A new case of Worster-Drought syndrome

2012

Introduction: Worster-Drought syndrome (WDS) consists of a congenital pseudobulbar palsy and is usually associated with spastic tetraplegia, learning impairment, behavioural problems, and epilepsy. Congenital bilateral perisylvian syndrome (CBPS) is characterized by bilateral perisylvian polymicrogyria on imaging. Clark et al, have previously proposed a WDS spectrum that includes CBPS, speculating that it may be due to malformation of the perisylvian region due to various perinatal or congenital causes, whether demonstrable on imaging, or functional and not visible with current imaging techniques. Worster-Drought suggested that the syndrome is probably a developmental defect of the motor tr…