Search results for "Phenotype"

showing 10 items of 1875 documents

CiliaCarta: An integrated and validated compendium of ciliary genes

2019

The cilium is an essential organelle at the surface of mammalian cells whose dysfunction causes a wide range of genetic diseases collectively called ciliopathies. The current rate at which new ciliopathy genes are identified suggests that many ciliary components remain undiscovered. We generated and rigorously analyzed genomic, proteomic, transcriptomic and evolutionary data and systematically integrated these using Bayesian statistics into a predictive score for ciliary function. This resulted in 285 candidate ciliary genes. We generated independent experimental evidence of ciliary associations for 24 out of 36 analyzed candidate proteins using multiple cell and animal model systems (mouse…

ProteomicsSensory ReceptorsNematodaSocial SciencesCiliopathiesBiochemistrySensory disorders Donders Center for Medical Neuroscience [Radboudumc 12]Transcriptome0302 clinical medicineAnimal CellsPsychologyRETINAL PHOTORECEPTOR CELLSExomeNeurons0303 health sciences030302 biochemistry & molecular biologyEukaryotaGenomicsPRIMARY CILIUMthecilium3. Good healthNucleic acidsGenetic interferenceOsteichthyesMedicineEpigeneticsCellular Structures and OrganellesCellular Typesproteomic databasesSensory Receptor CellsScienceeducationCiliary genesLEBER CONGENITAL AMAUROSISGenomics03 medical and health sciencesGeneticsCiliaCaenorhabditis elegansIDENTIFICATIONMUTATIONSEmbryosciliaOrganismsBiology and Life SciencesBayes TheoremMolecular Sequence Annotationmedicine.diseaseInvertebratesFishciliary proteomeAnimal StudiesCaenorhabditisGene expressionembryos030217 neurology & neurosurgeryDevelopmental BiologyNeurosciencePhotoreceptorsCandidate geneEmbryologyOligonucleotidesMorpholinoDatabase and Informatics MethodsRNA interferenceBayesian classifierTRANSITION ZONEZebrafishAntisense OligonucleotidesZebrafishGeneticsMultidisciplinarySpectrometric Identification of ProteinsProteomic DatabasesNucleotidesCiliumQStable Isotope Labeling by Amino Acids in Cell CultureRphotoreceptorsMetabolic Disorders Radboud Institute for Molecular Life Sciences [Radboudumc 6]Animal ModelsPhenotypeINTRAFLAGELLAR TRANSPORTDIFFERENTIATIONPhenotypeExperimental Organism SystemsCaenorhabditis ElegansVertebratesSensory PerceptionResearch ArticleSignal TransductionEXPRESSIONStable isotope labeling by amino acids in cell cultureComputational biologyBiologyResearch and Analysis MethodsSOLUTE-CARRIER-PROTEINModel OrganismsmedicineAnimalsdata integration030304 developmental biologyAfferent NeuronsReproducibility of ResultsCell Biologyzebrafishbiology.organism_classificationCiliopathyRenal disorders Radboud Institute for Molecular Life Sciences [Radboudumc 11]Biological DatabasesCellular NeuroscienceRNAOSCP1CiliaCartaPLoS ONE
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Surface proteomic analysis of differentiated versus stem-like osteosarcoma human cells.

2013

Cancer stem cell characterization represents a breakthrough in cancer research. Despite evidence showing the existence and the role of cancer stem cells in osteosarcoma (OS) onset and progression, little is known about their specific surface phenotype. To address this issue, we carried out a cytometric analysis with an antibody-array comprising 245 membrane proteins comparing the stem and differentiated OS cells. As experimental model, we chose the stem-like cell line 3aminobenzamide-OS and its parental, differentiated, cell line MG63. We identified 50 differentially expressed, 23 homogeneously expressed, and 172 not expressed proteins in the two cell line models, thus defining a surface pr…

ProteomicsSurface phenotypeProteomeBiologyProteomicsStem cell markerBiochemistryCancer stem cellSettore BIO/10 - BiochimicamedicineHumansCancer stem cell Cell biology Osteosarcoma Surface proteomeProtein Interaction MapsMolecular BiologyOsteosarcomaKinaseMembrane ProteinsCell Differentiationmedicine.diseaseCell biologyMembrane proteinCell cultureNeoplastic Stem CellsOsteosarcomacancer stem cells proteomics osteosarcoma
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Feasibility of shotgun urinary proteomics for investigating prematurely born preschoolers (PBP)

2016

Background: Preterms and twins are at higher risk of respiratory morbidity later in life. Advances in proteomic approaches may allow the characterization of biomarkers involved in respiratory diseases (Mauri et al. Imm. Lett. 2014;162:2-10). Gel-free approach quantitatively identify differentially expressed proteins in relation to physiopathological conditions (Mauri&Dehò, Meth Enzymology 2008;447:99-117). This can improve the clinical reliability of the next generation of biomarkers to discriminate multiple phenotypes of childhood respiratory diseases. Aim: To assess the ability of gel-free proteomics for identifying specific protein profiles related to PBP. Methods: Urine samples were…

