Search results for "lysine"

showing 10 items of 170 documents

Monitoring of transglutaminase crosslinking reaction by 1H NMR spectroscopy on model substrates

2015

International audience; A new method based on 1H NMR spectroscopy was developed for monitoring transglutaminase crosslinking reaction with model molecules (CBZ-Gln-Gly and N-α-acetyl-lysine). The transglutaminase reaction led to the appearance of new resonances on NMR spectrum as well as significant decrease in others. The new observed resonances, originated from newly formed ɛ-(γ-glutamyl)lysine isopeptide bonds, evidence the enzymatic reaction and allow to quantify the ɛ-(γ-glutamyl)lysine fragment. Moreover, the decrease in resonance intensity, originated from lysine, permit to determine the crosslinking degree. These results obtained by 1H NMR spectroscopy can be used as an alternative …

0106 biological sciences1h nmr spectroscopyTissue transglutaminaseLysineCrosslinking degreePhotochemistrycomplex mixtures01 natural sciences03 medical and health sciencesModel substratesɛ-(γ-glutamyl)-lysineColloid and Surface ChemistryLiquid chromatography–mass spectrometry010608 biotechnologyOrganic chemistryMolecule[SDV.BBM]Life Sciences [q-bio]/Biochemistry Molecular Biology030304 developmental biologyAlternative methods0303 health sciencesbiologyChemistryResonanceNuclear magnetic resonance spectroscopyMicrobial transglutaminasebiology.proteinColloids and Surfaces A: Physicochemical and Engineering Aspects
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Shelf life extension of mozzarella cheese contaminated with Penicillium spp. using the antifungal compound ɛ-polylysine.

2019

Molds are one of the most important spoilage organisms on cheese which can lead to economic loss as well as raising public health concerns due to the production of mycotoxins. This study investigates the use of ɛ-polylysine as natural antimicrobial to inhibit fungal growth. The minimal inhibitory concentrations and minimal fungicidal concentrations of ɛ-polylysine were determined against Penicillium roqueforti, Penicillium nordicum, and Penicillium solitum. Then, polylysine was tested as surface antimicrobial for the preservation of mozzarella slice cheese inoculated with these Penicillium spp. and stored in plastic trays during 25 days. The minimal inhibitory concentrations calculated for…

0106 biological sciencesAntifungal AgentsFood HandlingGeneral Chemical EngineeringFood spoilageMicrobial Sensitivity TestsShelf life01 natural sciencesIndustrial and Manufacturing EngineeringPenicillium solitumchemistry.chemical_compound0404 agricultural biotechnologyAnti-Infective AgentsCheese010608 biotechnologyFood PreservationPolylysineFood scienceMycotoxinbiologyFungiPenicilliumfood and beveragesPenicillium roqueforti04 agricultural and veterinary sciencesbiology.organism_classificationAntimicrobial040401 food sciencechemistryFood StoragePenicilliumFood MicrobiologyPenicillium nordicumFood ScienceFood science and technology international = Ciencia y tecnologia de los alimentos internacional
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Bifunctional poly(acrylamide) hydrogels through orthogonal coupling chemistries

2019

Biomaterials for cell culture allowing simple and quantitative presentation of instructive cues enable rationalization of the interplay between cells and their surrounding microenvironment. Poly(acrylamide) (PAAm) hydrogels are popular 2D-model substrates for this purpose. However, quantitative and reproducible biofunctionalization of PAAm hydrogels with multiple ligands in a trustable, controlled, and independent fashion is not trivial. Here, we describe a method for bifunctional modification of PAAm hydrogels with thiol- and amine- containing biomolecules with controlled densities in an independent, orthogonal manner. We developed copolymer networks of AAm with 9% acrylic acid and 2% N-(4…

0301 basic medicine570Polymers and PlasticsPolymersOtras Ciencias BiológicasPoly(acrylamide)Acrylic ResinsBiocompatible MaterialsBioengineeringINGENIERÍAS Y TECNOLOGÍAS02 engineering and technologyBiotecnología IndustrialCiencias BiológicasBiomaterialsMice03 medical and health scienceschemistry.chemical_compoundUltraviolet visible spectroscopyPolymer chemistryMaterials ChemistryCopolymerAnimalsPolylysineBifunctionalCells CulturedAcrylic acidNeuronschemistry.chemical_classificationOtras Ciencias QuímicasBiomoleculeCiencias QuímicasHydrogels021001 nanoscience & nanotechnologyMice Inbred C57BL030104 developmental biologychemistryChemical engineeringAcrylamideSelf-healing hydrogelsAmine gas treatingLaminin0210 nano-technologyCIENCIAS NATURALES Y EXACTAS
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Bifunctional Hydrogels Containing the Laminin Motif IKVAV Promote Neurogenesis

