6533b82efe1ef96bd129342b

RESEARCH PRODUCT

Hereditary Angioedema Associated with Subacute Cutaneous Lupus Erythematosus

Werner GudatKonrad Bork

subject

AdultSystemic diseaseLupus erythematosusAngioedemabusiness.industryDermatologymedicine.diseaseHistocompatibilitySubacute cutaneous lupus erythematosusimmune system diseasesImmunopathologyImmunologyHereditary angioedemaLupus Erythematosus CutaneousmedicineHumansFemaleAngioedemamedicine.symptomskin and connective tissue diseasesbusinessAnti-SSA/Ro autoantibodies

description

The increased occurrence of various autoimmune diseases has recently been reported in patients with hereditary angioedema (HAE). This is especially the case in different forms of lupus erythematosus, but also other autoimmune diseases. We report a 24-year-old female patient who 10 years ago developed the clinical symptoms of HAE which occurred at the same time as subacute cutaneous lupus erythematosus. The results of both immunological investigations and histocompatibility antigen genotyping gave no clear insight into the causal interrelationship of both diseases.

https://doi.org/10.1159/000248363