Search results for "MUTATION"

showing 10 items of 2830 documents

Rubinstein–Taybi syndrome 2 with cerebellar abnormality and neural tube defect

2019

Rubinstein-Taybi syndrome (RSTS) is a rare dominant disorder with intellectual disability, postnatal growth deficiency, and multiple congenital anomalies. Approximately 50-70% of the patients have a mutation in the CREBBP gene (RSTS1) and 5-10% display an EP300 gene mutation (RSTS2). Craniospinal abnormalities such as microcranium, scoliosis, and lordosis are frequent findings in RSTS1, but malformations of the brain or spinal cord are seen only occasionally. Here, we report on a 3-year-old boy with facial abnormalities of RSTS, broad thumbs and halluces, developmental delay, autistic features, cerebellar underdevelopment, and a neural tube defect. Molecular diagnostic of the CREBBP and EP3…

Malespeech delayHeterozygoteCerebellumGenotypecerebellar abnormalityScoliosisGene mutationPathology and Forensic MedicineCerebellummedicinetethered cordHumansmicrocephalyGenetic TestingNeural Tube DefectsFrameshift MutationEP300Genetic Association StudiesGenetics (clinical)Sequence DeletionRubinstein-Taybi Syndromeautistic behaviorRubinstein–Taybi syndromeNeural tube defectGenome Humanbusiness.industryNeural tubeHigh-Throughput Nucleotide Sequencingstereotypic movementsvesicoureteral refluxOriginal Articleslumbosacral myeloceleExonsGeneral MedicineAnatomymedicine.diseaseSpinal cordCREB-Binding Proteinmedicine.anatomical_structuresyringohydromyeliaChild PreschoolMutationPediatrics Perinatology and Child Healthbroad thumbs and hallucesAnatomybusinessE1A-Associated p300 ProteinClinical Dysmorphology
researchProduct

Pan-cancer analysis of whole genomes

2020

Publisher's version (útgefin grein)

Maletert promoter mutationsCancer development and immune defence Radboud Institute for Molecular Life Sciences [Radboudumc 2]DNA Mutational AnalysisNormal tissuesystematic analysisGermlineTranscriptome0302 clinical medicineAetiologyCàncerCellular SenescenceCancer0303 health sciencesdna-damageMassive parallel sequencingPan cancerREARRANGEMENTSHigh-Throughput Nucleotide SequencingGenomicsSciences bio-médicales et agricolesTelomereCOMPREHENSIVE3. Good healthTERT PROMOTER MUTATIONSsignatures030220 oncology & carcinogenesisScience & Technology - Other TopicsErfðarannsóknirHuman:Informàtica::Aplicacions de la informàtica::Bioinformàtica [Àrees temàtiques de la UPC]EvolutionRNA SplicingGenomicsArticleEvolution MolecularStructural variationRC025403 medical and health sciencesSDG 3 - Good Health and Well-beingGeneticgenomicsSYSTEMATIC ANALYSISGeneticsGenomics--Databases.HumansGenetic TestingMolecular BiologySIGNATURESWhole genome sequencing1000 MultidisciplinaryChromothripsisScience & TechnologyRC0254 Neoplasms. Tumors. Oncology (including Cancer)Information DisseminationResearchInstitutes_Networks_Beacons/mcrcPreventionBiology and Life SciencesMolecularOncogenesCloud Computingmedicine.diseaseGenòmicaCompute cloudsMutation570 Life sciences; biologyCOMPREHENSIVE CHARACTERIZATIONGenèticaWhole Genome Sequencing--methodsBackground informationDNA Mutational Analysis ; Evolution ; Genetic / genetics ; Genome ; Genomics ; Germ-Line Mutation / genetics ; High-Throughput Nucleotide Sequencing ; Human / genetics ; Humans ; ICGC/TCGA Pan-Cancer Analysis of Whole Genomes ConsortiumMedizinGenomeWhole-genomeGenome mappingNeoplasms2.1 Biological and endogenous factorsPromoter Regions GeneticCàncer -- Aspectes genèticsTelomeraseGeneticsWomen's cancers Radboud Institute for Molecular Life Sciences [Radboudumc 17]MultidisciplinaryChromothripsisGenomeManchester Cancer Research Centregenomics cancer profiling3rd-DAS10124 Institute of Molecular Life SciencesWomen's cancers Radboud Institute for Health Sciences [Radboudumc 17]Multidisciplinary SciencesParallel sequencingICGC/TCGA Pan-Cancer Analysis of Whole Genomes ConsortiumFemaleprofilingMedical GeneticsEngineering sciences. TechnologyBiotechnologyGeneral Science & TechnologyThe Cancer Genome Atlas610 Medicine & healthComputational biologyQH426 GeneticsBiologyConsortium of the International Cancer Genome ConsortiumPromoter RegionsGermline mutationPan-cancer analysisKrabbameinsrannsóknirmedicinecancerddc:610QH426Germ-Line MutationMedicinsk genetikKrabbamein030304 developmental biologyCell ProliferationLANDSCAPEGenome Humancomprehensive characterizationPan-cancer analysis of whole genomesPoint mutationHuman GenomeCancerReproducibility of ResultsSOMATIC MUTATIONSEVOLUTIONCancer sequencing Chromothripsis telomereDNA-DAMAGEMutagenesisPATTERNS3111 BiomedicineCHARACTERIZATION
researchProduct

