Search results for "MOSAICI"

showing 10 items of 68 documents

NEXMIF encephalopathy: an X-linked disorder with male and female phenotypic patterns

2021

Contains fulltext : 231688.pdf (Publisher’s version ) (Closed access) PURPOSE: Pathogenic variants in the X-linked gene NEXMIF (previously KIAA2022) are associated with intellectual disability (ID), autism spectrum disorder, and epilepsy. We aimed to delineate the female and male phenotypic spectrum of NEXMIF encephalopathy. METHODS: Through an international collaboration, we analyzed the phenotypes and genotypes of 87 patients with NEXMIF encephalopathy. RESULTS: Sixty-three females and 24 males (46 new patients) with NEXMIF encephalopathy were studied, with 30 novel variants. Phenotypic features included developmental delay/ID in 86/87 (99%), seizures in 71/86 (83%) and multiple comorbidi…

MalePediatricsmedicine.medical_specialtyINTELLECTUAL DISABILITYAutism Spectrum DisorderEncephalopathyNerve Tissue ProteinsILAE COMMISSIONMOSAICISMEpilepsy/geneticsCLASSIFICATIONEpilepsyBrain Diseases/geneticsGenes X-LinkedSeizuresIntellectual disabilityGenotypemedicineHumansdevelopmental and epileptic encephalopathyMYOCLONIAAtonic seizureGenetics (clinical)Brain Diseasesddc:618Neurodevelopmental disorders Donders Center for Medical Neuroscience [Radboudumc 7]KIAA2022business.industryMUTATIONSmedicine.diseasePhenotypeAutism Spectrum Disorder/geneticsGenes X-Linked/geneticsAutism spectrum disorderintellectual disabilityNEXMIFAutismepilepsyFemaleINACTIVATIONHuman medicineSeizures/geneticsbusinessPOSITION PAPERGenetics in Medicine
researchProduct

Faceting and structural anisotropy of nanopatterned CdO(110) layers

2005

CdO(110) layers with a self-organized surface structure have been grown on (10math0) sapphire (m plane) substrates by metal-organic vapor phase epitaxy. The epitaxial relationships between layer and substrate have been determined and a crystallographic model that accounts for the CdO in-plane orientation, which results in a reduced lattice mismatch when the CdO[001] direction is perpendicular to the sapphire c axis, has been proposed. Although the measured lattice parameters indicate that the layers are almost fully relaxed, an anisotropic mosaicity is detected with symmetrical rocking curves attaining minimum values when measured along the CdO[math10] direction. The layer morphology consis…

Materials scienceGeneral Physics and AstronomySemiconductor growthEpitaxyMosaicityVapour phase epitaxial growthCadmium compound ; Semiconductor epitaxial layers ; II-VI semiconductors ; Semiconductor growth ; Vapour phase epitaxial growth ; MOCVD ; Nanopatterning ; Self-assembly ; Lattice constants ; Mosaic structure ; Surface morphologyLattice constant:FÍSICA [UNESCO]PerpendicularMetalorganic vapour phase epitaxyAnisotropyCondensed matter physicsUNESCO::FÍSICASemiconductor epitaxial layersLattice constantsNanopatterningII-VI semiconductorsSelf-assemblyFacetingCrystallographyCadmium compoundMOCVDSapphireSurface morphologyMosaic structure
researchProduct

Tecsis: Low-Cost Methodology To Distinguish Archaeological Findings

2006

The automatic or semi-automatic research of archaeological findings includes some methodologies and algorithms of the Computer Vision. Reconstruction of a scene is one of the key step to get the solution to that challenge. This paper will address a methodology to reconstruction underwater scenes with mosaicing techniques. The reconstruction of scene will be the video-mosaic of sea bottom landscapes starting from single video frames. The methodology is based on the evaluation of the optic °ow in between frames, and its motion estimation has been evaluated on the extracted features from the common areas of consecutive pairs frames. This approach carried out the motion model from a geometric p…

Motion compensationEcologySettore INF/01 - InformaticaComputer scienceFrame (networking)ComputingMethodologies_IMAGEPROCESSINGANDCOMPUTERVISIONMotion modelArchaeologyGeometrical transformationMotion (physics)Motion estimationKey (cryptography)General Earth and Planetary SciencesArchaeological findingNoise (video)MosaicingProjection (set theory)Ecology Evolution Behavior and SystematicsComputingMethodologies_COMPUTERGRAPHICSGeneral Environmental ScienceReference frame
researchProduct

Inheritance and variable expression in Rubinstein-Taybi syndrome.

2010

Familial Rubinstein-Taybi syndrome (RTS) is very rare. Here we report on the 6th and 7th case of inherited RTS. Family 1 presents with incomplete or mild RTS over three generations; a 13-year-old girl (proband 1) with mild but typical facial features and learning disabilities, her very mildly affected mother (proband 2), and the maternal grandmother (proband 3). Family 2 includes three females with classical RTS (probands 4-6) and their father (proband 7) with broad thumbs and halluces. Proband 5 also had a brain tumor (ganglioglioma) at the age of 3 years. In probands 1-3, direct sequencing identified a novel CREBBP missense mutation, c.2728A > G (predicting p.Thr910Ala), that was absent i…

ProbandMaleRiskAdolescentDNA Mutational AnalysisMutation MissenseBiologyVariable ExpressionGenetic HeterogeneityGeneticsmedicineMissense mutationHumansPoint MutationFamilyAlleleGenetics (clinical)GeneticsRubinstein-Taybi SyndromeRubinstein–Taybi syndromeGenetic heterogeneityMosaicismPoint mutationmedicine.diseaseCREB-Binding ProteinPedigreePhenotypeChild PreschoolMutation (genetic algorithm)FemaleAmerican journal of medical genetics. Part A
researchProduct

