Search results for "Familial"

showing 10 items of 365 documents

Brain responses to speech sounds in infants and children with and without familial risk for dyslexia

2015

Dyslexia, a specific reading disability, runs in families. Therefore, the risk for a child to become dyslexic increases multifold if reading difficulties occur in the family. One risk factor for dyslexia is a deficit in speech perception. Using EEG, speech sound discrimination was found to be more demanding than non- speech discrimination in typical readers in Study I. In Study II, in children with dyslexia in 3rd grade, enhanced brain responses were observed and found to be associated with better performance in reading accuracy, spelling accuracy and phonemic length discrimination tasks. The brain responses of the most accurate readers in the dyslexia group originated from a more posterior…

Speech perceptionpuheääniherätevasteetvauvatriskitekijätkuulohavainnotperinnöllinen alttiusfonologinen tietoisuusDyslexiaevent-related potentials (ERP)puheen havaitseminendysleksiaelectroencephalography (EEG)EEGfamilial risklukihäiriötpoikkeavuusnegatiivisuusInfantsChildrensuvullinen riskilapset
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Du certificat médical exigé pour le versement des prestations familiales au titre d'un enfant étranger résidant en France

2012

International audience; Cour de cassation (2e Ch. civ.). - 16 décembre 2011

Sécurité socialeEnfant[SHS.DROIT]Humanities and Social Sciences/Law[SHS.DROIT] Humanities and Social Sciences/LawEntrée et séjour en FranceEnfant mineurDROIT ET LIBERTE FONDAMENTAUXEnfant étrangerETRANGERPrestations familialesVie privée et familiale
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Non-discrimination fondée sur la nationalité pour l'octroi des prestations familiales

2014

International audience; Cass., ass. plén., 5 avr. 2013, n° 11-18.947 et n° 11-17.520, D. 2013. 1009, et les obs. ; ibid. 1298, chron. O.-L. Bouvier ; ibid. 2014. 445, obs. O. Boskovic, S. Corneloup, F. Jault-Seseke, N. Joubert et K. Parrot ; AJ fam. 2013. 305, obs. I. Gallmeister, obs. S. Slama ; RDSS 2013. 527, note F. Monéger ; RTD eur. 2014. 472, obs. Ève Matringe et Mariana Lunca-Muller

Sécurité sociale[SHS.DROIT]Humanities and Social Sciences/Law[SHS.DROIT] Humanities and Social Sciences/LawEntrée et séjour en FranceEnfant mineurETRANGERPrestations familiales
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Familial amyloidosis: great progress for an orphan disease.

2015

Familial amyloidosis: Great progress for an orphan disease Ana Paula Barreiros1,2,*, Gerd Otto3, Bita Kahlen1, Andreas Teufel1,2, Peter R. Galle1 1Department of Internal Medicine I, Universitatsmedizin of the Johannes Gutenberg-University Mainz, Germany; 2Department of Internal Medicine I, Universitatsklinikum of the University Regensburg, Germany; 3Department of Hepatobiliary and Transplantation Surgery, Universitatmedizin of the Johannes Gutenberg-University Mainz, Germany. *Corresponding author. Address: Universitatsklinikum Regensburg, Department of Internal Medicine I, Franz-Josef-Strauss Allee 11, 93053 Regensburg, Germany. Tel.: +49 941-944-7021. E-mail address: Ana.Barreiros@ukr.de …

TafamidisFamilial amyloidosismedicine.medical_specialtyPathologyPharmacological therapymedicine.medical_treatmentDiseaseLiver transplantationGlobal Healthchemistry.chemical_compoundRare DiseasesMedicineHumansTransplantation surgeryLiver transplantationHepatologybusiness.industryGeneral surgerymusculoskeletal neural and ocular physiologyDisease ManagementPharmacological therapymedicine.diseaseTafamidissurgical procedures operativechemistryGERDMorbiditybusinessFamilial amyloidosisAmyloidosis FamilialJournal of hepatology
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Two-generation cardiovascular disease prevalence in familial hypercholesterolemia

2016

Two generationPediatricsmedicine.medical_specialtybusiness.industrymedicinePrevalenceFamilial hypercholesterolemiaCardiology and Cardiovascular Medicinebusinessmedicine.diseaseAtherosclerosis
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New Lipid Modulating Drugs: The Role of Microsomal Transport Protein Inhibitors