Increase in transmitted resistance to non-nucleoside reverse transcriptase inhibitors among newly diagnosed HIV-1 infections in Europe

2014

Background: One out of ten newly diagnosed patients in Europe was infected with a virus carrying a drug resistant mutation. We analysed the patterns over time for transmitted drug resistance mutations (TDRM) using data from the European Spread program.Methods: Clinical, epidemiological and virological data from 4317 patients newly diagnosed with HIV-1 infection between 2002 and 2007 were analysed. Patients were enrolled using a pre-defined sampling strategy.Results: The overall prevalence of TDRM in this period was 8.9% (95% CI: 8.1-9.8). Interestingly, significant changes over time in TDRM caused by the different drug classes were found. Whereas nucleoside resistance mutations remained con…

Malevirus strainResistanceHIV InfectionsDrug resistanceTHERAPYNucleoside Reverse Transcriptase InhibitorANTIRETROVIRAL DRUG-RESISTANCE0302 clinical medicineMedical microbiologyGenotypeMedicine and Health SciencesPrevalenceHIV Infection030212 general & internal medicineUNITED-KINGDOMPhylogeny0303 health sciencesCommunicable diseaseTransmission (medicine)adultvirus mutationUPDATED RECOMMENDATIONSvirus transmission3. Good healthEuropeInfectious Diseasesfemalerisk factorvirus resistanceFemaleNAIVE PATIENTSSOCIETY-USA PANELResearch ArticleHumanAdultmedicine.medical_specialtyGenotypeAnti-HIV AgentsVirusArticle03 medical and health sciencesSDG 3 - Good Health and Well-beingmaleMOLECULAR EPIDEMIOLOGYDrug Resistance Viralmedicineproteinase inhibitorHumansTransmissioncontrolled studyhumanmolecular phylogeny030304 developmental biologynonhumanMUTATIONSbusiness.industryAnti-HIV Agentnucleotide sequencenonnucleoside reverse transcriptase inhibitorHuman immunodeficiency virus 1 infectionVirologymajor clinical studyunindexed sequenceParasitology3121 General medicine internal medicine and other clinical medicineMutationHIV-1business
researchProduct

Multi-objective memetic optimization for the bi-objective obnoxious p -median problem

2018

Abstract Location problems have been studied extensively in the optimization literature, the p-median being probably one of the most tackled models. The obnoxious p-median is an interesting variant that appears in the context of hazardous location. The aim of this paper is to formally introduce a bi-objective optimization model for this problem, in which a solution consists of a set of p locations, and two conflicting objectives arise. On the one hand, the sum of the minimum distance between each client and their nearest open facility and, on the other hand, the dispersion among facilities. Both objective values should be kept as large as possible for a convenient location of dangerous faci…

Mathematical optimization021103 operations researchInformation Systems and Managementbusiness.industryComputer scienceCrossoverFeasible region0211 other engineering and technologiesContext (language use)02 engineering and technologySpace (commercial competition)Management Information SystemsSet (abstract data type)Artificial IntelligenceMutation (genetic algorithm)0202 electrical engineering electronic engineering information engineeringMemetic algorithm020201 artificial intelligence & image processingLocal search (optimization)businessSoftwareKnowledge-Based Systems
researchProduct

An open-source GA framework for optimizing the seismic upgrading design of RC frames through BRBs

2022

Abstract Optimizing seismic upgrading interventions in reinforced concrete (RC) structures is a difficult task, due to the inner non-linearity of the analyses usually performed. Additionally, it is well known that the displacement demand to the structure depends from the mass and stiffness of the system, and consequently its definition cannot be made a-priori. This paper presents the application of a soft-computing method -i.e. Genetic Algorithm (GA)- for the shaping optimization of code-compliant seismic upgrading interventions on plane RC frames through Buckling-Restrained Braces (BRB). The metaheuristic procedure allows to minimize the cost while ensuring the required safety level, witho…

Mathematical optimizationComputer scienceMonte Carlo methodCrossoverStability (learning theory)StiffnessPython (programming language)Settore ICAR/09 - Tecnica Delle CostruzioniGenetic algorithmMutation (genetic algorithm)medicineBRB Genetic algorithm Optimization Seismic upgradingmedicine.symptomcomputerMetaheuristicCivil and Structural Engineeringcomputer.programming_languageEngineering Structures
researchProduct

The distributed assembly permutation flowshop scheduling problem

2013

Nowadays, improving the management of complex supply chains is a key to become competitive in the twenty-first century global market. Supply chains are composed of multi-plant facilities that must be coordinated and synchronised to cut waste and lead times. This paper proposes a Distributed Assembly Permutation Flowshop Scheduling Problem (DAPFSP) with two stages to model and study complex supply chains. This problem is a generalisation of the Distributed Permutation Flowshop Scheduling Problem (DPFSP). The first stage of the DAPFSP is composed of f identical production factories. Each one is a flowshop that produces jobs to be assembled into final products in a second assembly stage. The o…

