Search results for "splice"

showing 3 items of 53 documents

Expression of IAPs (Inhibitory of Apoptosis Proteins) and of their alternative splice variants in hepatocellular carcinoma tissues and cells

2004

IAPs (inhibitors of apoptosis proteins) might have a major role in the apoptotic resistance that marks many cancers. The studies on IAPs in human HCC have focused on survivin or XIAP, indicating that their new or increased expression in this tumor is associated with a more unfavorable prognosis. The present results corroborate these findings, emphasizing the role that the coordinated expression of different IAPs and alternative splice variants might play in the adverse biology of hepatocellular carcinoma.

drug resistanceinhibitors of apoptosis proteinalternative splice varianthepatocellular carcinomaIAP
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Congenital secondary hypothyroidism caused by exon skipping due to a homozygous donor splice site mutation in the TSHbeta-subunit gene.

2002

Isolated TSH deficiency as a cause for congenital hypothyroidism is relatively uncommon. Even more rare is the identification of mutations in the TSHβ gene, only four of which have been identified. We here report a 4-month-old girl with isolated TSH deficiency born to consanguineous parents. Sequencing of the TSHβ-subunit gene revealed a homozygous G to A transition at position +5 of the donor splice site of intron 2. TSHβ gene transcript could not be obtained from fibroblasts or white blood cells by illegitimate amplification. Thus, to investigate further the mechanism leading to TSH deficiency in this patient, we used an in vitro exon-trapping system. The mutation at position +5 of the do…

medicine.medical_specialtyEndocrinology Diabetes and MetabolismClinical BiochemistryThyrotropinBiologymedicine.disease_causeBiochemistryExonConsanguinityEndocrinologyInternal medicinemedicineCongenital HypothyroidismMissense mutationHumansspliceRNA MessengerGeneGeneticsMutationSplice site mutationBiochemistry (medical)IntronInfantExonsExon skippingEndocrinologyMutationFemaleRNA Splice SitesThe Journal of clinical endocrinology and metabolism
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PGC-1 isoforms and their target genes are expressed differently in human skeletal muscle following resistance and endurance exercise

2015

The primary aim of the present study was to investigate the acute gene expression responses of PGC-1 isoforms and PGC-1a target genes related to mitochondrial biogenesis (cytochrome C), angiogenesis (VEGF-A), and muscle hypertrophy (myostatin), after a resistance or endurance exercise bout. In addition, the study aimed to elucidate whether the expression changes of studied transcripts were linked to phosphorylation of AMPK and MAPK p38. Nineteen physically active men were divided into resistance exercise (RE, n = 11) and endurance exercise (EE, n = 8) groups. RE group performed leg press exercise (10 9 10 RM, 50 min) and EE walked on a treadmill (~80% HRmax, 50 min). Muscle biopsies were ob…

medicine.medical_specialtybiologysplice variantPhysiologyVastus lateralis musclePGC-1αphysical activitySkeletal muscleta3141MyostatinMuscle hypertrophyExonmedicine.anatomical_structureEndocrinologyPGC1-1βMitochondrial biogenesisEndurance trainingPhysiology (medical)Internal medicineGene expressionmedicinebiology.proteinta315Original ResearchPhysiological Reports
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