH analysis, and if necessary for uniparental disomy and UBE3A gene mutation. Nineteen cases with abnormal methylation test result were identified. Seven of them had AS, including six (85.7%) due to 15q11-13 deletion and one paternal UPD15. Twelve subjects had PWS: 4 (33%) 15q11-13 deletions, 6 (50%) mate…
Debating Europe: Effects of the “Eurovision Debate” on EU Attitudes of Young German Voters and the Moderating Role Played by Political Involvement
2016
In the run-up to the elections to the European Parliament in 2014, EU citizens had the unprecedented opportunity to watch televised debates between the candidates running for president of the European Commission. The most important debate was the so-called "Eurovision debate", which was broadcasted in almost all EU member states. In this study we explore the responses of a sample of 110 young German voters, who watched this debate, to the candidates' messages and whether exposure to the debate caused a shift in the respondents' attitudes towards the EU. Combining data from a quasi-experiment, real-time response data, and data from a content analysis of the debate, we find that respondents' …
Representative Bureaucracy and the Role of Expertise in Politics
2015
This is an open access journal from Cogitatio http://www.cogitatiopress.com The vast majority of existing studies on bureaucratic representation focus on bureaucracies’ permanent and internal staff. Yet, the rising sophistication of modern democracies and the technocratization of political life are gradually inducing an increased reliance on external experts to assist in the development and implementation of policy decisions. This trend, we argue, raises the need to extend studies of bureaucratic representation to such external and non-permanent experts in governmental affairs. In this article, we take a first step in this direction using seconded national experts (SNEs) in the European Com…
Clinical efficacy of highly purified, doubly virus-inactivated factor VIII/von Willebrand factor concentrate (Fanhdi® ) in the treatment of von Wille…
2002
Summary. The goal of therapy in patients with von Willebrand disease (vWD) is to correct the dual defect of primary haemostasis and intrinsic coagulation reflected by low levels of von Willebrand factor (vWF) and factor VIII coagulant activity (FVIII:C). Factor VIII/von Willebrand factor (FVIII/vWF) concentrates are currently the treatment of choice in vWD patients unresponsive to desmopressin (DDAVP). However, only few studies on their clinical use are available so far. The main objective of this study was to retrospectively evaluate the clinical efficacy of a highly purified, doubly virus-inactivated FVIII/vWF concentrate with a high content of FVIII/vWF (Fanhdi®). Twenty-two patients wit…
THE ECONOMIC VALUE OF THE EXTERNALITIES ASSOCIATED WITH CULTURAL GOODS
2001
This study examined the economic value of the externalities associated with cultural goods. The purpose of this study is to clarify the willingness to pay to maintain the Central Finland museum of the ones which had filled a 18 year of Jyväskylä inhabitants and of factors which affect a payment willingness. From dichotomous choice valuation (DC-method) data we have estimated the cumulative probability density function (cdf). From estimated cdf we can calculate welfare measures such as median of the estimated distribution of CV. The study found firstly that the surplus of the consumer is thus 1.17 MFIM measured on the basis of the median value. In the respondents' opinion the value of the C…
Positive Predictive Value of Extraversion in Diagnosing L2 WTC
2021
Willingness to communicate in a foreign/second language (L2 WTC) is now considered an influential variable underlying the second and foreign language learning processes. It is also perceived in terms of a fundamental goal of second language education, because its higher levels result in a greater desire to practise oral communication, bringing about successful language learning. According to the pyramid model of L2 WTC, it is rooted in personality which produces both distal and enduring influences on a student’s verbal behaviour. It can thus be expected that extraversion, a personality dimension identified with energy and enthusiasm and characterised by sensitivity to reward and sociability…
POGLĄDY NA NAUKĘ JĘZYKA OBCEGO U OSÓB Z WYSOKĄ I NISKĄ GOTOWOŚCIĄ KOMUNIKACYJNĄ W JĘZYKU ANGIELSKIM
2019
Reflection is understood as an activity which enables the reproduction of past experiences, reflection and meditation about them and their evaluation. One of the most significant features shaping learner reflection may be willingness to communicate in a foreign language – one’s volitional readiness to enter a communicative event in this language. In spite of a wealth of research conducted in this area, it is still unclear why some students are willing to start communication in a foreign language, while others are adamant to avoid it. For the purpose of this paper a qualitative-quantitative study was performed, focusing on four students with very low levels of willingness to communicate in E…
Geschichte der Baltischen Freiwilligen Feuerwehr-Vereine in den Jahren 1862 bis 1882: Festgabe des Revaler Freiw. Feuerwehrvereines zum IV. Baltische…
1882
Vorwort . Die 21 ersten Baltischen freiwilligen Feuerwehren im Zeitraum von 1862 bis 1871; 1. Reval 2 ; Dorpat ; 3. Riga ; 4. Mitau ; 5. Pernau ; 6. Wenden ; 7. Lemsal ; 8. Arensburg ; 9. Tuckum ; 10. Wolmar ; 11. Walk ; 12. Fellin ; 13. Werro ; 14. Hapsal ; 15. Talsen ; 16. Friedrichstadt ; 17. Bauske ; 18. Hasenpoth ; 19. Doblen ; 20. Jacobstadt ; 21. Goldingen ; 22. Libau ; 23. Pskow -- Die Gründung von weitere 12 baltischen freiwilligen Feuerwehrvereinen innerhalb des Zeitraumes von 1871 bis 1882 : 24. Windau ; 25. Schaulen ; 26. Baltischport ; 27. Porchow ; 28. Schlock ; 29. Illuxt ; 30. Pargolowa ; 31. Allatzkiwwi ; 32. Dünaburg ; 33. Leal ; 34. Wesenburg ; 35. Dubbeln ; 36. Oberpahle…
Lignes et points : Illustration, impressionnisme littéraire et procédés
2020
International audience; Cette conférence a porté de manière générale sur les rapports entre illustration et procédés de reproduction. Elle est plus précisément consacrée à l’utilisation de la photogravure dans le livre illustré britannique de la fin du 19ème siècle. L’exemple choisi est le recueil d’essais London Impressions (Constable, 1898) d’Alice Meynell, illustré par l’artiste britannique William Hyde. Peintre et aquafortiste, Hyde collaborait avec l’inventeur écossais Donald Cameron-Swan (1863-1951) de la Swan Electric Engraving Company, spécialisée dans le cliché trait comme dans le cliché simili. À la croisée de pratiques autographiques et d’opérations mécaniques, la photogravure al…
Equity-worthiness and equity-willingness: key factors in private equity deals
2014
While access to private equity funds (PEFs) provides a unique opportunity for firms to set up sturdy growth paths, how PEFs select companies is an unknown process to entrepreneurs and business owners. This study aims to offer insights regarding the private equity market to entrepreneurs searching for external capital. We analyzed a novel dataset of 240 pre-deal negotiations between small- and medium-sized Italian companies and a closed-end fund. Results indicate that the successful closing of a deal depends on more than just the target firm's equity-worthiness (i.e., the company's ability to meet the expectations of a private equity investor). In fact, there is another dimension: the target…