Search results for "SPT"

showing 10 items of 79 documents

Expanding the β-III Spectrin-Associated Phenotypes toward Non-Progressive Congenital Ataxias with Neurodegeneration

2021

(1) Background: A non-progressive congenital ataxia (NPCA) phenotype caused by b-III spectrin (SPTBN2) mutations has emerged, mimicking spinocerebellar ataxia, autosomal recessive type 14 (SCAR14). The pattern of inheritance, however, resembles that of autosomal dominant classical spinocerebellar ataxia type 5 (SCA5). (2) Methods: In-depth phenotyping of two boys studied by a customized gene panel. Candidate variants were sought by structural modeling and protein expression. An extensive review of the literature was conducted in order to better characterize the SPTBN2-associated NPCA. (3) Results: Patients exhibited an NPCA with hypotonia, developmental delay, cerebellar syndrome, and cogni…

Male0301 basic medicineProbandPathologyProtein ConformationSequence Homology<i>SPTBN2 </i>geneb-III spectrin030105 genetics & heredityFluid-attenuated inversion recoveryCohort Studieslcsh:ChemistryNon-progressive congenital ataxia0302 clinical medicineβ-III spectrinSpectrin:enfermedades del sistema nervioso::enfermedades neurodegenerativas [ENFERMEDADES]Age of OnsetChildlcsh:QH301-705.5Spectroscopy:Otros calificadores::Otros calificadores::/genética [Otros calificadores]NeurodegenerationneurodegenerationNeurodegenerative Diseasesnon-progressive congenital ataxiaSyndromeGeneral MedicinePhenotypeHypotoniaComputer Science ApplicationsPhenotype:Nervous System Diseases::Neurodegenerative Diseases [DISEASES]Spinocerebellar ataxiamedicine.symptomSPTBN2 genemedicine.medical_specialtycongenital hereditary and neonatal diseases and abnormalitiesCerebellar AtaxiaNeuroimagingBiologyCatalysisArticleInorganic Chemistry03 medical and health sciences:Nervous System Diseases::Central Nervous System Diseases::Brain Diseases::Cerebellar Diseases::Cerebellar Ataxia [DISEASES]:Other subheadings::Other subheadings::/genetics [Other subheadings]medicineHumansAmino Acid SequencePhysical and Theoretical ChemistryNeurodegenerationMolecular BiologyGenetic Association StudiesOrganic ChemistrySpectrinmedicine.diseaseHyperintensitySistema nerviós - Degeneració - Aspectes genèticslcsh:Biology (General)lcsh:QD1-999:enfermedades del sistema nervioso::enfermedades del sistema nervioso central::enfermedades cerebrales::enfermedades cerebelosas::ataxia cerebelosa [ENFERMEDADES]Mutation030217 neurology & neurosurgeryInternational Journal of Molecular Sciences
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Phylogeography and demographic inference in Nacella (Patinigera) concinna (Strebel, 1908) in the western Antarctic Peninsula

2011

10 pages; International audience; Endemic to Antarctic ecosystems, the limpet Nacella (Patinigera) concinna (Strebel, 1908) is an abundant and dominant marine benthic invertebrate of the intertidal and shallow subtidal zone. In order to examine the phylogeographic pattern and historical demography of the species along the western Antarctic Peninsula, we amplified 663 bp of the mitochondrial DNA cytochrome oxidase subunit I of 161 N. concinna specimens from five localities, as well as two specimens from South Georgia and Sub-Antarctic Marion Island. As two different morphotypes, one characterized by an elevated shell in the intertidal and the other by a flat one in the subtidal, have been re…

Median-joining network0106 biological sciencesNacellaRange (biology)PopulationIntertidal zoneBiology[SDV.BID.SPT]Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomyOceanography010603 evolutionary biology01 natural sciencesCOI14. Life underwaterSouthern OceaneducationBottleneck effectGenetic diversityeducation.field_of_study[SDV.GEN.GPO]Life Sciences [q-bio]/Genetics/Populations and Evolution [q-bio.PE]Nacella concinnaEcology010604 marine biology & hydrobiologyLimpetElliptic FourieranalysisFounder effectbiology.organism_classification[SDV.BA.ZI]Life Sciences [q-bio]/Animal biology/Invertebrate Zoology[ SDV.GEN.GPO ] Life Sciences [q-bio]/Genetics/Populations and Evolution [q-bio.PE]PhylogeographyOceanographyGenetic structureAntarcticaGenetic structure[ SDV.BID.SPT ] Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomyDeep Sea Research Part II: Topical Studies in Oceanography
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Relationship of Weather Types on the Seasonal and Spatial Variability of Rainfall, Runoff, and Sediment Yield in the Western Mediterranean Basin