2017

Summary Engineering of biomaterials with specific biological properties has gained momentum as a means to control stem cell behavior. Here, we address the effect of bifunctionalized hydrogels comprising polylysine (PL) and a 19-mer peptide containing the laminin motif IKVAV (IKVAV) on embryonic and adult neuronal progenitor cells under different stiffness regimes. Neuronal differentiation of embryonic and adult neural progenitors was accelerated by adjusting the gel stiffness to 2 kPa and 20 kPa, respectively. While gels containing IKVAV or PL alone failed to support long-term cell adhesion, in bifunctional gels, IKVAV synergized with PL to promote differentiation and formation of focal adh…

0301 basic medicineCellular differentiationHYDROGELSCELL DIFFERENTIATION02 engineering and technologyBiochemistry//purl.org/becyt/ford/1 [https]MiceNeural Stem CellsIKVAVlcsh:QH301-705.5Cells Culturedlcsh:R5-920β(1)-integrinNeurogenesisHydrogelsMouse Embryonic Stem Cells021001 nanoscience & nanotechnologyNeural stem cellCell biologyStem celllcsh:Medicine (General)0210 nano-technologyCIENCIAS NATURALES Y EXACTASbiomaterialsPOLYLYSINENeurogenesisBiologyNEUROGENESISCiencias BiológicasFocal adhesion03 medical and health sciencesBiología Celular MicrobiologíalamininReportGeneticsΒ1-INTEGRINAnimalsProgenitor cell//purl.org/becyt/ford/1.6 [https]BIOMATERIALSCell adhesionFocal AdhesionsbioengineeringTissue Engineeringβ1-integrinCell BiologypolylysineNEURAL STEM CELLSMolecular biologyEmbryonic stem cellElasticityPeptide FragmentsBIOENGINEERINGLAMININMice Inbred C57BLcell differentiation030104 developmental biologylcsh:Biology (General)Developmental BiologyStem Cell Reports
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Effect of Food Thermal Processing on the Composition of the Gut Microbiota.

2018

Cooking modifies food composition due to chemical reactions. Additionally, food composition shapes the human gut microbiota. Thus, the objective of this research was to unravel the effect of different food cooking methods on the structure and functionality of the gut microbiota. Common culinary techniques were applied to five foods, which were submitted to in vitro digestion-fermentation. Furosine, 5-(hydroxymethyl)furfural, and furfural were used as Maillard reaction indicators to control the heat treatment. Short-chain fatty acids production was quantified as indicator of healthy metabolic output. Gut microbial community structure was analyzed through 16S rRNA. Both food composition and c…

0301 basic medicineHot TemperatureMeatGut flora03 medical and health sciencessymbols.namesakeRNA Ribosomal 16SVegetablesHumansFuraldehydeFood scienceCookingRoastingBifidobacterium030109 nutrition & dieteticsbiologyBacteriabusiness.industryChemistryRuminococcusLysinedigestive oral and skin physiologyfood and beveragesFood composition dataFabaceaeGeneral Chemistrybiology.organism_classificationFatty Acids VolatileGastrointestinal MicrobiomeMaillard ReactionMaillard reaction030104 developmental biologyFruitFermentationsymbolsFood processingComposition (visual arts)General Agricultural and Biological SciencesbusinessEdible GrainJournal of agricultural and food chemistry
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Wiedemann-Steiner syndrome as a major cause of syndromic intellectual disability: A study of 33 French cases.