Proteomicsbusiness.industryUrinary systemShotgunBioinformaticsProteomicsPulmonary function testingchildrenPretermRespiratory morbidityClinical informationPreterm childrenMedicinebusinessClinical phenotypeUrine sample
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Comparative Proteome Profiling and Functional Analysis of Chronic Myelogenous Leukemia Cell Lines

2007

The aim of the present study was the molecular profiling of different Ph+ chronic myelogenous leukemia (CML) cell lines (LAMA84, K562, and KCL22) by a proteomic approach. By employing two-dimensional gel electrophoresis combined with mass spectrometry analysis, we have identified 191 protein spots corresponding to 142 different proteins. Among these, 63% were cancer-related proteins and 74% were described for the first time in leukemia cells. Multivariate analysis highlighted significant differences in the global proteomic profile of the three CML cell lines. In particular, the detailed analysis of 35 differentially expressed proteins revealed that LAMA84 cells preferentially expressed prot…

Proteomicschronic myelogenous leukemia cell lineBiologyProteomicsBiochemistrySettore BIO/13 - Biologia ApplicataCell MovementCell Line TumorEthidiumLeukemia Myelogenous Chronic BCR-ABL Positivehemic and lymphatic diseases[SDV.BBM] Life Sciences [q-bio]/Biochemistry Molecular BiologymedicineHumansElectrophoresis Gel Two-DimensionalNeoplasm InvasivenessGel electrophoresisdrug resistanceProteomic ProfileGene Expression Regulation LeukemicGene Expression ProfilingGeneral Chemistrytumor invasionmedicine.diseasePhenotypeMolecular biologyAcridine OrangeGene expression profilingLeukemiaPhenotypeDrug Resistance Neoplasmproteome profilingMultivariate AnalysisDisease ProgressionK562 CellsChronic myelogenous leukemiaK562 cellsJournal of Proteome Research
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N-acyl-homoserine-lactone quorum sensing in tomato phytopathogenic Pseudomonas spp. is involved in the regulation of lipodepsipeptide production

2012

Pseudomonas corrugata and Pseudomonas mediterranea are two closely related phytopathogenic bacteria both causal agents of tomato pith necrosis. P. corrugata produces phytotoxic and antimicrobial cationic lipodepsipeptides (LDPs) which are thought to act as major virulence factors. Previous studies have demonstrated that P. corrugata CFBP 5454 has an N-acyl homoserine lactone (AHL) quorum sensing (QS) system PcoI/PcoR and that LDP production occurs at high population densities. No molecular studies on virulence have thus far been reported for P. mediterranea. In this study, we show that P. mediterranea also produces LDPs as well as possessing an AHL-dependent QS system, designated PmeI/PmeR,…

Pseudomonas mediterraneaVirulence FactorsLipoproteinsPlant DiseaseHomoserineVirulenceBioengineeringBiologyAcyl-ButyrolactonesPseudomonaAcyl-ButyrolactoneApplied Microbiology and BiotechnologyTomatoMicrobiologychemistry.chemical_compoundSolanum lycopersicumVirulence FactorDepsipeptidesPseudomonasLycopersicon esculentumLipoproteinPromoter Regions GeneticDepsipeptidePlant DiseasesAntimicrobial Cationic PeptideVirulencePseudomonasGeneral MedicineLipodepsipeptidesbiology.organism_classificationPseudomonas corrugataQuorum sensingPseudomonas corrugataQuorum sensingN-Acyl homoserine lactonePhenotypechemistryPseudomonas mediterranea; Pseudomonas corrugata; Quorum sensing; Lipodepsipeptides; Virulence; TomatoMutationLipodepsipeptidePseudomonas mediterraneaBacteriaBiotechnologyAntimicrobial Cationic PeptidesJournal of Biotechnology
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GOLD 2017 on the way to a phenotypic approach? Analysis from the Phenotypes of COPD in Central and Eastern Europe (POPE) Cohort.

2017

The distribution of patients based on exacerbations solely is the most profound consequence of the 2017 GOLD Report http://ow.ly/4UJa309fLbM

Pulmonary and Respiratory MedicineCOPDPathologymedicine.medical_specialtybusiness.industryPulmonary diseasemedicine.diseasePhenotype03 medical and health sciencesPulmonary Disease Chronic Obstructive0302 clinical medicineCross-Sectional StudiesPhenotype030228 respiratory systemMulticenter studyCohortMedicineHumans030212 general & internal medicineEurope EasternbusinessDemographyThe European respiratory journal
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Phenotypes contribute to treatments.

