Search results for "Angel"

showing 10 items of 287 documents

Prader–Willi Syndrome with Angelman Syndrome in the Offspring

2021

We report the second case, to the best of our knowledge, of a mother with Prader–Willi syndrome (PWS) who gave birth to a daughter with Angelman syndrome (AS). The menarche occurred when she was 16, and the following menstrual cycles were irregular, but she never took sexual hormone replacement therapy. At the age of 26, our patient with PWS became pregnant. The diagnosis was confirmed by molecular genetic testing that revealed a ~5.7 Mb deletion in the 15q11.1–15q13 region on the paternal allele in the mother with PWS and the maternal one in the daughter with AS, respectively. Both the mother with PWS and the daughter with AS showed peculiar clinical and genetic features of the two syndrom…

Medicine (General)congenital hereditary and neonatal diseases and abnormalitiesPediatricsmedicine.medical_specialtyPrader–Willi syndromeOffspringmedia_common.quotation_subjectCase Report030209 endocrinology & metabolismFertilityHuman sexuality03 medical and health sciencesR5-9200302 clinical medicinePregnancyAngelman syndromeHumansMedicineAllelemedia_commonfertilityDaughter030219 obstetrics & reproductive medicineoffspringbusiness.industrynutritional and metabolic diseasesGeneral Medicinemedicine.diseaseSettore MED/39 - Neuropsichiatria Infantilenervous system diseasesTransgender hormone therapyAngelman syndromeMenarcheFemaleAngelman syndrome Fertility Offspring Prader–Willi syndrome Female Fertility Humans Pregnancy Angelman Syndrome Prader-Willi SyndromebusinessPrader-Willi SyndromeMedicina
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The angelman syndrome: A brief review

2017

Angelman's Syndrome (AS) was described for the first time by Harry Angelman in the 1960s, based on obervation of three child patients with similar physical and behavioral features such as severe intellectual impairment, lack of language, motor disorders and happy behaviour. Many years later the typical patients' features were identified as linked to genetic abnormalities mainly characterized by neurological symptoms. Life expectancy is good although the symptoms tend to be stable and severe.

Medicine (all)Angelman syndromeUBE3AAngelman syndrome; Behavioural abnormalities; EEG abnormalities; Mental retardation; UBE3A; Medicine (all)Mental retardationEEG abnormalitieBehavioural abnormalitie
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The endemic vascular flora of Peloritani Mountains (NE Sicily): Plant functional traits and phytogeographical relationships in the most isolated and …

2014

This study is aimed at (1) producing a complete and updated inventory of the endemic vascular flora of Peloritani Mountains, (2) defining the geographical limits of Peloritani, regarded here as a biogeographical district and (3) highlighting possible paleogeographic connections with other Mediterranean lands. The heterogeneity analysis of the endemic flora was performed by means of contingency tables, through the x 2 test. The endemic flora of this area consists of 129 specific and infraspecific taxa, of which 15 are restricted to the Peloritani Mountains. The analysis of habitats revealed that endemic taxa are most abundant on cliffs, rangelands, woods and garrigues. A large number of surv…

Mediterranean climateFloraMediterranean RegionEcologyErucastrum virgatumEndemic floraPlant SciencepaleogeographyErucastrum virgatumGeographyTaxonHabitatSettore BIO/03 - Botanica Ambientale E ApplicataMicro plateAlpine orogenyPetagnaea gussoneiRangelandCalabrian-Peloritani OrogenEndemic flora Calabrian-Peloritani Orogen Mediterranean Region Erucastrum virgatum Petagnaea gussonei paleogeographyEcology Evolution Behavior and Systematics
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Molecular analysis of the fungal community associated with phyllosphere and carposphere of fruit crops

Metagenomics Olive Strawberry Citrus Orange Tangelo Apple Metabarcoding Aplicon Metagenomics Fungi Fungal Diversity Bioinformatics Biostatistics Molecular Biology Pathogens Plant Pathology Plant Diseases Organic Qiime Alpha Diversity Beta Diversity
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Michelangelon veistämisen muotokielen yhtäläisyyksistä eri mediumeissa - taiteenala mediumina

2007

Michelangelo Buonarrotimediumtilamuotoveisto
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Il Carteggio di Michelangelo. Una biografia attraverso le lettere.

