Search results for "DEGENERATION"

showing 10 items of 601 documents

2021

Age-related macular degeneration (AMD) is a common irreversible ocular disease characterized by vision impairment among older people. Many risk factors are related to AMD and interact with each other in its pathogenesis. Notably, oxidative stress and choroidal vascular dysfunction were suggested to be critically involved in AMD pathogenesis. In this review, we give an overview on the factors contributing to the pathophysiology of this multifactorial disease and discuss the role of reactive oxygen species and vascular function in more detail. Moreover, we give an overview on therapeutic strategies for patients suffering from AMD.

0301 basic medicinegenetic structuresBioinformaticsmedicine.disease_causeCatalysisInorganic ChemistryPathogenesis03 medical and health sciences0302 clinical medicineAge relatedMedicinePhysical and Theoretical ChemistryOcular diseaseMolecular BiologySpectroscopychemistry.chemical_classificationReactive oxygen speciesbusiness.industryOrganic ChemistryGeneral MedicineMacular degenerationmedicine.diseaseeye diseasesPathophysiologyComputer Science Applications030104 developmental biologychemistry030221 ophthalmology & optometrysense organsVascular functionbusinessOxidative stressInternational Journal of Molecular Sciences
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Cohen Syndrome-Associated Cataract Is Explained by VPS13B Functions in Lens Homeostasis and Is Modified by Additional Genetic Factors

2020

International audience; Purpose: Cohen syndrome (CS) is a rare genetic disorder caused by variants of the VPS13B gene. CS patients are affected with a severe form of retinal dystrophy, and in several cases cataracts also develop. The purpose of this study was to investigate the mechanisms and risk factors for cataract in CS, as well as to report on cataract surgeries in CS patients.Methods: To understand how VPS13B is associated with visual impairments in CS, we generated the Vps13b∆Ex3/∆Ex3 mouse model. Mice from 1 to 3 months of age were followed by ophthalmoscopy and slit-lamp examinations. Phenotypes were investigated by histology, immunohistochemistry, and western blot. Literature anal…

0301 basic medicinegenetic structuresDevelopmental DisabilitiesVesicular Transport Proteins030105 genetics & hereditysurgerygenetic backgroundchemistry.chemical_compoundLensMyopiaHomeostasisMice KnockoutCohen syndrome[SDV.MHEP] Life Sciences [q-bio]/Human health and pathologymedicine.diagnostic_testRetinal DegenerationGenetic disorderinflamma- tionVPS13BcataractKnockout mouseMicrocephalyMuscle Hypotoniamedicine.medical_specialtymouse modelBlotting WesternRetinitisFingersOphthalmoscopy03 medical and health sciencesCataractsIntellectual DisabilityOphthalmologyVPS13BLens CrystallinemedicineAnimalsObesityCohen syndromebusiness.industryfibrosisRetinalgenetic modifiersmedicine.diseaseeye diseasesMice Inbred C57BLDisease Models Animalophthalmology030104 developmental biologyGene Expression RegulationchemistryinflammationRNAsense organsbusiness[SDV.MHEP]Life Sciences [q-bio]/Human health and pathologyInvestigative Ophthalmology & Visual Science
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New Highlights of Resveratrol: A Review of Properties against Ocular Diseases

2021

Eye diseases are currently a major public health concern due to the growing number of cases resulting from both an aging of populations and exogenous factors linked to our lifestyles. Thus, many treatments including surgical pharmacological approaches have emerged, and special attention has been paid to prevention, where diet plays a preponderant role. Recently, potential antioxidants such as resveratrol have received much attention as potential tools against various ocular diseases. In this review, we focus on the mechanisms of resveratrol against ocular diseases, in particular age-related macular degeneration, glaucoma, cataract, diabetic retinopathy, and vitreoretinopathy. We analyze, in…

