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RESEARCH PRODUCT

Chronic atrial fibrillation in presence of aortic stenosis in a patient with polysplenia syndrome.

Giuseppe BrancatelliRosaria Linda TrovatoVincenzo SucatoPietro CandelaR Di MiceliSalvatore NovoEnrico Bronte

subject

Aortic valvemedicine.medical_specialtyPolysplenia syndromeRegurgitation (circulation)Heterotaxy SyndromePolysplenia Aortic Stenosis Atrial Fibrillationmedicine.arteryInternal medicineAscending aortaAtrial FibrillationMedicineChronic atrial fibrillationHumanscardiovascular diseasesAortaAgedHeart Valve Prosthesis ImplantationEjection fractionbusiness.industryGeneral MedicineAortic Valve Stenosismedicine.diseasePulmonary hypertensionSettore MED/11 - Malattie Dell'Apparato CardiovascolareStenosismedicine.anatomical_structureTreatment OutcomeChronic Diseasecardiovascular systemCardiologyFemalebusiness

description

We report a rare case of “situs viscerum ambiguous” with polysplenia syndrome, in a 69 year old female patient with aortic stenosis and chronic atrial fibrillation. The presenting symptom was dyspnoea on moderate exertion and an ECG showed supra ventricular arrhythmia. Patients trans-thoracic echocardiogram revealed a dilated left atrium, reduced ejection fraction, mild tricuspid regurgitation, moderate-severe pulmonary hypertension and severe aortic stenosis. The patient was successfully treated with a replacement of her aortic valve and ascending aorta.

10.2143/acb.3378https://pubmed.ncbi.nlm.nih.gov/24635332