Search results for "PEDIATRIA"
showing 10 items of 692 documents
PARVOVIRUS INFECTION AND KAWASAKI DISEASE: ONE DISEASE FOR TWO SIBLINGS
2018
Introduction: Kawasaki disease (KD) is rarely described in siblings in the same time. In these cases, an infectious trigger must be excluded. Objectives: We describe the clinical course of two brothers who showed severe KD all at once, secondary to Parvovirus infection. Methods: A 9-month-old female showed fever, pallor, vomiting, bilateral non-secreting conjunctivitis, rash. Anamnesis revealed that 12 days before, she had fever, spontaneously resolved. At admission, 9 days after fever onset, she showed fever, conjunctivitis, pharyngitis, rash, and cervical adenopathy. Haematological parameters showed: leukocytosis, neutrophilia; anaemia; CRP: 2.31; ESR: 120. ECG and echocardiography were n…
DUE FRATELLI, IL PARVOVIRUS E DUE KAWASAKI CON FENOTIPO ATIPICO
2018
E' rara la descrizione della Malattia di Kawasaki (MK) in fratelli, ma -se presente- è necessario escludere un trigger infettivo. Riportiamo il caso di due fratelli affetti da MK esordita contemporaneamente in seguito ad un’infezione da Parvovirus. Una bambina di 9 mesi ha presentato febbre, vomito, esantema, congiuntivite non purulenta bilaterale, linfoadenite. All’anamnesi, emergeva un episodio febbrile 12 giorni prima, con risoluzione spontanea in 5 giorni. Presentava: leucocitosi neutrofila, anemia, con transaminasi, Na, albumina, creatinina, urine nella norma. PCR: 2,31 mg/dl; VES: 120. ECG ed ecocardio sono risultati nella norma, con Z-score coronarici normali. IgM anti-Parvovirus era…
Autoimmune thyroiditis and phenilketonuria: a new association
2011
Generalized anasarca as way of presentation of severe protein losing enteropathy.
2009
Familial Protein Losing Enteropathy
2006
LO STUDIO DEI POTENZIALI EVOCATI VISIVI E UDITIVI IN PAZIENTI CON MALATTIA DI KAWASAKI: CASISTICA DELLA CLINICA PEDIATRICA DI PALERMO
2018
La Malattia di Kawasaki (MK), una vasculite sistemica con elettivo interessamento coronarico, può portare a complicanze a carico di diversi distretti quali fegato, reni, polmoni, intestino, occhi, cute, SNC. La sordità neurosensoriale è descritta in casi sporadici e può essere persistente. Lo studio dei potenziali evocati uditivi (ABR) e visivi (PEV) è metodica efficace per identificare, in assenza di sintomi uditivi e/o visivi, alterazioni degli stessi. Abbiamo studiato 52 pazienti (31 M; 21 F; età: 3 mesi-10 anni) con MK mediante PEV e ABR, sia in fase acuta di malattia che durante il follow-up ed abbiamo correlato i risultati dei potenziali con i parametri clinici, la forma della MK (tip…
DOWN REGULATION OF LYMPHOCYTES APOPTOSIS IN GIRLS WITH PRECOCIOUS PUBERTY
2011
The effects of sexual hormones secretion in children with precocious puberty induce significant somatic and psychological changes, with systemic implications on several organs and tissues. Besides immune system and blood cells are involved in these changes. Recent studies on mice lymphocytes have demonstrated a protection of estrogens against apoptosis Fas-FasL pathway. These data could partially elucidate why autoimmune diseases are more frequent in females adolescents, whereas males have higher mortality associated with infectious diseases. We studied ten girls (age: 4-7 years) affected by idiopathic precocious puberty, with pubertal stage B3-PH3-4. All presented increased bone age/chrono…
ISOLATED PYODERMA GANGRENOSUM AND ADALIMUMAB:CASE REPORT IN PAEDIATRIC AGE
2018
Introduction: Pyoderma Gangrenosum (PG) is a sterile neutrophilic disorder, rarely described in children and adolescents, and frequently it is known as secondary to other chronic inflammatory diseases. However, epidemiological, clinical and therapeutic data on paediatric PG are numerically limited and no randomized controlled trials have been published. Associated diseases in paediatric cases are inflammatory bowel diseases, vasculitis, immune deficiencies, PAPA Syndrome. The treatment with systemic steroids and cyclosporine is well documented in the literature as the first-line treatment. In nonresponders, other treatment lines are indicated, as: corticosteroids and mycophenolate mofetil, …
SOFT TISSUE SARCOMAS: Surgical Results from Italian Spft Tissue Sarcoma Group
1993
The Authors report the experience of the Italian Society of Paediatric Haematology and Oncology (AIEOP) in the treatment of Rhabdomyosarcoma, according to the Protocol ICS-RMS 88, is here reported.