2014

MichelangeloCarteggioSettore L-FIL-LET/10 - Letteratura ItalianaEpistolarioBuonarroti
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Apoteosis ideológica / 3

2004

Militantismo bíblicoIntegrismo ideológicoNeomesianismo secularizadoRELIGIÓNVidal-Beneyto JoséNacional-catolicismoESTADOS UNIDOSCondición nacionalLiberalismo monetaristaEE UUConversiónRezarPublicaciones: Obra periodística: Columnas y artículos de opiniónApoteosisComunidad moralEuropaNación americanaIndividualismoIDEOLOGÍAFundamentalismo evangélicoBibliaUSAReligión civilNacional-evangelismo
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A New Evangelization in the life of the family and the church

2018

The Church is at all times guiding the truth and credibility of the Gospel. Reflecting on the role of the New Evangelization in the family, it is worth stopping at the concept and meaning of the family. The family is holy, as St. John Paul II is a place where life is properly protected and can develop. The family is a community of people who aspires to eternal life. In Christian terms, the family is a community of parents and children built on the relationship of man and woman. As the Dogmatic Constitution on the Church of Lumen Gentium emphasizes, the family is referred to as the home church. This is where the functions of the Church are fulfilled: priesthood, royal and prophetic.

New evangelizationfamilyFamiliaris consortioLumen GentiumSt. John Paul IIChurchWorld Scientific News
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Brief an Garlieb H. Merkel

1799

Ms. 930a, Nr. 8, Bl. 22r-23v Böttiger, Karl August. Brief an Garlieb H. Merkel, Weimar, d[en] 13. November 1797 Autora rokraksts / Autograph, vācu, angļu un latīņu val. / Deutsch, Englisch und Latein [4] lpp. / S. Attēlu numuri / Bildnummern: 930a-008-1 – 930a-008-4 Der Verfasser nennt in diesem inhaltsreichen Brief zahlreiche Namen und hält nicht nur die Verbindung mit Merkel, die aus dessen erstem Aufenthalt in Weimar resultierte, aufrecht, sondern gibt ihm weitere Hinweise und Empfehlung für seinen weiteren Aufenthalt in Dänemark. So rät er zur Übersetzung dreier Romane aus dem Englischen, darunter Jane Wests „A gossip's story“ (London 1796). Ferner bittet der Verfasser Merkel um Gefälli…