0301 basic medicinegenetic structuresEye DiseasesReviewDiseaseresveratrolAMDResveratrolBioinformaticsAntioxidantsEpigenesis Geneticlcsh:Chemistryangiogenesischemistry.chemical_compoundDrug Delivery Systems0302 clinical medicineSirtuin 1Gene Regulatory Networkslcsh:QH301-705.5Spectroscopy3309.20 Propiedades de Los AlimentosClinical Trials as TopicGeneral MedicineDiabetic retinopathyComputer Science Applicationsdiabetic retinopathycataract3201.09 OftalmologíanutraceuticalCatalysisInorganic Chemistry03 medical and health sciences2302 BioquímicamedicineHumansPhysical and Theoretical ChemistryMolecular BiologypolyphenolsMolecular signalingbusiness.industryocular diseasesOrganic ChemistryeyesMacular degenerationmedicine.diseaseeye diseasesClinical trial030104 developmental biologylcsh:Biology (General)lcsh:QD1-999Gene Expression Regulationchemistry030221 ophthalmology & optometryReactive Oxygen SpeciesbusinessInternational Journal of Molecular Sciences
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2019

Purpose This study analyzed whether low birth weight is linked to prevalence and incidence of age-related maculopathy (AMD) in adulthood. Methods The Gutenberg Health Study (GHS) is a population-based, observational cohort study in Germany. GHS participants at an age from 35 to 74 years were included. An ophthalmologic examination with fundus photography was carried out. Fundus photographs were graded according to the Rotterdam Grading Scheme for AMD at baseline and at the 5-year follow-up examination. Participants were divided into three different birth weight groups (low: 4000 g). Poisson regression analysis with adjustment for several confounders was used to assess associations between b…

0301 basic medicinegenetic structuresmedicine.diagnostic_testbusiness.industryBirth weightConfoundingFundus photographyMacular degenerationmedicine.diseaseeye diseases03 medical and health sciencesLow birth weightsymbols.namesake030104 developmental biology0302 clinical medicine030221 ophthalmology & optometrymedicinesymbolsCumulative incidencesense organsPoisson regressionmedicine.symptombusinessCohort studyDemographyInvestigative Opthalmology & Visual Science
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Biomarkers of Neurodegeneration in Autoimmune-Mediated Encephalitis

2018

Progranulin (PGRN), Total-Tau (t-tau), and Neurofilament light chain (NfL) are well known biomarkers of neurodegeneration. The objective of the present study was to investigate whether these parameters represent also biomarkers in autoimmune-mediated Encephalitis (AE) and may give us insights into the pathomechanisms of AE. We retrospectively examined the concentration of PGRN in the cerebrospinal fluid (CSF) and serum of 38 patients suffering from AE in acute phase and/or under treatment. This AE cohort comprises patients with autoantibodies against: NMDAR (n = 18 patients), Caspr2 (n = 8), Lgi-1 (n = 10), GABAB(R) (n = 1), and AMPAR (n = 1). Additionally, the concentrations of NfL (n = 25…

0301 basic medicinemedicine.medical_specialtyCaspr2 encephalitisLgi-1 encephalitisNMDAR encephalitisGastroenterologyCaspr2 encephalitis; Lgi-1 encephalitis; NMDAR encephalitis; autoimmune encephalitis; neurofilament light chain; progranulin; taulcsh:RC346-429Faculty of Medicine03 medical and health sciences0302 clinical medicineCerebrospinal fluidModified Rankin ScaleMedizinische FakultätInternal medicineprogranulinMedicineddc:6ddc:610taulcsh:Neurology. Diseases of the nervous systemOriginal ResearchAutoimmune encephalitisHippocampal sclerosisbusiness.industryNeurodegenerationAutoantibodyarticleNMDAR encephalitis ; neurofilament light chain ; Caspr2 encephalitis ; autoimmune encephalitis ; progranulin ; Lgi-1 encephalitis ; taumedicine.diseaseautoimmune encephalitis030104 developmental biologyneurofilament light chainNeurologyBiomarker (medicine)Neurology (clinical)business030217 neurology & neurosurgeryEncephalitis
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Early increased density of cyclooxygenase-2 (COX-2) immunoreactive neurons in Down syndrome

