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RESEARCH PRODUCT
Pterygium axillae as a rare manifestation of Poland syndrome
Oliver J. MuenstererJan GoedekeAnne-sophie Hollersubject
PediatricRib cagemedicine.medical_specialtybusiness.industryPoland syndromePectoralis major muscle030204 cardiovascular system & hematologymedicine.diseaseResectionRight Anterior ChestPterygiumSurgery03 medical and health sciences0302 clinical medicinePterygium axillaePoland syndrome030220 oncology & carcinogenesisPediatrics Perinatology and Child HealthMedicineSurgeryContracturemedicine.symptombusinessPectoralis Muscledescription
Abstract Poland syndrome is characterized by a combination of absent pectoralis muscle, abnormalities of the rib cage, the breast, as well as brachy-syndactyly. We report a case of a 3 month old girl who was born with right sided axillary pterygium combined with flattening of the right anterior chest wall. Resection of a sclerotic band with reconstruction by Z-plasty was performed. Intraoperative and histopathological findings confirmed that the axillary pterygium developed on the basis of a scarred, hypoplastic pectoralis major muscle. Our case adds to the body of evidence that Poland syndrome may present in a heterogeneous fashion, including the rare finding of axillary pterygium with associated contracture. In these cases, early intervention prevents functional impairment.
| year | journal | country | edition | language |
|---|---|---|---|---|
| 2016-12-01 | Journal of Pediatric Surgery Case Reports |