Mathematical optimizationJob shop schedulingStrategy and ManagementSupply chainESTADISTICA E INVESTIGACION OPERATIVANeighbourhood (graph theory)Management Science and Operations ResearchIndustrial and Manufacturing EngineeringDistributed assembly flowshopVariable neighborhood descentVariable (computer science)PermutationConstructive algorithmsKey (cryptography)ORGANIZACION DE EMPRESASProduction (computer science)Mathematics
researchProduct

Developing Domain-Knowledge Evolutionary Algorithms for Network-on-Chip Application Mapping

2013

This paper addresses the Network-on-Chip (NoC) application mapping problem. This is an NP-hard problem that deals with the optimal topological placement of Intellectual Property cores onto the NoC tiles. Network-on-Chip application mapping Evolutionary Algorithms are developed, evaluated and optimized for minimizing the NoC communication energy. Two crossover and one mutation operators are proposed. It is analyzed how each optimization algorithm performs with every genetic operator, in terms of solution quality and convergence speed. Our proposed operators are compared with state-of-the-art genetic operators for permutation problems. Finally, the problem is approached in a multi-objective w…

Mathematical optimizationMutation operatorTheoretical computer scienceComputer Networks and CommunicationsComputer scienceQuality control and genetic algorithmsCrossoverEvolutionary algorithmGenetic operatorMulti-objective optimizationNetwork on a chipArtificial IntelligenceHardware and ArchitectureSimulated annealingGenetic algorithmGenetic representationSoftwareMicroprocessors and Microsystems
researchProduct

Stochastic anticipative calculus on the path space over a compact Riemannian manifold

1998

Abstract In this paper, we shall first give another expression for Cruzeiro-Malliavin structure equation, by means of the Skorohod integral. The torsion tensor with respect to the Markovian connection used in [CF] is computed. This is the key step to establish a Stroock-like formula of commutation on the derivative of the Skorohod integral, which enables us to prove an Ito formula. As an application, we shall give a maximal inequality for Skorohod integrals following [AN2].

Mathematics(all)General MathematicsApplied MathematicsMathematical analysisMarkov processDerivativeExpression (computer science)Riemannian manifoldConnection (mathematics)symbols.namesakeTorsion tensorMathematics::ProbabilitysymbolsPath spaceCommutationMathematicsJournal de Mathématiques Pures et Appliquées
researchProduct

Combinatorial Gray codes for classes of pattern avoiding permutations

2007

The past decade has seen a flurry of research into pattern avoiding permutations but little of it is concerned with their exhaustive generation. Many applications call for exhaustive generation of permutations subject to various constraints or imposing a particular generating order. In this paper we present generating algorithms and combinatorial Gray codes for several families of pattern avoiding permutations. Among the families under consideration are those counted by Catalan, Schr\"oder, Pell, even index Fibonacci numbers and the central binomial coefficients. Consequently, this provides Gray codes for $\s_n(\tau)$ for all $\tau\in \s_3$ and the obtained Gray codes have distances 4 and 5.

Mathematics::CombinatoricsFibonacci numberPattern avoiding permutationsGeneral Computer ScienceOrder (ring theory)Generating algorithms94B25Gray codesCombinatorial algorithms05A05; 94B25; 05A15Theoretical Computer ScienceCombinatoricsSet (abstract data type)Constraint (information theory)Gray codePermutation05A05ComputingMethodologies_SYMBOLICANDALGEBRAICMANIPULATIONFOS: MathematicsMathematics - CombinatoricsCombinatorics (math.CO)05A15Binomial coefficientComputer Science(all)MathematicsTheoretical Computer Science
researchProduct

Combinatorics of generalized Bethe equations

2012

A generalization of the Bethe ansatz equations is studied, where a scalar two-particle S-matrix has several zeroes and poles in the complex plane, as opposed to the ordinary single pole/zero case. For the repulsive case (no complex roots), the main result is the enumeration of all distinct solutions to the Bethe equations in terms of the Fuss-Catalan numbers. Two new combinatorial interpretations of the Fuss-Catalan and related numbers are obtained. On the one hand, they count regular orbits of the permutation group in certain factor modules over \({\mathbb{Z}^M}\), and on the other hand, they count integer points in certain M-dimensional polytopes.

Mathematics::CombinatoricsNonlinear Sciences - Exactly Solvable and Integrable Systems010308 nuclear & particles physics010102 general mathematicsScalar (mathematics)Complex systemFOS: Physical sciencesStatistical and Nonlinear PhysicsPolytopeMathematical Physics (math-ph)Permutation group01 natural sciencesBethe ansatzCombinatorics0103 physical sciencesEnumerationFOS: MathematicsMathematics - CombinatoricsCombinatorics (math.CO)0101 mathematicsExactly Solvable and Integrable Systems (nlin.SI)Complex numberComplex planeMathematical PhysicsMathematics
researchProduct