Advantages of binaural hearing provided through bimodal stimulation via a cochlear implant and a conventional hearing aid: a 6-month comparative study.

Our study data demonstrate the additional benefit derived from continued use of a contralateral hearing aid (HA) post-cochlear implantation for speech recognition ability in quiet and in noise. Postoperative bimodal stimulation is recommended for all subjects who show some speech recognition ability in the contralateral ear as it may offer binaural listening advantages in various listening situations encountered in everyday life.To assess the benefits derived from bimodal stimulation for experienced HA users implanted with a cochlear implant (CI) (score=20% in disyllabic test). The correlation between pre- and postoperative performance on speech perception measures was examined to determine…

Analysis of the Ush2a Gene in Medaka Fish (Oryzias latipes)

Patients suffering from Usher syndrome (USH) exhibit sensorineural hearing loss, retinitis pigmentosa (RP) and, in some cases, vestibular dysfunction. USH is the most common genetic disorder affecting hearing and vision and is included in a group of hereditary pathologies associated with defects in ciliary function known as ciliopathies. This syndrome is clinically classified into three types: USH1, USH2 and USH3. USH2 accounts for well over one-half of all Usher cases and mutations in the USH2A gene are responsible for the majority of USH2 cases, but also for atypical Usher syndrome and recessive non-syndromic RP. Because medaka fish (Oryzias latypes) is an attractive model organism for ge…

Genetic and phenotypic heterogeneity in two novel cases of Waardenburg syndrome type IV.

Tratamiento de la mastoiditis aguda en niños con implante coclear

Resumen Introduccion La mastoiditis aguda es una complicacion infecciosa otitica que plantea una problematica especifica en el caso de pacientes implantados. Objetivo Revisar los casos de mastoiditis aguda en el programa de implantes cocleares para valorar su incidencia y los problemas asociados. Materiales y metodos Se realizo un estudio retrospectivo en 248 ninos implantados con edades entre los 8 meses y 14 anos desde 1994 hasta 2009 en nuestro programa de implantes cocleares. Se analizan los datos demograficos, clinicos y su tratamiento. Resultados Cinco pacientes desarrollaron mastoiditis aguda (incidencia de 2,01%), 3 de ellos con absceso subperiostico (incidencia de 1,21%), La edad m…

Treatment of acute mastoiditis in children with cochlear implants

Abstract Introduction Acute mastoiditis (AM) is a paediatric infectious complication that raises a specific problem in case of implanted patients. Objective To review the cases of AM in a paediatric cochlear implant (CI) programme to study its incidence and associated problems. Materials and methods A retrospective study was conducted on 248 children aged between 8 months and 14 years who underwent CI from 1994 to 2009. The demographics, clinical data and their treatment were analyzed. Results Five patients developed acute mastoiditis (2.01%), three of them with subperiosteal abscess (1.21%). The mean age of implantation was 2 years and 4 months, and the complication presented between 1 and…