2020

Producción Científica

Mediterranean climateWestern MediterraneanRainfallAtmospheric ScienceWater en Landgebruik010504 meteorology & atmospheric sciencesClimateanalysesSedimentació02 engineering and technology[SDV.BID.SPT]Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomy01 natural sciencesMediterranean BasinSoilBodemLluviaSoil Water and Land UseGeologíaweather types; rainfall; runoff; erosion; sediment yield; seasonal analyses; Mediterranean basinErosion Mediterranean basin Rainfall Runoff Seasonal analyses Sediment yield Weather types020701 environmental engineeringPrecipitacions (Meteorologia)Sediment yieldEdafología[SDV.BV.BOT]Life Sciences [q-bio]/Vegetal Biology/BotanicsPE&RC2502 ClimatologíaDrenatge6. Clean waterWeather typesTipos de climaErosiónPrecipitations (Meteorology)2511 Ciencias del Suelo (Edafología)2508.10 PrecipitaciónSeasonal analysesAnticycloneErosióErosionErosionDrainageMediterrània occidentalSoil erosion--Climatic factorsCuenca mediterraneaRunoff0207 environmental engineeringEnvironmental Science (miscellaneous)lcsh:QC851-999complex mixtures[SDV.EE.ECO]Life Sciences [q-bio]/Ecology environment/EcosystemsAtmospheric instabilitySettore AGR/08 - Idraulica Agraria E Sistemazioni Idraulico-ForestaliDatasets0105 earth and related environmental sciencesMediterraneanbasinHydrologyWater and Land UseRainfalfungiMediterranean basinSedimentSedimentation and depositionseasonal15. Life on landAtmosfera -- Aspectes ambientalsBodem Water en Landgebruik13. Climate action:Enginyeria agroalimentària::Ciències de la terra i de la vida [Àrees temàtiques de la UPC]Soil erosionEnvironmental scienceRainfall frequenciesSpatial variabilitylcsh:Meteorology. ClimatologyClima[SDE.BE]Environmental Sciences/Biodiversity and EcologySurface runoff
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Origin and phylogeography of the Chagas disease main vector Triatoma infestans based on nuclear rDNA sequences and genome size

2004

For about half of all Chagas disease cases T. infestans has been the responsible vector. Contributing to its genetic knowledge will increase Our understanding of the capacity of geographic expansion and domiciliation of triatomines. Populations of all infestans subcomplex species, T. infestans, T. delpontei, T. platensis and T. melanosoma and the so-called T. infestans "dark morph", from many South American countries were studied. A total of 10 and 7 different ITS-2 and ITS-1 haplotypes, respectively, were found. The total intraspecific ITS-2 nucleotide variability detected in T. infestans is the highest hitherto known in triatomines. ITS-1 minisatellites, detected for the first time in tri…

Microbiology (medical)Chagas disease030231 tropical medicinePopulationDNA quantificationtriatoma infestans subcomplex rDNA ITS 1. 5.8S and ITS 2 sequencesPopulation geneticsDisease Vectorsphylogeography[SDV.BID.SPT]Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomyMicrobiologyDNA RibosomalGene flow03 medical and health sciences0302 clinical medicinepopulation genetics analysisTriatoma infestansGenetic variationDNA Ribosomal SpacerGeneticsAnimalsTriatomaeducationMolecular BiologyGenome sizeEcology Evolution Behavior and SystematicsPhylogenyComputingMilieux_MISCELLANEOUS030304 developmental biologyGenetics0303 health scienceseducation.field_of_study[SDV.GEN.GPO]Life Sciences [q-bio]/Genetics/Populations and Evolution [q-bio.PE]biologyflow cytometrymolecular clockbiology.organism_classificationInsect VectorsRNA Ribosomal 5.8S[SDV.BA.ZI]Life Sciences [q-bio]/Animal biology/Invertebrate ZoologyPhylogeographyInfectious DiseasesMinisatelliteGenetics PopulationEvolutionary biology[SDE.BE]Environmental Sciences/Biodiversity and Ecology
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Modelling Photoionisation in Isocytosine: Potential Formation of Longer‐Lived Excited State Cations in its Keto Form

2021

Abstract Studying the effects of UV and VUV radiation on non‐canonical DNA/RNA nucleobases allows us to compare how they release excess energy following absorption with respect to their canonical counterparts. This has attracted much research attention in recent years because of its likely influence on the origin of our genetic lexicon in prebiotic times. Here we present a CASSCF and XMS‐CASPT2 theoretical study of the photoionisation of non‐canonical pyrimidine nucleobase isocytosine in both its keto and enol tautomeric forms. We analyse their lowest energy cationic excited states including 2π+ , 2nO+ and 2nN+ and compare these to the corresponding electronic states in cytosine. Investigat…