2017

iNeuroinflammation is one of the hallmarks of Alzheimer's disease. One of the enzymes involved in neuroinflammation, even in early stages of the disease, is COX-2, an inducible cyclooxygenase responsible for the generation of eicosanoids and for the generation of free radicals. Individuals with Down syndrome develop Alzheimer's disease early in life. Previous studies pointed to the possible overexpression of COX-2 and correlated it to brain regions affected by the disease. We analysed the COX-2 expression levels in individuals with Down syndrome and in young, adult and old mice of the Ts65Dn mouse model for Down syndrome. We have observed an overexpression of COX-2 in both, Down syndrome in…

0301 basic medicinemedicine.medical_specialtyDown syndromelcsh:MedicineMice TransgenicDiseasePathology and Forensic Medicineneuroinflammationmicroglia</i>Mice03 medical and health sciences0302 clinical medicineInternal medicinemedicineAnimalsHumansPostnatal dayNeuroinflammationNeuronschemistry.chemical_classificationMicrogliabiologybusiness.industryNeurodegenerationlcsh:RBrainmedicine.disease<i>Ts65Dn030104 developmental biologyEndocrinologymedicine.anatomical_structureEnzymechemistryCyclooxygenase 2biology.proteinNeurology (clinical)CyclooxygenaseDown SyndromebusinessNeuroscienceAlzheimer’s disease030217 neurology & neurosurgeryFolia Neuropathologica
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Obesogenic Diets Cause Alterations on Proteins and Theirs Post-Translational Modifications in Mouse Brains

2021

Obesity constitutes a major global health threat and is associated with a variety of diseases ranging from metabolic and cardiovascular disease, cancer to neurodegeneration. The hallmarks of neurodegeneration include oxidative stress, proteasome impairment, mitochondrial dysfunction and accumulation of abnormal protein aggregates as well as metabolic alterations. As an example, in post-mortem brain of patients with Alzheimer’s disease (AD), several studies have reported reduction of insulin, insulin-like growth factor 1 and insulin receptor and an increase in tau protein and glycogen-synthase kinase-3β compared to healthy controls suggesting an impairment of metabolism in the AD patient’s …

0301 basic medicinemedicine.medical_specialtyRC620-627Endocrinology Diabetes and Metabolismmedicine.medical_treatmentTau proteinObesity nutrition brain impairment proteomics post-translational modificationsBrain damageMitochondrionProteomicsmedicine.disease_causeSettore BIO/09 - Fisiologia03 medical and health sciencesproteomics0302 clinical medicineInternal medicinepost-translational modificationsmedicineTX341-641ObesityNutritional diseases. Deficiency diseasesOriginal ResearchSettore MED/04 - Patologia GeneraleNutrition and DieteticsbiologyNutrition. Foods and food supplyInsulinNeurodegenerationmedicine.diseasebrain impairmentInsulin receptornutrition030104 developmental biologyEndocrinologybiology.proteinmedicine.symptom030217 neurology & neurosurgeryOxidative stressFood ScienceNutrition and Metabolic Insights
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Prevalence of Age-Related Macular Degeneration in Europe

2017

Manuscript no. 2016-1147 Supplemental material is available at www.aaojournal.org/; International audience; [u]Purpose:[/u] Age-related macular degeneration (AMD) is a frequent, complex disorder in elderly of European ancestry. Risk profiles and treatment options have changed considerably over the years, which may have affected disease prevalence and outcome. We determined the prevalence of early and late AMD in Europe from 1990 to 2013 using the European Eye Epidemiology (E3) consortium, and made projections for the future. [u]Design:[/u] Meta-analysis of prevalence data. [u]Participants:[/u] A total of 42 080 individuals 40 years of age and older participating in 14 population-based cohor…

