Search results for "Intellect"

showing 10 items of 642 documents

AICA-ribosiduria due to ATIC deficiency: Delineation of the phenotype with three novel cases, and long-term update on the first case.

2020

5-Amino-4-imidazolecarboxamide-ribosiduria (AICA)-ribosiduria is an exceedingly rare autosomal recessive condition resulting from the disruption of the bifunctional purine biosynthesis protein PURH (ATIC), which catalyzes the last two steps of de novo purine synthesis. It is characterized biochemically by the accumulation of AICA-riboside in urine. AICA-ribosiduria had been reported in only one individual, 15 years ago. In this article, we report three novel cases of AICA-ribosiduria from two independent families, with two novel pathogenic variants in ATIC. We also provide a clinical update on the first patient. Based on the phenotypic features shared by these four patients, we define AICA-…

Hydroxymethyl and Formyl TransferasesMalemedicine.medical_specialtyCyclohydrolase activityBioinformaticsCongenital AbnormalitiesEpilepsyMultienzyme ComplexesIntellectual DisabilityGeneticsmedicineHumansBifunctional Purine Biosynthesis Protein PURHChildGenetics (clinical)ATIC DEFICIENCYEpilepsybusiness.industryInfant NewbornInfantmedicine.diseaseAminoimidazole CarboxamidePhenotypePhenotypeNucleotide DeaminasesChild PreschoolMutationMedical geneticsFemaleRibonucleosidesNephrocalcinosisbusinessRare diseaseJournal of inherited metabolic diseaseREFERENCES
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INTELLECTUAL CAPITAL IN THE NON PROFIT SECTOR. MEASUREMENT PROBLEMS AND EMPIRICAL EVIDENCE

2007

In doctrine, there is wide agreement on what is the main purpose of a company, identified as a firm’s capacity to create sustainable value. In the present economy, known as the knowledge economy, the main company value drivers are considered intangible resources and activities. The present work focuses on analysing the definition and measurement of Intellectual Capital in the non-profit or third sector organizations, and in particular in the health care sector, chosen for its relevance within the third sector.The contribution that this work seeks to provide is to give the reader a better comprehension of the IC theme in third sector organizations, by analysing the empirical evidence of IC n…

INTELLECTUAL CAPITALNON PROFIT
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Autistic Adult Health and Professional Perceptions of It: Evidence From the ASDEU Project

2021

The Autism Spectrum Disorders in the European Union (ASDEU) survey investigated the knowledge and health service experiences of users and providers to generate new hypotheses and scientific investigations that would contribute to improvement in health care for autistic adults. An online survey designed for autistic adults, carers of autistic adults, and professionals in adult services was translated into 11 languages and distributed electronically by organizations and in-country adult service facilities in 2017; 522 autistic adults, 442 carers, and 113 professionals provided answers to the health questions. Professionals, the majority in non-medical services, appeared to be poorly informed …

INTELLECTUAL DISABILITYAutism Spectrum DisorderRC435-571ServicesUS CHILDREN3124 Neurology and psychiatry0302 clinical medicineHealth careIntellectual disabilityYOUNG-ADULTSadultsSpectrum disorderYoung adult10. No inequalityOriginal Researchmedia_commonPsychiatryCo-occurring Conditions4. Education05 social scienceshealth3. Good healthEuropePsychiatry and Mental healthAutism spectrum disorderHealthPsychology050104 developmental & child psychologymedicine.medical_specialtyservices515 PsychologyAGED 8 YEARSco-occurring conditionsUNITED-STATESEMERGENCY-DEPARTMENT VISITSautism spectrum disorder03 medical and health sciencesautism spectrum disorder adults health co-occurring conditions servicesmedicinemedia_common.cataloged_instanceAdults0501 psychology and cognitive sciencesEuropean unionPsychiatrySPECTRUM DISORDERService (business)business.industryDEVELOPMENTAL-DISABILITIESmedicine.diseaseDISABILITIES MONITORING NETWORKPerturbações do Desenvolvimento Infantil e Saúde MentalAutism[SDV.SPEE]Life Sciences [q-bio]/Santé publique et épidémiologiePSYCHIATRIC COMORBIDITYbusiness030217 neurology & neurosurgery
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Socioloģija

2006

Ikdienas dzīveSocial stratificationKultūras socioloģijaSociālā stratifikācija:SOCIAL SCIENCES::Social sciences::Sociology [Research Subject Categories]IntellectualitySociology of cultureDzīves kvalitāteIntelektuālismsSociālie procesiSocial processesEtnicitāte
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Universidad Social Capital and the Competitiveness of Entrepreneurs: A Review of the Literature and Proposals

2008

The essential question asked in this study is "How can social capital become a competitive tool for entrepreneurs". The answer lies in showing how their own networks can provide the value and competitiveness that entrepreneurs need for their business projects.