2011

Microsomal triglyceride transfer protein (MTP) is involved in the synthesis of very low density lipoprotein in the liver. Its deficiency results in abetalipoproteinemia. MTP inhibitors target the assembly and secretion of apolipoprotein B-containing lipoproteins. These agents may potentially play a role, alone or in combination, in the treatment of hypercholesterolemia or hypertriglyceridemia. Clinical applications of MTP inhibitors initially focused primarily on high-dose monotherapy in order to produce substantial reductions in LDL-cholesterol levels but these proved to induce significant hepatic steatosis and transaminase elevations. However, likely orphan indications for MTP inhibitors,…

Very low-density lipoproteinApolipoprotein BHypercholesterolemiaFamilial hypercholesterolemiaLipoproteins VLDLPharmacologyMicrosomal triglyceride transfer proteinHyperlipoproteinemia Type IIchemistry.chemical_compoundMicrosomesDrug DiscoveryClinical endpointHumansMedicineApolipoproteins BHypertriglyceridemiaPharmacologybiologybusiness.industryCholesterolAbetalipoproteinemiamedicine.diseaseAbetalipoproteinemiaBiochemistrychemistryMTP-inhibitors lipids lipoproteins atherosclerosis cardiovascular prevention.biology.proteinlipids (amino acids peptides and proteins)SteatosisCarrier ProteinsbusinessCurrent Pharmaceutical Design
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Les suites de l'arrêt Mazurek dans le droit interne français

2001

International audience

Vocation successorale réduite[SHS.DROIT]Humanities and Social Sciences/Law[SHS.DROIT] Humanities and Social Sciences/LawSUCCESSIONFiliation naturelleEnfant adultérinDROIT ET LIBERTE FONDAMENTAUXVie familialeDroits successorauxComputingMilieux_MISCELLANEOUS
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Evaluation agroécologique de systèmes de culture en zone tropicale humide : Cas de la mise en valeur agricole d'une savane herbacée acide (Plaine des…

2013

Dans les régions tropicales humides, concilier intensification agricole et protection des ressources naturelles est un défi majeur et difficile à relever. Dans les savanes acides du nord-est laotien, des systèmes de culture de semis direct sur couverture végétale (SCV), basés sur les trois principes du non-labour, d’une couverture permanente du sol, et sur la pratique de rotations culturales diversifiées, sont proposés comme alternative technique à l’intensification agricole conventionnelle basée sur le labour. Si ces systèmes ont connu une diffusion importante et rapide dans les grandes agricultures mécanisées, leur diffusion reste néanmoins à ce jour limitée en contexte de petite agricult…

[SDE] Environmental SciencesH01 - Protection des végétaux - Considérations généralesSemis directhttp://aims.fao.org/aos/agrovoc/c_28568http://aims.fao.org/aos/agrovoc/c_28766solF08 - Systèmes et modes de culturesavane tropicale acideagroécologieBiologie du solhttp://aims.fao.org/aos/agrovoc/c_7193Performance de cultureNon-travail du sol[SDV.BV] Life Sciences [q-bio]/Vegetal Biologyhttp://aims.fao.org/aos/agrovoc/c_2018Savanehttp://aims.fao.org/aos/agrovoc/c_8511http://aims.fao.org/aos/agrovoc/c_3145http://aims.fao.org/aos/agrovoc/c_35657Petite agricultureévaluation agroécologiquehttp://aims.fao.org/aos/agrovoc/c_7182Sol acidehttp://aims.fao.org/aos/agrovoc/c_25803http://aims.fao.org/aos/agrovoc/c_1919http://aims.fao.org/aos/agrovoc/c_765http://aims.fao.org/aos/agrovoc/c_92381[SDV] Life Sciences [q-bio]Pratique culturaleLaosagriculture de conservationhttp://aims.fao.org/aos/agrovoc/c_7979Micro-organisme du solhttp://aims.fao.org/aos/agrovoc/c_89Zone tropicaleP33 - Chimie et physique du solÉcologieExploitation agricole familialehttp://aims.fao.org/aos/agrovoc/c_37938Spectroscopie infrarougeChampignonAnalyse coût avantageCulture sous couvert végétalMatière organique du solhttp://aims.fao.org/aos/agrovoc/c_36167http://aims.fao.org/aos/agrovoc/c_4176http://aims.fao.org/aos/agrovoc/c_12076http://aims.fao.org/aos/agrovoc/c_35199Propriété physicochimique du solécologie microbienneBacteriaProductivité des terressemis direct sur couverture végétaleP35 - Fertilité du solÉvaluation de l'impacthttp://aims.fao.org/aos/agrovoc/c_7160P34 - Biologie du solE80 - Économie familiale et artisanaleAnalyse économiqueTaxonomiehttp://aims.fao.org/aos/agrovoc/c_25706structure agrairehttp://aims.fao.org/aos/agrovoc/c_6825http://aims.fao.org/aos/agrovoc/c_2787Système de culturehttp://aims.fao.org/aos/agrovoc/c_2469http://aims.fao.org/aos/agrovoc/c_1971http://aims.fao.org/aos/agrovoc/c_17299U30 - Méthodes de recherchePlante de culturehttp://aims.fao.org/aos/agrovoc/c_2467http://aims.fao.org/aos/agrovoc/c_1972Cycle du carbonehttp://aims.fao.org/aos/agrovoc/c_7631
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Identification and diagnosis of patients with familial chylomicronaemia syndrome (FCS): Expert panel recommendations and proposal of an "FCS score".

