Search results for "orage"
showing 10 items of 1343 documents
Mucopolysaccharidoses and other lysosomal storage diseases.
2013
Mucopolysaccharidosis and other lysosomal storage diseases are rare, chronic, and progressive inherited diseases caused by a deficit of lysosomal enzymes. Patients are affected by a wide variety of symptoms. For some lysosomal storage diseases, effective treatments to arrest disease progression, or slow the pathologic process, and increase patient life expectancy are available or being developed. Timely diagnosis is crucial. Rheumatologists, orthopedics, and neurologists are commonly consulted due to unspecific musculoskeletal signs and symptoms. Pain, stiffness, contractures of joints in absence of clinical signs of inflammation, bone pain or abnormalities, osteopenia, osteonecrosis, secon…
'We have a solution': Delivering on the promise to take national responsibility for nuclear waste management
2022
We examine the realization of the umbrella promise to assume national responsibility for the final disposal of spent nuclear fuel. Three case studies are used to illustrate how Finland delivers on the promise to take care of its own nuclear waste - a promise that has greatly contributed to the legitimacy of nuclear power in Finland. The article shows how this promise is being challenged by new competitors, business visionaries, and the public. The case studies illustrate the tensions between those who made the promise and the actors who interpret and mobilize the promise for varying purposes and under changing circumstances. We investigate techno-scientific promises by looking at debates ab…
Sensor to safeguard quality in the conservation of siciian extra virgin olive oil
2020
The production of olive oil in Sicily, in recent decades, has implemented the use of technologies that have as their main objective the sustainable safeguarding of food quality. Food quality both from the point of view of the transformation process, and from the point of view of product conservation, from olive oil is not a simple condiment but involves important nutritional attentions with health implications. The preservation of bottled olive oil is fundamental in order to improve the life cycle of the product after its transformation, in shelf life. The parameters observed during the observed conservation and storage period; temperature and relative humidity. The information collected is…
Impact of Ageing on Pea Protein Volatile Compounds and Correlation with Odor
2022
Vegetal proteins are of high interest for their many positive aspects, but their ‘beany’ off-flavor is still limiting the consumer’s acceptance. The aim of this work was to investigate the conservation of pea protein isolate (PPI) during time and especially the evolution of their organoleptic quality under two storage conditions. The evolution of the volatile compounds, the odor and the color of a PPI has been investigated during one year of storage. PPI was exposed to two treatments mimicking a lack of control of storage conditions: treatment A with light exposition at ambient temperature (A—Light 20 °C) and treatment B in the dark but with a higher temperature …
Optimization of BESS Capacity Under a Peak Load Shaving Strategy
2018
Battery energy storage systems (BESSs) are becoming increasingly competitive in the global energy landscape, thanks to the strong cost reduction that has taken place in recent years and it is expected to continue in the next future. Among the many benefits BESSs can provide, time shifting can be exploited by electricity consumers to save on the electricity bill, charging the storage during the off-peak hours and discharging when the cost of electricity is high. This paper describes a simple procedure to optimize the BESS capacity under a peak load shaving strategy, in presence of a time-of-use (TOU) electricity rate, able to guarantee, at the same time, the flattest daily power diagram and …
DEMAND Project: A Peak Load Shaving Strategy for End-User Consumers
2018
Battery energy storage systems (BESS) are becoming increasingly widespread in modern power systems, thanks to the important benefits they can provide to the electricity grid. Indeed, BESS can be used in time shifting applications, storing energy during off-peak periods and discharging during peak times (when the cost of electricity is high). When BESS are used for peak shaving purposes, they also contribute to relieve peak demand charges, thus ensuring a saving for the consumers. This paper describes a peak load shaving strategy defined within the DEMAND project. The strategy is able to guarantee the flattest daily power diagram and the maximum benefit for the electricity consumers, reducin…
Neuropsychological Alterations in Children Affected by Obstructive Sleep Apnea Syndrome
2020
Sleep-related breathing disorders are a group of clinical conditions ranging from habitual snoring to obstructive sleep apnea syndrome (OSAS) during the lifespan. In children, other risk factors are represented by adenotonsillar hypertrophy, rhinitis, nasal structure alteration, cleft palate, velopharyngeal flap surgery, pharyngeal masses, craniofacial malformations, genetic syndrome (i.e. Down syndrome, Crouzon syndrome, and Apert syndrome), genetic hypoplasia mandibular (i.e. Pierre Robin syndrome, Treacher Collins syndrome, Shy-Drager syndrome, and Cornelia De Lange syndrome), craniofacial traumas, chronic or seasonal rhinitis, asthma, neuromuscular syndromes, brainstem pathologies (i.e.…
Diversifying crop rotations with temporary grasslands: potentials for weed management and farmland biodiversity
2010
Fruchtfolgen können dazu dienen, die kontinuierliche Selektion von Unkrautarten zu verhindern, die an eine bestimmte Kultur angepasst sind. Dies könnte dem Unkrautmanagement, der Einsparung von Herbiziden, und der Biodiversität dienen. Heutige, sehr einfache Furchtfolgen könnten durch mehrjährige Futterkulturen diversifiziert werden. Die Einflüsse solcher mehrjähriger Kulturen auf Unkräuter wurden in vier Ansätzen untersucht : 1) Vegetationsaufnahmen auf 632 Feldern in Westfrankreich zeigten, dass die Unkrautzusammensetzung zwischen mehrjährigen Futterkulturen und einjährigen Kulturen stark variiert. Der Vergleich von Feldern vor, während und nach mehrjährigen Futterkulturen legte nahe, das…
Hard x-ray photoelectron spectroscopy: a snapshot of the state-of-the-art in 2020
2021
Journal of physics / Condensed matter 33(23), 233001 (1-44) (2021). doi:10.1088/1361-648X/abeacd