Individual capitalEmprendedoresHuman capitalIntellectual capitalFinancial capitalValue (economics)EconomicsClassical economicsCompetitividadEconomic systemMediciónCapital SocialSocial capital
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Contractual Solutions for Digitalized Cross-Company Value Networks in Industry 4.0 - Part 1: Introduction

2021

This series of papers deals with issues of contract law in Industrie 4.0. It is based on the law of the Federal Republic of Germany. Part 1 introduces the topic and explains the legal problems that arise in Industrie 4.0. Part 2 deals with issues of contract law: How are contracts concluded among autonomous software agents, what types of contracts come into question, and how must general terms and conditions be structured. Part 3 looks at issues of licensing law and intellectual property in data. Part 4 looks at the liability of autonomous systems in Industry and provides an outlook on possible future solutions. Industrial production is increasingly taking place in digitized value chains in…

Industry 4.0business.industryCommon lawLiabilityTechnical standardInformation technologyLegislationBusinessIntellectual propertyDue diligenceLaw and economicsSSRN Electronic Journal
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Juridiskā zinātne, Nr.6 

2014

Journal “Law” of the University of Latvia is financed by the Faculty of Law of the University of Latvia

Infringement of the inviolability of the homeNotary servicesIntellectual property:LAW/JURISPRUDENCE [Research Subject Categories]New York ConventionOwnership claimPrinciple of flexicurity in European UnionProcedure of the Constitutional CourtVictims in criminal proceedings
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The role of IPR arrangements in the crowdsourcing for innovation contest: an empirical investigation of the Innocentive challenges

2017

In this study, we identify three different Intellectual Property Right arrangements- strong IPR (acquiring an IP), weak IPR (licensing agreement) and flexible IPR. Integrating Property Rights Theory and the open innovation literature, we propose that specific challenge attributes affect the seekers organizations’ choice between alternative IPR arrangements and how this choice, in turn, affects the self-selection of external solvers into solving the problem. We collected multi-source, interview data with open innovation directors and a unique data set of 819 closed and awarded challenges broadcasted on InnoCentive platform from 2010 to 2016. Our findings contribute to the emerging literature…

InnoCentiveCrowdsourcing for innovation Intellectual Property Rights Challenge performanceProperty rights theory
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Intellectual Capital Management Increase in Offshoring

2021

Offshoring is a method for companies from automotive software development industry to have access to a larger pool of talents or to reduce the development costs. In order to have success, the management must be prepared for knowledge transfer process that will be different while compared to training a new employee at the headquarters. Many companies fail when this step is made and instead of reducing the costs, the loss can drag down the business even to the bankruptcy. In this paper, it is presented a solution for a systematic knowhow increase for the new offshore team, applicable to the processes of knowledge transfer. Complex trainings and various methods of solving the orders are not re…

Intellectual capital managementOffshoringComputingMilieux_THECOMPUTINGPROFESSIONProcess (engineering)BankruptcyOrder (exchange)TA1-2040Automotive software developmentEngineering (General). Civil engineering (General)Knowledge transferIndustrial organizationMATEC Web of Conferences
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La disclosure del capitale intellettuale. Un’analisi empirica delle società quotate italiane

2012

Nell’attuale ambiente economico la ricchezza che un’azienda è in grado di generare è sempre più condizionata dalla sua capacità di apprendere, innovare, capitalizzare conoscenze e sviluppare relazioni. Tali elementi, identificati nella letteratura con il termine di capitale intellettuale, rappresentano per le aziende una risorsa chiave capace di generare vantaggi competitivi sulla concorrenza. Diventa pertanto essenziale comunicare e adeguatamente rappresentare tale risorsa. I documenti in cui è possibile trovare informazioni sul capitale intellettuale sono sia quelli di rendicontazione volontaria sia obbligatoria.Obiettivo del volume è di analizzare l’importanza del capitale intellettuale …

Intellectual capitalDisclosuresocietà quotate
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