Models MolecularCASPT2Ultraviolet RaysADNPhysics Atomic Molecular & ChemicalRELAXATION DYNAMICSCASSCFArticleCytosineMOLECULAR WAVE-FUNCTIONSCationsIMPLEMENTATION0307 Theoretical and Computational ChemistryPhysical and Theoretical Chemistry0306 Physical Chemistry (incl. Structural)Radiació ionitzantScience & TechnologyChemical PhysicsMolecular StructureChemistry PhysicalConical IntersectionsPhysicsSPECTROSCOPIC FINGERPRINTSDNAArticlesKetonesPhotochemical ProcessesURACILAtomic and Molecular Physics and OpticsChemistryPhotostability2ND-ORDER PERTURBATION-THEORYPhotoionisationPhysical SciencesANO BASIS-SETSSIMULATION0202 Atomic Molecular Nuclear Particle and Plasma PhysicsCASSCF/CASPT2RNAELECTRON CORRELATIONDNA/RNAChemPhysChem
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Photoinduced Formation Mechanism of the Thymine−Thymine (6−4) Adduct

2013

The photoinduced mechanism leading to the formation of the thymine-thymine (6-4) photolesion has been studied by using the CASPT2//CASSCF approach over a dinucleotide model in vacuo. Following light absorption, localization of the excitation on a single thymine leads to fast singlet-triplet crossing that populates the triplet (3)(nπ*) state of thymine. This state, displaying an elongated C(4)═O bond, triggers (6-4) dimer formation by reaction with the C(5)═C(6) double bond of the adjacent thymine, followed by a second intersystem crossing, which acts as a gate between the excited state of the reactant and the ground state of the photoproduct. The requirement of localized excitation on just …

Models MolecularDouble bondUltraviolet RaysphotolesionDimerÀcids nucleicsQuantum yieldthymine−thymine dimer010402 general chemistryPhotochemistry01 natural sciencesAdductDNA Adductschemistry.chemical_compound0103 physical sciencesMaterials ChemistryPhysical and Theoretical Chemistrychemistry.chemical_classificationphotochemistry010304 chemical physicsChemistryDNA3. Good health0104 chemical sciencesSurfaces Coatings and FilmsThymineIntersystem crossingPyrimidine DimersExcited stateCASPT2//CASSCFQuantum TheoryGround stateFisicoquímica
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L’audition chez les primates : entre forme, fonction, écologie et comportement

2019

The order Primates is composed of species whose morphologies, life history traits and behaviors are very diversified. The oldest representatives are dated about 65 million years. Because of this diversity, studies have focused on understanding the relationships between different parameters. Among the morphological structures studied, the basicranium, in particular the characters of the ear, have very often been considered in a phylogenetic perspective. Since the development of new acquisition techniques such as micro-tomography (μCT), new data are available. Thus, the interest for the morphology of the inner and middle ear, hitherto difficult to access, is growing. The structures of the ear…

MorphologyPrimatesOreilleHearing[SDV.BID.SPT] Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomyEar[SDU.STU.PG] Sciences of the Universe [physics]/Earth Sciences/PaleontologyPaleoecology[SDU.STU.PG]Sciences of the Universe [physics]/Earth Sciences/Paleontology[SDV.BID.SPT]Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomyMorphologieAudition
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Tremadocian Stylophoran Echinoderms From The Taebaeksan Basin, Korea.

2006

15 pages; International audience; Abundant isolated elements of cornute and mitrate stylophorans were recovered from the upper Tremadocian Tumugol Formation in the Taebaeksan Basin, Korea. Cornute skeletal elements comprise a diverse assemblage of marginals and brachials of cothurnocystid affinities, suggesting the presence of no fewer than four different species. Mitrate remains include numerous isolated adorals, marginals, and aulacophoral plates with typical peltocystidan morphologies. Two adorals are identified as Anatifopsis sp., while all the others are attributable to A. cocaban. However, the two previously documented peltocystidans of Korea, A. cocaban and A. truncata, are sufficien…

PaleontologyMitrateStructural basinBiologybiology.organism_classificationAffinitiesTremadocianCladisticsPaleontologySister groupGenus[SDV.BID.SPT] Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomy[SDU.STU.PG] Sciences of the Universe [physics]/Earth Sciences/PaleontologyClade[ SDV.BID.SPT ] Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomy[ SDU.STU.PG ] Sciences of the Universe [physics]/Earth Sciences/Paleontology
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Les ammonites du Pliensbachien et du Toarcien basal dans la carrière de la Roche Blain (Fresnay-le-Puceux, Calvados, Basse-Normandie, France). Taxono…