0301 basic medicinemedicine.medical_specialtyVisual acuityOPTICAL COHERENCE TOMOGRAPHYMACULOPATHYgenetic structuresPopulationPrevalenceHEART-DISEASEchoroidal neovascularizationSensory disorders Donders Center for Medical Neuroscience [Radboudumc 12]03 medical and health sciencesRotterdam Study0302 clinical medicineAll institutes and research themes of the Radboud University Medical CenterBEAVER DAM EYEEpidemiologygeographic atrophymedicineVISUAL IMPAIRMENT[SDV.MHEP.OS]Life Sciences [q-bio]/Human health and pathology/Sensory OrganseducationPOPULATIONeducation.field_of_studyBIRTH COHORTbusiness.industryMacular degenerationmedicine.diseaseTRENDSConfidence intervaleye diseases3. Good healthEuropean Prospective Investigation into Cancer and NutritionOphthalmology030104 developmental biologyAge-related Macular DegenerationENDOTHELIAL GROWTH-FACTORBLINDNESS030221 ophthalmology & optometryOptometryAge-related Macular Degeneration choroidal neovascularization geographic atrophysense organsmedicine.symptombusiness[SDV.MHEP]Life Sciences [q-bio]/Human health and pathologyDemography
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Regular Intake of Pistachio Mitigates the Deleterious Effects of a High Fat-Diet in the Brain of Obese Mice

2020

Obesity has been associated with neurodegeneration and cognitive dysfunctions. Recent data showed that pistachio consumption is able to prevent and ameliorate dyslipidemia, hepatic steatosis, systemic and adipose tissue inflammation in mice fed a high-fat diet (HFD). The present study investigated the neuroprotective effects of pistachio intake in HFD mice. Three groups of mice were fed a standard diet (STD), HFD, or HFD supplemented with pistachio (HFD-P) for 16 weeks. Metabolic parameters (oxidative stress, apoptosis, and mitochondrial dysfunction) were analyzed by using specific assays and biomarkers. The pistachio diet significantly reduced the serum levels of triglycerides and choleste…

0301 basic medicinemedicine.medical_specialtyobesityPhysiologyClinical BiochemistryAdipose tissuepistachiomedicine.disease_causeBiochemistryArticleSuperoxide dismutase03 medical and health sciences0302 clinical medicineInsulin resistanceInternal medicinemedicineoxidative stressMolecular Biologychemistry.chemical_classificationReactive oxygen speciesoxidative strebiologybusiness.industrylcsh:RM1-950digestive oral and skin physiologyneurodegenerationfood and beveragesnutritional and metabolic diseasesCell Biologymedicine.diseaseHeme oxygenaselcsh:Therapeutics. Pharmacology030104 developmental biologyEndocrinologychemistrybiology.proteinlipids (amino acids peptides and proteins)HFDSteatosisbusiness030217 neurology & neurosurgeryDyslipidemiaOxidative stresshormones hormone substitutes and hormone antagonists
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2019

Aging causes many changes in the human body, and is a high risk for various diseases. Dementia, a common age-related disease, is a clinical disorder triggered by neurodegeneration. Brain damage caused by neuronal death leads to cognitive decline, memory loss, learning inabilities and mood changes. Numerous disease conditions may cause dementia; however, the most common one is Alzheimer’s disease (AD), a futile and yet untreatable illness. Adult neurogenesis carries the potential of brain self-repair by an endogenous formation of newly-born neurons in the adult brain; however it also declines with age. Strategies to improve the symptoms of aging and age-related diseases have included differe…

0301 basic medicinemedicine.medical_treatmentDiseaseBrain damageCatalysisInorganic Chemistry03 medical and health sciences0302 clinical medicineMedicineDementiaPhysical and Theoretical ChemistryCognitive declineMolecular BiologySpectroscopybusiness.industryOrganic ChemistryNeurodegenerationNeurogenesisGeneral MedicineStem-cell therapymedicine.diseaseComputer Science Applications030104 developmental biologymedicine.symptomStem cellbusinessNeuroscience030217 neurology & neurosurgeryInternational Journal of Molecular Sciences
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