6533b7d1fe1ef96bd125cd8c
RESEARCH PRODUCT
Parenteral nutrition improves nutritional status, autonomic symptoms and QoL in patients with TTR-FAP
Claudia StancanelliMassimo RussoSonia MessinaGianluca VitaGiuseppe VitaAnna Mazzeosubject
medicine.medical_specialtyMalabsorptionbiologybusiness.industryAmyloidosisGeneral Medicinemedicine.diseaseGastroenterologyTransthyretinParenteral nutritionInternal medicinePoster Presentationmedicinebiology.proteinPharmacology (medical)In patientWasting SyndromebusinessPolyneuropathyBody mass indexGenetics (clinical)description
Background Transthyretin related familial amyloidotic polyneuropathy (TTR-FAP) is an inherited form of amyloidosis, leading to death in about 10 years in most cases for cardiac failure or wasting syndrome. Previous study showed that modified body mass index (mBMI) was related to time before death, duration of gastrointestinal disturbances, malabsorption and functional capacity. Futhermore, outcome after liver tranplantation was greater in patients with an mBMI over 600.
| year | journal | country | edition | language |
|---|---|---|---|---|
| 2015-11-02 | Orphanet Journal of Rare Diseases |