Tissue-specific mosaicism in a patient with Rubinstein–Taybi syndrome and CREBBP exon 1 duplication

2019

Rubinstein-Taybi SyndromeGeneticsRubinstein–Taybi syndromeMosaicismbusiness.industryFaciesExonsGeneral Medicinemedicine.diseaseCREB-Binding ProteinPathology and Forensic MedicineExonOrgan SpecificityGene DuplicationPediatrics Perinatology and Child HealthGene duplicationmedicineHumansTissue specificFemaleAnatomyChildbusinessE1A-Associated p300 ProteinGenetics (clinical)Clinical Dysmorphology
researchProduct

Madonie, L'arte e la storia

2021

Il volume esamina il patrimonio storico artistico dei seguenti paesi delle Madonie: Caltavuturo, Castelbuono, Cefalù, Collesano, Geraci Siculo, Gangi, Gratteri, Isnello, Petralia Soprana, Petralia Sottana, Polizzi Generosa, Pollina, San Mauro Castelverde e Sclafani Bagni. Per ogni singolo borgo si affronta brevemente la storia della città e successivamente si esaminano le chiese e le opere d’arte ivi contenute, iniziando dalla Chiesa Madre o dalla Basilica per poi continuare con gli altri edifici chiesastici e i palazzi nobiliari. Particolare attenzione viene riservata all’architettura, come le chiese medievali e rinascimentali di Castelbuono, Gratteri e Isnello o quelle barocche e rococò d…

Sacred art painting sculpture architecture Madonie Museums Antonello da Messina Flemish painting commissioning Manner Renaissance Baroque medieval works painted crosses mosaics SicilyArte sacra pittura scultura architettura Madonie Musei Antonello da Messina pittura fiamminga committenza Maniera Rinascimento Barocco opere medievali croci dipinte mosaici SiciliaSettore L-ART/02 - Storia Dell'Arte Moderna
researchProduct

La rappresentazione dell'architettura in alcuni rivestimenti musivi di epoca medievale in Sicilia

2019

Nei mosaici che decorano le chiese costruite in Sicilia nel XII dai re normanni compaiono rappresentazioni di edifici. Tali rappresentazioni, come frequentemente accade in epoca pre-rinascimentale, condensano, per accostamento, diverse ‘viste’ dello stesso edificio. La presenza negli edifici normanni di pavimenti e manufatti lignei decorati secondo pattern geometrici, ha suggerito la ricerca di analoghi tracciati nei rivestimenti musivi. L’analisi grafica propone la presenza di quadrati e ottagoni stellati in un mosaico della Cappella palatina di Palermo che raffigura un padiglione coperto da una cupola. Many buildings are depicted in the mosaic panels that enrich the churches built in Sici…

Settore ICAR/17 - DisegnoMosaic Norman Sicily Medieval painting Geometric patterns Palatine Chapel.Mosaici Normanni Pittura medievale Tracciati regolatori Cappella Palatina
researchProduct

Frammenti di mosaico riportati su calcestruzzo:le interazioni con il supporto e il progetto di conservazione

2010

Settore ING-IND/22 - Scienza E Tecnologia Dei Materialimosaics concrete deterioration Villa del CasaleSettore GEO/05 - Geologia Applicatamosaici romanidegrado materiali costitutivi
researchProduct

Super-resolution-based magnification of endothelium cells from biomicroscope videos of the cornea

2018

We present a practical, robust, and effective pipeline to compute a high-resolution (HR) image of the corneal endothelium starting from a low-resolution (LR) video sequence obtained with a general purpose slit lamp biomicroscope. An image quality typical of dedicated and more expensive confocal microscopes is achieved via software magnification by exploiting information redundancy in the video sequence. In particular, the HR image is generated from the best LR frames, obtained by identifying the most suitable endothelium video subsequence using a support vector machine-based learning approach, followed by a robust graph-based frame registration. Results on long, real sequences show that the…

Settore ING-INF/05 - Sistemi Di Elaborazione Delle InformazioniImage fusionSettore INF/01 - InformaticaImage qualityComputer sciencebusiness.industryFrame (networking)ComputingMethodologies_IMAGEPROCESSINGANDCOMPUTERVISIONImage registrationMagnificationsuper-resolutionImage segmentationAtomic and Molecular Physics and Opticsslit lamp biomicroscope image enhancementComputer Science ApplicationsSupport vector machinecorneal endotheliumSoftwaremachine learningComputer visionimage mosaicingArtificial intelligenceElectrical and Electronic Engineeringbusiness
researchProduct

Color Correction for Image Stitching by Monotone Cubic Spline Interpolation

2015

This paper proposes a novel color correction scheme for image stitching where the color map transfer is modelled by a monotone Hermite cubic spline and smoothly propagated into the target image. A three-segments monotone cubic spline minimizing color distribution statistics and gradient differences with respect to both the source and target images is used. While the spline model can handle non-linear color maps, the minimization over the gradient differences limits strong alterations on the image structure. Adaptive heuristics are introduced to reduce the minimization search space and thus computational time. Experimental comparisons with respect to the state-of-the-art linear mapping model…

Settore ING-INF/05 - Sistemi Di Elaborazione Delle InformazioniImage stitchingDemosaicingSettore INF/01 - Informaticabusiness.industryColor correctionMathematicsofComputing_NUMERICALANALYSISComputingMethodologies_IMAGEPROCESSINGANDCOMPUTERVISIONMonotone cubic interpolationPhotometric blendingCubic Hermite splineSmoothing splineColor transferComputer visionArtificial intelligenceColor transfer image stitching photometric blendingbusinessSpline interpolationThin plate splineAlgorithmImage gradientComputingMethodologies_COMPUTERGRAPHICSMathematics
researchProduct