2008

65 pages; International audience; Résumé Ce travail étudie les riches faunes d'ammonites du Pliensbachien et de la base du Toarcien dans la localité très fossilifère de la carrière de la Roche Blain (Calvados). Une cinquantaine d'espèces pliensbachiennes, récoltées dans une douzaine de niveaux distincts sont toutes décrites et illustrées. Leur préservation est parfois remarquable. Des structures fragiles comme les péristomes ou les mégastries sont assez souvent préservées. A l'exception de deux spécimens d'affinités téthysiennes (Arieticeras cf. amalthei (Oppel, 1853) et Dactylioceras (Eodactylites) sp.), les ammonites récoltées à la Roche Blain se rattachent toutes, sans ambiguïté, aux fau…

PaléobiodiversitéPaléobiodiversité.Systématique[ SDU.STU.ST ] Sciences of the Universe [physics]/Earth Sciences/StratigraphyPliensbachien[SDV.BID.SPT]Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomyNormandieBiostratigraphieAmmonites[SDU.STU.ST]Sciences of the Universe [physics]/Earth Sciences/Stratigraphy[SDV.BID.SPT] Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomy[SDU.STU.ST] Sciences of the Universe [physics]/Earth Sciences/Stratigraphy[SDU.STU.PG] Sciences of the Universe [physics]/Earth Sciences/PaleontologyToarcien basalBassin anglo-parisien[SDU.STU.PG]Sciences of the Universe [physics]/Earth Sciences/Paleontology[ SDV.BID.SPT ] Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomy[ SDU.STU.PG ] Sciences of the Universe [physics]/Earth Sciences/PaleontologyPaléobiogéographie
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Do distantly related parasites rely on the same proximate factors to alter the behaviour of their hosts?

2006

Phylogenetically unrelated parasites often increase the chances of their transmission by inducing similar phenotypic changes in their hosts. However, it is not known whether these convergent strategies rely on the same biochemical precursors. In this paper, we explored such aspects by studying two gammarid species ( Gammarus insensibilis and Gammarus pulex ; Crustacea: Amphipoda: Gammaridae) serving as intermediate hosts in the life cycle of two distantly related parasites: the trematode, Microphallus papillorobustus and the acanthocephalan, Polymorphus minutus . Both these parasite species are known to manipulate the behaviour of their amphipod hosts, bringing them towards the water surfa…

Proteomics0106 biological sciences[SDV]Life Sciences [q-bio]MESH : Host-Parasite InteractionsMESH : Behavior Animal[SDV.BID.SPT]Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomyMESH: Peptide Mapping01 natural sciencesAcanthocephalaMESH : ProteomicsMESH: AmphipodatrematodeMESH: Behavior Animal[ SDV.EE.IEO ] Life Sciences [q-bio]/Ecology environment/SymbiosisMESH: AnimalsElectrophoresis Gel Two-DimensionalMESH: PhylogenyPhylogenyComputingMilieux_MISCELLANEOUSGeneral Environmental Science0303 health sciencesMESH : Peptide MappingBehavior AnimalbiologyEcologyMESH : AcanthocephalaMESH: ProteomicsGeneral MedicineMESH : Amphipodamanipulative parasiteMESH : TrematodaMESH: TrematodaMicrophallusTrematodaTrematodagammaridGeneral Agricultural and Biological SciencesAcanthocephalaResearch Article[ SDV.MP.PAR ] Life Sciences [q-bio]/Microbiology and Parasitology/Parasitologymolecular convergenceAmphipodaZoology[ SDV.BBM.BM ] Life Sciences [q-bio]/Biochemistry Molecular Biology/Molecular biologyMESH: Host-Parasite InteractionsPeptide Mapping010603 evolutionary biologyGeneral Biochemistry Genetics and Molecular BiologyHost-Parasite Interactions03 medical and health sciencesproteomicsPhylogeneticsAnimals[SDV.MP.PAR]Life Sciences [q-bio]/Microbiology and Parasitology/ParasitologyAmphipoda030304 developmental biologyGeneral Immunology and MicrobiologyHost (biology)MESH : Phylogeny[SDV.BBM.BM]Life Sciences [q-bio]/Biochemistry Molecular Biology/Molecular biologyMESH : Electrophoresis Gel Two-DimensionalMESH: AcanthocephalaMESH: Electrophoresis Gel Two-Dimensionalbiology.organism_classificationacanthocephalanGammarus pulexPulexMESH : Animals[ SDV.BID.SPT ] Life Sciences [q-bio]/Biodiversity/Systematics Phylogenetics and taxonomy[SDV.EE.IEO]Life Sciences [q-bio]/Ecology environment/Symbiosis
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