2018

International audience; Wiedemann-Steiner syndrome (WSS) is a rare syndromic condition in which intellectual disability (ID) is associated with hypertrichosis cubiti, short stature, and characteristic facies. Following the identification of the causative gene (KMT2A) in 2012, only 31 cases of WSS have been described precisely in the literature. We report on 33 French individuals with a KMT2A mutation confirmed by targeted gene sequencing, high-throughput sequencing or exome sequencing. Patients' molecular and clinical features were recorded and compared with the literature data. On the molecular level, we found 29 novel mutations. We observed autosomal dominant transmission of WSS in 3 fami…

0301 basic medicineHypertrichosisMalePediatrics[SDV]Life Sciences [q-bio]MESH: Magnetic Resonance ImagingPathognomonicMESH: ChildIntellectual disabilityMESH: SyndromeChildMESH: High-Throughput Nucleotide SequencingGenetics (clinical)Exome sequencingComputingMilieux_MISCELLANEOUSbiologyWiedemann-Steiner syndromeHigh-Throughput Nucleotide SequencingSyndromeKMT2AMESH: Amino Acid SubstitutionMagnetic Resonance Imaginghypertrichosis3. Good healthhairinessKMT2APhenotypeWiedemann-Steiner syndromeChild Preschoolcardiovascular systemFemaleDisease SusceptibilityFrancemedicine.symptomMESH: Tomography X-Ray ComputedMyeloid-Lymphoid Leukemia Proteinmedicine.medical_specialtyMESH: MutationAdolescentMESH: Disease SusceptibilityMESH: PhenotypeShort statureMESH: Intellectual Disability03 medical and health sciencesHypertrichosis cubitiIntellectual DisabilityGeneticsmedicineHumanshistone methylationMESH: Adolescent[SDV.GEN]Life Sciences [q-bio]/GeneticsMESH: Humansbusiness.industryMESH: Child PreschoolMESH: Histone-Lysine N-MethyltransferaseHistone-Lysine N-Methyltransferasemedicine.diseaseMESH: MaleMESH: France030104 developmental biology[SDV.GEN.GH]Life Sciences [q-bio]/Genetics/Human geneticsAmino Acid SubstitutionMESH: Myeloid-Lymphoid Leukemia ProteinMutationbiology.proteinbusinessTomography X-Ray ComputedMESH: FemaleClinical genetics
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Loss-of-function and missense variants in NSD2 cause decreased methylation activity and are associated with a distinct developmental phenotype

2021

Purpose Despite a few recent reports of patients harboring truncating variants in NSD2, a gene considered critical for the Wolf–Hirschhorn syndrome (WHS) phenotype, the clinical spectrum associated with NSD2 pathogenic variants remains poorly understood. Methods We collected a comprehensive series of 18 unpublished patients carrying heterozygous missense, elongating, or truncating NSD2 variants; compared their clinical data to the typical WHS phenotype after pooling them with ten previously described patients; and assessed the underlying molecular mechanism by structural modeling and measuring methylation activity in vitro. Results The core NSD2-associated phenotype includes mostly mild dev…

0301 basic medicineIn silicoBiologyArticleREGION03 medical and health sciencesROGERS-DANKS-SYNDROME0302 clinical medicineMissense mutationHISTONE H3GeneGenetics (clinical)Loss functionGeneticsNeurodevelopmental disorders Donders Center for Medical Neuroscience [Radboudumc 7]DELETIONDEFECTSMethylationPhenotypeLYSINE 36030104 developmental biologyMolecular mechanismWOLF-HIRSCHHORN-SYNDROME030217 neurology & neurosurgeryFunction (biology)Rare cancers Radboud Institute for Health Sciences [Radboudumc 9]Genetics in Medicine
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Lysyl Oxidase (LOX) Family Members: Rationale and Their Potential as Therapeutic Targets for Liver Fibrosis.

2019

The cross-linking of structural extracellular matrix (ECM) components, especially fibrillar collagens and elastin, is strongly implicated in fibrosis progression and resistance to fibrosis reversal. Lysyl oxidase family members (LOX and LOXL1 [lysyl oxidase-like 1], LOXL2 [lysyl oxidase-like 2], LOXL3 [lysyl oxidase-like 3], and LOXL4 [lysyl oxidase like 4]) are extracellular copper-dependent enzymes that play a key role in ECM cross-linking, but have also other intracellular functions relevant to fibrosis and carcinogenesis. Although the expression of most LOX family members is elevated in experimental liver fibrosis of diverse etiologies, their individual contribution to fibrosis is incom…

0301 basic medicineLiver CirrhosisLysyl oxidaseExtracellular matrixProtein-Lysine 6-Oxidase03 medical and health sciences0302 clinical medicineFibrosisExtracellularmedicineAnimalsHumansLOXL3integumentary systemHepatologyLOXL2biologybusiness.industrymedicine.diseaseenzymes and coenzymes (carbohydrates)030104 developmental biologySimtuzumabCancer researchbiology.protein030211 gastroenterology & hepatologyAmino Acid OxidoreductasesbusinessElastinHepatology (Baltimore, Md.)References
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Biallelic variants in LARS2 and KARS cause deafness and (ovario)leukodystrophy

2019

Supplemental Digital Content is available in the text.

