6533b82cfe1ef96bd128f5c8

RESEARCH PRODUCT

Steroid-resistant eosinophilic fasciitis successfully treated with addition of extracorporeal photopheresis.

Rosa Goterris-viciedoVíctor Alegre De MiquelMaria Macarena Giacaman-von Der WethAmparo Pérez-ferriolsFelipe Partarrieu-mejías

subject

medicine.medical_specialtyFibrosing diseaseDermatology030207 dermatology & venereal diseases03 medical and health sciences0302 clinical medicineExtracorporeal PhotopheresisEosinophiliamedicineHumansFasciitisGlucocorticoidsTherapeutic strategyAgedTreatment regimenbusiness.industryGeneral MedicineFasciamedicine.diseaseDermatologySteroid resistantEosinophilic fasciitismedicine.anatomical_structureTreatment Outcome030220 oncology & carcinogenesisPhotopheresisFemalebusiness

description

Eosinophilic fasciitis (EF) is an uncommon fibrosing disease of the fascia with characteristic cutaneous and hematologic manifestations. Although EF is most commonly treated with corticosteroids at the beginning, a considerable number of patients show an inadequate response and hence various therapeutic strategies have been tried, including extracorporeal photopheresis (ECP). We describe the case of a 66-year-old woman with steroid-resistant EF that improved significantly after ECP was added to her treatment regimen. To date, only six cases of this therapeutic strategy have been reported in English literature.

10.1111/dth.12926https://pubmed.ncbi.nlm.nih.gov/31025428