Ostermessepodagras slimniekiJagemann von Heygersdorff Karoline (1777-1848)Schimmelmann Heinrich Ernst Graf (1747-1831)kāzasjaunais gads"Latvieši"RollenbesetzungLiteraturbaumasTalleyrand-Périgord Charles Maurice de (1754-1838)dāņu valoda„Musenalmanach“neuzticībaPerthes Friedrich Christoph (1772-1843)cukurfabrikaKotzebue Christina von (?-1803)„Die Letten”„Hanseatisches Magazin“„Piccolini“ [Teil von Schillers „Wallenstein“]Jenaer ProfessorenFranz II. Kaiser (1768-1835)„Hamburger Damen- Kunst- und Modejournal“Moldenhauer Johannes Jakob Paul„Die Ritter des Aristophanes“Schlegel August Wilhelm von (1767-1845)Jēnas evanģēlijsJambusHelvig Anna Amalie v. (geb. v. Imhoff 1776-1831)patriotiskā sabiedrība 1765Herders Johans Gotfrīds (1744-1803)LieldienasAttisches MuseumMerķelis Garlībs Helvigs (1769-1850)Meyer Heinrich (1760-1832)öffentliche VorlesungPasquilleFalk Karoline (1778-1841)Theaterpilsētas brīvīva] [Brīvības dieviete [šeit]augšāmcelšanās svētkiKonsularverfassungJean Paul (Richter Johann Paul Friedrich 1763-1825)konstitūcijaPanegyrikus [lit. Lobesdichtung]Marezoll Johann Gottlob (1761-1828)vara gravīraSander Johann Daniel (1759-1825)Fichte Johann Gottlieb (1762-1814)Luise Herzogin von Sachsen-Weimar-Eisenach (1757-1830)Apgaismības laikmetskareivjiStudentenordenložaVoss’sche BuchhandlungHerzogin Luise von Sachsen-Weimar-Eisenach (1757-1830)Jenaisches Evangeliumliterarischer Schlagaustausch] [Messgericht [hier]Prinz Bernhard von Sachsen-Weimar-Eisenach (1792-1862)FreimütigkeitFrancis II (1768-1835)Isländische SprachediktatorsReimarus Johann Albert Heinrich (1729-1814)studentu ordenis„Der neue teutsche Merkur“Napoleons I (1769-1821)KupferstichBerliner KonsistoriumJakobīņu franču revolūcijaHuber Ludwig Ferdinand (1764-1804)Raštates kongress 1797-1799Berlīnes konsistorijsvēstules no Osmaņu impērijasapmācības brīvībaJohanneum [Gymnasium in Hamburg]Fabel vom Haushund und dem HerrnMerkel] [Lazarus [hier]Buchhandlung von F. C. Perthes:HUMANITIES and RELIGION [Research Subject Categories]Jēnas profesoriKöniglich-Preußische Akademie der Wissenschaftennāve duelīHamburgas dziednīcaSchelling Dorothea Caroline Albertina von (1763-1809) [Ehefrau A. W. Schlegels]paskvilaBertuch Friedrich Justin (1747-1822)Patriotische Gesellschaft von 1765RezensionDiktatorŠlēgels Augusts Vilhelms (1767-1845)Ramberg Johann Heinrich (1763-1840)städtische Freiheit] [Göttin Libertas [hier]Pāvils I Romanovs (Krievijas impērijas ķeizars)OsternHanseGroßherzogin Luise von Sachsen-Weimar-Eisenach (1757-1830)Industriecomptoir [Weimarer Verlag]Vohs Friederike Margarethe (1777-1860)Soldatenliterārās debatesdomas un preses brīvība DānijāHerder Carolina Maria (1750-1809)NeujahrAbtrünnigkeitgrāmatu tirdzniecībalomu sadalījumsHanzas noliktavaatklāts priekšlasījumsPodagristen [Gichtleidende]Fihte Johans Gotlībs (1762-1814)literatūralieldienu tirgusGerüchteorientālismsAbildgaard (?) 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Oppeln 1757-1831)Merkel Garlieb Helvig (1769-1850)Großherzog Karl August zu Sachsen-Weimar-Eisenach (1757-1828)Boulton Matthew (1728-1809)EpigrammPaul I Kaiser von Russland (1754-1801)Graff Johann Jakob (1768-1848)OrientalismusMeusel Johann Georg (1747-1806)Weimarer Theaterstudentu nemieriTheater „Die Piccolomini“Böttiger EleonorMünter Friedrich Christian Karl Heinrich (1761-1830)Intelligenzblatt [„Allgemeine Literatur-Zeitung“]„Propyläen“Mounier Jean Joseph (1758-1806)Atikas muzejsslavas dziedājumiBürger Reinhard [Reinhard Karl Friedrich Graf von (1761-1837)Ridel Cornelius Johann Rudolf (1759-1821)Iffland August Wilhelm (1759-1814)„Der neue teutsche Merkur“] [„Mercur“ [gemeint]Wieland Christoph Martin (1733-1813)luSchauspielDenk- und Pressefreiheit in DänemarkVeimāras teātrisPrūsijas Karaliskā zinātņu akadēmijaFrölich Heinrich (?-1806)SpottgedichtAuferstehungsfestRunkelzuckerfabrikJakobiner Französische RevolutionFeßler Ignaz Aurelius (1756-1839)Herder Johann Gottfried (1744-1803)atklātībaLogeAufklärungGroße Reichstrompete [„Kaiserlich privilegirter Reichs-Anzeiger“]PapiergeldBonaparte Napoleon (1769-1821)papīrnaudaLichtenstein Anton August Heinrich (1753-1816)HanzaHanseatisches MagazinSchiller F. „Wallenstein“Schlegel Carl Wilhelm Friedrich von (1772-1829)Ramdohr Friedrich Wilhelm Basilius von (1757-1822)Hamburger Krankenanstalt [Allgemeine Armenanstalt?]LehrfreiheitjēnietisDuellmordSuhm Peter Frederik (1728-1798)Tieck Johann Ludwig (1773-1853)islandiešu valodaAtheismusstreitfabula par suni un saimnieku„Athenaeum“epigrammaDänische Sprache
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SYNTHESIS OF PYRROLO[3,2-H]QUINOLINONES WITH GOOD PHOTOCHEMOTHERAPEUTIC ACTIVITY AND NO DNA DAMAGE

2010

In the search for new photochemotherapeutic agents, a series of derivatives of the ring system pyrrolo[3,2-h]quinoline--bioisosters of the angular furocoumarin angelicin--were synthesized through a four-step synthetic approach, in reasonable overall yields. Eight of the synthesized derivatives showed a remarkable phototoxicity against a panel of four human tumor cell lines and a great dose UV-A dependence, reaching IC₅₀ values at submicromolar level. The mode of cellular death photoinduced by pyrrolo[3,2-h]quinolines was evaluated through a series of flow cytometric analysis and other tests were performed to clarify their mechanism of action.

PYRROLO[32-H]QUINOLINONESStereochemistryDNA damageClinical BiochemistryPharmaceutical SciencePhosphatidylserinesBiochemistryChemical synthesischemistry.chemical_compoundCell Line TumorFurocoumarinsDrug Discovery2-H]QUINOLINONESmedicineHumansPyrrolesPhotosensitizerMolecular BiologyMembrane Potential MitochondrialPhotosensitizing AgentsPYRROLO[3; 2-H]QUINOLINONES; ANGELICIN HETEROANALOGUES; PHOTOCHEMOTHERAPY; PHOTOTOXICITYFurocoumarinOrganic ChemistryBiological activitySettore CHIM/08 - Chimica FarmaceuticaPHOTOCHEMOTHERAPYPHOTOTOXICITYPYRROLO[3ANGELICIN HETEROANALOGUESMechanism of actionchemistryQuinolinesLactamMolecular Medicinemedicine.symptomReactive Oxygen SpeciesPhototoxicityDNA Damage
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