2017

Chronic obstructive pulmonary disease (COPD) represents a major health problem in Central and Eastern European (CEE) countries; however, there are no data regarding clinical phenotypes of these patients in this region. Participation in the Phenotypes of COPD in Central and Eastern Europe (POPE) study was offered to stable patients with COPD in a real-life setting. The primary aim of this study was to assess the prevalence of phenotypes according to predefined criteria. Secondary aims included analysis of differences in symptom load, comorbidities and pharmacological treatment. 3362 patients with COPD were recruited in 10 CEE countries. 63% of the population were nonexacerbators, 20.4% frequ…

Pulmonary and Respiratory MedicineChronic bronchitismedicine.medical_specialtyExacerbation1InflammationDisease03 medical and health sciencesPulmonary Disease Chronic Obstructive0302 clinical medicineInternal medicinemedicineHumansCOPD030212 general & internal medicineCOPDbusiness.industryOriginal Articlesmedicine.diseasePhenotypeObstructive lung diseaserespiratory tract diseasesPhenotype030228 respiratory systemImmunologymedicine.symptomAirwaybusinessThe European respiratory journal
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Validation and utility of ARDS subphenotypes identified by machine-learning models using clinical data: an observational, multicohort, retrospective …

2022

Item does not contain fulltext BACKGROUND: Two acute respiratory distress syndrome (ARDS) subphenotypes (hyperinflammatory and hypoinflammatory) with distinct clinical and biological features and differential treatment responses have been identified using latent class analysis (LCA) in seven individual cohorts. To facilitate bedside identification of subphenotypes, clinical classifier models using readily available clinical variables have been described in four randomised controlled trials. We aimed to assess the performance of these models in observational cohorts of ARDS. METHODS: In this observational, multicohort, retrospective study, we validated two machine-learning clinical classifie…

Pulmonary and Respiratory MedicineClinical SciencesAcute Lung InjuryArticleMachine LearningPositive-Pressure RespirationRare DiseasesClinical ResearchRetrospective StudieSettore MED/41 - ANESTESIOLOGIAHumansLungAcute Respiratory Distress SyndromeRetrospective StudiesRespiratory Distress SyndromeOther Medical and Health SciencesLUNG SAFE Investigators and the ESICM Trials Grouplnfectious Diseases and Global Health Radboud Institute for Health Sciences [Radboudumc 4]PhenotypeGood Health and Well BeingArea Under CurveARDS: PhenotypeRespiratoryPublic Health and Health ServicesARDSHuman
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Mucus and MUC in asthma.

2005

Asthma is characterized by chronic airway inflammation and a mucus hypersecretory phenotype comprising excess mucus secretion, goblet cell hyperplasia and submucosal gland hypertrophy. This augmented mucus secretion has been relatively undervalued in asthma compared with airway inflammation. However, mucus plugging contributes to airflow limitation and airway hyperresponsiveness, and to morbidity and mortality in asthma. We review recent contributions to this field and therapeutic avenues to control mucus hypersecretion.A distinct mucus hypersecretory phenotype may present in asthma. Overexpression of MUC5AC, MUC5B and MUC2 have been described in asthma secretions, but identification of def…

Pulmonary and Respiratory MedicineGoblet cell hyperplasiabusiness.industryMucinMucinsRespiratory Mucosarespiratory systemmedicine.diseaseMucusPhenotypeAsthmarespiratory tract diseasesMuscle hypertrophyMucusfluids and secretionsPhenotypeImmunologyChronic DiseaseMedicineHumansSecretionbusinessAirwayAsthmaCurrent opinion in pulmonary medicine
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Does early onset asthma increase childhood obesity risk? A pooled analysis of 16 European cohorts

2018

The parallel epidemics of childhood asthma and obesity over the past few decades have spurred research into obesity as a risk factor for asthma. However, little is known regarding the role of asthma in obesity incidence. We examined whether early-onset asthma and related phenotypes are associated with the risk of developing obesity in childhood.This study includes 21 130 children born from 1990 to 2008 in Denmark, France, Germany, Greece, Italy, The Netherlands, Spain, Sweden and the UK. We followed non-obese children at 3-4 years of age for incident obesity up to 8 years of age. Physician-diagnosed asthma, wheezing and allergic rhinitis were assessed up to 3-4 years of age.Children with ph…

Pulmonary and Respiratory MedicineMaleAllergyPediatricsmedicine.medical_specialtyPediatric ObesityInfants -- MalaltiesCHILDRENOverweightPROFILEChildhood obesityArticleCohort Studies03 medical and health sciences0302 clinical medicineSDG 3 - Good Health and Well-beingRisk FactorsWheezemedicineHumans030212 general & internal medicineRisk factorAge of OnsetChildAsmaAsthmaRespiratory SoundsOVERWEIGHTbusiness.industryINCIDENT ASTHMAmedicine.diseaseObesityRhinitis AllergicAsthma3. Good healthrespiratory tract diseasesBODY-MASS INDEXALLERGYEuropePhenotype030228 respiratory systemChild PreschoolObesitatFemaleAge of onsetmedicine.symptombusiness
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