0301 basic medicineLysine-tRNA LigaseMalePathologyMagnetic Resonance SpectroscopyMedizinmembrane proteins030204 cardiovascular system & hematologyMitochondrionDeafnessmedicine.disease_causeCompound heterozygosityCorrectionsLeukoencephalopathyMyelin0302 clinical medicineCytosolLeukoencephalopathies030212 general & internal medicineOvarian DiseasesTransfer RNA AminoacylationChildZebrafishMUTATIONExome sequencing10012MutationBrainMetabolic Disorders Radboud Institute for Molecular Life Sciences [Radboudumc 6]General MedicineMiddle AgedDisorders of movement Donders Center for Medical Neuroscience [Radboudumc 3]Magnetic Resonance ImagingMitochondriaProtein Transportendoplasmic reticulummedicine.anatomical_structureChild PreschoolTransfer RNAComputingMethodologies_DOCUMENTANDTEXTPROCESSING/dk/atira/pure/sustainabledevelopmentgoals/good_health_and_well_being[SDV.NEU]Life Sciences [q-bio]/Neurons and Cognition [q-bio.NC]Biological AssayFemaleWRBRare cancers Radboud Institute for Health Sciences [Radboudumc 9]Adultcardiomyopathiesmedicine.medical_specialtyMitochondrial diseaseAminoacylationMuscle disorderBiologyArticleMEDIATES INSERTIONAmino Acyl-tRNA Synthetases03 medical and health sciencesSDG 3 - Good Health and Well-beingmedicineAnimalsPoint MutationHumansAmino Acid SequenceAlleleAllelesCOMPLEXGenetic heterogeneitybusiness.industryArsenite Transporting ATPasesLeukodystrophyGenetic Variation10090Original ArticlesZebrafish Proteinsbiology.organism_classificationDILATED CARDIOMYOPATHYmedicine.diseasezebrafishGENEMolecular biologyDisease Models Animal030104 developmental biologyMembrane protein[SDV.GEN.GH]Life Sciences [q-bio]/Genetics/Human genetics10084Neurology (clinical)Transfer RNA AminoacylationMEMBRANEbusinessSequence Alignment030217 neurology & neurosurgeryexomeNeurology
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Broad neurodevelopmental features and cortical anomalies associated with a novel de novo KMT2A variant in Wiedemann-Steiner syndrome.

2021

Abstract Wiedemann-Steiner syndrome (WDSTS) is a rare genetic disorder including developmental delay/intellectual disability (DD/ID), hypertrichosis cubiti, short stature, and distinctive facial features, caused by mutation in KMT2A gene, which encodes a histone methyltransferase (H3K4) that regulates chromatin-mediated transcription. Different neurodevelopmental phenotypes have been described within the WDSTS spectrum, including a peculiar Autism Spectrum Disorder (ASDs) subtype in some affected individuals. Here, we report a 9-year-old Caucasian male found by next-generation panel sequencing to carry a novel heterozygous de novo KMT2A frameshift variant (NM_001197104.2:c.4433delG; p. Arg1…

0301 basic medicineMaleDevelopmental Disabilities030105 genetics & heredityBiologyFocal cortical dysplasiaPalilaliaFrameshift mutation03 medical and health sciencesHypertrichosis cubitiIntellectual DisabilityGeneticsmedicineHumansChildFrameshift MutationGenetics (clinical)GeneticsCerebral CortexWiedemann-steiner syndrome.Genetic disorderHypertrichosis cubitiGeneral MedicineHistone-Lysine N-MethyltransferaseSyndromeKMT2ACortical dysplasiamedicine.diseasePalilaliaMalformations of Cortical Development030104 developmental biologyKMT2AWiedemann-Steiner syndromeAutism spectrum disorderbiology.proteinmedicine.symptomMyeloid-Lymphoid Leukemia ProteinEuropean journal of medical genetics
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