2018

Familial chylomicronaemia syndrome (FCS) is a rare, inherited disorder characterised by impaired clearance of triglyceride (TG)-rich lipoproteins from plasma, leading to severe hypertriglyceridaemia (HTG) and a markedly increased risk of acute pancreatitis. It is due to the lack of lipoprotein lipase (LPL) function, resulting from recessive loss of function mutations in the genes coding LPL or its modulators. A large overlap in the phenotype between FCS and multifactorial chylomicronaemia syndrome (MCS) contributes to the inconsistency in how patients are diagnosed and managed worldwide, whereas the incidence of acute hypertriglyceridaemic pancreatitis is more frequent in FCS. A panel of Eu…

[SDV]Life Sciences [q-bio]Diagnosis toolpopulation030204 cardiovascular system & hematologyburdenapoa50302 clinical medicineLoss of Function MutationRisk FactorsChylomicrons030212 general & internal medicineAge of OnsetHypolipidemic AgentsBIOMEDICINA I ZDRAVSTVO. Kliničke medicinske znanosti. Interna medicina.Lipoprotein lipaseplasma triglycerideshyperlipoproteinemiaPrognosis3. Good healthUp-RegulationPhenotypeAcute pancreatitislipids (amino acids peptides and proteins)Hyperlipoproteinemia Type IAcute pancreatitis ; Familial chylomicronaemia syndrome ; Major hypertriglyceridaemia ; Multifactorial chylomicronaemiaCardiology and Cardiovascular MedicineFamilial chylomicronaemia syndromeAlgorithmsacute-pancreatitismedicine.medical_specialtyConsensushypertriglyceridemiaetiologyAcute pancreatitis; Familial chylomicronaemia syndrome; Major hypertriglyceridaemia; Multifactorial chylomicronaemia/Decision Support TechniquesDiagnosis Differential03 medical and health sciencesAcute pancreatitis; Familial chylomicronaemia syndrome; Major hypertriglyceridaemia; Multifactorial chylomicronaemia; Cardiology and Cardiovascular MedicinePredictive Value of TestsInternal medicinemedicineHumansGenetic Predisposition to DiseaseAcute pancreatitiBIOMEDICINE AND HEALTHCARE. Clinical Medical Sciences. Internal Medicine.GenotypingTriglyceridesPregnancyReceiver operating characteristicbusiness.industrysevereMultifactorial chylomicronaemiaReproducibility of Resultsmutationslipoprotein-lipase genemedicine.diseaseConfidence intervalAcute pancreatitisLipoprotein LipasePancreatitisCardiovascular System & CardiologyPancreatitisMajor hypertriglyceridaemiabusinessBiomarkersAtherosclerosis
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Des relations familiales modifiées : de conjointe ou fille à aidante

2018

International audience

[SHS.DEMO] Humanities and Social Sciences/Demographyfille[SHS] Humanities and Social Sciences[SHS.DEMO]Humanities and Social Sciences/DemographyaidanteconjointeComputingMilieux_MISCELLANEOUS[SHS]Humanities and Social Sciencesrelations familiales
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