6533b863fe1ef96bd12c78b8

RESEARCH PRODUCT

Small omphalocele with umbilical evagination of the bladder: a distinct entity?

Thomas WernerVeronika EngelSteffen Berger

subject

Bladder exstrophyInferior marginOmphaloceleEvaginationbusiness.industryUrologyEmbryologyPediatrics Perinatology and Child HealthmedicineNormal bladderAnatomymedicine.diseasebusiness

description

A neonatal case of umbilical evagination of the bladder combined with a small omphalocele is presented. This rare congenital malformation has previously been described in only three cases. Umbilical evagination can be understood as a disturbance of development of both the vitelline and allantoic ducts, resulting in a non-descended but otherwise normal bladder opening to the inferior margin of a small omphalocele. Diagnosis is made by clinical inspection and ultrasound. Since other malformations are not present, this entity may be regarded as a minor form of a lower midline defect with excellent prognosis.

10.1016/j.jpurol.2006.02.005https://pubmed.ncbi.nlm.nih.gov/18947705