Primary perireticulin amyloidosis in a 14-year-old girl.

6533b86dfe1ef96bd12c9814

RESEARCH PRODUCT

Primary perireticulin amyloidosis in a 14-year-old girl.

H. Hake H. Hake U. Goll U. Goll W. Thoenes W. Thoenes

subject

medicine.medical_specialty Pathology Nephrotic Syndrome Adolescent media_common.quotation_subject Biopsy Rectum Kidney medicine Humans Radiology Nuclear Medicine and imaging Girl media_common business.industry Amyloidosis Rectum General Medicine Amyloidosis medicine.disease Dermatology Steroid-resistant nephrotic syndrome Clinical trial medicine.anatomical_structure Pediatrics Perinatology and Child Health Female business Nephrotic syndrome

description

A primary perireticulin amyloidosis is reported in a 14-year-old girl, which showed the symptoms of a steroid-resistant nephrotic syndrome. The diagnosis was established by biopsies of kidney and rectum. Occurrence of amyloidosis in childhood and the clinical picture are discussed and references to clinical trials carried out are given.

year	journal	country	edition	language
1976-12-09	European journal of pediatrics

10.1007/bf00452413 https://pubmed.ncbi.nlm.nih.gov/1001327

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